Page last updated: 2024-10-18

diacetyl and Phenylketonurias

diacetyl has been researched along with Phenylketonurias in 1 studies

butane-2,3-dione : An alpha-diketone that is butane substituted by oxo groups at positions 2 and 3. It is a metabolite produced during the malolactic fermentation.

Phenylketonurias: A group of autosomal recessive disorders marked by a deficiency of the hepatic enzyme PHENYLALANINE HYDROXYLASE or less frequently by reduced activity of DIHYDROPTERIDINE REDUCTASE (i.e., atypical phenylketonuria). Classical phenylketonuria is caused by a severe deficiency of phenylalanine hydroxylase and presents in infancy with developmental delay; SEIZURES; skin HYPOPIGMENTATION; ECZEMA; and demyelination in the central nervous system. (From Adams et al., Principles of Neurology, 6th ed, p952).

Research

Studies (1)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Rangan, C1
Barceloux, DG1

Reviews

1 review available for diacetyl and Phenylketonurias

ArticleYear
Food additives and sensitivities.
    Disease-a-month : DM, 2009, Volume: 55, Issue:5

    Topics: Anti-Bacterial Agents; Antioxidants; Aspartame; Bronchiolitis Obliterans; Coloring Agents; Cyclamate

2009