Compounds > dermatan sulfate
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dermatan sulfate and Acetyl-CoA:alpha-Glucosaminide N-Acetyltransferase Deficiency

dermatan sulfate has been researched along with Acetyl-CoA:alpha-Glucosaminide N-Acetyltransferase Deficiency in 8 studies

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19901 (12.50)18.7374
1990's1 (12.50)18.2507
2000's1 (12.50)29.6817
2010's5 (62.50)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Fukao, T; Giugliani, R; Khan, SA; Kobayashi, H; Mason, RW; Orii, K; Orii, T; Suzuki, Y; Tomatsu, S; Yamaguchi, S1
Millington, DS; Wood, T; Young, SP; Zhang, H1
Arasaradnam, M; Bigger, BW; Langford-Smith, K; Wraith, JE; Wynn, R1
Esko, JD; Lamanna, WC; Lawrence, R; Sarrazin, S1
de Ru, MH; de Ruijter, J; Ijlst, L; Lund, AM; Orchard, PJ; Schaefer, GB; van Vlies, N; Wagemans, T; Wijburg, FA1
Dietrich, CP; Nader, HB; Toma, L1
Hinek, A; Wilson, SE1
Constantopoulos, G; Dekaban, AS1

Other Studies

8 other study(ies) available for dermatan sulfate and Acetyl-CoA:alpha-Glucosaminide N-Acetyltransferase Deficiency

ArticleYear
Glycosaminoglycans analysis in blood and urine of patients with mucopolysaccharidosis.
    Molecular genetics and metabolism, 2018, Volume: 125, Issue:1-2

    Topics: Adolescent; Adult; Biomarkers; Child; Child, Preschool; Dermatan Sulfate; Female; Glycosaminoglycans; Heparitin Sulfate; Humans; Keratan Sulfate; Male; Mucopolysaccharidoses; Mucopolysaccharidosis II; Mucopolysaccharidosis III; Mucopolysaccharidosis IV; Mucopolysaccharidosis VI; Tandem Mass Spectrometry; Young Adult

2018
A straightforward, quantitative ultra-performance liquid chromatography-tandem mass spectrometric method for heparan sulfate, dermatan sulfate and chondroitin sulfate in urine: an improved clinical screening test for the mucopolysaccharidoses.
    Molecular genetics and metabolism, 2015, Volume: 114, Issue:2

    Topics: Adolescent; Adult; Aged; Child; Child, Preschool; Chondroitin Sulfates; Chromatography, Liquid; Dermatan Sulfate; Glycosaminoglycans; Heparitin Sulfate; Humans; Infant; Middle Aged; Mucopolysaccharidoses; Mucopolysaccharidosis II; Mucopolysaccharidosis III; Mucopolysaccharidosis IV; Mucopolysaccharidosis VI; Radioisotope Dilution Technique; Reference Values; Spectrometry, Mass, Electrospray Ionization; Tandem Mass Spectrometry; Young Adult

2015
Evaluation of heparin cofactor II-thrombin complex as a biomarker on blood spots from mucopolysaccharidosis I, IIIA and IIIB mice.
    Molecular genetics and metabolism, 2010, Volume: 99, Issue:3

    Topics: Animals; Biomarkers; Blood Specimen Collection; Dermatan Sulfate; Disease Models, Animal; Enzyme-Linked Immunosorbent Assay; Heparin Cofactor II; Heparitin Sulfate; Humans; Mice; Mice, Inbred C57BL; Mucopolysaccharidosis I; Mucopolysaccharidosis III; Thrombin

2010
Secondary storage of dermatan sulfate in Sanfilippo disease.
    The Journal of biological chemistry, 2011, Mar-04, Volume: 286, Issue:9

    Topics: Cells, Cultured; Chondroitin Sulfates; Dermatan Sulfate; Enzyme Replacement Therapy; Fibroblasts; Glucuronidase; Heparitin Sulfate; Humans; Hydrolases; Iduronate Sulfatase; In Vitro Techniques; Lysosomes; Mucopolysaccharidosis III

2011
Heparan sulfate and dermatan sulfate derived disaccharides are sensitive markers for newborn screening for mucopolysaccharidoses types I, II and III.
    Molecular genetics and metabolism, 2012, Volume: 107, Issue:4

    Topics: Biomarkers; Child; Child, Preschool; Dermatan Sulfate; Disaccharides; Heparitin Sulfate; Humans; Infant; Infant, Newborn; Mucopolysaccharidoses; Mucopolysaccharidosis I; Mucopolysaccharidosis II; Mucopolysaccharidosis III; Neonatal Screening; Reproducibility of Results; Tandem Mass Spectrometry

2012
Differences in the nonreducing ends of heparan sulfates excreted by patients with mucopolysaccharidoses revealed by bacterial heparitinases: a new tool for structural studies and differential diagnosis of Sanfilippo's and Hunter's syndromes.
    Laboratory investigation; a journal of technical methods and pathology, 1996, Volume: 75, Issue:6

    Topics: Biomarkers; Carbohydrate Sequence; Chondroitin Sulfates; Dermatan Sulfate; Diagnosis, Differential; Electrophoresis, Agar Gel; Heparitin Sulfate; Humans; Molecular Sequence Data; Mucopolysaccharidosis II; Mucopolysaccharidosis III; Polysaccharide-Lyases; Reference Values; Substrate Specificity

1996
Impaired elastogenesis in Hurler disease: dermatan sulfate accumulation linked to deficiency in elastin-binding protein and elastic fiber assembly.
    The American journal of pathology, 2000, Volume: 156, Issue:3

    Topics: Adolescent; Cell Count; Cell Division; Cells, Cultured; Child; Child, Preschool; Coronary Vessels; Dermatan Sulfate; Elastic Tissue; Elastin; Female; Fetus; Fibroblasts; Fibronectins; Fluorescent Antibody Technique, Indirect; Heparitin Sulfate; Humans; Infant; Male; Mitral Valve; Mucopolysaccharidosis I; Mucopolysaccharidosis III; Receptors, Cell Surface; Skin; Tropoelastin

2000
Mucopolysaccharidosis type I, II, IIIA and V. Pathological and biochemical abnormalities in the neural and mesenchymal elements of the brain.
    Acta neuropathologica, 1977, Jul-15, Volume: 39, Issue:1

    Topics: Adult; Brain; Brain Chemistry; Child; Connective Tissue; Connective Tissue Cells; Dermatan Sulfate; Glycosaminoglycans; Humans; Meninges; Microscopy, Electron; Mucopolysaccharidoses; Mucopolysaccharidosis I; Mucopolysaccharidosis II; Mucopolysaccharidosis III; Neurons

1977