cysteine and Cystinuria

cysteine has been researched along with Cystinuria in 72 studies

Research

Studies (72)

TimeframeStudies, this research(%)All Research%
pre-199046 (63.89)18.7374
1990's11 (15.28)18.2507
2000's6 (8.33)29.6817
2010's3 (4.17)24.3611
2020's6 (8.33)2.80

Authors

AuthorsStudies
Bazin, D; Belletti, G; Colombo, E; Daudon, M; Frochot, V; Hessou, EP; Li, K; Lucas, IT; Moussadik, A; Quaino, P; Rouzière, S; Su, Y; Tielens, F1
Goldfarb, DS; Latyshev, S; Mikel, CC; Ponte, A; Steigelman, K1
Bar-Yosef, DL; Chakraborty, P; Do, TD; Gazit, E; Limbach, MN; Oluwatoba, DS1
Dai, Y; He, F; Ji, H; Qi, Z; Xue, T; Zheng, Y1
Beckermann, TM; Ikizler, TA; Mortlock, DP; Sha, F; Welch, RC; Williams, FM; Wilson, MH; Woodard, LE1
Birwé, H; Bitterlich, N; Hesse, A; Siener, R1
Alfonso, I; Lafuente, M; Solà, J1
Bellomo, F; Bertucci, P; Boenzi, S; Dello Strologo, L; Dionisi-Vici, C; Emma, F; Laurenzi, C; Masotti, A; Muraca, M; Pastore, A; Taranta, A1
Marickar, YM1
CLELAND, JB1
Cara Fuentes, GM; Espinosa Roman, L; Melgosa Hijosa, M; Navarro Torres, M1
Arcelloni, C; Fermo, I; Paroni, R1
FRIMPTER, GW3
VASIL'EV, LI1
HARTLEY, BS; WALSHE, JM1
CRAWHALL, JC; THOMPSON, CJ1
BOYCE, WH; KING, JS1
COLLINI, WR; HARRIS, RC; MATTERN, SR; SHAPIRO, P; ZINSSER, HH1
DOCTOR, F; MERENYI, I1
Asplin, JR; Dolin, DJ; Flagel, L; Goldfarb, DS; Grasso, M1
Bartsch, G; Lunacek, A; Oswald, J; Radmayr, C; Schwentner, C1
Brauers, E; Eggermann, T; Vester, U; Zerres, K1
Crawhall, JC; Rosenberg, LE; Segal, S1
Boström, H; Wester, PO1
Rootwelt, K1
Mårtensson, J; Sjödahl, R; Tobiasson, P1
Johnson, S; Kaung, C; Roboz, J; Yu, TF1
Asper, R; Schmucki, O1
Elkas, G; Goodyer, P; Ong, P; Rozen, R; Saadi, I1
Celli, M; D'Eufemia, P; Finocchiaro, R; Giardini, O; Mannarino, O; Troiani, P; Viozzi, L; Zaccagnini, M1
Avino, P; Campanella, L; Crescentini, G1
Coe, FL; Nakagawa, Y1
Gitomer, WL; Pak, CY; Reed, BY1
Bergeron, M; Craan, AG1
Gaull, GE; Longhi, RC; Rassin, DK; Sternowsky, HJ; Sturman, JA1
Gundalakh, AI; Mel'k, MV; Shcheglova, SA; Volkova, ZA1
Carpena, J; Martínez-Lozano, C; Pérez-Ruiz, T; Tomás, V1
Bain, M; Chalmers, R; Hammond, J; Jones, M; Patton, MA; Sharland, M1
Birwé, H; Hesse, A; Schneeberger, W1
Aebi, S; Assereto, R; Lauterburg, BH1
Birwé, H; Hesse, A1
Chrastil, J1
Denneberg, T; Lindell, A; Mårtensson, J; Textorius, O1
Aposhian, HV; Bruce, DC; Maiorino, RM1
Marquez, M; Perez-Bendito, D; Silva, M1
Berg, W; Kilian, O1
Hammond, JW; Sampson, DC; Stewart, PM1
Berg, W; Brundig, P; Kilian, O1
Mauermayer, W; Wenzl, H1
Clark, ML; Perrett, D; Scowen, EF; Silk, DB; Stephens, AD1
Deetjen, P; Silbernagl, S1
Chavez, Y; Cobo, A; Lisker, R; Zavala, C1
Kuzel, K1
Denneberg, T; Ekberg, M; Jeppsson, JO1
Chatagner, F1
Charpentier, C; Lemonnier, A; Levillain, P; Moatti, N1
Christensen, MF; Henriksen, O; Nielsen, JA1
Copeland, W; Kelly, S; Leikhim, E1
Georges, RJ; Politzer, WM1
Stephens, AD; Watts, RW1
Crawhall, JC; Lietman, PS; Schneider, JA; Seegmiller, JE1
Aboulker, P; Balan, A; Charpentier, C; Leluc, R; Lemonnier, A; Levillain, L; Thomas, J; Thuong, CT1
King, JS1
Foley, TH; London, DR2
Fernandez, AA; Henry, RJ1
Durant, JL; Holland, JM; Rosenberg, LE1
Crawhall, JC; Segal, S2
Bradley, KH; Crawhall, JC; Thompson, CJ1

Reviews

1 review(s) available for cysteine and Cystinuria

ArticleYear
[Biochemical aspects of some congenital anomalies of the metabolism of sulfur amino acids].
    Exposes annuels de biochimie medicale, 1967, Volume: 28

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Animals; Cysteine; Cystinuria; Homocysteine; Homocystinuria; Humans; Hydro-Lyases; L-Serine Dehydratase; Methionine; Rats

1967

Trials

3 trial(s) available for cysteine and Cystinuria

ArticleYear
The Impact of Diet on Urinary Risk Factors for Cystine Stone Formation.
    Nutrients, 2021, Feb-06, Volume: 13, Issue:2

    Topics: Adult; Cysteine; Cystine; Cystinuria; Diet; Diet, Vegetarian; Diet, Western; Healthy Volunteers; Humans; Hydrogen-Ion Concentration; Male; Phosphates; Regression Analysis; Risk Factors; Sulfates; Urine; Urolithiasis; Young Adult

2021
Investigations of the efficacy of ascorbic acid therapy in cystinuria.
    Urological research, 1991, Volume: 19, Issue:3

    Topics: Ascorbic Acid; Chromatography, High Pressure Liquid; Cysteine; Cystinuria; Humans; Oxalates; Oxalic Acid

1991
The treatment of cystinuria with N-acetyl-D-penicillamine, a comparison with the results of D-penicillamine treatment.
    The Quarterly journal of medicine, 1971, Volume: 40, Issue:159

    Topics: Acylation; Adolescent; Adult; Child; Cysteine; Cystinuria; Desensitization, Immunologic; Drug Hypersensitivity; Edema; Female; Humans; Hypoproteinemia; Kidney Diseases; Male; Penicillamine; Prednisolone; Proteinuria; Serum Albumin; Urea; Urinary Calculi

1971

Other Studies

68 other study(ies) available for cysteine and Cystinuria

ArticleYear
Crystalline structures of L-cysteine and L-cystine: a combined theoretical and experimental characterization.
    Amino acids, 2022, Volume: 54, Issue:8

    Topics: Cysteine; Cystine; Cystinosis; Cystinuria; Disulfides; Humans

2022
Accurate 24-h urine cystine quantification for patients on cystine-binding thiol drugs.
    Urolithiasis, 2022, Volume: 50, Issue:6

    Topics: Cysteine; Cystine; Cystinuria; Humans; Quality of Life; Sulfhydryl Compounds; Tandem Mass Spectrometry; Tiopronin

2022
Self-Assembly of Cysteine into Nanofibrils Precedes Cystine Crystal Formation: Implications for Aggregation Inhibition.
    ACS applied materials & interfaces, 2023, Jul-12, Volume: 15, Issue:27

    Topics: Amino Acids; Amyloid; Cysteine; Cystine; Cystinuria; Disulfides; Humans

2023
A novel fluorescent probe for rapidly detection cysteine in cystinuria urine, living cancer/normal cells and BALB/c nude mice.
    Spectrochimica acta. Part A, Molecular and biomolecular spectroscopy, 2020, Jan-15, Volume: 225

    Topics: Animals; Cell Line; Colorimetry; Cysteine; Cystinuria; Fluorescent Dyes; Hep G2 Cells; Hepatocytes; Humans; Mice; Mice, Inbred BALB C; Mice, Nude; Molecular Structure; Spectrometry, Fluorescence; Spectrophotometry; Spectrophotometry, Ultraviolet

2020
CRISPR/Cas9 engineering of albino cystinuria Type A mice.
    Genesis (New York, N.Y. : 2000), 2020, Volume: 58, Issue:5

    Topics: Amino Acid Transport Systems, Basic; Amino Acid Transport Systems, Neutral; Animals; CRISPR-Cas Systems; Cysteine; Cystinuria; Disease Models, Animal; Mice; Mice, Inbred C57BL; Mutation

2020
A Dynamic Chemical Network for Cystinuria Diagnosis.
    Angewandte Chemie (International ed. in English), 2018, 07-09, Volume: 57, Issue:28

    Topics: Cysteine; Cystine; Cystinuria; Humans; Molecular Dynamics Simulation; Molecular Structure; Spectrometry, Fluorescence

2018
Gender-related effects on urine L-cystine metastability.
    Amino acids, 2014, Volume: 46, Issue:2

    Topics: Adenosine; Adult; Chemical Precipitation; Cysteine; Cystinuria; Female; Guanosine; Humans; Inosine; Male; Middle Aged; Sex Characteristics; Solubility; Vanilmandelic Acid

2014
Cystinuria: the South Indian experience.
    Urological research, 2009, Volume: 37, Issue:6

    Topics: Cysteine; Cystinuria; Humans; Incidence; India; Retrospective Studies; Spectroscopy, Fourier Transform Infrared; Urinary Calculi

2009
Cystine, methionine and sulphate excretion in cystinuria.
    The Australian journal of experimental biology and medical science, 1946, Volume: 24, Issue:3

    Topics: Biochemical Phenomena; Body Fluids; Cysteine; Cystine; Cystinuria; Humans; Methionine; Sulfates; Sulfur; Sulfur Oxides; Urine

1946
Acute renal failure due to bilateral pieloureteral stone impaction in a 10-month-old boy.
    Clinical and experimental nephrology, 2010, Volume: 14, Issue:4

    Topics: Acute Kidney Injury; Cysteine; Cystinuria; Fluid Therapy; Humans; Infant; Isotonic Solutions; Male; Potassium Citrate; Sodium Chloride; Treatment Outcome; Ureteral Calculi; Ureteral Obstruction; Urinary Catheterization; Urinary Tract Infections

2010
High-performance liquid chromatographic method to quantify total cysteine excretion in urine.
    Analytical biochemistry, 2002, Aug-01, Volume: 307, Issue:1

    Topics: Adolescent; Adult; Aged; Amino Acids, Diamino; Borohydrides; Calibration; Case-Control Studies; Chromatography, High Pressure Liquid; Cystamine; Cysteine; Cystinuria; Disulfides; Female; Fluorescent Dyes; Fluorobenzenes; Humans; Male; Middle Aged; o-Phthalaldehyde; Oxidation-Reduction; Reference Standards; Sensitivity and Specificity; Sulfhydryl Reagents

2002
The disulfide of L-cysteine and L-homocysteine in urine of patients with cystinuria.
    The Journal of biological chemistry, 1961, Volume: 236

    Topics: Body Fluids; Cysteine; Cystinuria; Disulfides; Humans

1961
[On cystinuria and cysteine calculi].
    Terapevticheskii arkhiv, 1961, Volume: 33

    Topics: Calculi; Cysteine; Cystinuria; Humans

1961
PENICILLAMINE AND MIXED DISULPHIDE EXCRETION IN WILSON'S DISEASE.
    Lancet (London, England), 1963, Aug-31, Volume: 2, Issue:7305

    Topics: Cysteine; Cystinuria; Disulfides; Hepatolenticular Degeneration; Humans; Penicillamine; Sulfides

1963
CYSTINURIA: METABOLISM OF THE DISULFIDE OF CYSTEINE AND HOMOCYSTEINE.
    The Journal of clinical investigation, 1963, Volume: 42

    Topics: Amino Acids; Chromatography; Cysteine; Cystinuria; Disulfides; Dogs; Hepatolenticular Degeneration; Homocysteine; Ion Exchange Resins; Kidney Diseases; Metabolic Diseases; Methionine; Proteins; Rats; Sulfonic Acids; Sulfur Isotopes

1963
CYSTINURIA: EFFECT OF D-PENICILLAMINE ON PLASMA AND URINARY CYSTINE CONCENTRATIONS.
    Science (New York, N.Y.), 1965, Mar-19, Volume: 147, Issue:3664

    Topics: Arginine; Blood; Cysteine; Cystine; Cystinuria; Drug Therapy; Humans; Lysine; Penicillamine; Sulfides; Urine

1965
EFFECT OF PENICILLAMINE ON CYSTINURIA.
    Investigative urology, 1965, Volume: 2

    Topics: Arginine; Body Fluids; Cysteine; Cystinuria; Drug Therapy; Homocysteine; Humans; Lysine; Ornithine; Penicillamine; Urine

1965
METHODS OF DIMINISHING CYSTINE EXCRETION IN CYSTINURIA.
    The Journal of urology, 1965, Volume: 93

    Topics: Acetylcysteine; Amino Acids; Cysteine; Cystine; Cystinuria; Diet; Diet Therapy; Drug Therapy; Fluids and Secretions; Indoles; Oxandrolone; Penicillamine; Rats; Sulfur; Vitamin B 6 Deficiency

1965
[Cysteine calculi in the kidney pelvis].
    Magyar sebeszet, 1962, Volume: 15

    Topics: Cysteine; Cystinuria; Humans; Kidney Pelvis; Urinary Calculi

1962
Effect of cystine-binding thiol drugs on urinary cystine capacity in patients with cystinuria.
    Journal of endourology, 2005, Volume: 19, Issue:3

    Topics: Administration, Oral; Adult; Captopril; Case-Control Studies; Cysteine; Cystinuria; Dose-Response Relationship, Drug; Drug Administration Schedule; Female; Follow-Up Studies; Humans; Male; Middle Aged; Penicillamine; Probability; Prospective Studies; Reference Values; Risk Assessment; Tiopronin; Treatment Outcome; Urinalysis

2005
Giant cystine stone in an infant bladder with no evidence of cystinuria--valence of possible pathomechanisms.
    Urologia internationalis, 2005, Volume: 75, Issue:3

    Topics: Child, Preschool; Cysteine; Cystinuria; Diagnosis, Differential; Female; Humans; Magnetic Resonance Imaging; Risk Factors; Urinary Bladder Calculi

2005
Search for mutations in SLC1A5 (19q13) in cystinuria patients.
    Journal of inherited metabolic disease, 2005, Volume: 28, Issue:6

    Topics: Adolescent; Amino Acid Transport System ASC; Chromosomes, Human, Pair 19; Cysteine; Cystinuria; Family Health; Gene Expression Regulation; Genetic Linkage; Humans; Infant; Minor Histocompatibility Antigens; Mutation; Polymerase Chain Reaction

2005
Intestinal transport of cystine and cysteine in man: evidence for separate mechanisms.
    The Journal of clinical investigation, 1967, Volume: 46, Issue:1

    Topics: Arginine; Biological Transport; Cysteine; Cystine; Cystinuria; Humans; Intestinal Mucosa; Jejunum; Lysine; Radioisotopes; Statistics as Topic

1967
Excretion of trace elements in two penicillamine-treated cases of cystinuria.
    Acta medica Scandinavica, 1967, Volume: 181, Issue:4

    Topics: Activation Analysis; Adult; Amino Acids; Calcium; Chromatography, Paper; Cysteine; Cystinuria; Female; Humans; Male; Middle Aged; Penicillamine; Phosphorus; Potassium; Sodium; Trace Elements

1967
Quantitative determination of thiols and disulphides in urine by means of Ellman's reagent and thiolated Sephadex and its application in cystinuria.
    Scandinavian journal of clinical and laboratory investigation, 1967, Volume: 19, Issue:4

    Topics: Ammonium Chloride; Cysteine; Cystinuria; Dextrans; Humans; Indicators and Reagents; Sulfhydryl Compounds; Sulfides; Urinary Catheterization

1967
Effect of gastrointestinal surgery and bacterial overgrowth on the urinary excretion of sulfur amino acids and their main degradation products.
    Scandinavian journal of gastroenterology, 1984, Volume: 19, Issue:4

    Topics: Adult; Aged; Amino Acids, Sulfur; Cysteine; Cystinuria; Digestive System; Digestive System Surgical Procedures; Female; Humans; Ileum; Intestinal Absorption; Intestines; Jejunum; Male; Methionine; Middle Aged; Stomach

1984
Studies on the metabolism of D-penicillamine and its interaction with probenecid in cystinuria and rheumatoid arthritis.
    The Journal of rheumatology, 1984, Volume: 11, Issue:4

    Topics: Arthritis, Rheumatoid; Cysteine; Cystinuria; Drug Therapy, Combination; Female; Humans; Male; Penicillamine; Pilot Projects; Probenecid; Time Factors

1984
[Cystinuria therapy by ascorbic acid (author's transl)].
    Urologia internationalis, 1982, Volume: 37, Issue:2

    Topics: Ascorbic Acid; Cysteine; Cystine; Cystinuria; Humans; Intestinal Absorption; Kidney; Penicillamine; Tiopronin

1982
Cystinuria subtype and the risk of nephrolithiasis.
    Kidney international, 1998, Volume: 54, Issue:1

    Topics: Adolescent; Adult; Amino Acid Transport Systems, Basic; Carrier Proteins; Child; Child, Preschool; Cohort Studies; Creatinine; Cysteine; Cystinuria; Humans; Kidney Calculi; Kidney Tubules, Proximal; Membrane Glycoproteins; Mutation; Phenotype; Risk Factors; Solubility

1998
Usefulness of cyanide-nitroprusside test in detecting incomplete recessive heterozygotes for cystinuria: a standardized dilution procedure.
    Urological research, 1998, Volume: 26, Issue:6

    Topics: Adolescent; Child; Child, Preschool; Cyanides; Cysteine; Cystinuria; False Negative Reactions; False Positive Reactions; Genetic Carrier Screening; Genetic Testing; Humans; Indicator Dilution Techniques; Indicators and Reagents; Nitroprusside; Reproducibility of Results; Sensitivity and Specificity

1998
Simultaneous determination of cysteine, cystine and 18 other amino acids in various matrices by high-performance liquid chromatography.
    Journal of chromatography. A, 1999, Feb-19, Volume: 833, Issue:2

    Topics: Amino Acids; Chromatography, High Pressure Liquid; Cysteine; Cystine; Cystinuria; Humans; Reproducibility of Results; Sensitivity and Specificity; Spectrophotometry, Ultraviolet; Thyroid Gland; Vegetables

1999
A modified cyanide-nitroprusside method for quantifying urinary cystine concentration that corrects for creatinine interference.
    Clinica chimica acta; international journal of clinical chemistry, 1999, Volume: 289, Issue:1-2

    Topics: Adult; Artifacts; Ascorbic Acid; Captopril; Chlorides; Colorimetry; Creatinine; Cyanides; Cysteine; Cystinuria; Dose-Response Relationship, Drug; Female; Ferrous Compounds; Humans; Male; Middle Aged; Nitroprusside; Penicillamine; Reference Values; Reproducibility of Results; Serum Albumin; Tiopronin; Zinc Compounds

1999
Identification of two novel mutations [P122S (364C>T) and 1601delAC] in the SLC3A1 gene in type I cystinurics.
    Human mutation, 2000, Volume: 15, Issue:4

    Topics: Amino Acid Substitution; Amino Acid Transport Systems, Basic; Asparagine; Carrier Proteins; Cysteine; Cystinuria; Female; Genes, Recessive; Homozygote; Humans; Male; Membrane Glycoproteins; Mutation, Missense; Point Mutation; Sequence Deletion; Threonine; Valine

2000
Experimental cystinuria: the cycloleucine model. II. Amino acid efflux from intestinal and renal tissues.
    Metabolism: clinical and experimental, 1978, Volume: 27, Issue:11

    Topics: Amino Acids; Animals; Biological Transport; Cycloleucine; Cysteine; Cystine; Cystinuria; Female; In Vitro Techniques; Intestinal Mucosa; Lysine; Microvilli; Models, Biological; Rats; Valine

1978
Homocysteine and cysteine loads in patients with homocystinuria due to cystathionine synthase deficiency: effects of vitamin B-6.
    Clinica chimica acta; international journal of clinical chemistry, 1977, Aug-15, Volume: 79, Issue:1

    Topics: Cystathionine beta-Synthase; Cysteine; Cystine; Cystinuria; Disulfides; Female; Homocysteine; Homocystine; Homocystinuria; Humans; Hydro-Lyases; Male; Pyridoxine; Time Factors

1977
[Some indices of nitrogen metabolism in patients with viral hepatitis].
    Terapevticheskii arkhiv, 1975, Volume: 47, Issue:8

    Topics: Adolescent; Adult; Alanine; Ammonia; Asparagine; Chronic Disease; Cysteine; Cystinuria; Glutamates; Glycine; Hepatitis A; Humans; Isoleucine; Leucine; Methionine; Middle Aged; Nitrogen; Phenylalanine; Serine; Threonine; Urea; Valine

1975
Spectrofluorimetric flow injection method for the individual and successive determination of L-cysteine and L-cystine in pharmaceutical and urine samples.
    The Analyst, 1992, Volume: 117, Issue:6

    Topics: Cysteine; Cystinuria; Flow Injection Analysis; Humans; Indicators and Reagents; Spectrometry, Fluorescence

1992
Balanced translocation (14;20) in a mentally handicapped child with cystinuria.
    Journal of medical genetics, 1992, Volume: 29, Issue:7

    Topics: Child, Preschool; Chromosomes, Human, Pair 14; Chromosomes, Human, Pair 20; Cysteine; Cystinuria; Female; Heterozygote; Humans; Intellectual Disability; Translocation, Genetic; White People

1992
High-dose intravenous glutathione in man. Pharmacokinetics and effects on cyst(e)ine in plasma and urine.
    European journal of clinical investigation, 1991, Volume: 21, Issue:1

    Topics: Adult; Cisplatin; Cysteine; Cystine; Cystinuria; Female; Glutathione; Humans; Infusions, Intravenous; Male; Middle Aged; Urinary Tract

1991
High-performance liquid chromatographic determination of urinary cysteine and cystine.
    Clinica chimica acta; international journal of clinical chemistry, 1991, May-31, Volume: 199, Issue:1

    Topics: Chromatography, High Pressure Liquid; Cysteine; Cystinuria; Dithiothreitol; Humans; Indicators and Reagents; o-Phthalaldehyde; Oxidation-Reduction; Spectrometry, Fluorescence

1991
Spectrophotometric determination of cysteine and cystine in urine.
    The Analyst, 1990, Volume: 115, Issue:10

    Topics: Cysteine; Cystinuria; Humans; Spectrophotometry, Ultraviolet

1990
Sulfur amino acid metabolism in cystinuria: a biochemical and clinical study of patients.
    Kidney international, 1990, Volume: 37, Issue:1

    Topics: Acetylcysteine; Adult; Amino Acids, Sulfur; Cysteine; Cystinuria; Female; Homozygote; Humans; Male; Penicillamine; Tiopronin

1990
Determination and metabolism of dithiol chelating agents. VI. Isolation and identification of the mixed disulfides of meso-2,3-dimercaptosuccinic acid with L-cysteine in human urine.
    Toxicology and applied pharmacology, 1989, Volume: 97, Issue:2

    Topics: Adult; Biotransformation; Chromatography, High Pressure Liquid; Chromatography, Thin Layer; Copper; Cysteine; Cystinuria; Disulfides; Humans; Lead; Male; Species Specificity; Succimer; Sulfhydryl Compounds; Zinc

1989
Semi-automatic catalytic titration method for the analysis of cystine-cysteine mixtures and its application to urine samples.
    The Analyst, 1988, Volume: 113, Issue:9

    Topics: Catalysis; Cysteine; Cystine; Cystinuria; Humans

1988
[A semiquantitative rapid test for cysteine: possible use for monitoring the ascorbic acid therapy in cystinuria and cystine lithiasis].
    Journal of clinical chemistry and clinical biochemistry. Zeitschrift fur klinische Chemie und klinische Biochemie, 1988, Volume: 26, Issue:4

    Topics: Ascorbic Acid; Cysteine; Cystinuria; Humans; Monitoring, Physiologic; Urinary Calculi

1988
Measurement of urinary cystine and cysteinyl-penicillamine in patients with cystinuria.
    Biomedical chromatography : BMC, 1986, Volume: 1, Issue:1

    Topics: Amino Acids; Chromatography, Gas; Chromatography, High Pressure Liquid; Cysteine; Cystinuria; Electrochemistry; Humans; Penicillamine; Sulfhydryl Compounds

1986
[Simple rapid test with carbonate/nitroprusside for the semiquantitative determination of cysteine in the urine--possible use for control of ascorbic acid therapy in cystine urolithiasis].
    Urologia internationalis, 1987, Volume: 42, Issue:4

    Topics: Ascorbic Acid; Carbonates; Cysteine; Cystinuria; Ferricyanides; Humans; Nitroprusside; Potassium; Urinary Calculi

1987
[Satisfactory prophylaxis of urinary lithiasis with D-penicillamine in cystinuria].
    La semaine des hopitaux : organe fonde par l'Association d'enseignement medical des hopitaux de Paris, 1970, Apr-08, Volume: 46, Issue:17

    Topics: Adult; Cysteine; Cystine; Cystinuria; Diet Therapy; Female; Humans; Penicillamine; Urinary Calculi

1970
Intestinal absorption of cystine and cysteine in normal human subjects and patients with cystinuria.
    Clinical science and molecular medicine, 1974, Volume: 47, Issue:4

    Topics: Adult; Biological Transport; Carbon Radioisotopes; Cysteine; Cystine; Cystinuria; Humans; Intestinal Absorption; Perfusion; Polyethylene Glycols

1974
The tubular reabsorption of L-cystine and L-cysteine. A common transport system with L-arginine or not?
    Pflugers Archiv : European journal of physiology, 1972, Volume: 337, Issue:4

    Topics: Absorption; Animals; Arginine; Biological Transport, Active; Carbon Isotopes; Cysteine; Cystine; Cystinuria; Glycine; Guanidines; Inulin; Kidney Tubules; Kidney Tubules, Proximal; Lysine; Male; Ornithine; Perfusion; Pimelic Acids; Rats; Tritium

1972
Frequency of homocystinuria amongst the blind.
    Clinical genetics, 1973, Volume: 4, Issue:2

    Topics: Adolescent; Adult; Aged; Blindness; Child, Preschool; Chromatography, Paper; Cysteine; Cystinuria; False Positive Reactions; Female; Homocystine; Homocystinuria; Humans; Male; Mexico; Middle Aged

1973
Simple polarographic determination of cystine in urine with cystinuria.
    Clinica chimica acta; international journal of clinical chemistry, 1973, Nov-15, Volume: 48, Issue:4

    Topics: Amino Acids; Blood Proteins; Cobalt; Cysteine; Cystinuria; Evaluation Studies as Topic; Homocysteine; Humans; Manganese; Methods; Nickel; Oxidation-Reduction; Penicillamine; Polarography; Polyethylene Glycols; Sulfites; Time Factors; Zinc

1973
Penicillamine treatment of cystinuria.
    Acta medica Scandinavica, 1974, Volume: 195, Issue:5

    Topics: Adult; Autoanalysis; Ceruloplasmin; Chromatography, Ion Exchange; Copper; Cysteine; Cystinuria; Depression, Chemical; Female; Follow-Up Studies; Humans; Male; Middle Aged; Penicillamine; Time Factors; Zinc

1974
[Modification of aminoaciduria in the rat after administration of cycloleucine: comparison with human cystinuria].
    Clinica chimica acta; international journal of clinical chemistry, 1971, Volume: 33, Issue:2

    Topics: Amino Acids; Animals; Antineoplastic Agents; Arginine; Chromatography, Ion Exchange; Chromatography, Paper; Cyclopentanes; Cysteine; Cystine; Cystinuria; Diet; Disulfides; Diuresis; Electrophoresis; Homocysteine; Injections, Intraperitoneal; Lysine; Male; Metabolism; Ornithine; Paper; Rats; Time Factors

1971
Treatment of cystinosis with a diet poor in cystine and methionine.
    Acta paediatrica Scandinavica, 1970, Volume: 59, Issue:6

    Topics: Amino Acids; Body Height; Body Weight; Child; Child, Preschool; Cysteine; Cystine; Cystinosis; Cystinuria; Diet Therapy; Dwarfism; Ergocalciferols; Female; Humans; Ketoglutaric Acids; Male; Methionine; Pedigree; Penicillamine; Pyruvates; Renal Tubular Transport, Inborn Errors

1970
Amino acid excretion patterns in the offspring of a 'doubly-heterozygous' cystine stone former.
    Experientia, 1970, Dec-15, Volume: 26, Issue:12

    Topics: Alleles; Amino Acid Metabolism, Inborn Errors; Amino Acids; Arginine; Child; Child, Preschool; Chromatography, Paper; Cysteine; Cystinosis; Cystinuria; Female; Ferrocyanides; Heterozygote; Homocysteine; Humans; Lysine; Molecular Biology; Ornithine

1970
pH dependency of the cyanide-nitroprusside colour reaction of cystine.
    Clinica chimica acta; international journal of clinical chemistry, 1970, Volume: 30, Issue:3

    Topics: Acetone; Cyanides; Cysteine; Cystine; Cystinuria; Ferricyanides; Humans; Hydrogen-Ion Concentration

1970
Cystinosis. Plasma cystine and cysteine concentrations and the effect of D-penicillamine and dietary treatment.
    The American journal of medicine, 1968, Volume: 44, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Blood Chemical Analysis; Cysteine; Cystine; Cystinosis; Cystinuria; Diet Therapy; Female; Humans; Infant; Male; Methionine; Nitrogen; Penicillamine; Pyruvates

1968
[New attempts at the reduction of cystinuria].
    Journal d'urologie et de nephrologie, 1968, Volume: 74, Issue:12

    Topics: Amides; Animals; Chromatography; Cysteine; Cystinuria; Dogs; Electrophoresis; Glycine; Humans; Penicillamine; Propionates; Rats

1968
Treatment of cystinuria with alpha-mercaptopropionylglycine: a preliminary report with some notes on column chromatography of mercaptans.
    Proceedings of the Society for Experimental Biology and Medicine. Society for Experimental Biology and Medicine (New York, N.Y.), 1968, Volume: 129, Issue:3

    Topics: Amino Acids; Chromatography; Cysteine; Cystinuria; Humans; Taurine

1968
Cystine metabolism in cystinuria.
    Clinical science, 1965, Volume: 29, Issue:1

    Topics: Adult; Blood Chemical Analysis; Cysteine; Cystine; Cystinuria; Dietary Proteins; Humans; Middle Aged; Neomycin; Sulfates; Urine

1965
A highly specific new method for the determination of cystine and cysteine and its application to urine.
    Analytical biochemistry, 1965, Volume: 11, Issue:2

    Topics: Cysteine; Cystine; Cystinuria; Humans; In Vitro Techniques; Quinones; Spectrophotometry; Urine

1965
Intestinal absorption and renal extraction of cystine and cysteine in cystinuria.
    The New England journal of medicine, 1965, Dec-02, Volume: 273, Issue:23

    Topics: Biological Transport; Blood Chemical Analysis; Chromatography; Cysteine; Cystinuria; Humans; Intestinal Absorption; Kidney

1965
Cysteine metabolism in cystinuria.
    Clinical science, 1965, Volume: 29, Issue:3

    Topics: Blood; Cysteine; Cystine; Cystinuria; Female; Humans; Intestinal Absorption; Intestine, Small; Kidney Tubules; Male; Urine

1965
Sulphocysteine in the urine of the blotched Kenya genet.
    Nature, 1965, Dec-25, Volume: 208, Issue:5017

    Topics: Animals; Carnivora; Cysteine; Cystinuria; Sulfhydryl Compounds

1965
Separation of cystine, penicillamine disulfide and cysteine-penicillamine mixed disulfide by automatic amino acid analysis.
    Analytical biochemistry, 1966, Volume: 14, Issue:3

    Topics: Autoanalysis; Blood Chemical Analysis; Chemistry, Clinical; Chromatography, Ion Exchange; Cysteine; Cystine; Cystinuria; Humans; In Vitro Techniques; Penicillamine; Sulfides; Urine

1966
Cystinuria: intravenous administration of [35S]cystine and [35S]cysteine.
    Clinical science, 1966, Volume: 31, Issue:2

    Topics: Chromatography, Ion Exchange; Cysteine; Cystine; Cystinuria; Humans; Sulfur Isotopes

1966
Dithiothreitol in the study of cysteine transport.
    Biochimica et biophysica acta, 1966, May-26, Volume: 121, Issue:1

    Topics: Alcohols; Animals; Arginine; Biological Transport; Cysteine; Cystine; Cystinuria; Humans; In Vitro Techniques; Kidney; Lysine; Ornithine; Rats; Sulfhydryl Compounds

1966