cystine and Corneal Diseases

cystine has been researched along with Corneal Diseases in 14 studies

Research

Studies (14)

TimeframeStudies, this research(%)All Research%
pre-19906 (42.86)18.7374
1990's1 (7.14)18.2507
2000's4 (28.57)29.6817
2010's2 (14.29)24.3611
2020's1 (7.14)2.80

Authors

AuthorsStudies
Csorba, A; Kelen, K; Maka, E; Nagy, ZZ; Reusz, G; Szabó, A1
Baudouin, C; Labbé, A; Le Mouhaër, J; Liang, H; Plisson, C1
Arevalo, JF; Kozak, I; Shoughy, SS1
Ahishali, B; Altunsoy, M; Kocabora, MS; Ozbilen, KT; Taskapili, M1
Baudouin, C; Charbit, M; Guest, G; Labbé, A; Loirat, C; Niaudet, P1
Coelho, D; Macário, MC; Murta, J; Quadrado, MJ; Tavares, R; Torres, A1
KENNEDY, JA1
DE LA MOTTE, GW; GOAR, EL1
ALGAN, B; CORDIER, J; THOMAS, C1
Alsuhaibani, AH; Khan, AO; Wagoner, MD1
Gahl, WA; Iwata, F; Kaiser-Kupfer, MI; Kuehl, EM; McCain, LM; Reed, GF1
Dodd, MJ; Green, WR; Pusin, SM1
Huismans, H1
Bernsmeier, H; Lenz, W; Sons, HU; Weber, U1

Trials

2 trial(s) available for cystine and Corneal Diseases

ArticleYear
A New Viscous Cysteamine Eye Drops Treatment for Ophthalmic Cystinosis: An Open-Label Randomized Comparative Phase III Pivotal Study.
    Investigative ophthalmology & visual science, 2017, 04-01, Volume: 58, Issue:4

    Topics: Adolescent; Cornea; Corneal Diseases; Cysteamine; Cystine; Cystine Depleting Agents; Cystinosis; Dose-Response Relationship, Drug; Female; Follow-Up Studies; Humans; Male; Microscopy, Confocal; Ophthalmic Solutions; Retrospective Studies; Tomography, Optical Coherence; Treatment Outcome; Visual Acuity; Young Adult

2017
A randomized clinical trial of topical cysteamine disulfide (cystamine) versus free thiol (cysteamine) in the treatment of corneal cystine crystals in cystinosis.
    Molecular genetics and metabolism, 1998, Volume: 64, Issue:4

    Topics: Administration, Topical; Adolescent; Adult; Child; Child, Preschool; Cornea; Corneal Diseases; Cystamine; Cystine; Cystinosis; Female; Follow-Up Studies; Humans; Male; Sulfhydryl Compounds; Visual Acuity

1998

Other Studies

12 other study(ies) available for cystine and Corneal Diseases

ArticleYear
Ocular treatment of cystinosis with eye drop containing cysteamine
    Orvosi hetilap, 2022, May-22, Volume: 163, Issue:21

    Topics: Cornea; Corneal Diseases; Cysteamine; Cystine; Cystinosis; Humans; Photophobia; Quality of Life; Visual Acuity

2022
Intraretinal Crystals in Nephopathic Cystinosis and Fanconi Syndrome.
    JAMA ophthalmology, 2017, 03-09, Volume: 135, Issue:3

    Topics: Adolescent; Corneal Diseases; Cystine; Cystinosis; Fanconi Syndrome; Female; Humans; Nephrotic Syndrome; Retinal Diseases; Slit Lamp; Tomography, Optical Coherence; Vision Disorders; Visual Acuity

2017
Clinicopathological features of ocular cystinosis.
    Clinical & experimental ophthalmology, 2008, Volume: 36, Issue:8

    Topics: Adult; Conjunctiva; Corneal Diseases; Corneal Stroma; Cystine; Cystinosis; Diagnosis, Differential; Female; Humans; Microscopy, Confocal; Microscopy, Electron, Transmission; Photophobia; Tomography, Optical Coherence

2008
In vivo confocal microscopy and anterior segment optical coherence tomography analysis of the cornea in nephropathic cystinosis.
    Ophthalmology, 2009, Volume: 116, Issue:5

    Topics: Adolescent; Adult; Child; Cornea; Corneal Diseases; Crystallization; Cystine; Cystinosis; Diagnostic Techniques, Ophthalmological; Female; Humans; Intraocular Pressure; Male; Microscopy, Confocal; Nephrotic Syndrome; Prospective Studies; Tomography, Optical Coherence; Visual Acuity; Young Adult

2009
Evaluation of treatment with cysteamine eyedrops for cystinosis with confocal microscopy.
    Cornea, 2009, Volume: 28, Issue:8

    Topics: Corneal Diseases; Crystallization; Crystallography; Cysteamine; Cystine; Cystinosis; Drug Administration Schedule; Female; Humans; Kidney Diseases; Kidney Transplantation; Medical Records; Microscopy, Confocal; Ophthalmic Solutions; Photophobia; Treatment Outcome; Visual Acuity; Young Adult

2009
Cystinosis with crystal deposits in the cornea and conjunctiva; report of a case.
    American journal of ophthalmology, 1952, Volume: 35, Issue:11

    Topics: Conjunctiva; Conjunctival Diseases; Cornea; Corneal Diseases; Cystine; Cystinosis; Disease; Humans

1952
Cystine crystals in the cornea and conjunctiva.
    A.M.A. archives of ophthalmology, 1954, Volume: 51, Issue:3

    Topics: Conjunctiva; Conjunctival Diseases; Cornea; Corneal Diseases; Cystine; Disease; Humans

1954
[Ophthalmological contributions to the diagnosis of dwarfism: cystinosis of the cornea].
    Bulletin des societes d'ophtalmologie de France, 1954, Volume: 6

    Topics: Cornea; Corneal Diseases; Cystine; Cystinosis; Disease; Dwarfism; Metabolic Diseases

1954
Confocal microscopy of the cornea in nephropathic cystinosis.
    The British journal of ophthalmology, 2005, Volume: 89, Issue:11

    Topics: Child; Corneal Diseases; Crystallization; Cystine; Cystinosis; Epithelium, Corneal; Humans; Male; Microscopy, Confocal

2005
Adult cystinosis. A case report.
    Archives of ophthalmology (Chicago, Ill. : 1960), 1978, Volume: 96, Issue:6

    Topics: Adolescent; Adult; Child; Conjunctiva; Corneal Diseases; Crystallization; Cystine; Cystinosis; Female; Humans; Hypertension; Kidney Diseases; Male; Retinal Detachment

1978
[Alport's syndrome (author's transl)].
    Klinische Monatsblatter fur Augenheilkunde, 1978, Volume: 172, Issue:5

    Topics: Actihaemyl; Adult; Corneal Diseases; Cystine; Eye Manifestations; Gels; Humans; Male; Nephritis, Hereditary; Ophthalmic Solutions; Pedigree; Scopolamine; Scotoma

1978
Experimentally induced cystine keratopathy in rabbits.
    Graefe's archive for clinical and experimental ophthalmology = Albrecht von Graefes Archiv fur klinische und experimentelle Ophthalmologie, 1986, Volume: 224, Issue:5

    Topics: Animals; Cornea; Corneal Diseases; Crystallization; Cystine; Endothelium; Microscopy, Electron, Scanning; Rabbits

1986