cysteine and Cystic Fibrosis

cysteine has been researched along with Cystic Fibrosis in 34 studies

Research

Studies (34)

Timeframe	Studies, this research(%)	All Research%
pre-1990	13 (38.24)	18.7374
1990's	4 (11.76)	18.2507
2000's	9 (26.47)	29.6817
2010's	6 (17.65)	24.3611
2020's	2 (5.88)	2.80

Authors

Authors	Studies
Bar-Yoseph, R; Bentur, L; Gur, M; Hakim, F; Hanna, M; Laghi, L; Levanon, S; Marazzato, M; Masarweh, K; Wilschanski, M; Zuckerman-Levin, N	1
Bizzotto, G; Cavazzini, D; Cavozzi, C; Delfino, D; Grigoletto, A; Malatesta, M; Mori, G; Pasut, G; Percudani, R; Rivetti, C	1
Bedwell, DM; Bridges, RJ; Keeling, KM; Mobley, J; Mutyam, V; Rowe, SM; Thakerar, A; Xue, X	1
Bienvenu, T; Burgel, PR; Chapron, J; Dusser, D; Gaitch, N; Génin, E; Girodon, E; Honoré, I; Hubert, D; Kanaan, R; Martinez, B; Viel, M	1
Frank, MW; Mayasundari, A; Rock, CO; Zhang, YM; Zhu, K	1
Dragomir, A; Gaston, B; Hjelte, L; Jiang, S; Roomans, GM; Servetnyk, Z	1
Galietta, LJ; Melani, R; Tomati, V; Zegarra-Moran, O	1
Holstead, RG; Li, MS; Linsdell, P	1
Couetdic, G; Gauthier, F; Gorna, E; Joulin-Giet, A; Kasprzykowski, F; Lalmanach, G; Lecaille, F; Naudin, C; Plésiat, P; Szymanska, A	1
REAS, HW	3
SUDDARTH, SB	1
LYNN, HB	1
WEBB, WR	1
MEEKER, IA	1
LAWSON, D; SAGGERS, BA	1
DOCTER, J; STAMM, SJ	1
Aleksandrov, AA; Aleksandrov, L; Chen, JH; Cui, L; Gentzsch, M; Hou, YX; Riordan, JR	1
Clarke, DM; Loo, TW	1
Ballmann, M; Naim, HY; Stanke, F; Tümmler, B; van Barneveld, A	1
Bourgeois, C; Gochuico, BR; Levine, RL; Moss, J; Paone, G; Steagall, WK; Stevens, LA	1
Aggarwal, S; Misso, N; Reid, DW; Thompson, PJ; Walters, EH	1
Atkuri, KR; Herzenberg, LA; Mantovani, JJ	1
Ferraris, S; Zannini, G	1
Holmberg, L; Kornfält, R; Kristoffersson, AC; Schaedel, C	1
Cohn, JA; Cole, JL; Cutting, GR; Dawson, DC; Macek, M; Mansoura, MK; Smit, LS; Strong, TV; Wilkinson, DJ; Wood, DL	1
Ambrosioni, A; Cantù-Rajnoldi, A; Costantini, D; Fiori, S; Giunta, A; Padoan, R; Prandoni, S; Russo, MC; Seia, M	1
Bartlett, MC; Clarke, DM; Loo, TW	1
Marchi, AG; Nordio, S	1
Cahill, TC; David, DN; Dean, M; Greene, AA; Kaskel, FJ; Pellett, OL; Schneider, JA; Smith, ML; Smolin, LA; Weissbecker, K	1
King, M; Mantle, M; Stewart, G; Zayas, G	1
Brezina, M; Cervenka, J; Hruskovic, I; Kayserová, H; Langsádl, L	1
Harnapp, GO	1

Reviews

1 review(s) available for cysteine and Cystic Fibrosis

Article	Year
N-Acetylcysteine--a safe antidote for cysteine/glutathione deficiency. Current opinion in pharmacology, 2007, Volume: 7, Issue:4 Topics: Acetaminophen; Acetylcysteine; Antidotes; Controlled Clinical Trials as Topic; Cysteine; Cystic Fibrosis; Free Radical Scavengers; Glutathione; HIV Infections; Humans; Prodrugs; Quality of Life	2007

Trials

1 trial(s) available for cysteine and Cystic Fibrosis

Article	Year
[Further study on the possibility of using carbocysteine in cystic fibrosis]. Minerva pediatrica, 1983, Nov-30, Volume: 35, Issue:22 Topics: Carbocysteine; Child; Clinical Trials as Topic; Cysteine; Cystic Fibrosis; Double-Blind Method; Female; Humans; Male; Mucus; Viscosity	1983

Other Studies

32 other study(ies) available for cysteine and Cystic Fibrosis

Article	Year
The effect of probiotic administration on metabolomics and glucose metabolism in CF patients. Pediatric pulmonology, 2022, Volume: 57, Issue:10 Topics: Adolescent; Adult; Arabinose; Blood Glucose; Blood Glucose Self-Monitoring; Child; Cysteine; Cystic Fibrosis; Cytokines; Diabetes Mellitus; Dysbiosis; Glucose Intolerance; Glutamine; Humans; Indoles; Insulin Resistance; Lactates; Lactulose; Mannitol; Pilot Projects; Probiotics; Prospective Studies; Quality of Life; Young Adult	2022
Actin-Resistant DNase1L2 as a Potential Therapeutics for CF Lung Disease. Biomolecules, 2021, 03-10, Volume: 11, Issue:3 Topics: Actins; Amino Acid Sequence; Calcium; Catalytic Domain; Conserved Sequence; Cysteine; Cystic Fibrosis; Deoxyribonuclease I; DNA; Humans; Mucus; Oxidation-Reduction; Pichia; Plasmids; Polyethylene Glycols; Protein Binding; Recombinant Proteins	2021
Identification of the amino acids inserted during suppression of CFTR nonsense mutations and determination of their functional consequences. Human molecular genetics, 2017, 08-15, Volume: 26, Issue:16 Topics: Amino Acids; Codon; Codon, Nonsense; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Genes, Suppressor; HEK293 Cells; Humans; Leucine; Mutation; Protein Biosynthesis; Tryptophan	2017
DCTN4 as a modifier of chronic Pseudomonas aeruginosa infection in cystic fibrosis. The clinical respiratory journal, 2016, Volume: 10, Issue:6 Topics: Adolescent; Adult; Child; Child, Preschool; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Dynactin Complex; Female; Genetic Predisposition to Disease; Humans; Incidence; Infant; Male; Middle Aged; Mutation, Missense; Pseudomonas aeruginosa; Pseudomonas Infections; Retrospective Studies; Sex Factors; Tyrosine; Young Adult	2016
PqsD is responsible for the synthesis of 2,4-dihydroxyquinoline, an extracellular metabolite produced by Pseudomonas aeruginosa. The Journal of biological chemistry, 2008, Oct-24, Volume: 283, Issue:43 Topics: 3-Oxoacyl-(Acyl-Carrier-Protein) Synthase; Amino Acid Sequence; Animals; Bacterial Proteins; Catalysis; Catalytic Domain; Cysteine; Cystic Fibrosis; Kinetics; Mice; Models, Chemical; Molecular Sequence Data; Pseudomonas aeruginosa; Quinolines; Sequence Homology, Amino Acid; Time Factors	2008
The effect of S-nitrosoglutathione and L-cysteine on chloride efflux from cystic fibrosis airway epithelial cells. Experimental and molecular pathology, 2011, Volume: 90, Issue:1 Topics: Bronchodilator Agents; Cell Line; Chlorides; Cysteine; Cystic Fibrosis; Drug Synergism; Humans; Respiratory Mucosa; S-Nitrosoglutathione; Time Factors	2011
Modulation of cystic fibrosis transmembrane conductance regulator (CFTR) activity and genistein binding by cytosolic pH. The Journal of biological chemistry, 2010, Dec-31, Volume: 285, Issue:53 Topics: Amino Acids; Animals; Binding Sites; Cell Membrane; Chloride Channels; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Cytosol; Epithelium; Genistein; Hydrogen-Ion Concentration; Kinetics; Mutation; Protein Kinase Inhibitors; Rats	2010
Functional differences in pore properties between wild-type and cysteine-less forms of the CFTR chloride channel. The Journal of membrane biology, 2011, Volume: 243, Issue:1-3 Topics: Animals; Anions; Cells, Cultured; Cricetinae; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; Intracellular Fluid; Mutant Proteins; Mutation; Permeability	2011
Human cysteine cathepsins are not reliable markers of infection by Pseudomonas aeruginosa in cystic fibrosis. PloS one, 2011, Volume: 6, Issue:9 Topics: Biomarkers; Cathepsins; Cystatins; Cysteine; Cysteine Proteinase Inhibitors; Cystic Fibrosis; Humans; Kinetics; Kininogens; Pseudomonas aeruginosa; Pseudomonas Infections; Sputum	2011
The effect of N-acetylcysteine on the viscosity of tracheobronchial secretions in cystic fibrosis of the pancreas. The Journal of pediatrics, 1963, Volume: 62 Topics: Acetylcysteine; Bronchi; Cysteine; Cystic Fibrosis; Humans; Trachea; Viscosity	1963
Acetylcysteine, a new and effective mucolytic agent. Bulletin - Geisinger Medical Center, 1963, Volume: 15 Topics: Acetylcysteine; Bronchi; Cysteine; Cystic Fibrosis; Expectorants; Humans; Lung Diseases	1963
THE USE OF N-ACETYLCYSTEINE IN THE TREATMENT OF CYSTIC FIBROSIS. Southern medical journal, 1963, Volume: 56 Topics: Acetylcysteine; Adolescent; Child; Cysteine; Cystic Fibrosis; Expectorants; Humans; Lung Diseases; Respiration; Respiratory Therapy	1963
MECONIUM ILEUS. The American surgeon, 1964, Volume: 30 Topics: Acetylcysteine; Child; Cysteine; Cystic Fibrosis; Diagnosis; Humans; Ileus; Infant; Infant Nutritional Physiological Phenomena; Infant, Newborn; Infant, Newborn, Diseases; Intestinal Obstruction; Intestinal Pseudo-Obstruction; Intussusception; Meconium; Pancreatic Extracts; Rectal Prolapse; Surgical Procedures, Operative	1964
NEW MUCOLYTIC AGENTS FOR SPUTUM LIQUEFACTION. Postgraduate medicine, 1964, Volume: 36 Topics: Acetylcysteine; Asthma; Bronchial Diseases; Cysteine; Cystic Fibrosis; Expectorants; Fibrin; Humans; Lung Diseases; Mucus; Sputum; Toxicology	1964
ACETYLCYSTEINE USED TO LIQUEFY INSPISSATED MECONIUM CAUSING INTESTINAL OBSTRUCTION IN THE NEWBORN. Surgery, 1964, Volume: 56 Topics: Acetylcysteine; Cysteine; Cystic Fibrosis; Fetal Diseases; Hernia, Umbilical; Humans; Infant; Infant, Newborn; Infant, Newborn, Diseases; Intestinal Obstruction; Intestinal Perforation; Meconium; Peritonitis; Surgical Procedures, Operative	1964
THE USE OF N-ACETYLCYSTEINE IN THE TREATMENT OF CYSTIC FIBROSIS. The Journal of pediatrics, 1964, Volume: 65 Topics: Acetylcysteine; Adolescent; Child; Cysteine; Cystic Fibrosis; Humans; Infant; Klebsiella; Lung Diseases; Pneumonia; Proteus Infections; Pseudomonas Infections; Pulmonary Emphysema; Radiography, Thoracic; Respiratory Function Tests; Respiratory Therapy; Spirometry; Staphylococcal Infections	1964
N.A.C. AND ANTIBIOTICS IN CYSTIC FIBROSIS. British medical journal, 1965, Jan-30, Volume: 1, Issue:5430 Topics: Acetylcysteine; Ampicillin; Anti-Bacterial Agents; Antibiotics, Antitubercular; Cysteine; Cystic Fibrosis; Erythromycin; Fusidic Acid; Humans; Penicillins; Pharmacology; Protein Synthesis Inhibitors; Tetracycline	1965
CLINICAL EVALUATION OF ACETYLCYSTEINE AS A MUCOLYTIC AGENT IN CYSTIC FIBROSIS. Diseases of the chest, 1965, Volume: 47 Topics: Acetylcysteine; Adolescent; Aerosols; Blood Gas Analysis; Child; Cysteine; Cystic Fibrosis; Drug Therapy; Expectorants; Humans; Respiratory Function Tests	1965
The role of cystic fibrosis transmembrane conductance regulator phenylalanine 508 side chain in ion channel gating. The Journal of physiology, 2006, Apr-15, Volume: 572, Issue:Pt 2 Topics: Action Potentials; Adenosine Triphosphate; Animals; Blotting, Western; Cell Line; Chloride Channels; Cricetinae; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Electrophoresis, Polyacrylamide Gel; Gene Expression Regulation; Hydrolysis; Ion Channel Gating; Microscopy, Fluorescence; Mutation; Phenylalanine; Protein Binding; Protein Structure, Tertiary	2006
Using a cysteine-less mutant to provide insight into the structure and mechanism of CFTR. The Journal of physiology, 2006, Apr-15, Volume: 572, Issue:Pt 2 Topics: Animals; Cell Line; Chloride Channels; Cricetinae; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelium; Mutation; Temperature	2006
Ex vivo biochemical analysis of CFTR in human rectal biopsies. Biochimica et biophysica acta, 2006, Volume: 1762, Issue:4 Topics: Adolescent; Adult; Biopsy; Carbachol; Child; Child, Preschool; Colforsin; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Electrophysiology; Histamine; Humans; Immunoprecipitation; In Vitro Techniques; Intestinal Mucosa; Isotope Labeling; Middle Aged; Rectum; Sulfur Radioisotopes	2006
ADP-ribosyltransferase-specific modification of human neutrophil peptide-1. The Journal of biological chemistry, 2006, Jun-23, Volume: 281, Issue:25 Topics: ADP Ribose Transferases; alpha-Defensins; Animals; Asthma; Bronchoalveolar Lavage Fluid; Cysteine; Cystic Fibrosis; Epithelial Cells; Escherichia coli; GPI-Linked Proteins; Humans; Leukocytes; Mice; Pulmonary Fibrosis; Smoking; Transfection	2006
Oxidative stress and lipid-derived inflammatory mediators during acute exacerbations of cystic fibrosis. Respirology (Carlton, Vic.), 2007, Volume: 12, Issue:1 Topics: Adolescent; Adult; Anti-Bacterial Agents; Biomarkers; Cysteine; Cystic Fibrosis; Dinoprost; Disease Progression; Female; Follow-Up Studies; Forced Expiratory Volume; Humans; Immunoenzyme Techniques; Leukotrienes; Male; Oxidative Stress; Prognosis; Sputum	2007
A novel cystic fibrosis mutation, Y109C, in the first transmembrane domain of CFTR. Human molecular genetics, 1994, Volume: 3, Issue:6 Topics: Adolescent; Chloride Channels; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; DNA Primers; Exons; Female; Frameshift Mutation; Humans; Introns; Membrane Proteins; Point Mutation; Polymerase Chain Reaction; Tyrosine	1994
Missense mutation (G480C) in the CFTR gene associated with protein mislocalization but normal chloride channel activity. Human molecular genetics, 1995, Volume: 4, Issue:2 Topics: Animals; Base Sequence; Cells, Cultured; Chloride Channels; Cyclic AMP; Cysteine; Cystic Fibrosis; Female; Glycine; Humans; Immunoblotting; Mammals; Membrane Proteins; Molecular Sequence Data; Oocytes; Point Mutation; Temperature; Xenopus laevis	1995
A novel missense mutation (Y89C) in exon 3 of the CFTR (ABCC7) gene in a young male. Human mutation, 2000, Volume: 15, Issue:5 Topics: Adult; Amino Acid Substitution; Animals; ATP-Binding Cassette Transporters; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Exons; Humans; Male; Mice; Mutation, Missense; Rats; Tyrosine	2000
Introduction of the most common cystic fibrosis mutation (Delta F508) into human P-glycoprotein disrupts packing of the transmembrane segments. The Journal of biological chemistry, 2002, Aug-02, Volume: 277, Issue:31 Topics: Amino Acid Substitution; ATP Binding Cassette Transporter, Subfamily B, Member 1; Cell Line; Cell Membrane; Cross-Linking Reagents; Cysteine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; Mutagenesis; Mutation; Oxidation-Reduction; Phenylalanine; Protein Folding; Recombinant Proteins; Sequence Deletion; Transfection	2002
[Therapy of cystic fibrosis]. Minerva pediatrica, 1976, Jan-28, Volume: 28, Issue:2 Topics: Anti-Bacterial Agents; Arginine; Bicarbonates; Cysteine; Cystic Fibrosis; Humans; Infant	1976
Biochemical and genetic analysis of a child with cystic fibrosis and cystinosis. American journal of medical genetics, 1991, Apr-01, Volume: 39, Issue:1 Topics: Cysteine; Cystic Fibrosis; Cystinosis; Female; Humans; Infant, Newborn; Male; Mutation; Pedigree	1991
The disulphide-bond content and rheological properties of intestinal mucins from normal subjects and patients with cystic fibrosis. The Biochemical journal, 1990, Mar-01, Volume: 266, Issue:2 Topics: Cysteine; Cystic Fibrosis; Disulfides; Gels; Humans; In Vitro Techniques; Intestines; Mucins; Oxidation-Reduction; Rheology	1990
[Carbocysteine--an effective mucolytic in cystic fibrosis of the lungs]. Ceskoslovenska pediatrie, 1988, Volume: 43, Issue:10 Topics: Adolescent; Adult; Carbocysteine; Child; Cysteine; Cystic Fibrosis; Female; Humans; Male; Respiration	1988
[Mucoviscidosis, diagnosis and new methods in its management]. Zeitschrift fur arztliche Fortbildung, 1967, Jul-15, Volume: 61, Issue:14 Topics: Anti-Bacterial Agents; Cysteine; Cystic Fibrosis; Diet Therapy; Humans; Intestinal Obstruction; Meconium; Pulmonary Fibrosis; Radiography; Respiratory Therapy	1967