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dermatan sulfate and Carbohydrate Metabolism, Inborn Error

dermatan sulfate has been researched along with Carbohydrate Metabolism, Inborn Error in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19904 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Beck, M; Kresse, H; Lücke, R1
Constantopoulos, G; Dekaban, AS1
Cantz, M; Gehler, J; O'Brien, JF; Spranger, J1
Lamberg, SI; Stoolmiller, AC1

Reviews

1 review(s) available for dermatan sulfate and Carbohydrate Metabolism, Inborn Error

ArticleYear
Glycosaminoglycans. A biochemical and clinical review.
    The Journal of investigative dermatology, 1974, Volume: 63, Issue:6

    Topics: Carbohydrate Metabolism, Inborn Errors; Cells, Cultured; Chondroitin; Cornea; Corneal Opacity; Dermatan Sulfate; Fibroblasts; Galactose; Glucosamine; Glycosaminoglycans; Heparin; Humans; Hyaluronic Acid; Hyaluronoglucosaminidase; Intellectual Disability; Male; Mucopolysaccharidoses; Mucopolysaccharidosis IV; Proteoglycans; Retinitis Pigmentosa; Skin; Staining and Labeling; Sulfatases; Testis

1974

Other Studies

3 other study(ies) available for dermatan sulfate and Carbohydrate Metabolism, Inborn Error

ArticleYear
Dyggve-Melchior-Clausen syndrome: normal degradation of proteodermatan sulfate, proteokeratan sulfate and heparan sulfate.
    Clinica chimica acta; international journal of clinical chemistry, 1984, Aug-15, Volume: 141, Issue:1

    Topics: Carbohydrate Metabolism, Inborn Errors; Cells, Cultured; Child; Chondroitin; Chondroitin Lyases; Chondroitin Sulfate Proteoglycans; Dermatan Sulfate; Electrophoresis, Polyacrylamide Gel; Endocytosis; Fibroblasts; Glycosaminoglycans; Heparitin Sulfate; Humans; Keratan Sulfate; Leucine; Lumican; Male; Molecular Weight; Proteoglycans; Skin

1984
Chemical definition of the mucopolysaccharidoses.
    Clinica chimica acta; international journal of clinical chemistry, 1975, Mar-24, Volume: 59, Issue:3

    Topics: Adolescent; Adult; Bone and Bones; Carbohydrate Metabolism, Inborn Errors; Child; Child, Preschool; Chondroitin; Dermatan Sulfate; Female; Glycosaminoglycans; Heparitin Sulfate; Humans; Hypertrichosis; Infant; Intellectual Disability; Joint Diseases; Male; Mucopolysaccharidoses; Mucopolysaccharidosis I; Mucopolysaccharidosis II; Retinitis Pigmentosa

1975
Letter: Chondroitinsulphaturia with alpha-L-iduronidase deficiency.
    Lancet (London, England), 1974, Nov-02, Volume: 2, Issue:7888

    Topics: Carbohydrate Metabolism, Inborn Errors; Chondroitin; Dermatan Sulfate; Female; Glycoside Hydrolases; Heterozygote; Humans; Mutation

1974