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deferiprone and Congenital Erythropoietic Porphyria

deferiprone has been researched along with Congenital Erythropoietic Porphyria in 1 studies

Deferiprone: A pyridone derivative and iron chelator that is used in the treatment of IRON OVERLOAD in patients with THALASSEMIA.
deferiprone : A member of the class of 4-pyridones that is pyridin-4(1H)-one substituted at positions 1 and 2 by methyl groups and at position 3 by a hydroxy group. A lipid-soluble iron-chelator used for treatment of thalassaemia.

Research Excerpts

ExcerptRelevanceReference
"Treatment with deferiprone of UROS-deficient erythroid cell lines and peripheral blood CD34+-derived erythroid cultures from a patient with CEP inhibited iron-dependent protein ALAS2 and iron-responsive element-binding protein 2 expression and reduced porphyrin production."1.56Iron chelation rescues hemolytic anemia and skin photosensitivity in congenital erythropoietic porphyria. ( Bedel, A; Blouin, JM; Costet, P; Daher, R; Ged, C; Gouya, L; Karim, Z; Lalanne, M; Lamrissi-Garcia, I; Moreau-Gaudry, F; Morice-Picard, F; Puy, H; Richard, E, 2020)

Research

Studies (1)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's1 (100.00)2.80

Authors

AuthorsStudies
Blouin, JM1
Ged, C1
Lalanne, M1
Lamrissi-Garcia, I1
Morice-Picard, F1
Costet, P1
Daher, R1
Moreau-Gaudry, F1
Bedel, A1
Puy, H1
Gouya, L1
Karim, Z1
Richard, E1

Other Studies

1 other study available for deferiprone and Congenital Erythropoietic Porphyria

ArticleYear
Iron chelation rescues hemolytic anemia and skin photosensitivity in congenital erythropoietic porphyria.
    Blood, 2020, 11-19, Volume: 136, Issue:21

    Topics: 5-Aminolevulinate Synthetase; Adult; Anemia, Hemolytic; Animals; Cell Line; Cell Line, Tumor; CRISPR

2020