cysteine and Huntington Disease

cysteine has been researched along with Huntington Disease in 14 studies

Research

Studies (14)

TimeframeStudies, this research(%)All Research%
pre-19902 (14.29)18.7374
1990's0 (0.00)18.2507
2000's3 (21.43)29.6817
2010's7 (50.00)24.3611
2020's2 (14.29)2.80

Authors

AuthorsStudies
Paul, BD1
Araki, S; Takata, T; Tsuchiya, Y; Watanabe, Y1
Paul, BD; Sbodio, JI; Snyder, SH2
Cha, JY; Paul, BD; Sbodio, JI; Snowman, AM; Snyder, SH; Vandiver, MS; Xu, R1
Cappai, R; Coleman, BM; Han, S; Hatters, DM; Hill, AF; Nisbet, RM1
Alexander, J; Aronin, N; Difiglia, M; Kegel, KB; Li, X; Masso, N; Reeves, P; Sapp, E; Valencia, A1
Barrow, RK; Mealer, RG; Sixt, KM; Snyder, SH; Subramaniam, S; Usiello, A1
Askew, C; Davis, NG; Hayden, MR; Huang, K; Kang, MH; Kang, R; Sanders, SS; Wan, J1
Banks, M; Berezovska, O; Bush, AI; Cherny, RA; Connor, T; DiFiglia, M; Dorsey, K; Fox, JH; Hersch, SM; Kama, J; Lieberman, G; Liebermann, G; Lu, Z; Sapp, E; Stiles, M; Volitakis, I1
Cannella, M; Simonelli, M; Squitieri, F1
Barber, DS; Buzescu, R; Chopra, R; Ferrante, RJ; Fox, JH; Hersch, SM; Kazantsev, A; Norflus, F; Singh, B; Swindell, MK; Zucker, B1
Bird, ED; Chen, MS; Huang, WM; Wu, JY1
Gray, PN; May, PC1

Reviews

2 review(s) available for cysteine and Huntington Disease

ArticleYear
Cysteine metabolism and hydrogen sulfide signaling in Huntington's disease.
    Free radical biology & medicine, 2022, Volume: 186

    Topics: Cystathionine gamma-Lyase; Cysteine; Humans; Huntington Disease; Hydrogen Sulfide; Neurodegenerative Diseases; Signal Transduction

2022
Oxidative Stress Orchestrates MAPK and Nitric-Oxide Synthase Signal.
    International journal of molecular sciences, 2020, Nov-19, Volume: 21, Issue:22

    Topics: Animals; Calcium-Calmodulin-Dependent Protein Kinase Type 1; Calcium-Calmodulin-Dependent Protein Kinase Type 2; Cysteine; Glutathione; Humans; Huntington Disease; Nitric Oxide; Nitric Oxide Synthase Type I; Oxidation-Reduction; Oxidative Stress; Phosphorylation; Protein Processing, Post-Translational; Reactive Oxygen Species; Ribosomal Protein S6 Kinases, 90-kDa; Signal Transduction

2020

Other Studies

12 other study(ies) available for cysteine and Huntington Disease

ArticleYear
Golgi stress response reprograms cysteine metabolism to confer cytoprotection in Huntington's disease.
    Proceedings of the National Academy of Sciences of the United States of America, 2018, 01-23, Volume: 115, Issue:4

    Topics: Activating Transcription Factor 4; Animals; Cell Line; Cystathionine gamma-Lyase; Cysteine; Golgi Apparatus; Huntington Disease; Mice; Monensin; Stress, Physiological

2018
Cystathionine γ-lyase deficiency mediates neurodegeneration in Huntington's disease.
    Nature, 2014, May-01, Volume: 509, Issue:7498

    Topics: Animals; Brain; Corpus Striatum; Cystathionine gamma-Lyase; Cysteine; Dietary Supplements; Disease Models, Animal; Drinking Water; Gene Deletion; Gene Expression Regulation, Enzymologic; Huntingtin Protein; Huntington Disease; Male; Mice; Mutant Proteins; Nerve Tissue Proteins; Neuroprotective Agents; Oxidative Stress; Sp1 Transcription Factor; Transcription, Genetic

2014
Transcriptional control of amino acid homeostasis is disrupted in Huntington's disease.
    Proceedings of the National Academy of Sciences of the United States of America, 2016, 08-02, Volume: 113, Issue:31

    Topics: Activating Transcription Factor 4; Amino Acids; Animals; Cell Line; Cells, Cultured; Cystathionine gamma-Lyase; Cysteine; Gene Expression Regulation; Homeostasis; Humans; Huntington Disease; Mice, Inbred C57BL; Mice, Knockout; Motor Activity; Oxidative Stress

2016
Conformational detection of prion protein with biarsenical labeling and FlAsH fluorescence.
    Biochemical and biophysical research communications, 2009, Mar-13, Volume: 380, Issue:3

    Topics: Alzheimer Disease; Animals; Cysteine; Fluoresceins; Fluorescence; Huntington Disease; Luminescent Measurements; Mice; Neurodegenerative Diseases; Organometallic Compounds; Parkinson Disease; Prion Diseases; Protein Folding; Protein Structure, Secondary; PrPC Proteins; Recombinant Proteins

2009
Aberrant Rab11-dependent trafficking of the neuronal glutamate transporter EAAC1 causes oxidative stress and cell death in Huntington's disease.
    The Journal of neuroscience : the official journal of the Society for Neuroscience, 2010, Mar-31, Volume: 30, Issue:13

    Topics: Animals; Cell Death; Cells, Cultured; Cerebral Cortex; Cysteine; Excitatory Amino Acid Transporter 3; Gene Knock-In Techniques; Glutathione; Humans; Huntingtin Protein; Huntington Disease; Mice; Nerve Tissue Proteins; Neurons; Nuclear Proteins; Oxidative Stress; Protein Transport; rab GTP-Binding Proteins; Reactive Oxygen Species

2010
Rhes, a physiologic regulator of sumoylation, enhances cross-sumoylation between the basic sumoylation enzymes E1 and Ubc9.
    The Journal of biological chemistry, 2010, Jul-02, Volume: 285, Issue:27

    Topics: Animals; Corpus Striatum; Cysteine; Glutamine; GTP-Binding Proteins; Humans; Huntington Disease; Lysine; Mice; Mice, Knockout; Mutation; Small Ubiquitin-Related Modifier Proteins; Ubiquitin-Conjugating Enzymes; Ubiquitin-Protein Ligases

2010
Palmitoylation and function of glial glutamate transporter-1 is reduced in the YAC128 mouse model of Huntington disease.
    Neurobiology of disease, 2010, Volume: 40, Issue:1

    Topics: Animals; Cell Line; Chlorocebus aethiops; COS Cells; Cysteine; Disease Models, Animal; Down-Regulation; Excitatory Amino Acid Transporter 2; Glutamic Acid; Huntington Disease; Lipoylation; Mice; Mice, Transgenic; Mutagenesis, Site-Directed; Neuroglia; Rats

2010
Cysteine oxidation within N-terminal mutant huntingtin promotes oligomerization and delays clearance of soluble protein.
    The Journal of biological chemistry, 2011, May-20, Volume: 286, Issue:20

    Topics: Animals; Chlorocebus aethiops; COS Cells; Cysteine; Disease Models, Animal; Humans; Huntingtin Protein; Huntington Disease; Mice; Mutation, Missense; Nerve Tissue Proteins; Nuclear Proteins; Oxidation-Reduction; Protein Multimerization; Protein Structure, Tertiary; Solubility

2011
CAG mutation effect on rate of progression in Huntington's disease.
    Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology, 2002, Volume: 23 Suppl 2

    Topics: Age of Onset; Alanine; Cysteine; Disease Progression; DNA Mutational Analysis; Female; Follow-Up Studies; Glycine; Humans; Huntington Disease; Male; Mutation; Phenotype; Trinucleotide Repeat Expansion

2002
Cystamine increases L-cysteine levels in Huntington's disease transgenic mouse brain and in a PC12 model of polyglutamine aggregation.
    Journal of neurochemistry, 2004, Volume: 91, Issue:2

    Topics: Animals; Antioxidants; Brain; Buthionine Sulfoximine; Cystamine; Cysteine; Cytoprotection; Disease Models, Animal; Disease Progression; Enzyme Inhibitors; Female; Gene Expression Regulation; Glutathione; Humans; Huntington Disease; Male; Mice; Mice, Transgenic; Neurons; Neuroprotective Agents; Oxidative Stress; PC12 Cells; Peptides; Rats

2004
Abnormalities of neurotransmitter enzymes in Huntington's chorea.
    Neurochemical research, 1979, Volume: 4, Issue:5

    Topics: 4-Aminobutyrate Transaminase; Carboxy-Lyases; Choline O-Acetyltransferase; Cross Reactions; Cysteic Acid; Cysteine; Glutamate Decarboxylase; Humans; Huntington Disease; Immunodiffusion; Neurotransmitter Agents

1979
L-Homocysteic acid as an alternative cytotoxin for studying glutamate-induced cellular degeneration of Huntington's disease and normal skin fibroblasts.
    Life sciences, 1985, Oct-21, Volume: 37, Issue:16

    Topics: Aspartic Acid; Cell Survival; Cells, Cultured; Cysteic Acid; Cysteine; Fibroblasts; Glutamates; Glutamic Acid; Homocysteine; Humans; Huntington Disease; In Vitro Techniques; Isomerism; Kainic Acid; Kinetics; N-Methylaspartate; Neurotransmitter Agents; Skin; Time Factors

1985