dapsone has been researched along with alpha 1-Antitrypsin Deficiency in 14 studies
alpha 1-Antitrypsin Deficiency: Deficiency of the protease inhibitor ALPHA 1-ANTITRYPSIN that manifests primarily as PULMONARY EMPHYSEMA and LIVER CIRRHOSIS.
Excerpt | Relevance | Reference |
---|---|---|
"Patients presenting with panniculitis and systemic illness show high mortality risk." | 2.82 | Alpha-1 antitrypsin deficiency-associated panniculitis. ( Buckley, C; Carroll, TP; Franciosi, AN; Gulmann, C; McElvaney, NG; O'Farrell, NJ; O'Kane, M; Ralph, J, 2022) |
"Panniculitis is a recognized, but rare complication of α1-antitrypsin (A1AT) deficiency." | 2.50 | Alpha-1-antitrypsin deficiency-associated panniculitis: a case report. ( Cardoso, J; Carvalho, R; Chaveiro, A; Laureano, A, 2014) |
"We report a case of panniculitis in a patient with alpha(1)-antitrypsin deficiency and describe briefly the pathophysiology of the disease and current treatment possibilities." | 2.43 | Alpha1-antitrypsin deficiency-associated panniculitis: case report and review of treatment options. ( Benfeldt, E; Ortiz, PG; Skov, BG, 2005) |
"Ten patients with AATD panniculitis were included." | 1.48 | Alpha-1 antitrypsin deficiency panniculitis: clinical and pathologic characteristics of 10 cases. ( Gibson, LE; Johnson, EF; Tolkachjov, SN, 2018) |
"We report two cases of AATD-related panniculitis." | 1.46 | Alpha-1-antitrypsin deficiency-related panniculitis: two cases with diverse clinical courses. ( Aalto, L; Hawkins, P; Markham, T; Murphy, A; O' Gorman, SM; Storan, ER, 2017) |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 2 (14.29) | 18.7374 |
1990's | 4 (28.57) | 18.2507 |
2000's | 2 (14.29) | 29.6817 |
2010's | 5 (35.71) | 24.3611 |
2020's | 1 (7.14) | 2.80 |
Authors | Studies |
---|---|
Franciosi, AN | 1 |
Ralph, J | 1 |
O'Farrell, NJ | 1 |
Buckley, C | 1 |
Gulmann, C | 1 |
O'Kane, M | 1 |
Carroll, TP | 1 |
McElvaney, NG | 1 |
Storan, ER | 1 |
O' Gorman, SM | 1 |
Hawkins, P | 1 |
Aalto, L | 1 |
Murphy, A | 1 |
Markham, T | 1 |
Johnson, EF | 1 |
Tolkachjov, SN | 1 |
Gibson, LE | 1 |
Laureano, A | 1 |
Carvalho, R | 1 |
Chaveiro, A | 1 |
Cardoso, J | 1 |
Streicher, JL | 1 |
Sheehan, MP | 1 |
Armstrong, AB | 1 |
Mousdicas, N | 1 |
Elsensohn, AN | 1 |
Curtis, JA | 1 |
Secrest, AM | 1 |
Liaqat, M | 1 |
Florell, SR | 1 |
Duffy, KL | 1 |
Edholm, K | 1 |
Summers, EM | 1 |
Yesudian, PD | 1 |
Dobson, CM | 1 |
Wilson, NJ | 1 |
Ortiz, PG | 1 |
Skov, BG | 1 |
Benfeldt, E | 1 |
Schadendorf, D | 1 |
Haas, N | 1 |
Nürnberger, F | 1 |
Czarnetzki, BM | 1 |
Martinón Sánchez, F | 1 |
Fernández Villar, MC | 1 |
Otero Esteban, JJ | 1 |
García Rodríguez, JL | 1 |
Werner, A | 1 |
Mera Varela, A | 1 |
Cea Pereiro, JC | 1 |
Irvine, C | 1 |
Neild, V | 1 |
Stephens, C | 1 |
Black, M | 1 |
Pittelkow, MR | 2 |
Smith, KC | 2 |
Su, WP | 2 |
5 reviews available for dapsone and alpha 1-Antitrypsin Deficiency
Article | Year |
---|---|
Alpha-1 antitrypsin deficiency-associated panniculitis.
Topics: alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Dapsone; Glucocorticoids; Humans; Panniculitis | 2022 |
Alpha-1-antitrypsin deficiency-associated panniculitis: a case report.
Topics: alpha 1-Antitrypsin Deficiency; Biopsy; Colchicine; Contraindications; Dapsone; Erythema; Female; Gl | 2014 |
alpha1-Antitrypsin deficiency panniculitis (phenotype PiZZ) precipitated postpartum and successfully treated with dapsone.
Topics: Adult; alpha 1-Antitrypsin Deficiency; Anti-Inflammatory Agents, Non-Steroidal; Cesarean Section; Da | 2004 |
Alpha1-antitrypsin deficiency-associated panniculitis: case report and review of treatment options.
Topics: Administration, Oral; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Anti-Inflammatory Agents, | 2005 |
Panniculitis associated with severe alpha 1-antitrypsin deficiency. Treatment and review of the literature.
Topics: Adipose Tissue; Adult; Aged; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Biopsy; Blood Prot | 1987 |
9 other studies available for dapsone and alpha 1-Antitrypsin Deficiency
Article | Year |
---|---|
Alpha-1-antitrypsin deficiency-related panniculitis: two cases with diverse clinical courses.
Topics: Adult; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Colchicine; Dapsone; Female; Humans; Inf | 2017 |
Alpha-1 antitrypsin deficiency panniculitis: clinical and pathologic characteristics of 10 cases.
Topics: Adolescent; Adult; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Anti-Infective Agents; Dapso | 2018 |
Cutaneous manifestation of α₁-antitrypsin deficiency: panniculitis absent on biopsy.
Topics: alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Anti-Infective Agents; Dapsone; Female; Humans; | 2014 |
Alpha-1-antitrypsin deficiency panniculitis presenting with severe anasarca, pulmonary embolus and hypogammaglobulinaemia.
Topics: Adult; Agammaglobulinemia; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Anti-Inflammatory Ag | 2015 |
[Recurrent nodular panniculitis in alpha 1-antitrypsin deficiency. Successful dapsone therapy].
Topics: alpha 1-Antitrypsin Deficiency; Complement C3; Dapsone; Diagnosis, Differential; Female; Fluorescent | 1993 |
[Panniculitis associated with alpha 1-atitrypsin deficiency].
Topics: alpha 1-Antitrypsin Deficiency; Child; Dapsone; Enzyme Inhibitors; Female; Humans; Panniculitis | 1993 |
[Dapsone and panniculitis due to alpha 1-antitrypsin deficiency].
Topics: alpha 1-Antitrypsin Deficiency; Anti-Inflammatory Agents, Non-Steroidal; Biopsy; Dapsone; Female; Hu | 1999 |
Alpha-1-antitrypsin deficiency panniculitis.
Topics: Adult; alpha 1-Antitrypsin Deficiency; Dapsone; Humans; Male; Panniculitis; Skin | 1990 |
Alpha-1-antitrypsin deficiency and panniculitis. Perspectives on disease relationship and replacement therapy.
Topics: Adult; Aged; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Blood Proteins; Dapsone; Debrideme | 1988 |