Page last updated: 2024-08-21

d-alpha tocopherol and Amyotonia Congenita

d-alpha tocopherol has been researched along with Amyotonia Congenita in 16 studies

Research

Studies (16)

TimeframeStudies, this research(%)All Research%
pre-199012 (75.00)18.7374
1990's2 (12.50)18.2507
2000's1 (6.25)29.6817
2010's1 (6.25)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Cross, CE; Gohil, K; Vasu, VT1
Prensky, AL1
Kobayashi, Y; Konno, T; Nakagawa, M; Suzuki, H; Tada, K; Tazawa, Y; Yamada, M1
Iannaccone, ST; Sokol, RJ1
Grabert, BE; Guggenheim, MA; Neville, HE; Ringel, SP; Silverman, A1
Grabert, BE; Guggenheim, MA; Ringel, SP; Silverman, A1
Mortier, W; Pothmann, R1
Amit, R; Rachmilewitz, E; Shapira, Y1
Battisti, C; Bonuccelli, U; Carrai, M; Dotti, MT; Federico, A; Formichi, P; Malandrini, A; Tripodi, SA1
Kohlschütter, A1
Andrews, GA; Finley, MR; Grotelueschen, DM; Hall, DG; Harmon, BG; Johnson, G; Moisan, PG; Nietfeld, JC; Rushton, SD; Sanderson, MW; Steffen, DJ; Williamson, L1
Barlow, RM; Foggin, C; Lawrence, JA; Rudert, CP1
Accurso, F; Butler-Simon, N; Hammond, K; Heubi, JE; Heyman, M; Iannaccone, ST; McClung, HJ; Riely, C; Sinatra, F; Sokol, RJ1
Black, A; Bourne, AJ; Knight, RE; Lawson, MJ; Newton, M; Wilson, P1
Hübner, C; Jansen, W; Kohlschütter, A; Lindner, SG1
Esslen, E1

Reviews

1 review(s) available for d-alpha tocopherol and Amyotonia Congenita

ArticleYear
Dietary alpha-tocopherol and neuromuscular health: search for optimal dose and molecular mechanisms continues!
    Molecular nutrition & food research, 2010, Volume: 54, Issue:5

    Topics: Adipose Tissue; alpha-Tocopherol; Animals; Ataxia; Atrophy; Carrier Proteins; Diet; Disease Models, Animal; Exercise; Free Radicals; Humans; Mice; Mice, Knockout; Neuromuscular Diseases; Physical Endurance; Vitamin D Deficiency

2010

Other Studies

15 other study(ies) available for d-alpha tocopherol and Amyotonia Congenita

ArticleYear
Vitamin E and the nervous system.
    Developmental medicine and child neurology, 1984, Volume: 26, Issue:5

    Topics: Humans; Lipid Metabolism; Lipid Peroxides; Nerve Degeneration; Nervous System Diseases; Neuromuscular Diseases; Neuronal Ceroid-Lipofuscinoses; Peripheral Nervous System Diseases; Reflex, Abnormal; Vitamin E; Vitamin E Deficiency

1984
Familial intrahepatic cholestasis associated with progressive neuromuscular disease and vitamin E deficiency.
    Journal of pediatric gastroenterology and nutrition, 1984, Volume: 3, Issue:3

    Topics: Adolescent; Bile Acids and Salts; Child, Preschool; Cholestasis, Intrahepatic; Cholestyramine Resin; Female; Humans; Infant; Male; Neuromuscular Diseases; Vitamin E; Vitamin E Deficiency

1984
Normal vitamin E status in spinal muscular atrophy.
    Annals of neurology, 1983, Volume: 13, Issue:3

    Topics: Adolescent; Adult; Child; Child, Preschool; Humans; Infant; Lipids; Middle Aged; Neuromuscular Diseases; Spinal Cord Diseases; Vitamin E

1983
Progressive neuromuscular disease in children with chronic cholestasis and vitamin E deficiency: clinical and muscle biopsy findings and treatment with alpha-tocopherol.
    Annals of the New York Academy of Sciences, 1982, Volume: 393

    Topics: Adolescent; Biopsy; Child; Child, Preschool; Cholestasis; Humans; Liver Diseases; Muscles; Neuromuscular Diseases; Vitamin E; Vitamin E Deficiency

1982
Progressive neuromuscular disease in children with chronic cholestasis and vitamin E deficiency: diagnosis and treatment with alpha tocopherol.
    The Journal of pediatrics, 1982, Volume: 100, Issue:1

    Topics: Adolescent; Child; Child, Preschool; Cholestasis; Humans; Infant; Injections, Intramuscular; Muscles; Neuromuscular Diseases; Vitamin E; Vitamin E Deficiency

1982
[Chronic cholestasis and progressive neuromyopathy. Diagnostic problems and therapeutic possibilities in a vitamin E deficiency disease (author's transl)].
    Monatsschrift Kinderheilkunde : Organ der Deutschen Gesellschaft fur Kinderheilkunde, 1982, Volume: 130, Issue:7

    Topics: Adolescent; Cerebellar Ataxia; Cholestasis, Extrahepatic; Female; Humans; Injections, Intramuscular; Liver Function Tests; Neuromuscular Diseases; Reflex, Abnormal; Vitamin E; Vitamin E Deficiency

1982
Vitamin E deficiency in Werdnig-Hoffmann disease.
    Annals of neurology, 1981, Volume: 10, Issue:3

    Topics: Child; Child, Preschool; Humans; Infant; Muscular Atrophy; Neuromuscular Diseases; Vitamin E; Vitamin E Deficiency

1981
Disappearance of skin lipofuscin storage and marked clinical improvement in adult onset coeliac disease and severe vitamin E deficiency after chronic vitamin E megatherapy.
    Journal of submicroscopic cytology and pathology, 1996, Volume: 28, Issue:3

    Topics: Brain Diseases, Metabolic; Celiac Disease; Cerebellar Ataxia; Humans; Lipofuscin; Male; Middle Aged; Nervous System Diseases; Neuromuscular Diseases; Skin; Vitamin E; Vitamin E Deficiency

1996
Vitamin E and neurological problems in childhood: a curable neurodegenerative process.
    Developmental medicine and child neurology, 1993, Volume: 35, Issue:7

    Topics: Abetalipoproteinemia; Ataxia; Child; Erythrocytes; Hemolysis; Humans; Hydrogen Peroxide; Neuromuscular Diseases; Vitamin E; Vitamin E Deficiency

1993
A familial degenerative neuromuscular disease of Gelbvieh cattle.
    Journal of veterinary diagnostic investigation : official publication of the American Association of Veterinary Laboratory Diagnosticians, Inc, 2002, Volume: 14, Issue:2

    Topics: Animals; Antioxidants; Ataxia; Cattle; Cattle Diseases; Fatal Outcome; Female; Kidney Diseases; Male; Metabolic Diseases; Muscle Weakness; Neuromuscular Diseases; Pedigree; Vitamin E

2002
A rigid lamb syndrome in sheep in Rhodesia.
    The Veterinary record, 1978, Apr-29, Volume: 102, Issue:17

    Topics: Animals; Female; Fertilizers; Humans; Maternal-Fetal Exchange; Nerve Degeneration; Neuromuscular Diseases; Pregnancy; Selenium; Sheep; Sheep Diseases; Syndrome; Vitamin E

1978
Vitamin E deficiency neuropathy in children with fat malabsorption. Studies in cystic fibrosis and chronic cholestasis.
    Annals of the New York Academy of Sciences, 1989, Volume: 570

    Topics: Cholestasis; Cystic Fibrosis; Humans; Infant; Malabsorption Syndromes; Neuromuscular Diseases; Polyethylene Glycols; Prospective Studies; Vitamin E; Vitamin E Deficiency

1989
Neurologic syndrome associated with low levels of vitamin E in primary biliary cirrhosis.
    Gastroenterology, 1986, Volume: 91, Issue:1

    Topics: Adult; Female; Humans; Liver Cirrhosis, Biliary; Nervous System Diseases; Neuromuscular Diseases; Peripheral Nervous System Diseases; Syndrome; Vitamin E

1986
A treatable familial neuromyopathy with vitamin E deficiency, normal absorption, and evidence of increased consumption of vitamin E.
    Journal of inherited metabolic disease, 1988, Volume: 11 Suppl 2

    Topics: Adult; Humans; Intestinal Absorption; Lipid Peroxides; Male; Neuromuscular Diseases; Time Factors; Vitamin E; Vitamin E Deficiency

1988
[Therapy of myopathies].
    Bibliotheca psychiatrica et neurologica, 1969, Volume: 139

    Topics: Humans; Muscular Diseases; Muscular Dystrophies; Myositis; Neuromuscular Diseases; Vitamin E

1969