Page last updated: 2024-08-21

d-alpha tocopherol and Neuronal Ceroid-Lipofuscinoses

d-alpha tocopherol has been researched along with Neuronal Ceroid-Lipofuscinoses in 12 studies

Research

Studies (12)

TimeframeStudies, this research(%)All Research%
pre-19906 (50.00)18.7374
1990's3 (25.00)18.2507
2000's3 (25.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Griffin, JL; Hindmarsh, A; Jowatt, V; Martin, JE; Muller, D; Nicholson, JK; Woograsingh, R1
Glueck, SB; Järvelä, I1
Prensky, AL1
Aberg, L; Antila, E; Atroshi, F; Edlund, P; Santavuori, P; Westermarck, T1
Huszagh, VA; Infante, JP1
Koppang, N1
Heiskala, H; Johansson, E; Lindh, U; Santavuori, P; Westermarck, T1
Heiskala, H; Moren, R; Sainio, K; Santavuori, P; Westermarck, T1
Borel, J; Maumanee, I; Moser, H; Naidu, S; Olson, J1
Jongkind, JF; Poot, M; Verkerk, A1
Lappi, M; Moren, R; Pohja, P; Rapola, J; Santavuori, P; Vuonnala, U; Westermarck, T1
Jongkind, JF; Poot, M; Verkerk, A; Visser, WJ1

Reviews

1 review(s) available for d-alpha tocopherol and Neuronal Ceroid-Lipofuscinoses

ArticleYear
Secondary carnitine deficiency and impaired docosahexaenoic (22:6n-3) acid synthesis: a common denominator in the pathophysiology of diseases of oxidative phosphorylation and beta-oxidation.
    FEBS letters, 2000, Feb-18, Volume: 468, Issue:1

    Topics: Animals; Carnitine; Disease Models, Animal; Docosahexaenoic Acids; Humans; Metabolism, Inborn Errors; Mice; Mice, Knockout; Mitochondria; Mitochondrial Encephalomyopathies; Neuronal Ceroid-Lipofuscinoses; Oxidation-Reduction; Oxidative Phosphorylation; Phospholipids; Vitamin E

2000

Other Studies

11 other study(ies) available for d-alpha tocopherol and Neuronal Ceroid-Lipofuscinoses

ArticleYear
Vitamin E deficiency and metabolic deficits in neuronal ceroid lipofuscinosis described by bioinformatics.
    Physiological genomics, 2002, Dec-03, Volume: 11, Issue:3

    Topics: Animals; Brain; Cerebral Cortex; Computational Biology; Dietary Supplements; Magnetic Resonance Spectroscopy; Membrane Proteins; Mice; Mice, Inbred C57BL; Mice, Neurologic Mutants; Neuronal Ceroid-Lipofuscinoses; Phenotype; Principal Component Analysis; Vitamin E; Vitamin E Deficiency

2002
Charting the effects of antioxidant therapy in the diseased brain: focus on "vitamin E deficiency and metabolic deficits in neuronal ceroid lipofuscinosis described by bioinformatics".
    Physiological genomics, 2002, Dec-03, Volume: 11, Issue:3

    Topics: Animals; Antioxidants; Brain Diseases; Computational Biology; Mice; Neuronal Ceroid-Lipofuscinoses; Vitamin E; Vitamin E Deficiency

2002
Vitamin E and the nervous system.
    Developmental medicine and child neurology, 1984, Volume: 26, Issue:5

    Topics: Humans; Lipid Metabolism; Lipid Peroxides; Nerve Degeneration; Nervous System Diseases; Neuromuscular Diseases; Neuronal Ceroid-Lipofuscinoses; Peripheral Nervous System Diseases; Reflex, Abnormal; Vitamin E; Vitamin E Deficiency

1984
Evaluation of the possible role of coenzyme Q10 and vitamin E in juvenile neuronal ceroid-lipofuscinosis (JNCL).
    Molecular aspects of medicine, 1997, Volume: 18 Suppl

    Topics: Adolescent; Adult; Antioxidants; Child; Child, Preschool; Cholesterol; Coenzymes; Humans; Neuronal Ceroid-Lipofuscinoses; Ubiquinone; Vitamin E

1997
English setter model and juvenile ceroid-lipofuscinosis in man.
    American journal of medical genetics, 1992, Feb-15, Volume: 42, Issue:4

    Topics: Animals; Ascorbic Acid; Bone Marrow Transplantation; Brain; Butylated Hydroxytoluene; Disease Models, Animal; Dogs; Electroencephalography; Female; Humans; Infant; Liver Transplantation; Male; Methionine; Neuronal Ceroid-Lipofuscinoses; Pigment Epithelium of Eye; Vitamin E

1992
Altered elemental profiles in neuronal ceroid lipofuscinosis.
    Journal of trace elements and electrolytes in health and disease, 1990, Volume: 4, Issue:3

    Topics: Adolescent; Antioxidants; Blood Platelets; Calcium; Child; Copper; Female; Humans; Iron; Leukocytes, Mononuclear; Magnesium; Male; Neuronal Ceroid-Lipofuscinoses; Pyridoxine; Riboflavin; Selenium; Vitamin E; Zinc

1990
Experience over 17 years with antioxidant treatment in Spielmeyer-Sjögren disease.
    American journal of medical genetics. Supplement, 1988, Volume: 5

    Topics: Adolescent; Antioxidants; Ascorbic Acid; Butylated Hydroxytoluene; Drug Therapy, Combination; Female; Follow-Up Studies; Humans; Male; Methionine; Neuronal Ceroid-Lipofuscinoses; Vitamin E

1988
Selenium treatment in neuronal ceroid-lipofuscinosis.
    American journal of medical genetics. Supplement, 1988, Volume: 5

    Topics: Child; Child, Preschool; Drug Therapy, Combination; Erythrocytes; Follow-Up Studies; Glutathione Peroxidase; Humans; Lipid Peroxidation; Male; Neuronal Ceroid-Lipofuscinoses; Selenious Acid; Selenium; Vitamin E

1988
Accumulation of a high molecular weight glycoprotein during in vitro ageing and contact inhibition of growth.
    Mechanisms of ageing and development, 1986, Volume: 34, Issue:3

    Topics: Adult; Cell Division; Cell Line; Cell Survival; Child, Preschool; Cytosol; Female; Fibroblasts; Fluorescence; Glycoproteins; Humans; Male; Microsomes; Molecular Weight; Neuronal Ceroid-Lipofuscinoses; Syndrome; Time Factors; Vitamin E; Werner Syndrome

1986
Antioxidant treatment in Spielmeyer-Sjögren's disease.
    Acta neurologica Scandinavica, 1985, Volume: 71, Issue:2

    Topics: Adolescent; Adult; Antioxidants; Ascorbic Acid; Butylated Hydroxytoluene; Child; Drug Therapy, Combination; Electroencephalography; Evoked Potentials; Female; Follow-Up Studies; Humans; Intelligence; Male; Methionine; Neuronal Ceroid-Lipofuscinoses; Neuropsychological Tests; Selenious Acid; Selenium; Vitamin E

1985
Autofluorescence of human skin fibroblasts during growth inhibition and in vitro ageing.
    Gerontology, 1985, Volume: 31, Issue:3

    Topics: Adult; Aging; Cell Separation; Cells, Cultured; Child, Preschool; Female; Fibroblasts; Flow Cytometry; Humans; Lipid Peroxides; Male; Neuronal Ceroid-Lipofuscinoses; Skin; Skin Physiological Phenomena; Vitamin E; Werner Syndrome

1985