deferoxamine has been researched along with Congenital Erythropoietic Porphyria in 2 studies
Deferoxamine: Natural product isolated from Streptomyces pilosus. It forms iron complexes and is used as a chelating agent, particularly in the mesylate form.
desferrioxamine B : An acyclic desferrioxamine that is butanedioic acid in which one of the carboxy groups undergoes formal condensation with the primary amino group of N-(5-aminopentyl)-N-hydroxyacetamide and the second carboxy group undergoes formal condensation with the hydroxyamino group of N(1)-(5-aminopentyl)-N(1)-hydroxy-N(4)-[5-(hydroxyamino)pentyl]butanediamide. It is a siderophore native to Streptomyces pilosus biosynthesised by the DesABCD enzyme cluster as a high affinity Fe(III) chelator.
| Excerpt | Relevance | Reference |
|---|---|---|
| "Congenital erythropoietic porphyria is a rare autosomal recessive disorder of haem biosynthesis caused by a deficiency of uroporphyrinogen III synthetase." | 1.31 | Congenital erythropoietic porphyria: dilemmas in present day management. ( Creamer, JD; Dawe, SA; Du Vivier, A; Peters, TJ, 2002) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 1 (50.00) | 18.2507 |
| 2000's | 1 (50.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Dawe, SA | 1 |
| Peters, TJ | 1 |
| Du Vivier, A | 1 |
| Creamer, JD | 1 |
| Lange, B | 1 |
| Hofweber, K | 1 |
| Waldherr, R | 1 |
| Schärer, K | 1 |
2 other studies available for deferoxamine and Congenital Erythropoietic Porphyria
| Article | Year |
|---|---|
Congenital erythropoietic porphyria: dilemmas in present day management.
Topics: Adult; Anemia, Hemolytic; Blood Transfusion; Bone Diseases; Deferoxamine; Female; Hematopoietic Stem | 2002 |
Congenital erythropoietic porphyria associated with nephrotic syndrome and renal siderosis.
Topics: Anti-Inflammatory Agents; Child; Deferoxamine; Glomerular Filtration Rate; Humans; Iron Chelating Ag | 1995 |