Compounds > cysteamine
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cysteamine and Kidney Failure, Chronic

cysteamine has been researched along with Kidney Failure, Chronic in 22 studies

Research

Studies (22)

TimeframeStudies, this research(%)All Research%
pre-19901 (4.55)18.7374
1990's3 (13.64)18.2507
2000's4 (18.18)29.6817
2010's11 (50.00)24.3611
2020's3 (13.64)2.80

Authors

AuthorsStudies
Beck, BB; Bieniaś, B; Grenda, R; Kieć-Wilk, B; Kowalczyk, M; Marquardt, T; Nosek, H; Rubik, J; Sikora, P; Surowiec, P; Szymczak, M; Zaniew, M1
Ariceta, G; Awan, A; Besouw, M; Bockenhauer, D; Haffner, D; Harms, E; Hohenfellner, K; Janssen, MCH; Kanzelmeyer, N; Levtchenko, E; Niaudet, P; Novo, R; Pape, L; Servais, A; Sikora, P; Topaloglu, R; van den Heuvel, B; Veys, K; Wühl, E; Zadora, W1
Kasimer, RN; Langman, CB1
Alexander, SI; Clayton, PA; McTaggart, SJ; Spicer, RA; Zhang, GY1
Bernardini, I; Gahl, WA; Nesterova, G; Williams, C1
Bertholet-Thomas, A; Choukroun, G; Decramer, S; Goizet, C; Llanas, B; Novo, R; Servais, A1
Ariceta, G; Camacho, JA; Fernández-Obispo, M; Fernández-Polo, A; Gamez, J; García-Villoria, J; Güell, A; Lara Monteczuma, E; Leyes, P; Martín-Begué, N; Morell, GP; Oppenheimer, F; Perelló, M; Santandreu, AV; Torra, R1
Bultynck, G; De Smedt, H; Elmonem, MA; Ivanova, EA; Levtchenko, EN; Mekahli, D; Missiaen, L; Pastore, A; van den Heuvel, LP1
Abidi, K; Ben Turkia, H; Gargah, T; Hammi, Y; Jellouli, M1
Barshop, BA; Deschênes, G; Emma, F; Goodyer, P; Langman, CB; Levtchenko, EN; Lipkin, G; Midgley, JP; Ottolenghi, C; Servais, A; Soliman, NA; Thoene, JG1
Bazaraa, H; El-Baroudy, R; Rizk, A; Soliman, NA; Younan, A1
Brugnara, M; Emma, F; Greco, M; Pastore, A; Taranta, A; Zaffanello, M1
Besouw, M; Levtchenko, E1
Lund, AM; Oczachowska-Kulik, AE; Pedersen, EB; Skovby, F1
Antignac, C; Brodin-Sartorius, A; Charbit, M; Cochat, P; Guest, G; Legendre, C; Lesavre, P; Moyse, D; Niaudet, P; Ottolenghi, C; Servais, A; Tête, MJ1
Gahl, W; Nesterova, G1
Borowitz, MJ; Burns, KH; Confer, B; Emadi, A; Streiff, MB1
Gretz, N; Manz, F1
Brodehl, J; Offner, G; Schubert, M; Vester, U1
Bradbury, JA; Brocklebank, T; Danjoux, JP; Spencer, M; Voller, J1
Strife, CF; Strife, JL; Wacksman, J1
Blumberg, A; da Silva, VA; Lavanchy, P; Lüthy, CM; Oetliker, OH; Suter, H; Wyss, SR; Zurbrügg, RP1

Reviews

4 review(s) available for cysteamine and Kidney Failure, Chronic

ArticleYear
Adult complications of nephropathic cystinosis: a systematic review.
    Pediatric nephrology (Berlin, Germany), 2021, Volume: 36, Issue:2

    Topics: Adult; Cysteamine; Cystinosis; Fanconi Syndrome; Humans; Kidney Failure, Chronic; Kidney Transplantation

2021
[Cystinosis in adults: A systemic disease].
    Nephrologie & therapeutique, 2015, Volume: 11, Issue:3

    Topics: Adolescent; Adult; Cysteamine; Cystine Depleting Agents; Cystinosis; Fanconi Syndrome; Humans; Kidney Failure, Chronic; Kidney Transplantation; Renal Insufficiency

2015
[Improved prognosis of cystinosis achieved by treatment with cysteamine and by kidney transplantation].
    Ugeskrift for laeger, 2011, Aug-15, Volume: 173, Issue:33

    Topics: Cysteamine; Cystinosis; Fanconi Syndrome; Humans; Kidney Failure, Chronic; Kidney Transplantation; Prognosis; Treatment Outcome

2011
Nephropathic cystinosis: late complications of a multisystemic disease.
    Pediatric nephrology (Berlin, Germany), 2008, Volume: 23, Issue:6

    Topics: Administration, Oral; Adolescent; Adult; Child; Cysteamine; Cystinosis; Disease Progression; Fanconi Syndrome; Genetic Predisposition to Disease; Humans; Kidney Failure, Chronic; Kidney Transplantation; Life Expectancy; Male; Middle Aged; Severity of Illness Index; Treatment Outcome

2008

Trials

2 trial(s) available for cysteamine and Kidney Failure, Chronic

ArticleYear
Distal myopathy in nephropathic cystinosis.
    Pediatric nephrology (Berlin, Germany), 2000, Volume: 14, Issue:1

    Topics: Adolescent; Adult; Child; Cysteamine; Cystinosis; Electromyography; Female; Hand; Humans; Kidney Failure, Chronic; Male; Muscle Weakness; Muscular Diseases; Neural Conduction

2000
A randomised placebo-controlled trial of topical cysteamine therapy in patients with nephropathic cystinosis.
    Eye (London, England), 1991, Volume: 5 ( Pt 6)

    Topics: Adolescent; Child; Contrast Sensitivity; Cornea; Cysteamine; Cystine; Cystinosis; Double-Blind Method; Female; Humans; Kidney Failure, Chronic; Male; Ophthalmic Solutions; Visual Acuity

1991

Other Studies

16 other study(ies) available for cysteamine and Kidney Failure, Chronic

ArticleYear
Nephropathic cystinosis in Poland: a 40-year retrospective study.
    Polish archives of internal medicine, 2022, 11-25, Volume: 132, Issue:11

    Topics: Adult; Child; Cysteamine; Cystine; Cystinosis; Fanconi Syndrome; Humans; Kidney Failure, Chronic; Poland; Retrospective Studies; Young Adult

2022
Outcome of infantile nephropathic cystinosis depends on early intervention, not genotype: A multicenter sibling cohort study.
    Journal of inherited metabolic disease, 2023, Volume: 46, Issue:1

    Topics: Adolescent; Adult; Child; Child, Preschool; Cohort Studies; Cysteamine; Cystinosis; Fanconi Syndrome; Humans; Infant, Newborn; Kidney Failure, Chronic; Retrospective Studies; Siblings; Young Adult

2023
Patient and graft survival following kidney transplantation in recipients with cystinosis: a cohort study.
    American journal of kidney diseases : the official journal of the National Kidney Foundation, 2015, Volume: 65, Issue:1

    Topics: Adult; Australia; Cause of Death; Cohort Studies; Cysteamine; Cystine Depleting Agents; Cystinosis; Female; Graft Survival; Humans; Kidney Failure, Chronic; Kidney Transplantation; Male; Nervous System Diseases; Patient Outcome Assessment; Survival Analysis; Vascular Diseases

2015
Cystinosis: renal glomerular and renal tubular function in relation to compliance with cystine-depleting therapy.
    Pediatric nephrology (Berlin, Germany), 2015, Volume: 30, Issue:6

    Topics: Administration, Oral; Adolescent; Adult; Age Factors; Biomarkers; Child; Cysteamine; Cystine; Cystine Depleting Agents; Cystinosis; Fanconi Syndrome; Female; Humans; Kidney; Kidney Failure, Chronic; Kidney Function Tests; Leukocytes; Linear Models; Male; Maximum Tolerated Dose; Medication Adherence; Middle Aged; Retrospective Studies; Risk Factors; Time Factors; Treatment Outcome; Young Adult

2015
Cystinosis in adult and adolescent patients: Recommendations for the comprehensive care of cystinosis.
    Nefrologia : publicacion oficial de la Sociedad Espanola Nefrologia, 2015, Volume: 35, Issue:3

    Topics: Adolescent; Adult; Amino Acid Transport Systems, Neutral; Comprehensive Health Care; Corneal Diseases; Cysteamine; Cystinosis; Disease Management; Early Diagnosis; Endocrine System Diseases; Genetic Counseling; Humans; Interdisciplinary Communication; Kidney Failure, Chronic; Kidney Transplantation; Nervous System Diseases; Patient Education as Topic; Quality of Life; Self Care; Transition to Adult Care

2015
Altered mTOR signalling in nephropathic cystinosis.
    Journal of inherited metabolic disease, 2016, Volume: 39, Issue:3

    Topics: Amino Acid Transport Systems, Neutral; Autophagy; Cells, Cultured; Cysteamine; Cystinosis; Fanconi Syndrome; Humans; Kidney Failure, Chronic; Kidney Tubules, Proximal; Lysosomes; Mechanistic Target of Rapamycin Complex 1; Signal Transduction

2016
[Peculiarity of infantile cystinosis in Tunisian children].
    The Pan African medical journal, 2015, Volume: 22

    Topics: Adolescent; Child; Child, Preschool; Cysteamine; Cystine Depleting Agents; Cystinosis; Disease Progression; Female; Humans; Infant; Kidney Failure, Chronic; Kidney Function Tests; Male; Retrospective Studies; Tunisia

2015
Controversies and research agenda in nephropathic cystinosis: conclusions from a "Kidney Disease: Improving Global Outcomes" (KDIGO) Controversies Conference.
    Kidney international, 2016, Volume: 89, Issue:6

    Topics: Adolescent; Adult; Age Factors; Amino Acid Transport Systems, Neutral; Child; Congresses as Topic; Cysteamine; Cystine; Cystine Depleting Agents; Cystinosis; Fanconi Syndrome; Genetic Testing; Genetic Therapy; Graft vs Host Disease; Hematopoietic Stem Cell Transplantation; Humans; Immunosuppression Therapy; Infant; Kidney Failure, Chronic; Kidney Transplantation; Lysosomes; Mutation; Rare Diseases; Renal Dialysis

2016
Nephropathic cystinosis in children: An overlooked disease.
    Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi Arabia, 2009, Volume: 20, Issue:3

    Topics: Administration, Oral; Administration, Topical; Child; Child, Preschool; Cornea; Corneal Diseases; Cysteamine; Cystinosis; Diagnostic Techniques, Ophthalmological; Disease Progression; Fanconi Syndrome; Female; Humans; Infant; Kidney Failure, Chronic; Male; Medication Adherence; Ophthalmic Solutions; Predictive Value of Tests; Severity of Illness Index; Treatment Outcome

2009
Long-term outcome of nephropathic cystinosis: a 20-year single-center experience.
    Pediatric nephrology (Berlin, Germany), 2010, Volume: 25, Issue:12

    Topics: Adolescent; Angiotensin-Converting Enzyme Inhibitors; Child; Child, Preschool; Cysteamine; Cystinosis; Disease Progression; Drug Therapy, Combination; Early Diagnosis; Fanconi Syndrome; Female; Humans; Infant; Italy; Kaplan-Meier Estimate; Kidney; Kidney Failure, Chronic; Logistic Models; Male; Nephrotic Syndrome; Retrospective Studies; Risk Assessment; Risk Factors; Time Factors; Treatment Outcome

2010
Pharmacokinetics of cysteamine in a cystinosis patient treated with hemodialysis.
    Pediatric nephrology (Berlin, Germany), 2011, Volume: 26, Issue:4

    Topics: Area Under Curve; Cysteamine; Cystinosis; Humans; Kidney Failure, Chronic; Male; Renal Dialysis; Young Adult

2011
Cysteamine therapy delays the progression of nephropathic cystinosis in late adolescents and adults.
    Kidney international, 2012, Volume: 81, Issue:2

    Topics: Adolescent; Adult; Age Factors; Amino Acid Transport Systems, Neutral; Child; Child, Preschool; Cysteamine; Cystinosis; Diabetes Complications; Disease Progression; Educational Status; Employment; Fanconi Syndrome; Female; Follow-Up Studies; Humans; Hypothyroidism; Infant; Kaplan-Meier Estimate; Kidney Failure, Chronic; Male; Middle Aged; Nephrotic Syndrome; Nervous System Diseases; Neuromuscular Diseases; Radiation-Protective Agents; Young Adult

2012
Hematological manifestations of nephropathic cystinosis.
    Acta haematologica, 2008, Volume: 119, Issue:3

    Topics: Adult; Antilymphocyte Serum; Bone Marrow; Combined Modality Therapy; Crystallization; Cysteamine; Cystine; Cystinosis; Humans; Immunosuppressive Agents; Kidney Failure, Chronic; Kidney Transplantation; Macrophages; Male; Pancytopenia; Postoperative Complications; T-Lymphocytes

2008
Progression of chronic renal failure in a historical group of patients with nephropathic cystinosis. European Collaborative Study on Cystinosis.
    Pediatric nephrology (Berlin, Germany), 1994, Volume: 8, Issue:4

    Topics: Child, Preschool; Creatinine; Cysteamine; Cystinosis; Disease Progression; Humans; Kidney Failure, Chronic; Kidney Function Tests; Retrospective Studies; Survival Rate

1994
Acquired structural genitourinary abnormalities contributing to deterioration of renal function in older patients with nephropathic cystinosis.
    Pediatrics, 1991, Volume: 88, Issue:6

    Topics: Creatinine; Cysteamine; Cystinosis; Female; Glomerular Filtration Rate; Humans; Infant; Kidney Failure, Chronic; Male; Ultrasonography

1991
Long-term treatment of infantile nephropathic cystinosis with cysteamine.
    The New England journal of medicine, 1985, Dec-05, Volume: 313, Issue:23

    Topics: Bone Marrow; Child; Child, Preschool; Cysteamine; Cystine; Cystinosis; Fanconi Syndrome; Growth; Humans; Infant; Infant, Newborn; Kidney Failure, Chronic; Leukocytes; Male

1985