Page last updated: 2024-10-26

erythrosine and Maple Syrup Urine Disease

erythrosine has been researched along with Maple Syrup Urine Disease in 1 studies

Fluoresceins: A family of spiro(isobenzofuran-1(3H),9'-(9H)xanthen)-3-one derivatives. These are used as dyes, as indicators for various metals, and as fluorescent labels in immunoassays.

Maple Syrup Urine Disease: An autosomal recessive inherited disorder with multiple forms of phenotypic expression, caused by a defect in the oxidative decarboxylation of branched-chain amino acids (AMINO ACIDS, BRANCHED-CHAIN). These metabolites accumulate in body fluids and render a maple syrup odor. The disease is divided into classic, intermediate, intermittent, and thiamine responsive subtypes. The classic form presents in the first week of life with ketoacidosis, hypoglycemia, emesis, neonatal seizures, and hypertonia. The intermediate and intermittent forms present in childhood or later with acute episodes of ataxia and vomiting. (From Adams et al., Principles of Neurology, 6th ed, p936)

Research

Studies (1)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Bridi, R1
Latini, A1
Braum, CA1
Zorzi, GK1
Moacir, W1
Lissi, E1
Dutra-Filho, CS1

Other Studies

1 other study available for erythrosine and Maple Syrup Urine Disease

ArticleYear
Evaluation of the mechanisms involved in leucine-induced oxidative damage in cerebral cortex of young rats.
    Free radical research, 2005, Volume: 39, Issue:1

    Topics: Animals; Antioxidants; Brain; Catalase; Cerebral Cortex; Chromans; Disease Models, Animal; Enzyme In

2005