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dodecanedioic acid and Inborn Errors of Metabolism

dodecanedioic acid has been researched along with Inborn Errors of Metabolism in 2 studies

Research

Studies (2)

TimeframeStudies, this research(%)All Research%
pre-19901 (50.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's1 (50.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Bian, F; Brunengraber, H; Jin, Z; Kelleher, JK; Tomcik, K; Zhang, GF1
Draye, JP; Vamecq, J1

Other Studies

2 other study(ies) available for dodecanedioic acid and Inborn Errors of Metabolism

ArticleYear
Compartmentation of Metabolism of the C12-, C9-, and C5-n-dicarboxylates in Rat Liver, Investigated by Mass Isotopomer Analysis: ANAPLEROSIS FROM DODECANEDIOATE.
    The Journal of biological chemistry, 2015, Jul-24, Volume: 290, Issue:30

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Citric Acid Cycle; Coenzyme A; Dicarboxylic Acids; Fatty Acids; Glutarates; Humans; Liver; Malonyl Coenzyme A; Metabolism, Inborn Errors; Mitochondria; Myocardium; Oxidation-Reduction; Peroxisomes; Propionic Acidemia; Rats

2015
Comparison between the formation and the oxidation of dicarboxylylcarnitine esters in rat liver and skeletal muscle: possible implications for human inborn disorders of mitochondrial beta-oxidation.
    Journal of inherited metabolic disease, 1989, Volume: 12, Issue:1

    Topics: Animals; Coenzyme A; Dicarboxylic Acids; Humans; Male; Metabolism, Inborn Errors; Mitochondria, Liver; Mitochondria, Muscle; Oxidation-Reduction; Rats; Rats, Inbred Strains

1989