ethylmaleimide has been researched along with Adrenoleukodystrophy in 2 studies
Ethylmaleimide: A sulfhydryl reagent that is widely used in experimental biochemical studies.
Adrenoleukodystrophy: An X-linked recessive disorder characterized by the accumulation of saturated very long chain fatty acids in the LYSOSOMES of ADRENAL CORTEX and the white matter of CENTRAL NERVOUS SYSTEM. This disease occurs almost exclusively in the males. Clinical features include the childhood onset of ATAXIA; NEUROBEHAVIORAL MANIFESTATIONS; HYPERPIGMENTATION; ADRENAL INSUFFICIENCY; SEIZURES; MUSCLE SPASTICITY; and DEMENTIA. The slowly progressive adult form is called adrenomyeloneuropathy. The defective gene ABCD1 is located at Xq28, and encodes the adrenoleukodystrophy protein (ATP-BINDING CASSETTE TRANSPORTERS).
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 1 (50.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 1 (50.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Morita, M | 1 |
| Kawamichi, M | 1 |
| Shimura, Y | 1 |
| Kawaguchi, K | 1 |
| Watanabe, S | 1 |
| Imanaka, T | 1 |
| Tsuji, S | 1 |
| Ohno, T | 1 |
| Miyatake, T | 1 |
| Suzuki, A | 1 |
| Yamakawa, T | 1 |
2 other studies available for ethylmaleimide and Adrenoleukodystrophy
| Article | Year |
|---|---|
Brain microsomal fatty acid elongation is increased in abcd1-deficient mouse during active myelination phase.
Topics: Adrenoleukodystrophy; Animals; ATP Binding Cassette Transporter, Subfamily D, Member 1; ATP-Binding | 2015 |
Fatty acid elongation activity in fibroblasts from patients with adrenoleukodystrophy (ALD).
Topics: Adrenoleukodystrophy; Adult; Cells, Cultured; Child; Cytosol; Diffuse Cerebral Sclerosis of Schilder | 1984 |