d-alpha tocopherol has been researched along with Friedreich Disease in 25 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 4 (16.00) | 18.7374 |
1990's | 7 (28.00) | 18.2507 |
2000's | 9 (36.00) | 29.6817 |
2010's | 4 (16.00) | 24.3611 |
2020's | 1 (4.00) | 2.80 |
Authors | Studies |
---|---|
Amagata, A; Barnes, A; Hinman, A; Jankowski, O; Kheifets, V; Komatsuzaki, R; Lee, E; Miller, G; Mollard, P; Murase, K; Rioux, P; Shrader, WD; Wesson, K | 1 |
García Ron, A; Rodriguez Mesa, M | 1 |
Buompadre, MC | 1 |
Brassington, R; Fahey, M; Kearney, M; Orrell, RW; Pandolfo, M | 1 |
Bradley, JL; Cooper, JM; Hart, PE; Korlipara, LV; Schapira, AH | 1 |
Bjørnarå, KA; Jørum, E; Koht, J; Tallaksen, CM | 1 |
Brigatti, KW; Cotticelli, MG; Deutsch, EC; Hawi, A; Kucheruk, O; Lynch, DR; Miller, G; Rioux, P; Sciascia, T; Shrader, W; Willi, SM; Wilson, RB | 1 |
Jauslin, ML; Meier, T; Murphy, MP; Smith, RA | 1 |
ROBERT, J | 1 |
Blamire, AM; Bradley, JL; Cooper, JM; Crilley, JG; Hart, PE; Lodi, R; Manners, D; Rajagopalan, B; Schapira, AH; Styles, P; Turner, C | 1 |
Buzzoni, L; Ciliberti, N; Durini, E; Jauslin, ML; Manfredini, S; Meier, T; Palozza, P; Verdecchia, S; Vertuani, S | 1 |
Cooper, JM; Schapira, AH | 1 |
Elias, E; Muller, DP; Scott, J | 1 |
Rosenberg, RN | 1 |
Belal, S; Ben Hamida, C; Ben Hamida, M; Hentati, F | 1 |
Brill, G; Carmi, R; Doolman, R; Sela, BA; Shahar, E; Shorer, Z; Yahav, Y | 1 |
Bril, G; Moses, S; Parvari, R; Sela, BA; Shorer, Z | 1 |
Arai, H; Arita, M; Gotoda, T; Harino, S; Imai, T; Inoue, K; Kanda, T; Kiyosawa, M; Matsumoto, H; Mizusawa, H; Ohga, T; Shiojiri, T; Suzuki, J; Yokota, T | 1 |
Castelnovo, G; Cavalier, L; Ichalalène, L; Labauge, P | 1 |
Fryer, MJ | 1 |
Belal, S; Ben Hamida, M; Feki, H; Feki, M; Frih-Ayed, M; Hentati, F; Kaabachi, N; Mebazaa, A; Souissi, M | 1 |
Blamire, AM; Bradley, JL; Cooper, JM; Crilley, JG; Hart, PE; Lodi, R; Manners, D; Rajagopalan, B; Schapira, AH; Styles, P; Taylor, DJ | 1 |
Barbeau, A; Butterworth, RF; Filla, A | 1 |
Battisti, C; De Michele, G; De Stefano, N; Eusebi, MP; Federico, A; Filla, A | 1 |
Harding, AE; Matthews, S; Muller, DP | 1 |
4 review(s) available for d-alpha tocopherol and Friedreich Disease
Article | Year |
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[Therapeutic developments in chronic ataxias].
Topics: Adrenal Cortex Hormones; Ataxia; Cerebellar Ataxia; Chronic Disease; Frataxin; Friedreich Ataxia; Humans; Iron-Binding Proteins; Mitochondrial Diseases; Muscle Weakness; Ubiquinone; Vitamin E; Vitamin E Deficiency | 2013 |
Pharmacological treatments for Friedreich ataxia.
Topics: Antioxidants; Friedreich Ataxia; Heart; Humans; Hypertrophy, Left Ventricular; Randomized Controlled Trials as Topic; Rare Diseases; Ubiquinone; Ultrasonography; Vitamin E | 2016 |
Friedreich's ataxia: coenzyme Q10 and vitamin E therapy.
Topics: Animals; Ataxia; Benzoquinones; Coenzymes; Disease Models, Animal; Friedreich Ataxia; Humans; Iron; Mutation; Neurodegenerative Diseases; Oxidative Stress; Oxygen; Quinones; Time Factors; Ubiquinone; Vitamin E | 2007 |
Mitochondrial dysfunction in Friedreich's ataxia: from pathogenesis to treatment perspectives.
Topics: Antioxidants; Carrier Proteins; Coenzymes; Cytoprotection; Frataxin; Friedreich Ataxia; Humans; Iron-Binding Proteins; Mitochondria, Muscle; Muscle, Skeletal; Oxidative Stress; Point Mutation; Trinucleotide Repeats; Ubiquinone; Vitamin E | 2002 |
3 trial(s) available for d-alpha tocopherol and Friedreich Disease
Article | Year |
---|---|
Coenzyme Q10 and vitamin E deficiency in Friedreich's ataxia: predictor of efficacy of vitamin E and coenzyme Q10 therapy.
Topics: Adolescent; Adult; Antioxidants; Dose-Response Relationship, Drug; Electron Transport Chain Complex Proteins; Endpoint Determination; Energy Metabolism; Female; Friedreich Ataxia; Humans; Male; Mitochondria; Muscle, Striated; Oxidative Stress; Predictive Value of Tests; Treatment Outcome; Ubiquinone; Up-Regulation; Vitamin E; Vitamin E Deficiency; Young Adult | 2008 |
A0001 in Friedreich ataxia: biochemical characterization and effects in a clinical trial.
Topics: Adolescent; Adult; Animals; Antioxidants; Biomarkers; Double-Blind Method; Female; Fibroblasts; Frataxin; Friedreich Ataxia; Glucose; Glucose Tolerance Test; Humans; Iron-Binding Proteins; Lymphocytes; Male; Mice; Middle Aged; Mitochondria; Point Mutation; Sample Size; Treatment Outcome; Vitamin E; Young Adult | 2012 |
Antioxidant treatment of patients with Friedreich ataxia: four-year follow-up.
Topics: Adolescent; Adult; Antioxidants; Child; Coenzymes; Drug Therapy, Combination; Energy Metabolism; Follow-Up Studies; Frataxin; Friedreich Ataxia; Heart; Humans; Iron-Binding Proteins; Middle Aged; Mitochondria; Muscle, Skeletal; Myocardium; Oxidative Stress; Pilot Projects; Treatment Outcome; Ubiquinone; Vitamin E | 2005 |
18 other study(ies) available for d-alpha tocopherol and Friedreich Disease
Article | Year |
---|---|
Towards a modern definition of vitamin E-evidence for a quinone hypothesis.
Topics: alpha-Tocopherol; Animals; CHO Cells; Cricetinae; Dogs; Dose-Response Relationship, Drug; Drug Design; Fibroblasts; Friedreich Ataxia; Humans; Hydrolases; Mice; Micronucleus Tests; Models, Chemical; NAD(P)H Dehydrogenase (Quinone); Nutritional Sciences; Oxidation-Reduction; Oxidative Stress; Quinones; Rats; Vitamin E | 2012 |
Compassionate use of human recombinant insulin-like growth factor-1 therapy in Friedreich's ataxia.
Topics: Adolescent; Compassionate Use Trials; Female; Friedreich Ataxia; Humans; Insulin-Like Growth Factor I; Ubiquinone; Vitamin E | 2020 |
Ataxia with vitamin E deficiency in southeast Norway, case report.
Topics: Ataxia; Diagnosis, Differential; Female; Friedreich Ataxia; Genes, Recessive; Humans; Middle Aged; Vitamin E; Vitamin E Deficiency | 2009 |
Mitochondria-targeted antioxidants protect Friedreich Ataxia fibroblasts from endogenous oxidative stress more effectively than untargeted antioxidants.
Topics: Antioxidants; Benzoquinones; Cell Death; Drug Delivery Systems; Fibroblasts; Friedreich Ataxia; Humans; Mitochondria; Models, Biological; Organophosphorus Compounds; Oxidative Stress; Ubiquinone; Vitamin E | 2003 |
[Vitamin E in therapy of Friedreich's disease and muscular diseases].
Topics: Friedreich Ataxia; Humans; Muscular Diseases; Muscular Dystrophies; Vitamin E | 1951 |
Protective effects of Fe-Aox29, a novel antioxidant derived from a molecular combination of Idebenone and vitamin E, in immortalized fibroblasts and fibroblasts from patients with Friedreich Ataxia.
Topics: Animals; Antioxidants; Benzoquinones; Cell Line, Transformed; Cell Survival; Chromans; Fibroblasts; Friedreich Ataxia; Humans; Hydrogen Peroxide; Protective Agents; Rats; Reactive Oxygen Species; Ubiquinone; Vitamin E | 2007 |
Association of spinocerebellar disorders with cystic fibrosis or chronic childhood cholestasis and very low serum vitamin E.
Topics: Abnormalities, Multiple; Adolescent; Adult; Celiac Disease; Child; Child, Preschool; Cholestasis; Chronic Disease; Cystic Fibrosis; Female; Friedreich Ataxia; Humans; Infant; Male; Vitamin E; Vitamin E Deficiency | 1981 |
Spinocerebellar ataxias and ataxins.
Topics: Carrier Proteins; Friedreich Ataxia; Humans; Point Mutation; Spinocerebellar Degenerations; Vitamin E | 1995 |
Friedreich's ataxia-vitamin E responsive type. The chromosome 8 locus.
Topics: Child; Chromosomes, Human, Pair 8; Friedreich Ataxia; Genetic Linkage; Humans; Pedigree; Vitamin E; Vitamin E Deficiency | 1995 |
[Neurological symptoms associated with vitamin E deficiency].
Topics: Adolescent; Child; Female; Friedreich Ataxia; Humans; Male; Nervous System Diseases; Vitamin E; Vitamin E Deficiency | 1995 |
Ataxia with isolated vitamin E deficiency in four siblings.
Topics: Adult; Child; Consanguinity; Dose-Response Relationship, Drug; Erythrocytes; Female; Friedreich Ataxia; Humans; Neurologic Examination; Phenotype; Vitamin E; Vitamin E Deficiency | 1996 |
Friedreich-like ataxia with retinitis pigmentosa caused by the His101Gln mutation of the alpha-tocopherol transfer protein gene.
Topics: Aged; Blotting, Northern; Carrier Proteins; Drug Resistance; Electrophysiology; Female; Friedreich Ataxia; Gene Expression; Humans; Male; Middle Aged; Mutation; Pedigree; Retinitis Pigmentosa; Sural Nerve; Vitamin E | 1997 |
[Friedreich's ataxia and hereditary vitamin E deficiency. Case study].
Topics: Adult; Carrier Proteins; Consanguinity; Electromyography; Female; Friedreich Ataxia; Humans; Male; Pedigree; Point Mutation; Vitamin E; Vitamin E Deficiency | 1998 |
Rationale for clinical trials of selenium as an antioxidant for the treatment of the cardiomyopathy of Friedreich's ataxia.
Topics: Animals; Antioxidants; Cardiomyopathy, Dilated; Clinical Trials as Topic; Disease Models, Animal; Friedreich Ataxia; Glutathione Peroxidase; Humans; Selenium; Vitamin E; White Muscle Disease | 2002 |
Serum vitamin E and lipid-adjusted vitamin E assessment in Friedreich ataxia phenotype patients and unaffected family members.
Topics: Adolescent; Adult; Aged; Aged, 80 and over; Child; Child, Preschool; Cholesterol; Chromatography, High Pressure Liquid; Female; Friedreich Ataxia; Genotype; Humans; Male; Middle Aged; Triglycerides; Vitamin E | 2002 |
Pilot studies on membranes and some transport mechanisms in Friedreich's ataxia.
Topics: Adult; Aged; Blood Platelets; Cell Count; Erythrocyte Membrane; Erythrocytes, Abnormal; Friedreich Ataxia; Humans; Middle Aged; Phospholipids; Taurine; Vitamin E | 1979 |
Serum vitamin E in inherited ataxias.
Topics: Adolescent; Adult; Aged; Cerebellar Ataxia; Child; Friedreich Ataxia; Humans; Middle Aged; Vitamin E | 1990 |
Serum vitamin E concentrations are normal in Friedreich's ataxia.
Topics: Adolescent; Adult; Child; Cholesterol; Disability Evaluation; Female; Friedreich Ataxia; Humans; Male; Middle Aged; Vitamin E; Vitamin E Deficiency | 1987 |