cysteine and Hemophilia A

cysteine has been researched along with Hemophilia A in 15 studies

Research

Studies (15)

TimeframeStudies, this research(%)All Research%
pre-19901 (6.67)18.7374
1990's8 (53.33)18.2507
2000's3 (20.00)29.6817
2010's2 (13.33)24.3611
2020's1 (6.67)2.80

Authors

AuthorsStudies
Butera, D; Hogg, PJ; Ju, LA; Wang, HJ; Woon, HG; Zhao, YC1
Fay, PJ; Griffiths, AE; Monaghan, M; Wakabayashi, H1
Eckhardt, CL; Fijnvandraat, K; Geskus, RB; Kamphuisen, PW; Menke, LA; Peters, M; van der Lee, JH; van Ommen, CH1
Chi, X; Liu, Z; Miao, J; Qu, H; Zhu, F1
Hashiguchi, T; Ichinose, A1
Altisent Roca, C; Arbós Via, MA; Juárez Giménez, JC; López Galera, RM; Montoro Ronsano, JB; Segura Cardona, RM; Tusell Puigbert, JM1
Arai, M; Fukutake, K; Gale, K; Inoue, M; Kagawa, K; Kamisue, S; Morichika, S; Nakai, H; Shima, M; Suzuki, H; Tanaka, I; Tuddenham, EG; Yoshioka, A1
Healey, JF; Liu, M; Lollar, P; Murphy, ME; Saenko, EL; Scandella, D; Thompson, AR1
Gu, J; Lavergne, JM; Meyer, D; Ruan, C1
Kamisue, S; Kuwabara, I; Maruyama, H; Maruyama, IN; Shima, M; Yoshioka, A1
Aoki, M; Genka, I; Kikuchi, Y; Oka, S; Tachikawa, N; Teruya, K; Yamaguchi, M; Yamamoto, Y; Yasuoka, A; Yasuoka, C1
Fressinaud, E; Mazurier, C; Meyer, D1
Granier, C; Léonetti, JP; Piquer, D; Raut, S; Saint-Remy, JM; Villard, S1
O'Brien, DP; Pattinson, JK; Tuddenham, EG1
Jákó, J; László, C; Pálos, LA; Sas, G1

Reviews

1 review(s) available for cysteine and Hemophilia A

ArticleYear
Molecular genetics of type 2 von Willebrand disease.
    International journal of hematology, 2002, Volume: 75, Issue:1

    Topics: Adult; Amino Acid Substitution; Biopolymers; Blood Platelets; Chromosomes, Human, Pair 12; Collagen; Cysteine; DNA Mutational Analysis; Exocytosis; Exons; Female; Genes, Dominant; Genes, Recessive; Hemophilia A; Hemorrhagic Disorders; Humans; Infant, Newborn; Male; Molecular Weight; Mutation, Missense; Platelet Adhesiveness; Platelet Glycoprotein GPIb-IX Complex; Pregnancy; Pregnancy Complications, Hematologic; Protein Binding; Protein Precursors; Protein Processing, Post-Translational; Protein Structure, Tertiary; Structure-Activity Relationship; Thrombocytopenia; von Willebrand Diseases; von Willebrand Factor

2002

Other Studies

14 other study(ies) available for cysteine and Hemophilia A

ArticleYear
Mechano-covalent protection of coagulation factor VIII by von Willebrand factor.
    Blood advances, 2023, 05-23, Volume: 7, Issue:10

    Topics: Cysteine; Factor VIII; Hemophilia A; Hemostatics; Humans; Thrombosis; von Willebrand Factor

2023
Stabilizing interactions between D666-S1787 and T657-Y1792 at the A2-A3 interface support factor VIIIa stability in the blood clotting pathway.
    Journal of thrombosis and haemostasis : JTH, 2016, Volume: 14, Issue:5

    Topics: Blood Coagulation; Cysteine; Disulfides; Factor VIII; Factor VIIIa; Factor Xa; Genetic Variation; Hemophilia A; Humans; Hydrogen Bonding; Mutagenesis; Mutation; Protein Binding; Protein Multimerization; Thrombin; Thrombosis

2016
Intensive peri-operative use of factor VIII and the Arg593-->Cys mutation are risk factors for inhibitor development in mild/moderate hemophilia A.
    Journal of thrombosis and haemostasis : JTH, 2009, Volume: 7, Issue:6

    Topics: Adolescent; Adult; Arginine; Autoantibodies; Cysteine; Factor VIII; Hemophilia A; Humans; Longitudinal Studies; Middle Aged; Mutation; Perioperative Care; Retrospective Studies; Risk Factors; Severity of Illness Index; Young Adult

2009
Enhanced plasma factor VIII activity in mice via cysteine mutation using dual vectors.
    Science China. Life sciences, 2012, Volume: 55, Issue:6

    Topics: Adenoviridae; Animals; Cysteine; Cytomegalovirus; Factor VIII; Genetic Therapy; Genetic Vectors; Hemophilia A; Mice; Mice, Inbred C57BL; Mice, Transgenic; Mutation; Peptide Fragments

2012
Molecular and cellular basis of deficiency of the b subunit for factor XIII secondary to a Cys430-Phe mutation in the seventh Sushi domain.
    The Journal of clinical investigation, 1995, Volume: 95, Issue:3

    Topics: Animals; Base Sequence; Biological Transport; Cell Compartmentation; Cells, Cultured; Cricetinae; Cysteine; Factor VIII; Genetic Vectors; Hemophilia A; Heterozygote; Hexosaminidases; Humans; Immunoblotting; Immunohistochemistry; Molecular Sequence Data; Mutation; Protein Processing, Post-Translational; Recombinant Proteins; RNA Splicing; Transfection

1995
Glutathione and cysteine in HIV-infected hemophiliacs.
    Clinica chimica acta; international journal of clinical chemistry, 1996, Oct-15, Volume: 254, Issue:1

    Topics: Acquired Immunodeficiency Syndrome; Adolescent; Adult; Cysteine; Disease Progression; Female; Glutathione; Glutathione Disulfide; Hemophilia A; HIV Seropositivity; Humans; Male; Middle Aged

1996
Factor VIII Ise (R2159C) in a patient with mild hemophilia A, an abnormal factor VIII with retention of function but modification of C2 epitopes.
    Thrombosis and haemostasis, 1997, Volume: 77, Issue:5

    Topics: Adolescent; Amino Acid Sequence; Antibodies, Monoclonal; Arginine; Base Sequence; Cysteine; Deamino Arginine Vasopressin; DNA Primers; Enzyme-Linked Immunosorbent Assay; Epitopes; Exons; Factor VIII; Hemophilia A; Humans; Isoantibodies; Male; Point Mutation; Polymerase Chain Reaction; Polymorphism, Single-Stranded Conformational; von Willebrand Factor

1997
Loss of tolerance to exogenous and endogenous factor VIII in a mild hemophilia A patient with an Arg593 to Cys mutation.
    Blood, 1997, Sep-01, Volume: 90, Issue:5

    Topics: Adult; Arginine; Cysteine; Factor VIII; Hemophilia A; Humans; Immune Tolerance; Male; Point Mutation

1997
Detection by denaturing gradient gel electrophoresis of an Arg1689Cys mutation in a Chinese patient with mild hemophilia A.
    Chinese medical journal, 1997, Volume: 110, Issue:2

    Topics: Adolescent; Arginine; Cysteine; Electrophoresis, Gel, Pulsed-Field; Factor VIII; Hemophilia A; Humans; Male; Point Mutation; Polymerase Chain Reaction; Sequence Analysis, DNA

1997
Mapping of the minimal domain encoding a conformational epitope by lambda phage surface display: factor VIII inhibitor antibodies from haemophilia A patients.
    Journal of immunological methods, 1999, Apr-22, Volume: 224, Issue:1-2

    Topics: Absorption; Bacteriophage lambda; Base Sequence; Cysteine; Disulfides; Epitope Mapping; Epitopes, B-Lymphocyte; Factor VIII; Gene Library; Genetic Vectors; Hemophilia A; Humans; Isoantibodies; Molecular Sequence Data; Protein Conformation; Sequence Analysis, DNA; Structure-Activity Relationship

1999
Mitigation of hepato-cellular injury caused by HAART with glycyrrhizin compound in patients co-infected with HIV and HCV.
    Japanese journal of infectious diseases, 1999, Volume: 52, Issue:6

    Topics: Anti-HIV Agents; Chemical and Drug Induced Liver Injury; Cysteine; Drug Combinations; Drug Therapy, Combination; Glycine; Glycyrrhetinic Acid; Hemophilia A; Hepatitis C; HIV Infections; HIV Protease Inhibitors; Humans; Lamivudine; Reverse Transcriptase Inhibitors; Stavudine; Viral Load; Zalcitabine; Zidovudine

1999
Low molecular weight peptides restore the procoagulant activity of factor VIII in the presence of the potent inhibitor antibody ESH8.
    The Journal of biological chemistry, 2002, Jul-26, Volume: 277, Issue:30

    Topics: Amino Acid Motifs; Amino Acid Sequence; Animals; Antibodies, Monoclonal; Crystallography, X-Ray; Cysteine; Disease Models, Animal; Dose-Response Relationship, Drug; Enzyme-Linked Immunosorbent Assay; Epitopes; Factor VIII; Hemophilia A; Mice; Models, Molecular; Molecular Sequence Data; Peptide Library; Peptides; Protein Binding; Protein Structure, Tertiary; Thrombin; Time Factors

2002
Purification and characterization of factor VIII 372-Cys: a hypofunctional cofactor from a patient with moderately severe hemophilia A.
    Blood, 1990, Apr-15, Volume: 75, Issue:8

    Topics: Amino Acid Sequence; Arginine; Blotting, Western; Codon; Cysteine; DNA; Factor VIII; Hemophilia A; Humans; Molecular Sequence Data; Mutation; Nucleic Acid Hybridization; Plasma; Thrombin; von Willebrand Factor

1990
Oxidizing-reducing properties of the intrinsic prothrombin activator.
    Haematologia, 1970, Volume: 4, Issue:3

    Topics: Absorption; Aluminum Silicates; Barbiturates; Barium Sulfate; Biochemical Phenomena; Biochemistry; Blood Coagulation Tests; Cysteine; Enzyme Activation; Ethylmaleimide; Glutathione; Hemophilia A; Humans; Nitrogen; Oxidation-Reduction; Oxygen; Prothrombin; Thrombin

1970