Page last updated: 2024-08-17

cysteamine and Nephrotic Syndrome

cysteamine has been researched along with Nephrotic Syndrome in 12 studies

Research

Studies (12)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (8.33)29.6817
2010's11 (91.67)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Cairns, D; Di Salvo, A; Kay, G; Knott, RM; Omran, Z1
Cairns, D; Hector, EE; Kay, G; Knott, RM; Omran, Z1
Benylles, A; Cairns, D; Kay, G; Knott, RM; Moloney, KA; Omran, Z1
Higashi, S; Ito, S; Matsunoshita, N; Nozu, K; Otani, M; Tokuhiro, E1
Arcolino, FO; Elmonem, MA; Levtchenko, E; van den Heuvel, L; Veys, KR1
Dimitriou, E; Emma, F; Karavitakis, EM; Kosma, K; Michelakakis, H; Xaidara, A1
Brugnara, M; Emma, F; Greco, M; Pastore, A; Taranta, A; Zaffanello, M1
Antignac, C; Brodin-Sartorius, A; Charbit, M; Cochat, P; Guest, G; Legendre, C; Lesavre, P; Moyse, D; Niaudet, P; Ottolenghi, C; Servais, A; Tête, MJ1
Bouazza, N; Chadefaux-Vekemans, B; Deschenes, G; Niaudet, P; Ottolenghi, C; Ricquier, D; Tréluyer, JM; Urien, S1
Bagger, MJ; Cochat, P; Cornelissen, E; Deschênes, G; Gaillard, S; Greenbaum, LA; Grimm, P; Langman, CB; Matossian, D; Morin, D; Niaudet, P; Rioux, P; Sarwal, M1
Buchan, B; Cairns, D; Kay, G; Matthews, KH1
Cabrera, BL; Dohil, R1

Reviews

1 review(s) available for cysteamine and Nephrotic Syndrome

ArticleYear
Nephropathic cystinosis: an update.
    Current opinion in pediatrics, 2017, Volume: 29, Issue:2

    Topics: Cysteamine; Cystinosis; Female; Forecasting; Genetic Therapy; Humans; Infant; Infant, Newborn; Male; Nephrotic Syndrome; Prognosis; Risk Assessment; Severity of Illness Index; Stem Cell Transplantation; Treatment Outcome

2017

Trials

2 trial(s) available for cysteamine and Nephrotic Syndrome

ArticleYear
Population pharmacokinetics and pharmacodynamics of cysteamine in nephropathic cystinosis patients.
    Orphanet journal of rare diseases, 2011, Dec-23, Volume: 6

    Topics: Adolescent; Adult; Body Weight; Child; Child, Preschool; Cysteamine; Cystine; Cystinosis; Dose-Response Relationship, Drug; Fanconi Syndrome; Female; Humans; Infant; Male; Nephrotic Syndrome; Radiation-Protective Agents; Treatment Outcome; Young Adult

2011
A randomized controlled crossover trial with delayed-release cysteamine bitartrate in nephropathic cystinosis: effectiveness on white blood cell cystine levels and comparison of safety.
    Clinical journal of the American Society of Nephrology : CJASN, 2012, Volume: 7, Issue:7

    Topics: Adolescent; Adult; Child; Cross-Over Studies; Cysteamine; Cystine; Cystinosis; Delayed-Action Preparations; Fanconi Syndrome; Female; Humans; Leukocytes; Male; Nephrotic Syndrome; Young Adult

2012

Other Studies

9 other study(ies) available for cysteamine and Nephrotic Syndrome

ArticleYear
PEGylated derivatives of cystamine as enhanced treatments for nephropathic cystinosis.
    Bioorganic & medicinal chemistry letters, 2011, Jan-01, Volume: 21, Issue:1

    Topics: Cells, Cultured; Cystamine; Cystinosis; Fanconi Syndrome; Fibroblasts; Humans; Nephrotic Syndrome; Polyethylene Glycols; Prodrugs

2011
Folate pro-drug of cystamine as an enhanced treatment for nephropathic cystinosis.
    Bioorganic & medicinal chemistry letters, 2011, Apr-15, Volume: 21, Issue:8

    Topics: Administration, Oral; Cell Line; Cystamine; Cystinosis; Fanconi Syndrome; Humans; Nephrotic Syndrome; Prodrugs

2011
Synthesis and in vitro evaluation of novel pro-drugs for the treatment of nephropathic cystinosis.
    Bioorganic & medicinal chemistry, 2011, Jun-01, Volume: 19, Issue:11

    Topics: Cystamine; Cystinosis; Fanconi Syndrome; Fibroblasts; Glutarates; Humans; Nephrotic Syndrome; Prodrugs; Succinic Acid

2011
Diagnostic challenge in a patient with nephropathic juvenile cystinosis: a case report.
    BMC nephrology, 2017, Sep-26, Volume: 18, Issue:1

    Topics: Child; Cysteamine; Cystinosis; Fanconi Syndrome; Humans; Male; Nephrotic Syndrome; Slit Lamp Microscopy

2017
Chitotriosidase plasma activity in nephropathic cystinosis.
    Journal of inherited metabolic disease, 2009, Volume: 32 Suppl 1

    Topics: Child, Preschool; Cysteamine; Cystinosis; Fanconi Syndrome; Hexosaminidases; Humans; Nephrotic Syndrome

2009
Long-term outcome of nephropathic cystinosis: a 20-year single-center experience.
    Pediatric nephrology (Berlin, Germany), 2010, Volume: 25, Issue:12

    Topics: Adolescent; Angiotensin-Converting Enzyme Inhibitors; Child; Child, Preschool; Cysteamine; Cystinosis; Disease Progression; Drug Therapy, Combination; Early Diagnosis; Fanconi Syndrome; Female; Humans; Infant; Italy; Kaplan-Meier Estimate; Kidney; Kidney Failure, Chronic; Logistic Models; Male; Nephrotic Syndrome; Retrospective Studies; Risk Assessment; Risk Factors; Time Factors; Treatment Outcome

2010
Cysteamine therapy delays the progression of nephropathic cystinosis in late adolescents and adults.
    Kidney international, 2012, Volume: 81, Issue:2

    Topics: Adolescent; Adult; Age Factors; Amino Acid Transport Systems, Neutral; Child; Child, Preschool; Cysteamine; Cystinosis; Diabetes Complications; Disease Progression; Educational Status; Employment; Fanconi Syndrome; Female; Follow-Up Studies; Humans; Hypothyroidism; Infant; Kaplan-Meier Estimate; Kidney Failure, Chronic; Male; Middle Aged; Nephrotic Syndrome; Nervous System Diseases; Neuromuscular Diseases; Radiation-Protective Agents; Young Adult

2012
Suppository formulations as a potential treatment for nephropathic cystinosis.
    Journal of pharmaceutical sciences, 2012, Volume: 101, Issue:10

    Topics: Chemistry, Pharmaceutical; Cysteamine; Cystine; Cystinosis; Drug Stability; Excipients; Fanconi Syndrome; Nephrotic Syndrome; Polyethylene Glycols; Solubility; Suppositories

2012
Treatment of cystinosis with delayed-release cysteamine: 6-year follow-up.
    Pediatric nephrology (Berlin, Germany), 2013, Volume: 28, Issue:3

    Topics: Adolescent; Biomarkers; Chemistry, Pharmaceutical; Creatinine; Cysteamine; Cystinosis; Delayed-Action Preparations; Drug Administration Schedule; Fanconi Syndrome; Female; Glomerular Filtration Rate; Humans; Kidney; Leukocyte Count; Male; Nephrotic Syndrome; Time Factors; Treatment Outcome; Young Adult

2013