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etiocholanolone and Adrenal Hyperplasia, Congenital

etiocholanolone has been researched along with Adrenal Hyperplasia, Congenital in 18 studies

Etiocholanolone: The 5-beta-reduced isomer of ANDROSTERONE. Etiocholanolone is a major metabolite of TESTOSTERONE and ANDROSTENEDIONE in many mammalian species including humans. It is excreted in the URINE.
3alpha-hydroxy-5beta-androstan-17-one : An androstanoid that is 5beta-androstane substituted by an alpha-hydroxy group at position 3 and an oxo group at position 17. It is a metabolite of testosterone in mammals.

Adrenal Hyperplasia, Congenital: A group of inherited disorders of the ADRENAL GLANDS, caused by enzyme defects in the synthesis of cortisol (HYDROCORTISONE) and/or ALDOSTERONE leading to accumulation of precursors for ANDROGENS. Depending on the hormone imbalance, congenital adrenal hyperplasia can be classified as salt-wasting, hypertensive, virilizing, or feminizing. Defects in STEROID 21-HYDROXYLASE; STEROID 11-BETA-HYDROXYLASE; STEROID 17-ALPHA-HYDROXYLASE; 3-beta-hydroxysteroid dehydrogenase (3-HYDROXYSTEROID DEHYDROGENASES); TESTOSTERONE 5-ALPHA-REDUCTASE; or steroidogenic acute regulatory protein; among others, underlie these disorders.

Research

Studies (18)

TimeframeStudies, this research(%)All Research%
pre-199017 (94.44)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (5.56)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Kamrath, C1
Hochberg, Z1
Hartmann, MF1
Remer, T1
Wudy, SA1
CARA, J1
BEAS, F1
SPACH, C1
GARDNER, LI1
BRAILLARD, CA1
DEROSA, S1
Plewe, G1
Beyer, J1
Ferrante, L1
Matys, Z1
Gregorová, I2
Tomsová, Z1
Jarosová, M1
Schreiber, V1
Rivera, R1
Dorfman, RI1
Forchielli, E1
Rivarola, MA1
Saez, JM1
Migeon, CJ1
Conly, PW1
Sandberg, DH1
Cleveland, WW1
Göbel, P1
Cacciari, E1
Dallera, L1
Tassoni, P1
Cicognani, A1
Miano, A1
Garmendia, F1
Nicolis, GL1
Gabrilove, JL1
Sanghvi, A1
Wight, C1
Serenko, A1
Balachandran, R1
Lim, NY1
Mimica, N1
Dingman, JF1
Takahara, J1
Hashimoto, K1
Ofuji, T1
Horký, K1
Kuchel, O1
Stárka, L1
Hoek, W1
van Kampen, EJ1

Reviews

1 review available for etiocholanolone and Adrenal Hyperplasia, Congenital

ArticleYear
[CLINICAL SIGNIFICANCE OF FEVER-PRODUCING STEROIDS].
    La Semana medica, 1964, Mar-12, Volume: 124

    Topics: Abetalipoproteinemia; Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; Aspirin; Cortisone; E

1964

Trials

1 trial available for etiocholanolone and Adrenal Hyperplasia, Congenital

ArticleYear
Effect of aminoglutethimide on urinary steroid excretion in patients with congenital adrenal hyperplasia due to incomplete 21-hydroxylase deficiency.
    Metabolism: clinical and experimental, 1972, Volume: 21, Issue:4

    Topics: 17-alpha-Hydroxypregnenolone; 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Glands; Adrenal Hy

1972

Other Studies

16 other studies available for etiocholanolone and Adrenal Hyperplasia, Congenital

ArticleYear
Increased activation of the alternative "backdoor" pathway in patients with 21-hydroxylase deficiency: evidence from urinary steroid hormone analysis.
    The Journal of clinical endocrinology and metabolism, 2012, Volume: 97, Issue:3

    Topics: Adolescent; Adrenal Hyperplasia, Congenital; Adult; Androstenedione; Androsterone; Child; Child, Pre

2012
Increased urinary and plasma etiocholanolone and related steroids in a boy with virilizing adrenal hyperplasia and periodic fever.
    The Journal of pediatrics, 1963, Volume: 62

    Topics: 17-Ketosteroids; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adrenogenital Syndrome; An

1963
[Etiocholanolone and fever].
    Deutsche medizinische Wochenschrift (1946), 1984, Apr-13, Volume: 109, Issue:15

    Topics: Adrenal Hyperplasia, Congenital; Chromatography, Gas; Dose-Response Relationship, Drug; Etiocholanol

1984
[Complex biochemical aspects in virilizing adrenal gland syndromes].
    Minerva pediatrica, 1976, Jun-23, Volume: 28, Issue:22

    Topics: Adrenal Hyperplasia, Congenital; Androsterone; Dehydroepiandrosterone; Etiocholanolone; Female; Huma

1976
[Urinary excretion of steroids in congenital adrenogenital syndrome with successful pregnancy (author's transl)].
    Sbornik lekarsky, 1977, Volume: 79, Issue:7-8

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Androsterone; Etiocholanolone; Female; Huma

1977
A modified method for the analysis of urinary 17-ketosteroids, pregnanediol and pregnanetriol by gas liquid chromatography in normal subjects and subjects with various endocrine disorders.
    Acta endocrinologica, 1967, Volume: 54, Issue:1

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Androsterone; Chromatography, Gas; Cushing Syndrom

1967
Studies of androgens in patients with congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1967, Volume: 27, Issue:5

    Topics: Adolescent; Adrenal Glands; Adrenal Hyperplasia, Congenital; Adult; Androsterone; Carbon Isotopes; C

1967
Steroid metabolism in premature pubarche and virilizing adrenal hyperplasia.
    The Journal of pediatrics, 1967, Volume: 71, Issue:4

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adolescent; Adrenal Hyperplasia, Congenital; Androgens;

1967
[Adrenal hirsutism (3-beta-hydroxysteroid dehydrogenase deficiency). Studies using chromatographic separation of the urinary 17-ketosteroid fraction. 3. On the differential diagnosis of adrenal hirsutism (M. Cushing, congenital adrenogenital syndrome)].
    Endokrinologie, 1968, Volume: 52, Issue:5

    Topics: 17-Ketosteroids; Adenoma; Adolescent; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adre

1968
[Various aspects of steroidogenesis in congenital adrenogenital syndrome with or without salt loss (determination of the urinary excretion of aldosterone, androsterone, etiocholanolone, dehydroisoandrosterone, 17-hydroxy-11-desoxycorticosterone, pregnaned
    Minerva pediatrica, 1969, May-26, Volume: 21, Issue:21

    Topics: Adrenal Hyperplasia, Congenital; Aldosterone; Androgens; Androsterone; Child; Child, Preschool; Dehy

1969
The determination of urinary pregnanetriol and the neutral 17-ketosteroids by gas-liquid chromatography.
    Steroids, 1971, Volume: 18, Issue:2

    Topics: 17-Ketosteroids; Adenoma; Adolescent; Adrenal Gland Neoplasms; Adrenal Hyperplasia, Congenital; Adre

1971
Gas-liquid chromatography of underivatized steroids: simultaneous determination of urinary 17-ketosteroids, pregnanediol, pregnanetriol, and pregnanetriolone.
    Clinica chimica acta; international journal of clinical chemistry, 1974, Oct-15, Volume: 56, Issue:1

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Androsterone; Chromatography, Gas; Computers; Dehy

1974
Hyperaldosteronism in hypertensive congenital adrenal hyperplasia.
    The Journal of clinical endocrinology and metabolism, 1969, Volume: 29, Issue:12

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adrenal Rest Tumor; Adr

1969
[Gas liquid chromatography analysis of urinary neutral steroid fractions in normal persons and patients with various diseases].
    Nihon Naibunpi Gakkai zasshi, 1970, Jun-20, Volume: 46, Issue:3

    Topics: 17-Ketosteroids; Adrenal Gland Diseases; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormon

1970
[Evaluation of neutral urinary steroid analysis by gas liquid chromatography using OV-210].
    Horumon to rinsho. Clinical endocrinology, 1971, Volume: 19, Issue:11

    Topics: 17-Hydroxycorticosteroids; 17-Ketosteroids; Adrenal Cortex Hormones; Adrenal Gland Neoplasms; Adrena

1971
Urinary steroid spectra by gas chromatography.
    Clinica chimica acta; international journal of clinical chemistry, 1968, Volume: 19, Issue:3

    Topics: 17-Ketosteroids; Adrenal Hyperplasia, Congenital; Adult; Breast Neoplasms; Child; Chromatography, Ga

1968