cystine and Aminoaciduria, Renal

cystine has been researched along with Aminoaciduria, Renal in 20 studies

Research

Studies (20)

TimeframeStudies, this research(%)All Research%
pre-199020 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
CHANG, LT; CHI, M1
BLAIR, A; SEGAL, S1
GORDON, N; WILSON, VK1
Mann, GV; Perry, N1
GERRITSEN, T; WAISMAN, HA1
VOLKOV, VP1
GROSS, JB; JONES, JD; MAHER, FT; ULRICH, JA1
KIIL, R; ROKKONES, T1
GROSS, JB; JONES, JD; ULRICH, JA1
GIOACCHINI, B; LOMBARDI, R; MEMEO, SA1
CARSON, NA; GIBSON, JB; NEILL, DW1
DAVIDSON, DT; STAMBAUGH, R1
Thier, SO1
Holmgren, G; Lindqvist, B; Lundberg, E1
Potter, JL; Silvidi, AA; Timmons, GD1
Stuber, A1
Aaron, K; Canlas, Z; Delvin, E; Goldman, H; Scriver, CR1
Miura, R; Oyanagi, K; Yamanouchi, T1
Cohen, PA; Gaull, GE; Sturman, JA1
Christensen, HN; Cullen, AM1

Other Studies

20 other study(ies) available for cystine and Aminoaciduria, Renal

ArticleYear
AN INVESTIGATION INTO THE PROTEIN METABOLISM OF SCHIZOPHRENICS AND ITS CLINICAL SIGNIFICANCE.
    Chinese medical journal (Peking, China : 1932), 1963, Volume: 82

    Topics: China; Chromatography; Cysteine; Cystine; Indoles; Kidney; Proteins; Renal Aminoacidurias; Schizophrenia; Tryptophan

1963
IN VITRO EFFECT OF SALICYLATE ON AMINO ACID ACCUMULATION BY KIDNEY CORTEX SLICES.
    Nature, 1963, Oct-12, Volume: 200

    Topics: Amino Acids; Cystine; Glycine; Histidine; In Vitro Techniques; Kidney; Kidney Cortex; Lysine; Pharmacology; Phenylalanine; Proteins; Rats; Renal Aminoacidurias; Research; Salicylates

1963
ABNORMAL AMINO-ACID EXCRETION IN CEREBRAL DISEASE.
    Developmental medicine and child neurology, 1963, Volume: 5

    Topics: Brain Diseases; Cerebrospinal Fluid; Child; Chromatography; Cystine; Epilepsy; Glutamates; Humans; Intellectual Disability; Kidney; Renal Aminoacidurias; Taurine; Urine

1963
AMINOACIDURIA AFTER DIETARY LOADING IN HUMAN SUBJECTS.
    The American journal of clinical nutrition, 1964, Volume: 14

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Cystine; Diet; Dietary Proteins; Humans; Kidney; Lysine; Nitrogen; Ornithine; Proteins; Renal Aminoacidurias; Sulfur; Urine

1964
HOMOCYSTINURIA: ABSENCE OF CYSTATHIONINE IN THE BRAIN.
    Science (New York, N.Y.), 1964, Aug-07, Volume: 145, Issue:3632

    Topics: Amino Acids; Brain; Child; Chromatography; Cystathionine; Cystathionine beta-Synthase; Cystine; Homocystinuria; Humans; Hydro-Lyases; Kidney; Liver; Metabolic Diseases; Methionine; Nerve Tissue Proteins; Renal Aminoacidurias; Serine; Taurine; Transferases

1964
[FREE AMINO ACIDS IN THE BLOOD AND URINE OF PATIENTS WITH SOME FORMS OF DERMATOSIS].
    Vestnik dermatologii i venerologii, 1964, Volume: 38

    Topics: Alanine; Amino Acids; Arginine; Aspartic Acid; Blood; Cystine; Dermatitis; Eczema; Erythema Multiforme; Glutamates; Glycine; Histidine; Lupus Erythematosus, Systemic; Lysine; Proteins; Psoriasis; Renal Aminoacidurias; Serine; Skin Diseases; Taurine; Threonine; Toxicology; Tryptophan; Urticaria

1964
ENDOGENOUS RENAL CLEARANCES OF 12 INDIVIDUAL AMINO ACIDS IN FOUR APPARENTLY HEALTHY SUBJECTS AND IN FOUR AMINOACIDURIC PERSONS OF A KINDRED WITH HEREDITARY PANCREATITIS.
    The Journal of laboratory and clinical medicine, 1964, Volume: 63

    Topics: Amino Acids; Arginine; Biomedical Research; Cystine; Genetics, Medical; Glutamates; Healthy Volunteers; Histidine; Isoleucine; Kidney; Leucine; Lysine; Methionine; Pancreatitis; Pancreatitis, Chronic; Phenylalanine; Physiology; Renal Aminoacidurias; Threonine; Tryptophan; Tyrosine; Valine

1964
LATE MANIFESTING VARIANT OF BRANCHED-CHAIN KETOACIDURIA (MAPLE SYRUP URINE DISEASE).
    Acta paediatrica, 1964, Volume: 53

    Topics: Amino Acid Metabolism, Inborn Errors; Blood Proteins; Child; Chromatography; Cystine; Histidine; Humans; Infant; Isoleucine; Kidney; Leucine; Maple Syrup Urine Disease; Pathology; Renal Aminoacidurias; Valine

1964
URINARY EXCRETION OF AMINO ACIDS IN A KINDRED WITH HEREDITARY PANCREATITIS AND AMINOACIDURIA.
    Gastroenterology, 1964, Volume: 47

    Topics: Amino Acids; Arginine; Biomedical Research; Child; Cystine; Genetics, Medical; Humans; Kidney; Kidney Tubules; Lysine; Pancreatitis; Pancreatitis, Chronic; Renal Aminoacidurias; Urine

1964
[ON SOME FINDINGS CONCERNING PATHOLOGICAL AMINOACIDURIAS WITH CYSTINE CALCULOSIS].
    Giornale di gerontologia, 1964, Volume: 12

    Topics: Amino Acid Metabolism, Inborn Errors; Congenital Abnormalities; Cystine; Cystinosis; Cystinuria; Humans; Kidney; Kidney Calculi; Kidney Diseases; Kidney Tubules; Lithiasis; Renal Aminoacidurias

1964
PATHOLOGICAL FINDINGS IN HOMOCYSTINURIA.
    Journal of clinical pathology, 1964, Volume: 17

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Arachnodactyly; Child; Cystine; Fatty Liver; Homocystinuria; Humans; Intellectual Disability; Intracranial Embolism; Intracranial Embolism and Thrombosis; Kidney; Marfan Syndrome; Pathology; Renal Aminoacidurias; Thrombosis; Vascular Diseases

1964
EVALUATION OF THE AMINO ACID EXCRETION PATTERN OF MENTAL RETARDATES AS A SCREENING TECHNIQUE FOR INBORN ERRORS OF METABOLISM.
    The Journal of pediatrics, 1964, Volume: 65

    Topics: Adolescent; Alanine; Amino Acid Metabolism, Inborn Errors; Child; Chromatography; Creatine; Creatinine; Cystine; Glutamates; Glutamine; Glycine; Humans; Infant; Intellectual Disability; Mass Screening; Renal Aminoacidurias; Threonine

1964
Dibasic amino acid transport: lessons from human disease.
    Transactions of the American Clinical and Climatological Association, 1984, Volume: 95

    Topics: Absorption; Amino Acids, Diamino; Biological Transport; Cystine; Cystinuria; Humans; In Vitro Techniques; Kidney; Kidney Tubules; Lysine; Renal Aminoacidurias

1984
Hyperaminoaciduria in mild phosphate diabetes in adults.
    Acta medica Scandinavica, 1980, Volume: 207, Issue:6

    Topics: Adult; Cystine; Cystinuria; Female; Glutamine; Glycine; Humans; Hypophosphatemia, Familial; Male; Middle Aged; Phosphates; Renal Aminoacidurias

1980
Argininosuccinicaciduria: the hair abnormality revisited.
    American journal of diseases of children (1960), 1980, Volume: 134, Issue:11

    Topics: Amino Acids; Arginine; Argininosuccinic Acid; Child; Cystine; Female; Hair; Hair Diseases; Humans; Renal Aminoacidurias

1980
Screening tests and chromatography for the detection of inborn errors of metabolism.
    Clinica chimica acta; international journal of clinical chemistry, 1972, Volume: 36, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Child; Child, Preschool; Chromatography, Paper; Chromatography, Thin Layer; Copper; Cystine; Humans; Indicators and Reagents; Infant; Iron; Mass Screening; Metabolism, Inborn Errors; Naphthols; Renal Aminoacidurias; Toluidines

1972
Adolescent cystinosis: comparisons with infantile and adult forms.
    Pediatrics, 1971, Volume: 47, Issue:6

    Topics: Adolescent; Biopsy; Bone Marrow Examination; Cells, Cultured; Creatinine; Cystine; Cystinosis; Dithiothreitol; Fibroblasts; Glomerular Filtration Rate; Heterozygote; Humans; Kidney; Leukocytes; Male; Phenotype; Proteinuria; Renal Aminoacidurias

1971
Congenital lysinuria: a new inherited transport disorder of dibasic amino acids.
    The Journal of pediatrics, 1970, Volume: 77, Issue:2

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Arginine; Biological Transport; Child; Chromatography, Thin Layer; Consanguinity; Cystine; Cystinuria; Diarrhea; Female; Growth; Humans; Intellectual Disability; Lysine; Malabsorption Syndromes; Ornithine; Renal Aminoacidurias; Vomiting

1970
Metabolism of L- 35 S-methionine in vitamin B 6 deficiency: observations on cystathioninuria.
    Biochemical medicine, 1970, Volume: 3, Issue:6

    Topics: Animals; Brain; Cystathionine; Cystine; Kidney; Kinetics; Liver; Male; Methionine; Nerve Tissue Proteins; Pancreas; Proteins; Rats; Rats, Inbred Strains; Renal Aminoacidurias; Sulfur; Sulfur Isotopes; Taurine; Vitamin B 6 Deficiency

1970
Effects of non-metabolizable analogs on the distribution of amino acids in the rat.
    Biochimica et biophysica acta, 1968, Mar-01, Volume: 150, Issue:2

    Topics: Adrenalectomy; Amino Acids; Aminoisobutyric Acids; Animals; Autoanalysis; Carbon Isotopes; Chromatography, Ion Exchange; Cystine; Glycine; Liver; Lysine; Male; Muscles; Rats; Renal Aminoacidurias

1968