cysteine and Electron Transport Chain Deficiencies, Mitochondrial

cysteine has been researched along with Electron Transport Chain Deficiencies, Mitochondrial in 13 studies

Research

Studies (13)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's4 (30.77)29.6817
2010's7 (53.85)24.3611
2020's2 (15.38)2.80

Authors

AuthorsStudies
Chen, FF; Guan, XL; Ni, L; Wu, PF1
Banci, L; Ciofi-Baffoni, S; Nasta, V; Saudino, G; Suraci, D1
Boczonadi, V; Chinnery, PF; Gomez-Duran, A; Horvath, R; Pyle, A; Schara, U; Smith, PM; Tulinius, M1
Bastin, J; Bennett, MJ; Chen, J; Doulias, PT; Ischiropoulos, H; Tenopoulou, M1
Bartsakoulia, M; Boczonadi, V; Gomez-Duran, A; Horvath, R; Mϋller, JS; Yu-Wai-Man, P1
Darlin Quine, S; Sangeetha, T1
Bindoff, LA; Engelsen, BE; Ersland, L; Moen, G; Mørk, SJ; Neckelmann, G; Tzoulis, C; Viscomi, C; Zeviani, M1
Bossy, B; Bossy-Wetzel, E; Chen, J; Klinglmayr, E; Knott, AB; Lütz-Meindl, U; Masliah, E; Petrilli, A; Schwarzenbacher, R1
Dou, DQ; Gao, MB; Li, CB; Li, HC; Li, XT1
Lapatto, R; Leonard, JV; Rahman, S; Salmi, H1
Andrés-Martínez, L; González-Cortés, C; Maldonado, PD; Pedraza-Chaverrí, J; Pérez-De La Cruz, V; Santamaría, A1
Derenko, MV; Grzybowski, T; Malyarchuk, BA; Miścicka-Sliwka, D; Stopińska, K1
Brandt, U; Galkin, A; Karas, M; Meyer, B; Schägger, H; Vinogradov, A; Wittig, I1

Other Studies

13 other study(ies) available for cysteine and Electron Transport Chain Deficiencies, Mitochondrial

ArticleYear
S-methyl-L-cysteine Protects against Antimycin A-induced Mitochondrial Dysfunction in Neural Cells via Mimicking Endogenous Methionine-centered Redox Cycle.
    Current medical science, 2020, Volume: 40, Issue:3

    Topics: Animals; Antimycin A; Antioxidants; Cell Line, Tumor; Cysteine; Humans; Membrane Potential, Mitochondrial; Methionine; Methionine Sulfoxide Reductases; Mitochondria; Mitochondrial Diseases; Neurons; Oxidation-Reduction; Oxidative Stress; PC12 Cells; Rats

2020
Molecular Basis of Multiple Mitochondrial Dysfunctions Syndrome 2 Caused by CYS59TYR BOLA3 Mutation.
    International journal of molecular sciences, 2021, May-03, Volume: 22, Issue:9

    Topics: Cysteine; Glutaredoxins; Humans; Iron-Sulfur Proteins; Mitochondria; Mitochondrial Diseases; Mitochondrial Proteins; Molecular Docking Simulation; Multiprotein Complexes; Mutation; Nuclear Magnetic Resonance, Biomolecular; Phenotype

2021
Altered 2-thiouridylation impairs mitochondrial translation in reversible infantile respiratory chain deficiency.
    Human molecular genetics, 2013, Nov-15, Volume: 22, Issue:22

    Topics: Cell Line; Cysteine; Gene Expression Regulation; Humans; Mitochondria; Mitochondrial Diseases; Mitochondrial Encephalomyopathies; Mitochondrial Proteins; Muscle, Skeletal; Mutation; Myoblasts; Oxidative Phosphorylation; Protein Biosynthesis; RNA, Transfer; Thiouridine; tRNA Methyltransferases

2013
Strategies for correcting very long chain acyl-CoA dehydrogenase deficiency.
    The Journal of biological chemistry, 2015, Apr-17, Volume: 290, Issue:16

    Topics: Acetylcysteine; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenase, Long-Chain; Amino Acid Sequence; Carnitine; Congenital Bone Marrow Failure Syndromes; Cysteine; Dose-Response Relationship, Drug; Fatty Acids; Fibroblasts; Genetic Therapy; Humans; Kinetics; Lipid Metabolism, Inborn Errors; Mitochondrial Diseases; Molecular Sequence Data; Muscular Diseases; Mutation; Oxidation-Reduction; Primary Cell Culture; Skin

2015
Cysteine Supplementation May be Beneficial in a Subgroup of Mitochondrial Translation Deficiencies.
    Journal of neuromuscular diseases, 2016, 08-30, Volume: 3, Issue:3

    Topics: Acetylcysteine; Carrier Proteins; Cyclooxygenase 2; Cysteine; Dietary Supplements; Fibroblasts; Humans; In Vitro Techniques; MELAS Syndrome; MERRF Syndrome; Mitochondria; Mitochondrial Diseases; Mitochondrial Proteins; Mutation; Neoplasm Proteins; Oxygen Consumption; Protein Biosynthesis; RNA-Binding Proteins; tRNA Methyltransferases

2016
Preventive effect of S-allyl cysteine sulphoxide (Alliin) on mitochondrial dysfunction in normal and isoproterenol induced cardiotoxicity in male Wistar rats: a histopathological study.
    Molecular and cellular biochemistry, 2009, Volume: 328, Issue:1-2

    Topics: Animals; Cysteine; Isoproterenol; Male; Mitochondria; Mitochondrial Diseases; Mitochondrial Proteins; Myocardial Infarction; Myocardium; Rats; Rats, Wistar

2009
Localized cerebral energy failure in DNA polymerase gamma-associated encephalopathy syndromes.
    Brain : a journal of neurology, 2010, Volume: 133, Issue:Pt 5

    Topics: Arginine; Brain; Brain Diseases; Cerebellum; Cysteine; Diffuse Cerebral Sclerosis of Schilder; Diffusion Magnetic Resonance Imaging; Disease Progression; DNA Polymerase gamma; DNA-Directed DNA Polymerase; DNA, Mitochondrial; Electroencephalography; Energy Metabolism; Epilepsy; Glycine; Humans; Magnetic Resonance Angiography; Magnetic Resonance Imaging; Magnetic Resonance Spectroscopy; Mitochondrial Diseases; Mutation; Neocortex; Sensitivity and Specificity; Spinocerebellar Ataxias; Stroke; Syndrome; Thalamus; Tomography, X-Ray Computed

2010
S-Nitrosylation of DRP1 does not affect enzymatic activity and is not specific to Alzheimer's disease.
    Journal of Alzheimer's disease : JAD, 2010, Volume: 20 Suppl 2

    Topics: Aging; Alzheimer Disease; Biotin; Brain; Cell Line, Transformed; Cysteine; Dithiothreitol; Dynamins; GTP Phosphohydrolases; Humans; Microscopy, Electron, Transmission; Microtubule-Associated Proteins; Mitochondrial Diseases; Mitochondrial Proteins; Postmortem Changes; Protein Multimerization

2010
Protective effects on mitochondria and anti-aging activity of polysaccharides from cultivated fruiting bodies of Cordyceps militaris.
    The American journal of Chinese medicine, 2010, Volume: 38, Issue:6

    Topics: Aging; Animals; Antioxidants; Cordyceps; Cysteine; Disease Models, Animal; Dose-Response Relationship, Drug; Fruiting Bodies, Fungal; Galactose; Hydroxyl Radical; Injections, Subcutaneous; Liver; Male; Mice; Mice, Inbred Strains; Mitochondria; Mitochondrial Diseases; Phytotherapy; Polysaccharides; Reactive Oxygen Species; Superoxides; Thiobarbituric Acid Reactive Substances

2010
Plasma thiol status is altered in children with mitochondrial diseases.
    Scandinavian journal of clinical and laboratory investigation, 2012, Volume: 72, Issue:2

    Topics: Child; Child, Preschool; Cohort Studies; Cysteine; Female; Glucosephosphate Dehydrogenase; Glutathione; Glutathione Peroxidase; Glutathione Reductase; Glutathione Transferase; Humans; Male; Mitochondrial Diseases; Sulfhydryl Compounds

2012
Protective effect of S-allylcysteine on 3-nitropropionic acid-induced lipid peroxidation and mitochondrial dysfunction in rat brain synaptosomes.
    Brain research bulletin, 2006, Jan-30, Volume: 68, Issue:5

    Topics: Animals; Brain; Cysteine; Dose-Response Relationship, Drug; Drug Interactions; Lipid Peroxidation; Male; Mitochondrial Diseases; Neuroprotective Agents; Nitro Compounds; Propionates; Rats; Rats, Wistar; Synaptosomes; Tetrazolium Salts; Thiobarbituric Acid Reactive Substances

2006
Optimization of the Y831C mutation detection in human DNA polymerase gamma by allelic discrimination assay.
    Acta biochimica Polonica, 2006, Volume: 53, Issue:3

    Topics: Cysteine; DNA Polymerase gamma; DNA-Directed DNA Polymerase; DNA, Mitochondrial; Gene Frequency; Genetic Techniques; Humans; Mitochondrial Diseases; Parkinson Disease; Peripheral Nervous System Diseases; Point Mutation; Polymerase Chain Reaction; Polymorphism, Single Nucleotide; Tyrosine

2006
Identification of the mitochondrial ND3 subunit as a structural component involved in the active/deactive enzyme transition of respiratory complex I.
    The Journal of biological chemistry, 2008, Jul-25, Volume: 283, Issue:30

    Topics: Animals; Catalysis; Cattle; Chymotrypsin; Cysteine; Electron Transport Complex I; Electrophoresis, Polyacrylamide Gel; Fluorescent Dyes; Mass Spectrometry; Mitochondrial Diseases; Models, Biological; Myocardium; Nitric Oxide; Oxygen; Proteomics

2008