cysteine has been researched along with Cystinuria in 72 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 46 (63.89) | 18.7374 |
1990's | 11 (15.28) | 18.2507 |
2000's | 6 (8.33) | 29.6817 |
2010's | 3 (4.17) | 24.3611 |
2020's | 6 (8.33) | 2.80 |
Authors | Studies |
---|---|
Bazin, D; Belletti, G; Colombo, E; Daudon, M; Frochot, V; Hessou, EP; Li, K; Lucas, IT; Moussadik, A; Quaino, P; Rouzière, S; Su, Y; Tielens, F | 1 |
Goldfarb, DS; Latyshev, S; Mikel, CC; Ponte, A; Steigelman, K | 1 |
Bar-Yosef, DL; Chakraborty, P; Do, TD; Gazit, E; Limbach, MN; Oluwatoba, DS | 1 |
Dai, Y; He, F; Ji, H; Qi, Z; Xue, T; Zheng, Y | 1 |
Beckermann, TM; Ikizler, TA; Mortlock, DP; Sha, F; Welch, RC; Williams, FM; Wilson, MH; Woodard, LE | 1 |
Birwé, H; Bitterlich, N; Hesse, A; Siener, R | 1 |
Alfonso, I; Lafuente, M; Solà, J | 1 |
Bellomo, F; Bertucci, P; Boenzi, S; Dello Strologo, L; Dionisi-Vici, C; Emma, F; Laurenzi, C; Masotti, A; Muraca, M; Pastore, A; Taranta, A | 1 |
Marickar, YM | 1 |
CLELAND, JB | 1 |
Cara Fuentes, GM; Espinosa Roman, L; Melgosa Hijosa, M; Navarro Torres, M | 1 |
Arcelloni, C; Fermo, I; Paroni, R | 1 |
FRIMPTER, GW | 3 |
VASIL'EV, LI | 1 |
HARTLEY, BS; WALSHE, JM | 1 |
CRAWHALL, JC; THOMPSON, CJ | 1 |
BOYCE, WH; KING, JS | 1 |
COLLINI, WR; HARRIS, RC; MATTERN, SR; SHAPIRO, P; ZINSSER, HH | 1 |
DOCTOR, F; MERENYI, I | 1 |
Asplin, JR; Dolin, DJ; Flagel, L; Goldfarb, DS; Grasso, M | 1 |
Bartsch, G; Lunacek, A; Oswald, J; Radmayr, C; Schwentner, C | 1 |
Brauers, E; Eggermann, T; Vester, U; Zerres, K | 1 |
Crawhall, JC; Rosenberg, LE; Segal, S | 1 |
Boström, H; Wester, PO | 1 |
Rootwelt, K | 1 |
Mårtensson, J; Sjödahl, R; Tobiasson, P | 1 |
Johnson, S; Kaung, C; Roboz, J; Yu, TF | 1 |
Asper, R; Schmucki, O | 1 |
Elkas, G; Goodyer, P; Ong, P; Rozen, R; Saadi, I | 1 |
Celli, M; D'Eufemia, P; Finocchiaro, R; Giardini, O; Mannarino, O; Troiani, P; Viozzi, L; Zaccagnini, M | 1 |
Avino, P; Campanella, L; Crescentini, G | 1 |
Coe, FL; Nakagawa, Y | 1 |
Gitomer, WL; Pak, CY; Reed, BY | 1 |
Bergeron, M; Craan, AG | 1 |
Gaull, GE; Longhi, RC; Rassin, DK; Sternowsky, HJ; Sturman, JA | 1 |
Gundalakh, AI; Mel'k, MV; Shcheglova, SA; Volkova, ZA | 1 |
Carpena, J; Martínez-Lozano, C; Pérez-Ruiz, T; Tomás, V | 1 |
Bain, M; Chalmers, R; Hammond, J; Jones, M; Patton, MA; Sharland, M | 1 |
Birwé, H; Hesse, A; Schneeberger, W | 1 |
Aebi, S; Assereto, R; Lauterburg, BH | 1 |
Birwé, H; Hesse, A | 1 |
Chrastil, J | 1 |
Denneberg, T; Lindell, A; Mårtensson, J; Textorius, O | 1 |
Aposhian, HV; Bruce, DC; Maiorino, RM | 1 |
Marquez, M; Perez-Bendito, D; Silva, M | 1 |
Berg, W; Kilian, O | 1 |
Hammond, JW; Sampson, DC; Stewart, PM | 1 |
Berg, W; Brundig, P; Kilian, O | 1 |
Mauermayer, W; Wenzl, H | 1 |
Clark, ML; Perrett, D; Scowen, EF; Silk, DB; Stephens, AD | 1 |
Deetjen, P; Silbernagl, S | 1 |
Chavez, Y; Cobo, A; Lisker, R; Zavala, C | 1 |
Kuzel, K | 1 |
Denneberg, T; Ekberg, M; Jeppsson, JO | 1 |
Chatagner, F | 1 |
Charpentier, C; Lemonnier, A; Levillain, P; Moatti, N | 1 |
Christensen, MF; Henriksen, O; Nielsen, JA | 1 |
Copeland, W; Kelly, S; Leikhim, E | 1 |
Georges, RJ; Politzer, WM | 1 |
Stephens, AD; Watts, RW | 1 |
Crawhall, JC; Lietman, PS; Schneider, JA; Seegmiller, JE | 1 |
Aboulker, P; Balan, A; Charpentier, C; Leluc, R; Lemonnier, A; Levillain, L; Thomas, J; Thuong, CT | 1 |
King, JS | 1 |
Foley, TH; London, DR | 2 |
Fernandez, AA; Henry, RJ | 1 |
Durant, JL; Holland, JM; Rosenberg, LE | 1 |
Crawhall, JC; Segal, S | 2 |
Bradley, KH; Crawhall, JC; Thompson, CJ | 1 |
1 review(s) available for cysteine and Cystinuria
Article | Year |
---|---|
[Biochemical aspects of some congenital anomalies of the metabolism of sulfur amino acids].
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Animals; Cysteine; Cystinuria; Homocysteine; Homocystinuria; Humans; Hydro-Lyases; L-Serine Dehydratase; Methionine; Rats | 1967 |
3 trial(s) available for cysteine and Cystinuria
Article | Year |
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The Impact of Diet on Urinary Risk Factors for Cystine Stone Formation.
Topics: Adult; Cysteine; Cystine; Cystinuria; Diet; Diet, Vegetarian; Diet, Western; Healthy Volunteers; Humans; Hydrogen-Ion Concentration; Male; Phosphates; Regression Analysis; Risk Factors; Sulfates; Urine; Urolithiasis; Young Adult | 2021 |
Investigations of the efficacy of ascorbic acid therapy in cystinuria.
Topics: Ascorbic Acid; Chromatography, High Pressure Liquid; Cysteine; Cystinuria; Humans; Oxalates; Oxalic Acid | 1991 |
The treatment of cystinuria with N-acetyl-D-penicillamine, a comparison with the results of D-penicillamine treatment.
Topics: Acylation; Adolescent; Adult; Child; Cysteine; Cystinuria; Desensitization, Immunologic; Drug Hypersensitivity; Edema; Female; Humans; Hypoproteinemia; Kidney Diseases; Male; Penicillamine; Prednisolone; Proteinuria; Serum Albumin; Urea; Urinary Calculi | 1971 |
68 other study(ies) available for cysteine and Cystinuria
Article | Year |
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Crystalline structures of L-cysteine and L-cystine: a combined theoretical and experimental characterization.
Topics: Cysteine; Cystine; Cystinosis; Cystinuria; Disulfides; Humans | 2022 |
Accurate 24-h urine cystine quantification for patients on cystine-binding thiol drugs.
Topics: Cysteine; Cystine; Cystinuria; Humans; Quality of Life; Sulfhydryl Compounds; Tandem Mass Spectrometry; Tiopronin | 2022 |
Self-Assembly of Cysteine into Nanofibrils Precedes Cystine Crystal Formation: Implications for Aggregation Inhibition.
Topics: Amino Acids; Amyloid; Cysteine; Cystine; Cystinuria; Disulfides; Humans | 2023 |
A novel fluorescent probe for rapidly detection cysteine in cystinuria urine, living cancer/normal cells and BALB/c nude mice.
Topics: Animals; Cell Line; Colorimetry; Cysteine; Cystinuria; Fluorescent Dyes; Hep G2 Cells; Hepatocytes; Humans; Mice; Mice, Inbred BALB C; Mice, Nude; Molecular Structure; Spectrometry, Fluorescence; Spectrophotometry; Spectrophotometry, Ultraviolet | 2020 |
CRISPR/Cas9 engineering of albino cystinuria Type A mice.
Topics: Amino Acid Transport Systems, Basic; Amino Acid Transport Systems, Neutral; Animals; CRISPR-Cas Systems; Cysteine; Cystinuria; Disease Models, Animal; Mice; Mice, Inbred C57BL; Mutation | 2020 |
A Dynamic Chemical Network for Cystinuria Diagnosis.
Topics: Cysteine; Cystine; Cystinuria; Humans; Molecular Dynamics Simulation; Molecular Structure; Spectrometry, Fluorescence | 2018 |
Gender-related effects on urine L-cystine metastability.
Topics: Adenosine; Adult; Chemical Precipitation; Cysteine; Cystinuria; Female; Guanosine; Humans; Inosine; Male; Middle Aged; Sex Characteristics; Solubility; Vanilmandelic Acid | 2014 |
Cystinuria: the South Indian experience.
Topics: Cysteine; Cystinuria; Humans; Incidence; India; Retrospective Studies; Spectroscopy, Fourier Transform Infrared; Urinary Calculi | 2009 |
Cystine, methionine and sulphate excretion in cystinuria.
Topics: Biochemical Phenomena; Body Fluids; Cysteine; Cystine; Cystinuria; Humans; Methionine; Sulfates; Sulfur; Sulfur Oxides; Urine | 1946 |
Acute renal failure due to bilateral pieloureteral stone impaction in a 10-month-old boy.
Topics: Acute Kidney Injury; Cysteine; Cystinuria; Fluid Therapy; Humans; Infant; Isotonic Solutions; Male; Potassium Citrate; Sodium Chloride; Treatment Outcome; Ureteral Calculi; Ureteral Obstruction; Urinary Catheterization; Urinary Tract Infections | 2010 |
High-performance liquid chromatographic method to quantify total cysteine excretion in urine.
Topics: Adolescent; Adult; Aged; Amino Acids, Diamino; Borohydrides; Calibration; Case-Control Studies; Chromatography, High Pressure Liquid; Cystamine; Cysteine; Cystinuria; Disulfides; Female; Fluorescent Dyes; Fluorobenzenes; Humans; Male; Middle Aged; o-Phthalaldehyde; Oxidation-Reduction; Reference Standards; Sensitivity and Specificity; Sulfhydryl Reagents | 2002 |
The disulfide of L-cysteine and L-homocysteine in urine of patients with cystinuria.
Topics: Body Fluids; Cysteine; Cystinuria; Disulfides; Humans | 1961 |
[On cystinuria and cysteine calculi].
Topics: Calculi; Cysteine; Cystinuria; Humans | 1961 |
PENICILLAMINE AND MIXED DISULPHIDE EXCRETION IN WILSON'S DISEASE.
Topics: Cysteine; Cystinuria; Disulfides; Hepatolenticular Degeneration; Humans; Penicillamine; Sulfides | 1963 |
CYSTINURIA: METABOLISM OF THE DISULFIDE OF CYSTEINE AND HOMOCYSTEINE.
Topics: Amino Acids; Chromatography; Cysteine; Cystinuria; Disulfides; Dogs; Hepatolenticular Degeneration; Homocysteine; Ion Exchange Resins; Kidney Diseases; Metabolic Diseases; Methionine; Proteins; Rats; Sulfonic Acids; Sulfur Isotopes | 1963 |
CYSTINURIA: EFFECT OF D-PENICILLAMINE ON PLASMA AND URINARY CYSTINE CONCENTRATIONS.
Topics: Arginine; Blood; Cysteine; Cystine; Cystinuria; Drug Therapy; Humans; Lysine; Penicillamine; Sulfides; Urine | 1965 |
EFFECT OF PENICILLAMINE ON CYSTINURIA.
Topics: Arginine; Body Fluids; Cysteine; Cystinuria; Drug Therapy; Homocysteine; Humans; Lysine; Ornithine; Penicillamine; Urine | 1965 |
METHODS OF DIMINISHING CYSTINE EXCRETION IN CYSTINURIA.
Topics: Acetylcysteine; Amino Acids; Cysteine; Cystine; Cystinuria; Diet; Diet Therapy; Drug Therapy; Fluids and Secretions; Indoles; Oxandrolone; Penicillamine; Rats; Sulfur; Vitamin B 6 Deficiency | 1965 |
[Cysteine calculi in the kidney pelvis].
Topics: Cysteine; Cystinuria; Humans; Kidney Pelvis; Urinary Calculi | 1962 |
Effect of cystine-binding thiol drugs on urinary cystine capacity in patients with cystinuria.
Topics: Administration, Oral; Adult; Captopril; Case-Control Studies; Cysteine; Cystinuria; Dose-Response Relationship, Drug; Drug Administration Schedule; Female; Follow-Up Studies; Humans; Male; Middle Aged; Penicillamine; Probability; Prospective Studies; Reference Values; Risk Assessment; Tiopronin; Treatment Outcome; Urinalysis | 2005 |
Giant cystine stone in an infant bladder with no evidence of cystinuria--valence of possible pathomechanisms.
Topics: Child, Preschool; Cysteine; Cystinuria; Diagnosis, Differential; Female; Humans; Magnetic Resonance Imaging; Risk Factors; Urinary Bladder Calculi | 2005 |
Search for mutations in SLC1A5 (19q13) in cystinuria patients.
Topics: Adolescent; Amino Acid Transport System ASC; Chromosomes, Human, Pair 19; Cysteine; Cystinuria; Family Health; Gene Expression Regulation; Genetic Linkage; Humans; Infant; Minor Histocompatibility Antigens; Mutation; Polymerase Chain Reaction | 2005 |
Intestinal transport of cystine and cysteine in man: evidence for separate mechanisms.
Topics: Arginine; Biological Transport; Cysteine; Cystine; Cystinuria; Humans; Intestinal Mucosa; Jejunum; Lysine; Radioisotopes; Statistics as Topic | 1967 |
Excretion of trace elements in two penicillamine-treated cases of cystinuria.
Topics: Activation Analysis; Adult; Amino Acids; Calcium; Chromatography, Paper; Cysteine; Cystinuria; Female; Humans; Male; Middle Aged; Penicillamine; Phosphorus; Potassium; Sodium; Trace Elements | 1967 |
Quantitative determination of thiols and disulphides in urine by means of Ellman's reagent and thiolated Sephadex and its application in cystinuria.
Topics: Ammonium Chloride; Cysteine; Cystinuria; Dextrans; Humans; Indicators and Reagents; Sulfhydryl Compounds; Sulfides; Urinary Catheterization | 1967 |
Effect of gastrointestinal surgery and bacterial overgrowth on the urinary excretion of sulfur amino acids and their main degradation products.
Topics: Adult; Aged; Amino Acids, Sulfur; Cysteine; Cystinuria; Digestive System; Digestive System Surgical Procedures; Female; Humans; Ileum; Intestinal Absorption; Intestines; Jejunum; Male; Methionine; Middle Aged; Stomach | 1984 |
Studies on the metabolism of D-penicillamine and its interaction with probenecid in cystinuria and rheumatoid arthritis.
Topics: Arthritis, Rheumatoid; Cysteine; Cystinuria; Drug Therapy, Combination; Female; Humans; Male; Penicillamine; Pilot Projects; Probenecid; Time Factors | 1984 |
[Cystinuria therapy by ascorbic acid (author's transl)].
Topics: Ascorbic Acid; Cysteine; Cystine; Cystinuria; Humans; Intestinal Absorption; Kidney; Penicillamine; Tiopronin | 1982 |
Cystinuria subtype and the risk of nephrolithiasis.
Topics: Adolescent; Adult; Amino Acid Transport Systems, Basic; Carrier Proteins; Child; Child, Preschool; Cohort Studies; Creatinine; Cysteine; Cystinuria; Humans; Kidney Calculi; Kidney Tubules, Proximal; Membrane Glycoproteins; Mutation; Phenotype; Risk Factors; Solubility | 1998 |
Usefulness of cyanide-nitroprusside test in detecting incomplete recessive heterozygotes for cystinuria: a standardized dilution procedure.
Topics: Adolescent; Child; Child, Preschool; Cyanides; Cysteine; Cystinuria; False Negative Reactions; False Positive Reactions; Genetic Carrier Screening; Genetic Testing; Humans; Indicator Dilution Techniques; Indicators and Reagents; Nitroprusside; Reproducibility of Results; Sensitivity and Specificity | 1998 |
Simultaneous determination of cysteine, cystine and 18 other amino acids in various matrices by high-performance liquid chromatography.
Topics: Amino Acids; Chromatography, High Pressure Liquid; Cysteine; Cystine; Cystinuria; Humans; Reproducibility of Results; Sensitivity and Specificity; Spectrophotometry, Ultraviolet; Thyroid Gland; Vegetables | 1999 |
A modified cyanide-nitroprusside method for quantifying urinary cystine concentration that corrects for creatinine interference.
Topics: Adult; Artifacts; Ascorbic Acid; Captopril; Chlorides; Colorimetry; Creatinine; Cyanides; Cysteine; Cystinuria; Dose-Response Relationship, Drug; Female; Ferrous Compounds; Humans; Male; Middle Aged; Nitroprusside; Penicillamine; Reference Values; Reproducibility of Results; Serum Albumin; Tiopronin; Zinc Compounds | 1999 |
Identification of two novel mutations [P122S (364C>T) and 1601delAC] in the SLC3A1 gene in type I cystinurics.
Topics: Amino Acid Substitution; Amino Acid Transport Systems, Basic; Asparagine; Carrier Proteins; Cysteine; Cystinuria; Female; Genes, Recessive; Homozygote; Humans; Male; Membrane Glycoproteins; Mutation, Missense; Point Mutation; Sequence Deletion; Threonine; Valine | 2000 |
Experimental cystinuria: the cycloleucine model. II. Amino acid efflux from intestinal and renal tissues.
Topics: Amino Acids; Animals; Biological Transport; Cycloleucine; Cysteine; Cystine; Cystinuria; Female; In Vitro Techniques; Intestinal Mucosa; Lysine; Microvilli; Models, Biological; Rats; Valine | 1978 |
Homocysteine and cysteine loads in patients with homocystinuria due to cystathionine synthase deficiency: effects of vitamin B-6.
Topics: Cystathionine beta-Synthase; Cysteine; Cystine; Cystinuria; Disulfides; Female; Homocysteine; Homocystine; Homocystinuria; Humans; Hydro-Lyases; Male; Pyridoxine; Time Factors | 1977 |
[Some indices of nitrogen metabolism in patients with viral hepatitis].
Topics: Adolescent; Adult; Alanine; Ammonia; Asparagine; Chronic Disease; Cysteine; Cystinuria; Glutamates; Glycine; Hepatitis A; Humans; Isoleucine; Leucine; Methionine; Middle Aged; Nitrogen; Phenylalanine; Serine; Threonine; Urea; Valine | 1975 |
Spectrofluorimetric flow injection method for the individual and successive determination of L-cysteine and L-cystine in pharmaceutical and urine samples.
Topics: Cysteine; Cystinuria; Flow Injection Analysis; Humans; Indicators and Reagents; Spectrometry, Fluorescence | 1992 |
Balanced translocation (14;20) in a mentally handicapped child with cystinuria.
Topics: Child, Preschool; Chromosomes, Human, Pair 14; Chromosomes, Human, Pair 20; Cysteine; Cystinuria; Female; Heterozygote; Humans; Intellectual Disability; Translocation, Genetic; White People | 1992 |
High-dose intravenous glutathione in man. Pharmacokinetics and effects on cyst(e)ine in plasma and urine.
Topics: Adult; Cisplatin; Cysteine; Cystine; Cystinuria; Female; Glutathione; Humans; Infusions, Intravenous; Male; Middle Aged; Urinary Tract | 1991 |
High-performance liquid chromatographic determination of urinary cysteine and cystine.
Topics: Chromatography, High Pressure Liquid; Cysteine; Cystinuria; Dithiothreitol; Humans; Indicators and Reagents; o-Phthalaldehyde; Oxidation-Reduction; Spectrometry, Fluorescence | 1991 |
Spectrophotometric determination of cysteine and cystine in urine.
Topics: Cysteine; Cystinuria; Humans; Spectrophotometry, Ultraviolet | 1990 |
Sulfur amino acid metabolism in cystinuria: a biochemical and clinical study of patients.
Topics: Acetylcysteine; Adult; Amino Acids, Sulfur; Cysteine; Cystinuria; Female; Homozygote; Humans; Male; Penicillamine; Tiopronin | 1990 |
Determination and metabolism of dithiol chelating agents. VI. Isolation and identification of the mixed disulfides of meso-2,3-dimercaptosuccinic acid with L-cysteine in human urine.
Topics: Adult; Biotransformation; Chromatography, High Pressure Liquid; Chromatography, Thin Layer; Copper; Cysteine; Cystinuria; Disulfides; Humans; Lead; Male; Species Specificity; Succimer; Sulfhydryl Compounds; Zinc | 1989 |
Semi-automatic catalytic titration method for the analysis of cystine-cysteine mixtures and its application to urine samples.
Topics: Catalysis; Cysteine; Cystine; Cystinuria; Humans | 1988 |
[A semiquantitative rapid test for cysteine: possible use for monitoring the ascorbic acid therapy in cystinuria and cystine lithiasis].
Topics: Ascorbic Acid; Cysteine; Cystinuria; Humans; Monitoring, Physiologic; Urinary Calculi | 1988 |
Measurement of urinary cystine and cysteinyl-penicillamine in patients with cystinuria.
Topics: Amino Acids; Chromatography, Gas; Chromatography, High Pressure Liquid; Cysteine; Cystinuria; Electrochemistry; Humans; Penicillamine; Sulfhydryl Compounds | 1986 |
[Simple rapid test with carbonate/nitroprusside for the semiquantitative determination of cysteine in the urine--possible use for control of ascorbic acid therapy in cystine urolithiasis].
Topics: Ascorbic Acid; Carbonates; Cysteine; Cystinuria; Ferricyanides; Humans; Nitroprusside; Potassium; Urinary Calculi | 1987 |
[Satisfactory prophylaxis of urinary lithiasis with D-penicillamine in cystinuria].
Topics: Adult; Cysteine; Cystine; Cystinuria; Diet Therapy; Female; Humans; Penicillamine; Urinary Calculi | 1970 |
Intestinal absorption of cystine and cysteine in normal human subjects and patients with cystinuria.
Topics: Adult; Biological Transport; Carbon Radioisotopes; Cysteine; Cystine; Cystinuria; Humans; Intestinal Absorption; Perfusion; Polyethylene Glycols | 1974 |
The tubular reabsorption of L-cystine and L-cysteine. A common transport system with L-arginine or not?
Topics: Absorption; Animals; Arginine; Biological Transport, Active; Carbon Isotopes; Cysteine; Cystine; Cystinuria; Glycine; Guanidines; Inulin; Kidney Tubules; Kidney Tubules, Proximal; Lysine; Male; Ornithine; Perfusion; Pimelic Acids; Rats; Tritium | 1972 |
Frequency of homocystinuria amongst the blind.
Topics: Adolescent; Adult; Aged; Blindness; Child, Preschool; Chromatography, Paper; Cysteine; Cystinuria; False Positive Reactions; Female; Homocystine; Homocystinuria; Humans; Male; Mexico; Middle Aged | 1973 |
Simple polarographic determination of cystine in urine with cystinuria.
Topics: Amino Acids; Blood Proteins; Cobalt; Cysteine; Cystinuria; Evaluation Studies as Topic; Homocysteine; Humans; Manganese; Methods; Nickel; Oxidation-Reduction; Penicillamine; Polarography; Polyethylene Glycols; Sulfites; Time Factors; Zinc | 1973 |
Penicillamine treatment of cystinuria.
Topics: Adult; Autoanalysis; Ceruloplasmin; Chromatography, Ion Exchange; Copper; Cysteine; Cystinuria; Depression, Chemical; Female; Follow-Up Studies; Humans; Male; Middle Aged; Penicillamine; Time Factors; Zinc | 1974 |
[Modification of aminoaciduria in the rat after administration of cycloleucine: comparison with human cystinuria].
Topics: Amino Acids; Animals; Antineoplastic Agents; Arginine; Chromatography, Ion Exchange; Chromatography, Paper; Cyclopentanes; Cysteine; Cystine; Cystinuria; Diet; Disulfides; Diuresis; Electrophoresis; Homocysteine; Injections, Intraperitoneal; Lysine; Male; Metabolism; Ornithine; Paper; Rats; Time Factors | 1971 |
Treatment of cystinosis with a diet poor in cystine and methionine.
Topics: Amino Acids; Body Height; Body Weight; Child; Child, Preschool; Cysteine; Cystine; Cystinosis; Cystinuria; Diet Therapy; Dwarfism; Ergocalciferols; Female; Humans; Ketoglutaric Acids; Male; Methionine; Pedigree; Penicillamine; Pyruvates; Renal Tubular Transport, Inborn Errors | 1970 |
Amino acid excretion patterns in the offspring of a 'doubly-heterozygous' cystine stone former.
Topics: Alleles; Amino Acid Metabolism, Inborn Errors; Amino Acids; Arginine; Child; Child, Preschool; Chromatography, Paper; Cysteine; Cystinosis; Cystinuria; Female; Ferrocyanides; Heterozygote; Homocysteine; Humans; Lysine; Molecular Biology; Ornithine | 1970 |
pH dependency of the cyanide-nitroprusside colour reaction of cystine.
Topics: Acetone; Cyanides; Cysteine; Cystine; Cystinuria; Ferricyanides; Humans; Hydrogen-Ion Concentration | 1970 |
Cystinosis. Plasma cystine and cysteine concentrations and the effect of D-penicillamine and dietary treatment.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Blood Chemical Analysis; Cysteine; Cystine; Cystinosis; Cystinuria; Diet Therapy; Female; Humans; Infant; Male; Methionine; Nitrogen; Penicillamine; Pyruvates | 1968 |
[New attempts at the reduction of cystinuria].
Topics: Amides; Animals; Chromatography; Cysteine; Cystinuria; Dogs; Electrophoresis; Glycine; Humans; Penicillamine; Propionates; Rats | 1968 |
Treatment of cystinuria with alpha-mercaptopropionylglycine: a preliminary report with some notes on column chromatography of mercaptans.
Topics: Amino Acids; Chromatography; Cysteine; Cystinuria; Humans; Taurine | 1968 |
Cystine metabolism in cystinuria.
Topics: Adult; Blood Chemical Analysis; Cysteine; Cystine; Cystinuria; Dietary Proteins; Humans; Middle Aged; Neomycin; Sulfates; Urine | 1965 |
A highly specific new method for the determination of cystine and cysteine and its application to urine.
Topics: Cysteine; Cystine; Cystinuria; Humans; In Vitro Techniques; Quinones; Spectrophotometry; Urine | 1965 |
Intestinal absorption and renal extraction of cystine and cysteine in cystinuria.
Topics: Biological Transport; Blood Chemical Analysis; Chromatography; Cysteine; Cystinuria; Humans; Intestinal Absorption; Kidney | 1965 |
Cysteine metabolism in cystinuria.
Topics: Blood; Cysteine; Cystine; Cystinuria; Female; Humans; Intestinal Absorption; Intestine, Small; Kidney Tubules; Male; Urine | 1965 |
Sulphocysteine in the urine of the blotched Kenya genet.
Topics: Animals; Carnivora; Cysteine; Cystinuria; Sulfhydryl Compounds | 1965 |
Separation of cystine, penicillamine disulfide and cysteine-penicillamine mixed disulfide by automatic amino acid analysis.
Topics: Autoanalysis; Blood Chemical Analysis; Chemistry, Clinical; Chromatography, Ion Exchange; Cysteine; Cystine; Cystinuria; Humans; In Vitro Techniques; Penicillamine; Sulfides; Urine | 1966 |
Cystinuria: intravenous administration of [35S]cystine and [35S]cysteine.
Topics: Chromatography, Ion Exchange; Cysteine; Cystine; Cystinuria; Humans; Sulfur Isotopes | 1966 |
Dithiothreitol in the study of cysteine transport.
Topics: Alcohols; Animals; Arginine; Biological Transport; Cysteine; Cystine; Cystinuria; Humans; In Vitro Techniques; Kidney; Lysine; Ornithine; Rats; Sulfhydryl Compounds | 1966 |