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dehydroepiandrosterone and Galactosemias

dehydroepiandrosterone has been researched along with Galactosemias in 4 studies

Dehydroepiandrosterone: A major C19 steroid produced by the ADRENAL CORTEX. It is also produced in small quantities in the TESTIS and the OVARY. Dehydroepiandrosterone (DHEA) can be converted to TESTOSTERONE; ANDROSTENEDIONE; ESTRADIOL; and ESTRONE. Most of DHEA is sulfated (DEHYDROEPIANDROSTERONE SULFATE) before secretion.
dehydroepiandrosterone : An androstanoid that is androst-5-ene substituted by a beta-hydroxy group at position 3 and an oxo group at position 17. It is a naturally occurring steroid hormone produced by the adrenal glands.

Galactosemias: A group of inherited enzyme deficiencies which feature elevations of GALACTOSE in the blood. This condition may be associated with deficiencies of GALACTOKINASE; UDPGLUCOSE-HEXOSE-1-PHOSPHATE URIDYLYLTRANSFERASE; or UDPGLUCOSE 4-EPIMERASE. The classic form is caused by UDPglucose-Hexose-1-Phosphate Uridylyltransferase deficiency, and presents in infancy with FAILURE TO THRIVE; VOMITING; and INTRACRANIAL HYPERTENSION. Affected individuals also may develop MENTAL RETARDATION; JAUNDICE; hepatosplenomegaly; ovarian failure (PRIMARY OVARIAN INSUFFICIENCY); and cataracts. (From Menkes, Textbook of Child Neurology, 5th ed, pp61-3)

Research Excerpts

ExcerptRelevanceReference
"Almost every female classic galactosemia patient develops primary ovarian insufficiency (POI)."7.91Dehydroepiandrosterone supplementation attenuates ovarian ageing in a galactose-induced primary ovarian insufficiency rat model. ( Akouri, R; Demir, N; Erman, M; Gunduz, T; Ozekinci, M; Sozen, B, 2019)
"Almost every female classic galactosemia patient develops primary ovarian insufficiency (POI)."3.91Dehydroepiandrosterone supplementation attenuates ovarian ageing in a galactose-induced primary ovarian insufficiency rat model. ( Akouri, R; Demir, N; Erman, M; Gunduz, T; Ozekinci, M; Sozen, B, 2019)
"Aldose reductase catalyzes the NADPH-linked reduction of hexoses to their respective sugar-alcohols, which are involved in the pathogenesis of "sugar-cataracts"."3.68Effects of G-6-PD deficiency, experimentally induced or genetically transmitted, on the sorbitol pathway activity. In vitro and in vivo studies. ( Alvarez, A; Chávez, M; Chávez-Anaya, E; Medina, C; Medina, MD; Mendoza, R; Ramírez, MG; Sáenz, G; Vaca, G; Vargas, M, 1992)

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19902 (50.00)18.7374
1990's1 (25.00)18.2507
2000's0 (0.00)29.6817
2010's1 (25.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Sozen, B1
Ozekinci, M1
Erman, M1
Gunduz, T1
Demir, N1
Akouri, R1
Vaca, G1
Ramírez, MG1
Vargas, M1
Mendoza, R1
Chávez-Anaya, E1
Medina, MD1
Alvarez, A1
Medina, C1
Sáenz, G1
Chávez, M1
Schwarz, HP1
Zimmermann, A1
Carasso, A1
Zuppinger, K1
Kaufman, FR1
Donnell, GN1
Lobo, RA1

Other Studies

4 other studies available for dehydroepiandrosterone and Galactosemias

ArticleYear
Dehydroepiandrosterone supplementation attenuates ovarian ageing in a galactose-induced primary ovarian insufficiency rat model.
    Journal of assisted reproduction and genetics, 2019, Volume: 36, Issue:10

    Topics: Aging; Animals; Dehydroepiandrosterone; Dietary Supplements; Disease Models, Animal; Female; Galacto

2019
Effects of G-6-PD deficiency, experimentally induced or genetically transmitted, on the sorbitol pathway activity. In vitro and in vivo studies.
    Archives of medical research, 1992,Spring, Volume: 23, Issue:1

    Topics: Acetaminophen; Adolescent; Adult; Aged; Aged, 80 and over; Aldehyde Reductase; Animals; Black People

1992
Feminization in a galactosemic girl in the presence of hypergonadotropic hypogonadism.
    Acta endocrinologica. Supplementum, 1986, Volume: 279

    Topics: Adult; Amenorrhea; Dehydroepiandrosterone; Dehydroepiandrosterone Sulfate; Estradiol; Estrone; Femal

1986
Ovarian androgen secretion in patients with galactosemia and premature ovarian failure.
    Fertility and sterility, 1987, Volume: 47, Issue:6

    Topics: Adolescent; Adult; Androgens; Androstenedione; Chorionic Gonadotropin; Dehydroepiandrosterone; Dehyd

1987