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dapsone and alpha 1-Antitrypsin Deficiency

dapsone has been researched along with alpha 1-Antitrypsin Deficiency in 14 studies

alpha 1-Antitrypsin Deficiency: Deficiency of the protease inhibitor ALPHA 1-ANTITRYPSIN that manifests primarily as PULMONARY EMPHYSEMA and LIVER CIRRHOSIS.

Research Excerpts

ExcerptRelevanceReference
"Patients presenting with panniculitis and systemic illness show high mortality risk."2.82Alpha-1 antitrypsin deficiency-associated panniculitis. ( Buckley, C; Carroll, TP; Franciosi, AN; Gulmann, C; McElvaney, NG; O'Farrell, NJ; O'Kane, M; Ralph, J, 2022)
"Panniculitis is a recognized, but rare complication of α1-antitrypsin (A1AT) deficiency."2.50Alpha-1-antitrypsin deficiency-associated panniculitis: a case report. ( Cardoso, J; Carvalho, R; Chaveiro, A; Laureano, A, 2014)
"We report a case of panniculitis in a patient with alpha(1)-antitrypsin deficiency and describe briefly the pathophysiology of the disease and current treatment possibilities."2.43Alpha1-antitrypsin deficiency-associated panniculitis: case report and review of treatment options. ( Benfeldt, E; Ortiz, PG; Skov, BG, 2005)
"Ten patients with AATD panniculitis were included."1.48Alpha-1 antitrypsin deficiency panniculitis: clinical and pathologic characteristics of 10 cases. ( Gibson, LE; Johnson, EF; Tolkachjov, SN, 2018)
"We report two cases of AATD-related panniculitis."1.46Alpha-1-antitrypsin deficiency-related panniculitis: two cases with diverse clinical courses. ( Aalto, L; Hawkins, P; Markham, T; Murphy, A; O' Gorman, SM; Storan, ER, 2017)

Research

Studies (14)

TimeframeStudies, this research(%)All Research%
pre-19902 (14.29)18.7374
1990's4 (28.57)18.2507
2000's2 (14.29)29.6817
2010's5 (35.71)24.3611
2020's1 (7.14)2.80

Authors

AuthorsStudies
Franciosi, AN1
Ralph, J1
O'Farrell, NJ1
Buckley, C1
Gulmann, C1
O'Kane, M1
Carroll, TP1
McElvaney, NG1
Storan, ER1
O' Gorman, SM1
Hawkins, P1
Aalto, L1
Murphy, A1
Markham, T1
Johnson, EF1
Tolkachjov, SN1
Gibson, LE1
Laureano, A1
Carvalho, R1
Chaveiro, A1
Cardoso, J1
Streicher, JL1
Sheehan, MP1
Armstrong, AB1
Mousdicas, N1
Elsensohn, AN1
Curtis, JA1
Secrest, AM1
Liaqat, M1
Florell, SR1
Duffy, KL1
Edholm, K1
Summers, EM1
Yesudian, PD1
Dobson, CM1
Wilson, NJ1
Ortiz, PG1
Skov, BG1
Benfeldt, E1
Schadendorf, D1
Haas, N1
Nürnberger, F1
Czarnetzki, BM1
Martinón Sánchez, F1
Fernández Villar, MC1
Otero Esteban, JJ1
García Rodríguez, JL1
Werner, A1
Mera Varela, A1
Cea Pereiro, JC1
Irvine, C1
Neild, V1
Stephens, C1
Black, M1
Pittelkow, MR2
Smith, KC2
Su, WP2

Reviews

5 reviews available for dapsone and alpha 1-Antitrypsin Deficiency

ArticleYear
Alpha-1 antitrypsin deficiency-associated panniculitis.
    Journal of the American Academy of Dermatology, 2022, Volume: 87, Issue:4

    Topics: alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Dapsone; Glucocorticoids; Humans; Panniculitis

2022
Alpha-1-antitrypsin deficiency-associated panniculitis: a case report.
    Dermatology online journal, 2014, Jan-15, Volume: 20, Issue:1

    Topics: alpha 1-Antitrypsin Deficiency; Biopsy; Colchicine; Contraindications; Dapsone; Erythema; Female; Gl

2014
alpha1-Antitrypsin deficiency panniculitis (phenotype PiZZ) precipitated postpartum and successfully treated with dapsone.
    The British journal of dermatology, 2004, Volume: 150, Issue:6

    Topics: Adult; alpha 1-Antitrypsin Deficiency; Anti-Inflammatory Agents, Non-Steroidal; Cesarean Section; Da

2004
Alpha1-antitrypsin deficiency-associated panniculitis: case report and review of treatment options.
    Journal of the European Academy of Dermatology and Venereology : JEADV, 2005, Volume: 19, Issue:4

    Topics: Administration, Oral; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Anti-Inflammatory Agents,

2005
Panniculitis associated with severe alpha 1-antitrypsin deficiency. Treatment and review of the literature.
    Archives of dermatology, 1987, Volume: 123, Issue:12

    Topics: Adipose Tissue; Adult; Aged; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Biopsy; Blood Prot

1987

Other Studies

9 other studies available for dapsone and alpha 1-Antitrypsin Deficiency

ArticleYear
Alpha-1-antitrypsin deficiency-related panniculitis: two cases with diverse clinical courses.
    Clinical and experimental dermatology, 2017, Volume: 42, Issue:5

    Topics: Adult; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Colchicine; Dapsone; Female; Humans; Inf

2017
Alpha-1 antitrypsin deficiency panniculitis: clinical and pathologic characteristics of 10 cases.
    International journal of dermatology, 2018, Volume: 57, Issue:8

    Topics: Adolescent; Adult; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Anti-Infective Agents; Dapso

2018
Cutaneous manifestation of α₁-antitrypsin deficiency: panniculitis absent on biopsy.
    Cutis, 2014, Volume: 93, Issue:6

    Topics: alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Anti-Infective Agents; Dapsone; Female; Humans;

2014
Alpha-1-antitrypsin deficiency panniculitis presenting with severe anasarca, pulmonary embolus and hypogammaglobulinaemia.
    The British journal of dermatology, 2015, Volume: 173, Issue:1

    Topics: Adult; Agammaglobulinemia; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Anti-Inflammatory Ag

2015
[Recurrent nodular panniculitis in alpha 1-antitrypsin deficiency. Successful dapsone therapy].
    Der Hautarzt; Zeitschrift fur Dermatologie, Venerologie, und verwandte Gebiete, 1993, Volume: 44, Issue:10

    Topics: alpha 1-Antitrypsin Deficiency; Complement C3; Dapsone; Diagnosis, Differential; Female; Fluorescent

1993
[Panniculitis associated with alpha 1-atitrypsin deficiency].
    Anales espanoles de pediatria, 1993, Volume: 38, Issue:3

    Topics: alpha 1-Antitrypsin Deficiency; Child; Dapsone; Enzyme Inhibitors; Female; Humans; Panniculitis

1993
[Dapsone and panniculitis due to alpha 1-antitrypsin deficiency].
    Revista clinica espanola, 1999, Volume: 199, Issue:11

    Topics: alpha 1-Antitrypsin Deficiency; Anti-Inflammatory Agents, Non-Steroidal; Biopsy; Dapsone; Female; Hu

1999
Alpha-1-antitrypsin deficiency panniculitis.
    Journal of the Royal Society of Medicine, 1990, Volume: 83, Issue:11

    Topics: Adult; alpha 1-Antitrypsin Deficiency; Dapsone; Humans; Male; Panniculitis; Skin

1990
Alpha-1-antitrypsin deficiency and panniculitis. Perspectives on disease relationship and replacement therapy.
    The American journal of medicine, 1988, Jun-24, Volume: 84, Issue:6A

    Topics: Adult; Aged; alpha 1-Antitrypsin; alpha 1-Antitrypsin Deficiency; Blood Proteins; Dapsone; Debrideme

1988