Compounds > deamino-arginine-vasopressin

deamino-arginine-vasopressin and Albinism--Oculocutaneous

deamino-arginine-vasopressin has been researched along with Albinism--Oculocutaneous* in 1 studies

Other Studies

1 other study(ies) available for deamino-arginine-vasopressin and Albinism--Oculocutaneous

Article	Year
The Hermansky-Pudlak syndrome. Variable reaction to 1-desamino-8D-arginine vasopressin for correction of the bleeding time. Ophthalmic paediatrics and genetics, 1990, Volume: 11, Issue:3 The effect of the synthetic vasopressin derivative 1-desamino-8D-arginine vasopressin (DDAVP = Minrin) on bleeding time was studied in nine patients with Hermansky-Pudlak syndrome; four of them were Dutch, five were Belgian. Shortening of bleeding time was observed in four of the patients with this type of storage pool disease; in one patient the response was equivocal, in two patients the response was not dramatic and in two there was no response at all. DDAVP may be useful in managing the bleeding disorder in some patients with Hermansky-Pudlak syndrome. Therefore, every patient with this syndrome should be tested with DDAVP as a preventive measure. Topics: Adolescent; Adult; Albinism, Oculocutaneous; Bleeding Time; Child; Child, Preschool; Deamino Arginine Vasopressin; Factor VIII; Female; Humans; Male; Middle Aged; Phenotype; Platelet Aggregation; Platelet Count; Platelet Storage Pool Deficiency	1990

Article

Year

The Hermansky-Pudlak syndrome. Variable reaction to 1-desamino-8D-arginine vasopressin for correction of the bleeding time.

Ophthalmic paediatrics and genetics, 1990, Volume: 11, Issue:3

The effect of the synthetic vasopressin derivative 1-desamino-8D-arginine vasopressin (DDAVP = Minrin) on bleeding time was studied in nine patients with Hermansky-Pudlak syndrome; four of them were Dutch, five were Belgian. Shortening of bleeding time was observed in four of the patients with this type of storage pool disease; in one patient the response was equivocal, in two patients the response was not dramatic and in two there was no response at all. DDAVP may be useful in managing the bleeding disorder in some patients with Hermansky-Pudlak syndrome. Therefore, every patient with this syndrome should be tested with DDAVP as a preventive measure.

Topics: Adolescent; Adult; Albinism, Oculocutaneous; Bleeding Time; Child; Child, Preschool; Deamino Arginine Vasopressin; Factor VIII; Female; Humans; Male; Middle Aged; Phenotype; Platelet Aggregation; Platelet Count; Platelet Storage Pool Deficiency

1990