d-alpha tocopherol has been researched along with Metabolism, Inborn Errors in 10 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 3 (30.00) | 18.7374 |
1990's | 5 (50.00) | 18.2507 |
2000's | 1 (10.00) | 29.6817 |
2010's | 1 (10.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Blond, E; Charriere, S; Cuerq, C; Di Filippo, M; Drai, J; Lachaux, A; Levy, E; Michalski, MC; Peretti, N; Restier, L; Roux, A | 1 |
Pejaver, RK; Watson, AH | 1 |
Charpentier, C; Finckh, B; Gibson, KM; Hoffmann, GF; Hübner, C; Kohlschütter, A; Lehr, HA; Puhl, H | 1 |
Auld, PA; Buist, NR; Jain, A; Kennaway, NG; Mårtensson, J; Powell, BR | 1 |
Kolosova, NG; Salganik, RI; Shabalina, IG; Solov'eva, NA | 1 |
Artuch, R; Campistol, J; Moyano, D; Pineda, M; Póo, P; Sierra, C; Vernet, A; Vilaseca, MA | 1 |
Huszagh, VA; Infante, JP | 1 |
Schulman, JD | 1 |
Johnson, JD | 1 |
Elsas, LJ; McCormick, DB | 1 |
3 review(s) available for d-alpha tocopherol and Metabolism, Inborn Errors
Article | Year |
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Secondary carnitine deficiency and impaired docosahexaenoic (22:6n-3) acid synthesis: a common denominator in the pathophysiology of diseases of oxidative phosphorylation and beta-oxidation.
Topics: Animals; Carnitine; Disease Models, Animal; Docosahexaenoic Acids; Humans; Metabolism, Inborn Errors; Mice; Mice, Knockout; Mitochondria; Mitochondrial Encephalomyopathies; Neuronal Ceroid-Lipofuscinoses; Oxidation-Reduction; Oxidative Phosphorylation; Phospholipids; Vitamin E | 2000 |
Neonatal nonhemolytic jaundice.
Topics: Bile Acids and Salts; Bile Ducts; Biliary Tract Diseases; Bilirubin; Brain Damage, Chronic; Breast Feeding; Cholestyramine Resin; Chronic Disease; Diagnosis, Differential; Female; Glucuronidase; Glucuronosyltransferase; Hemolysis; Hepatitis; Humans; Hyperbilirubinemia, Hereditary; Infant, Newborn; Infant, Newborn, Diseases; Iodine Radioisotopes; Jaundice, Neonatal; Liver; Metabolism, Inborn Errors; Milk, Human; Phenobarbital; Pregnanediol; Vitamin E | 1975 |
Genetic defects in vitamin utilization. Part I: General aspects and fat-solumbe vitamins.
Topics: Avitaminosis; Chemical Phenomena; Chemistry; Humans; Metabolism, Inborn Errors; Nutritional Requirements; Vitamin A; Vitamin A Deficiency; Vitamin D; Vitamin D Deficiency; Vitamin E; Vitamin E Deficiency; Vitamin K; Vitamin K Deficiency; Vitamins | 1986 |
7 other study(ies) available for d-alpha tocopherol and Metabolism, Inborn Errors
Article | Year |
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Establishment of reference values of α-tocopherol in plasma, red blood cells and adipose tissue in healthy children to improve the management of chylomicron retention disease, a rare genetic hypocholesterolemia.
Topics: Adipose Tissue; Adolescent; alpha-Tocopherol; Child; Child, Preschool; Erythrocytes; Female; Humans; Hypobetalipoproteinemias; Infant; Infant, Newborn; Malabsorption Syndromes; Male; Metabolism, Inborn Errors; Prospective Studies; Reference Values; Vitamin E | 2016 |
High-dose vitamin E therapy in glutathione synthetase deficiency.
Topics: Female; Glutathione Synthase; Humans; Infant, Newborn; Metabolism, Inborn Errors; Vitamin E | 1994 |
Decreased plasma ubiquinone-10 concentration in patients with mevalonate kinase deficiency.
Topics: Cells, Cultured; Child; Child, Preschool; Creatine Kinase; Dolichols; Female; Fibroblasts; Humans; Infant; Lipoproteins, LDL; Male; Metabolism, Inborn Errors; Mevalonic Acid; Oxidation-Reduction; Phosphotransferases (Alcohol Group Acceptor); Ubiquinone; Vitamin E | 1993 |
Effect of ascorbate or N-acetylcysteine treatment in a patient with hereditary glutathione synthetase deficiency.
Topics: Acetylcysteine; Ascorbic Acid; Child, Preschool; Female; Glutathione Synthase; Humans; Lymphocytes; Metabolism, Inborn Errors; Vitamin E | 1994 |
[Level of tocopherol and lipid peroxidation products in tissues of rats with an inherited ability to hyperproduce reactive free radicals].
Topics: Adipose Tissue; Adrenal Glands; Animals; Epididymis; Lipid Peroxidation; Male; Malondialdehyde; Metabolism, Inborn Errors; Mitochondria, Liver; Myocardium; Rats; Rats, Wistar; Reactive Oxygen Species; Vitamin E | 1996 |
Tocopherol in inborn errors of intermediary metabolism.
Topics: Adolescent; Antioxidants; Case-Control Studies; Child; Cytosol; Erythrocytes; Free Radicals; Humans; Metabolism, Inborn Errors; Mitochondria; Vitamin E | 1997 |
Approaches to the treatment of inborn errors of sulphur amino acid and peptide metabolism.
Topics: Amino Acids, Sulfur; Ascorbic Acid; Aspirin; Cysteamine; Cystinosis; Dipyridamole; Glutathione; Glutathione Synthase; Homocystinuria; Humans; Metabolism, Inborn Errors; Pyridoxine; Vitamin E | 1979 |