d-alpha tocopherol has been researched along with Hypobetalipoproteinemias in 21 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 2 (9.52) | 18.7374 |
1990's | 8 (38.10) | 18.2507 |
2000's | 6 (28.57) | 29.6817 |
2010's | 4 (19.05) | 24.3611 |
2020's | 1 (4.76) | 2.80 |
Authors | Studies |
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Blond, E; Caussy, C; Charriere, S; Cuerq, C; Di Filippo, M; Drai, J; Henin, E; Lachaux, A; Laveille, C; Levy, E; Marçais, C; Michalski, MC; Moulin, P; Peretti, N; Poinsot, P; Reboul, E; Restier, L; Sassolas, A | 1 |
Blond, E; Charriere, S; Cuerq, C; Di Filippo, M; Drai, J; Lachaux, A; Levy, E; Michalski, MC; Peretti, N; Restier, L; Roux, A | 1 |
Burnett, JR; Clarke, MW; Croft, KD; Headlam, HA; Hooper, AJ; Wu, JH | 1 |
Bordat, C; Cochet, M; Collardeau-Frachon, S; Lacaille, F; Lachaux, A; Peretti, N; Poinsot, P; Sissaoui, S | 1 |
Burnett, JR; Hooper, AJ | 2 |
Davidson, JS; du Toit, S; George, PM; Homer, VM; Wilson, CJ | 1 |
Kairis, M; Karpouzas, J; Klontza, D; Matsaniotis, N; Pangalis, A; Roma, E | 1 |
Dehart, DB; Homanics, GE; Kayden, HJ; Maeda, N; Sulik, KK; Traber, MG | 1 |
Ayrault-Jarrier, M; Bihain, B; Flynn, LM; Jacotot, B; Sanan, DA; Young, SG | 1 |
Averna, M; Mankowitz, K; Schonfeld, G; Seip, RL | 1 |
Aguie, GA; Brewer, HB; Castro, G; Clavey, V; Fruchart, JC; Kayden, HJ; Rader, DJ; Torpier, G; Traber, MG | 1 |
Azzimondi, G; Barbiroli, B; Battino, M; Carelli, V; D'Alessandro, R; Gaddi, A; Iotti, S; Lodi, R; Rinaldi, R; Scoz, N; Zaniol, P | 1 |
Mabuchi, H; Tohdoh, Y | 2 |
Julius, U; Lattke, P; Pietzsch, J | 1 |
Kinoshita, M | 1 |
Ohashi, K | 1 |
Banin, E; Chowers, I; Cooper, M; Granot, E; Merin, S | 1 |
Blache, D; Bouma, ME; Feldmann, G; Gay, G; Roche, JF; Scoazec, JY; Verthier, N | 1 |
Kayden, HJ; Neville, HE; Ringel, SP; Sokol, RJ; Thellman, CA; Traber, MG | 1 |
7 review(s) available for d-alpha tocopherol and Hypobetalipoproteinemias
Article | Year |
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Update on primary hypobetalipoproteinemia.
Topics: Abetalipoproteinemia; Avitaminosis; Diet, Fat-Restricted; Humans; Hypobetalipoproteinemia, Familial, Apolipoprotein B; Hypobetalipoproteinemias; Vitamin A; Vitamin E; Vitamins | 2014 |
Vitamin E and oxidative stress in abetalipoproteinemia and familial hypobetalipoproteinemia.
Topics: Abetalipoproteinemia; Heterozygote; Homozygote; Humans; Hypobetalipoproteinemias; Oxidative Stress; Vitamin E | 2015 |
Brain and skeletal muscle bioenergetic failure in familial hypobetalipoproteinaemia.
Topics: Brain; Energy Metabolism; Female; Humans; Hypobetalipoproteinemias; Magnetic Resonance Imaging; Male; Middle Aged; Muscle, Skeletal; Phosphocreatine; Phosphorylation; Point Mutation; Ubiquinone; Vitamin E | 1997 |
[Familial hypo beta-lipoproteinemia].
Topics: Apolipoproteins B; Humans; Hypobetalipoproteinemias; Mutation; Triglycerides; Vitamin A; Vitamin A Deficiency; Vitamin E; Vitamin E Deficiency | 1998 |
[Hypo beta-lipoproteinemia with selective deletion of apo B-48].
Topics: Apolipoprotein B-48; Apolipoproteins B; Diet, Fat-Restricted; Humans; Hypobetalipoproteinemias; Infant; Infant, Newborn; Vitamin A; Vitamin E | 1998 |
[Familial hypobetalipoproteinemia].
Topics: Apolipoproteins B; Diagnosis, Differential; Diet, Fat-Restricted; Humans; Hypobetalipoproteinemias; Mutation; Vitamin E | 2001 |
[Anderson's disease/chylomicron retention disease].
Topics: Animals; Apolipoprotein B-100; Apolipoprotein B-48; Apolipoproteins B; Chylomicrons; Diagnosis, Differential; Diet, Fat-Restricted; Humans; Hypobetalipoproteinemias; Prognosis; Vitamin A; Vitamin E | 2001 |
1 trial(s) available for d-alpha tocopherol and Hypobetalipoproteinemias
Article | Year |
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Long-term assessment of combined vitamin A and E treatment for the prevention of retinal degeneration in abetalipoproteinaemia and hypobetalipoproteinaemia patients.
Topics: Abetalipoproteinemia; Adolescent; Adult; Child; Drug Therapy, Combination; Electrooculography; Electroretinography; Female; Follow-Up Studies; Humans; Hypobetalipoproteinemias; Male; Retinal Degeneration; Vitamin A; Vitamin E | 2001 |
13 other study(ies) available for d-alpha tocopherol and Hypobetalipoproteinemias
Article | Year |
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Efficacy of two vitamin E formulations in patients with abetalipoproteinemia and chylomicron retention disease.
Topics: Abetalipoproteinemia; Adult; alpha-Tocopherol; Biological Availability; Case-Control Studies; Drug Compounding; Drug Storage; Female; Humans; Hypobetalipoproteinemias; Intestinal Absorption; Malabsorption Syndromes; Male; Middle Aged; Safety; Vitamin E | 2018 |
Establishment of reference values of α-tocopherol in plasma, red blood cells and adipose tissue in healthy children to improve the management of chylomicron retention disease, a rare genetic hypocholesterolemia.
Topics: Adipose Tissue; Adolescent; alpha-Tocopherol; Child; Child, Preschool; Erythrocytes; Female; Humans; Hypobetalipoproteinemias; Infant; Infant, Newborn; Malabsorption Syndromes; Male; Metabolism, Inborn Errors; Prospective Studies; Reference Values; Vitamin E | 2016 |
Assessment of tocopherol metabolism and oxidative stress in familial hypobetalipoproteinemia.
Topics: Abetalipoproteinemia; Adult; alpha-Tocopherol; Apolipoproteins B; Biomarkers; Blood Platelets; Child, Preschool; Erythrocytes; F2-Isoprostanes; Female; gamma-Tocopherol; Heterozygote; Humans; Hypobetalipoproteinemias; Infant; Male; Oxidative Stress; Tocopherols; Vitamins | 2006 |
Lipids Responsible for Intestinal or Hepatic Disorder: When to Suspect a Familial Intestinal Hypocholesterolemia?
Topics: Abetalipoproteinemia; Adult; Apolipoproteins B; Child; Humans; Hypobetalipoproteinemias; Lipids; Vitamin E | 2021 |
Mental retardation and ataxia due to normotriglyceridemic hypobetalipoproteinemia.
Topics: Apolipoproteins B; Ataxia; Blotting, Western; Child; Child, Preschool; Cholesterol, LDL; Chylomicrons; Humans; Hypobetalipoproteinemias; Infant; Intellectual Disability; Male; Mutation; Obesity; Polymerase Chain Reaction; Triglycerides; Vitamin E | 2005 |
Familial hypobetalipoproteinaemia.
Topics: Diarrhea; Failure to Thrive; Humans; Hypobetalipoproteinemias; Hypolipoproteinemias; Infant; Jejunum; Male; Microvilli; Vitamin A; Vitamin E | 1984 |
Exencephaly and hydrocephaly in mice with targeted modification of the apolipoprotein B (Apob) gene.
Topics: Animals; Apolipoproteins B; Apoptosis; Disease Models, Animal; Female; Genotype; Gestational Age; Hydrocephalus; Hypobetalipoproteinemias; Male; Mice; Mice, Inbred C57BL; Mice, Knockout; Mice, Mutant Strains; Mice, Transgenic; Neural Tube Defects; Rhombencephalon; Vitamin E; Vitamin E Deficiency | 1995 |
Asymptomatic homozygous hypobetalipoproteinemia associated with apolipoprotein B45.2.
Topics: Alleles; Apolipoproteins B; Cholesterol, LDL; Female; Homozygote; Humans; Hypobetalipoproteinemias; Middle Aged; Mutation; Sequence Deletion; Vitamin E | 1994 |
Postprandial lipemia in subjects with hypobetalipoproteinemia and a single intestinal allele for apoB-48.
Topics: Adult; Aged; Apolipoprotein B-100; Apolipoprotein B-48; Apolipoproteins B; Apolipoproteins E; Chylomicrons; Diterpenes; Fasting; Female; Food; Heterozygote; Humans; Hypobetalipoproteinemias; Intestinal Absorption; Intestinal Mucosa; Lipid Metabolism; Lipids; Lipoproteins, HDL; Male; Middle Aged; Mutation; Phenotype; Retinyl Esters; Triglycerides; Vitamin A; Vitamin E | 1993 |
Lipoproteins containing apolipoprotein B isolated from patients with abetalipoproteinemia and homozygous hypobetalipoproteinemia: identification and characterization.
Topics: Abetalipoproteinemia; Adult; Apolipoprotein B-100; Apolipoproteins B; Cholesterol; Female; Fibroblasts; Homozygote; Humans; Hypobetalipoproteinemias; Lipoproteins; Lipoproteins, LDL; Male; Middle Aged; Particle Size; Vitamin E; Vitamin E Deficiency | 1995 |
Oxidation of apolipoprotein B-100 in circulating LDL is related to LDL residence time. In vivo insights from stable-isotope studies.
Topics: Adult; Aged; Amino Acids; Apolipoprotein B-100; Apolipoproteins B; Cholesterol; Cholesterol, LDL; Female; Gas Chromatography-Mass Spectrometry; Humans; Hypobetalipoproteinemias; Lipoproteins, LDL; Male; Middle Aged; Mutation; Oxidation-Reduction; Receptors, LDL; Time Factors; Vitamin E | 2000 |
Liver fibrosis in a patient with familial homozygous hypobetalipoproteinaemia: possible role of vitamin supplementation.
Topics: Adult; Female; Homozygote; Humans; Hypobetalipoproteinemias; Liver Cirrhosis; Vitamin A; Vitamin E | 1992 |
Lack of tocopherol in peripheral nerves of vitamin E-deficient patients with peripheral neuropathy.
Topics: Adipose Tissue; Adolescent; Adult; Aged; Aged, 80 and over; Female; Humans; Hypobetalipoproteinemias; Male; Middle Aged; Peripheral Nerves; Peripheral Nervous System Diseases; Sural Nerve; Vitamin E; Vitamin E Deficiency | 1987 |