Compounds > cystic fibrosis transmembrane conductance regulator (505-511)
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cystic fibrosis transmembrane conductance regulator (505-511) and Cystic Fibrosis of Pancreas

cystic fibrosis transmembrane conductance regulator (505-511) has been researched along with Cystic Fibrosis of Pancreas in 14 studies

Research

Studies (14)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's1 (7.14)18.2507
2000's9 (64.29)29.6817
2010's4 (28.57)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Bompadre, SG; Kopeikin, Z; Yang, HY; Yuksek, Z1
Mayor, S1
Ittenbach, RF; McBride, MG; Paridon, SM; Schall, JI; Stallings, VA; Zemel, BS1
Cooper-Knock, J; Garrard, K; Lo, C; Martindale, J; Shaw, P; Williams, T1
Banks-Schlegel, SP; Guggino, WB1
Aebischer, CC; Keller, BM; Kraemer, R; Schöni, MH1
Cabello, GM; Cabello, PH; Fernandes, O; Llerena, JC; Lopez-Camelo, JS1
Nau, JY1
Ratjen, F1
Ahrens, RC; Aitken, ML; Hilliard, KA; Kelley, TJ; Konstan, MW; Launspach, J; McCarty, NA; Milgram, LJ; Regelmann, WE; Standaert, TA; Teresi, M; Tuthill, C; Weatherly, MR1
Brooks, JG; Detzer, M; Kahn, R; Lever, T; Maddock, J; O'Connor, GT; Quinton, HB; Robichaud, P1
Bush, A; Crowley, S1
Borowitz, D; Cimino, M; Simon, D1
Chan, HC; Dedman, JR; Hazarika, P; Kaetzel, MA; Nelson, DJ1

Reviews

2 review(s) available for cystic fibrosis transmembrane conductance regulator (505-511) and Cystic Fibrosis of Pancreas

ArticleYear
Macromolecular interactions and ion transport in cystic fibrosis.
    American journal of respiratory and critical care medicine, 2004, Oct-01, Volume: 170, Issue:7

    Topics: Cell Membrane; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Endoplasmic Reticulum; Forecasting; Humans; Ion Transport; Macromolecular Substances; Mutation; Needs Assessment; Peptide Fragments; Protein Folding; Protein Interaction Mapping; Research

2004
New pulmonary therapies for cystic fibrosis.
    Current opinion in pulmonary medicine, 2007, Volume: 13, Issue:6

    Topics: Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Genetic Therapy; Humans; Hydroxymethylglutaryl-CoA Reductase Inhibitors; Lung Diseases; Peptide Fragments; Sodium Channel Blockers; Treatment Outcome

2007

Trials

1 trial(s) available for cystic fibrosis transmembrane conductance regulator (505-511) and Cystic Fibrosis of Pancreas

ArticleYear
A phase I randomized, multicenter trial of CPX in adult subjects with mild cystic fibrosis.
    Pediatric pulmonology, 2002, Volume: 33, Issue:2

    Topics: Adolescent; Adult; Chlorides; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Dose-Response Relationship, Drug; Female; Humans; Male; Membrane Potentials; Mutation, Missense; Nasal Mucosa; Peptide Fragments; Purinergic P1 Receptor Antagonists; Regression Analysis; Research Design; Sweat; Treatment Outcome; Xanthines

2002

Other Studies

11 other study(ies) available for cystic fibrosis transmembrane conductance regulator (505-511) and Cystic Fibrosis of Pancreas

ArticleYear
Combined effects of VX-770 and VX-809 on several functional abnormalities of F508del-CFTR channels.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2014, Volume: 13, Issue:5

    Topics: Adenosine Triphosphate; Aminophenols; Aminopyridines; Benzodioxoles; Carrier Proteins; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; In Vitro Techniques; Intracellular Signaling Peptides and Proteins; Patch-Clamp Techniques; Peptide Fragments; Quinolones

2014
Drug combination that corrects deficient protein in cystic fibrosis improves lung function.
    BMJ (Clinical research ed.), 2015, May-19, Volume: 350

    Topics: Aminophenols; Aminopyridines; Benzodioxoles; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Drug Therapy, Combination; Humans; Peptide Fragments; Quinolones; Randomized Controlled Trials as Topic; Respiratory Function Tests

2015
Clinical and genetic correlates of exercise performance in young children with cystic fibrosis.
    Perceptual and motor skills, 2010, Volume: 110, Issue:3 Pt 2

    Topics: Anthropometry; Child; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; DNA Mutational Analysis; Exercise Test; Female; Genotype; Heterozygote; Humans; Male; Malnutrition; Nutritional Status; Peptide Fragments; Respiratory Function Tests

2010
Concurrent amyotrophic lateral sclerosis and cystic fibrosis supports common pathways of pathogenesis.
    Amyotrophic lateral sclerosis & frontotemporal degeneration, 2013, Volume: 14, Issue:5-6

    Topics: Adult; Amyotrophic Lateral Sclerosis; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; DNA-Binding Proteins; Female; Humans; Mutation; Peptide Fragments; RNA Splicing

2013
Growth in prepubertal children with cystic fibrosis, homozygous for the Delta F508 mutation.
    Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society, 2003, Volume: 2, Issue:2

    Topics: Adolescent; Analysis of Variance; Body Height; Body Mass Index; Body Weight; Child; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Forced Expiratory Volume; Genotype; Growth Disorders; Homozygote; Hospitals, Pediatric; Humans; Linear Models; Longitudinal Studies; Male; Maximal Midexpiratory Flow Rate; Mutation; Peptide Fragments; Retrospective Studies; Switzerland; Vital Capacity

2003
Haplotype distribution of and linkage disequilibrium between four polymorphic markers near the CFTR locus in Brazilian cystic fibrosis patients.
    Human biology, 2005, Volume: 77, Issue:6

    Topics: Africa South of the Sahara; Alleles; Brazil; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Genetics, Population; Haplotypes; Humans; Linkage Disequilibrium; Mediterranean Islands; Peptide Fragments; Polymorphism, Genetic

2005
[Prenatal testing for cystic fibrosis].
    Revue medicale suisse, 2006, Sep-27, Volume: 2, Issue:80

    Topics: Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Humans; Mutation; Peptide Fragments; Pregnancy; Prenatal Diagnosis

2006
Case-mix adjustment for evaluation of mortality in cystic fibrosis.
    Pediatric pulmonology, 2002, Volume: 33, Issue:2

    Topics: Age Factors; Child; Child, Preschool; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Ethnicity; Female; Genotype; Humans; Infant; Male; Multivariate Analysis; Peptide Fragments; Proportional Hazards Models; Racial Groups; Registries; Risk Adjustment; Sex Factors; Socioeconomic Factors; Survival Analysis; United States

2002
Cystic fibrosis: keeping it in the family.
    Pediatric pulmonology, 2002, Volume: 33, Issue:2

    Topics: Adult; Chlorides; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Fertility; Homozygote; Humans; Infant; Male; Peptide Fragments; Phenotype; Pregnancy; Sweat

2002
Normal volume of distribution of tobramycin in a mother and daughter with a CFTR splice mutation (1717 - 1G --> A).
    Pediatric pulmonology, 2002, Volume: 33, Issue:4

    Topics: Adult; Anti-Bacterial Agents; Child; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Humans; Mutation; Peptide Fragments; Tobramycin

2002
Antibody against a cystic fibrosis transmembrane conductance regulator-derived synthetic peptide inhibits anion currents in human colonic cell line T84.
    The Journal of biological chemistry, 1992, Apr-25, Volume: 267, Issue:12

    Topics: Anions; Antibodies; Biological Transport; Blotting, Western; Calcium; Cations, Divalent; Cell Line; Chlorides; Colon; Cyclic AMP; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Diffusion; Humans; Membrane Proteins; Oligopeptides; Peptide Fragments; Peptides

1992