Compounds > dermatan sulfate
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dermatan sulfate and ARSB Deficiency

dermatan sulfate has been researched along with ARSB Deficiency in 19 studies

Research

Studies (19)

TimeframeStudies, this research(%)All Research%
pre-19904 (21.05)18.7374
1990's4 (21.05)18.2507
2000's5 (26.32)29.6817
2010's3 (15.79)24.3611
2020's3 (15.79)2.80

Authors

AuthorsStudies
Bhattacharyya, S; Tobacman, JK1
Bocart, S; Bouchot, A; Bournique, B; Broqua, P; Entchev, E; Jantzen, I; Junien, JL; Lacombe, O; Luccarini, JM; Masson, P; Tallandier, M1
Golda, A; Lalik, A; Pacholczyk, M; Poterala-Hejmo, A; Student, S; Tylki-Szymańska, A1
Fukao, T; Giugliani, R; Khan, SA; Kobayashi, H; Mason, RW; Orii, K; Orii, T; Suzuki, Y; Tomatsu, S; Yamaguchi, S1
Millington, DS; Wood, T; Young, SP; Zhang, H1
Bigger, BW; Church, HJ; Mercer, J; O'Meara, A; Thornley, M; Tylee, K; Wraith, JE; Wynn, RF1
An, Y; Auray-Blais, C; Bhérer, P; Clarke, JT; Gagnon, R; Millington, DS; Young, SP; Zhang, HH1
Amedeo, S; Castagnaro, M; De Maria, R; Divari, S; Macrì, B; Marino, F; Mazzullo, G; Trusso, A1
Tobacman, JK1
Bhattacharyya, S; Danziger, RS; Kotlo, K; Shukla, S; Tobacman, JK1
Klein, U; von Figura, K1
Desnick, RJ; Haskins, ME; McGovern, MM; Schuchman, EH; Vine, DT1
Crawley, AC; Hopwood, JJ; Muller, VJ; Yogalingam, G1
Kondo, N; Orii, T; Sukegawa, K; Tomatsu, S1
Brumfield, LK; Byers, S; Hopwood, JJ; Ranieri, E; Rozaklis, T1
Haskins, ME; Schuchman, EH; Simonaro, CM1
Donnelly, PV; Gniot-Szulzycka, J1
Gregersen, HN; Güttler, F; Tønnesen, T1
Cantz, M; O'Brien, JF; Spranger, J1

Reviews

3 review(s) available for dermatan sulfate and ARSB Deficiency

ArticleYear
Profound Impact of Decline in N-Acetylgalactosamine-4-Sulfatase (Arylsulfatase B) on Molecular Pathophysiology and Human Diseases.
    International journal of molecular sciences, 2022, Oct-29, Volume: 23, Issue:21

    Topics: Chondroitin Sulfates; Dermatan Sulfate; Humans; Mucopolysaccharidosis VI; N-Acetylgalactosamine-4-Sulfatase; Sulfates

2022
Does deficiency of arylsulfatase B have a role in cystic fibrosis?
    Chest, 2003, Volume: 123, Issue:6

    Topics: Bacterial Infections; Chondroitin Sulfates; Cystic Fibrosis; Dermatan Sulfate; Glycosaminoglycans; Humans; Ion Exchange; Lung; Mucopolysaccharidosis VI; N-Acetylgalactosamine-4-Sulfatase; Pseudomonas Infections; Sodium; Sulfates; Tuberculosis

2003
[Mucopolysaccharidosis type VI (Maroteaux-Lamy syndrome)].
    Ryoikibetsu shokogun shirizu, 1998, Issue:19 Pt 2

    Topics: Biomarkers; Chondro-4-Sulfatase; Dermatan Sulfate; Diagnosis, Differential; Humans; Mucopolysaccharidosis VI; Mutation; Prognosis

1998

Trials

1 trial(s) available for dermatan sulfate and ARSB Deficiency

ArticleYear
Improved metabolic correction in patients with lysosomal storage disease treated with hematopoietic stem cell transplant compared with enzyme replacement therapy.
    The Journal of pediatrics, 2009, Volume: 154, Issue:4

    Topics: Biomarkers; Chondroitin Sulfates; Dermatan Sulfate; Enzyme Therapy; Enzymes; Hematopoietic Stem Cell Transplantation; Humans; Mucopolysaccharidosis I; Mucopolysaccharidosis II; Mucopolysaccharidosis VI

2009

Other Studies

15 other study(ies) available for dermatan sulfate and ARSB Deficiency

ArticleYear
Odiparcil, a potential glycosaminoglycans clearance therapy in mucopolysaccharidosis VI-Evidence from in vitro and in vivo models.
    PloS one, 2020, Volume: 15, Issue:5

    Topics: Administration, Oral; Animals; Cattle; Cells, Cultured; Chondroitin Sulfates; Dermatan Sulfate; Disease Models, Animal; Endothelial Cells; Female; Glycosaminoglycans; Glycosides; Humans; In Vitro Techniques; Male; Mice; Mice, Inbred C57BL; Mice, Mutant Strains; Mucopolysaccharidosis VI; Rats; Rats, Sprague-Dawley

2020
A Possible Role for Arylsulfatase G in Dermatan Sulfate Metabolism.
    International journal of molecular sciences, 2020, Jul-12, Volume: 21, Issue:14

    Topics: Amino Acid Sequence; Arylsulfatases; Catalytic Domain; Dermatan Sulfate; Endothelial Cells; Gene Silencing; Humans; Models, Molecular; Mucopolysaccharidosis VI; Myocytes, Smooth Muscle; N-Acetylgalactosamine-4-Sulfatase; Organ Specificity; Protein Binding; Protein Conformation; Pulmonary Artery; RNA, Messenger; Sequence Alignment; Sequence Homology, Amino Acid; Tissue Array Analysis; Up-Regulation

2020
Glycosaminoglycans analysis in blood and urine of patients with mucopolysaccharidosis.
    Molecular genetics and metabolism, 2018, Volume: 125, Issue:1-2

    Topics: Adolescent; Adult; Biomarkers; Child; Child, Preschool; Dermatan Sulfate; Female; Glycosaminoglycans; Heparitin Sulfate; Humans; Keratan Sulfate; Male; Mucopolysaccharidoses; Mucopolysaccharidosis II; Mucopolysaccharidosis III; Mucopolysaccharidosis IV; Mucopolysaccharidosis VI; Tandem Mass Spectrometry; Young Adult

2018
A straightforward, quantitative ultra-performance liquid chromatography-tandem mass spectrometric method for heparan sulfate, dermatan sulfate and chondroitin sulfate in urine: an improved clinical screening test for the mucopolysaccharidoses.
    Molecular genetics and metabolism, 2015, Volume: 114, Issue:2

    Topics: Adolescent; Adult; Aged; Child; Child, Preschool; Chondroitin Sulfates; Chromatography, Liquid; Dermatan Sulfate; Glycosaminoglycans; Heparitin Sulfate; Humans; Infant; Middle Aged; Mucopolysaccharidoses; Mucopolysaccharidosis II; Mucopolysaccharidosis III; Mucopolysaccharidosis IV; Mucopolysaccharidosis VI; Radioisotope Dilution Technique; Reference Values; Spectrometry, Mass, Electrospray Ionization; Tandem Mass Spectrometry; Young Adult

2015
Efficient analysis of urinary glycosaminoglycans by LC-MS/MS in mucopolysaccharidoses type I, II and VI.
    Molecular genetics and metabolism, 2011, Volume: 102, Issue:1

    Topics: Adolescent; Adult; Biomarkers; Case-Control Studies; Child; Child, Preschool; Chromatography, Liquid; Creatinine; Dermatan Sulfate; Enzyme Replacement Therapy; Female; Glycosaminoglycans; Heparitin Sulfate; Humans; Infant; Male; Mucopolysaccharidosis I; Mucopolysaccharidosis II; Mucopolysaccharidosis VI; Reference Values; Tandem Mass Spectrometry; Young Adult

2011
Mucopolysaccharidosis VI in a Siamese/short-haired European cat.
    Journal of veterinary medicine. A, Physiology, pathology, clinical medicine, 2002, Volume: 49, Issue:8

    Topics: Animals; Breeding; Cat Diseases; Cats; Dermatan Sulfate; Diagnosis, Differential; Male; Mucopolysaccharidosis VI; N-Acetylgalactosamine-4-Sulfatase; Radiography

2002
Distinct effects of N-acetylgalactosamine-4-sulfatase and galactose-6-sulfatase expression on chondroitin sulfates.
    The Journal of biological chemistry, 2008, Apr-11, Volume: 283, Issue:15

    Topics: Antibodies; Cell Line, Tumor; Chondroitin ABC Lyase; Chondroitin Sulfates; Chondroitinsulfatases; Decorin; Dermatan Sulfate; Extracellular Matrix Proteins; Female; Gene Expression Regulation, Enzymologic; Gene Silencing; Heparin; Heparitin Sulfate; Humans; Mucopolysaccharidosis VI; N-Acetylgalactosamine-4-Sulfatase; Proteoglycans; RNA, Small Interfering; Syndecan-1

2008
Characterization of dermatan sulfate in mucopolysaccharidosis VI. Evidence for the absence of hyaluronidase-like enzymes in human skin fibroblasts.
    Biochimica et biophysica acta, 1980, Jun-05, Volume: 630, Issue:1

    Topics: Cells, Cultured; Chondroitin; Dermatan Sulfate; Fibroblasts; Glycosaminoglycans; Humans; Hyaluronoglucosaminidase; Molecular Weight; Mucopolysaccharidoses; Mucopolysaccharidosis VI; Skin

1980
Enhancement of residual arylsulfatase B activity in feline mucopolysaccharidosis VI by thiol-induced subunit association.
    The Journal of clinical investigation, 1982, Volume: 69, Issue:2

    Topics: Animals; Cats; Chondro-4-Sulfatase; Chromatography, Gel; Cysteamine; Dermatan Sulfate; Dithiothreitol; Leukocytes; Molecular Weight; Mucopolysaccharidoses; Mucopolysaccharidosis VI; Sulfatases; Sulfhydryl Compounds

1982
Two mutations within a feline mucopolysaccharidosis type VI colony cause three different clinical phenotypes.
    The Journal of clinical investigation, 1998, Jan-01, Volume: 101, Issue:1

    Topics: Animals; Arthrography; beta-N-Acetylhexosaminidases; Cats; Chondro-4-Sulfatase; Dermatan Sulfate; Disease Models, Animal; Female; Genotype; Humans; Joints; Leukocytes; Male; Mucopolysaccharidosis VI; Mutation; Pedigree; Phenotype

1998
Glycosaminoglycan accumulation and excretion in the mucopolysaccharidoses: characterization and basis of a diagnostic test for MPS.
    Molecular genetics and metabolism, 1998, Volume: 65, Issue:4

    Topics: Animal Diseases; Animals; Cats; Dermatan Sulfate; Electrophoresis, Polyacrylamide Gel; Glycosaminoglycans; Humans; Mucopolysaccharidoses; Mucopolysaccharidosis VI

1998
Articular chondrocytes from animals with a dermatan sulfate storage disease undergo a high rate of apoptosis and release nitric oxide and inflammatory cytokines: a possible mechanism underlying degenerative joint disease in the mucopolysaccharidoses.
    Laboratory investigation; a journal of technical methods and pathology, 2001, Volume: 81, Issue:9

    Topics: Animals; Apoptosis; Bone Matrix; Cartilage, Articular; Cats; Chondrocytes; Coculture Techniques; Cytokines; Dermatan Sulfate; Inflammation Mediators; Joint Diseases; Lipopolysaccharides; Mucopolysaccharidosis VI; Nitric Oxide; Rats; Tumor Necrosis Factor-alpha

2001
Arylsulphatase B (Maroteaux-Lamy factor): a part of the enzyme system responsible for sulphate release from mucopolysaccharide fragment.
    FEBS letters, 1976, May-15, Volume: 65, Issue:1

    Topics: Chondro-4-Sulfatase; Dermatan Sulfate; Glycosaminoglycans; Mucopolysaccharidoses; Mucopolysaccharidosis VI; Oligosaccharides; Sulfatases

1976
Normal MPS excretion, but dermatan sulphaturia, combined with a mild Maroteaux-Lamy phenotype.
    Journal of medical genetics, 1991, Volume: 28, Issue:7

    Topics: Adult; Cells, Cultured; Cetylpyridinium; Chondro-4-Sulfatase; Dermatan Sulfate; Diagnostic Errors; Fibroblasts; Glycosaminoglycans; Hip Dislocation; Humans; Kyphosis; Lysosomes; Male; Mucopolysaccharidosis IV; Mucopolysaccharidosis VI; Phenotype; Uronic Acids

1991
Proceedings: The defect in Maroteaux-Lamy disease (mucopolysaccharidosis VI, subtype A): deficiency of N-acetylgalactosamine-4-sulfatase.
    Hoppe-Seyler's Zeitschrift fur physiologische Chemie, 1974, Volume: 355, Issue:10

    Topics: Acetylgalactosamine; Dermatan Sulfate; Humans; Mucopolysaccharidoses; Mucopolysaccharidosis VI; Sulfatases

1974