Page last updated: 2024-08-17

cysteamine and Cystic Fibrosis of Pancreas

cysteamine has been researched along with Cystic Fibrosis of Pancreas in 14 studies

Research

Studies (14)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's11 (78.57)24.3611
2020's3 (21.43)2.80

Authors

AuthorsStudies
Cavallaro, G; Di Leonardo, A; Giammona, G; Lentini, L; Porsio, B; Quaglia, F; Ungaro, F1
Elie, J; Häfner, S; Kopp, BT; Meijer, L; Shrestha, CL; Wisniewski, B; Zhang, S1
Bourke, SJ; Daines, CL; Devereux, G; Doe, S; Dougherty, R; Franco, R; Fraser-Pitt, DJ; Innes, A; Kopp, BT; Lascano, J; Layish, D; Lovie, E; Lucidi, V; MacGregor, G; Murray, L; O'Neil, DA; Peckham, D; Robertson, J; Wrolstad, D1
Albastroiu, F; Amer, AO; Assani, KD; Kopp, BT; Rinehardt, H; Schlesinger, LS; Shell, R; Shrestha, CL; Zhang, S1
Kepp, O; Kroemer, G; Li, Y; Maiuri, L; Obrist, F; Pedro, JMBS; Sauvat, A; Sica, V; Stoll, G; Zamzami, N; Zhang, S1
Barlev, NA; Castaldo, A; Esposito, S; Ferrari, E; Kroemer, G; Maiuri, L; Marseglia, GL; Monzani, R; Piacentini, M; Raia, V; Romani, L; Rossin, F; Silano, M; Tosco, A; Villella, VR1
Bona, G; Bossi, A; De Gregorio, F; De Rosa, G; De Stefano, D; Esposito, S; Grassia, R; Guido, S; Kroemer, G; Leone, CA; Maiuri, L; Maiuri, MC; Mehta, A; Pettoello-Mantovani, M; Pinna, LA; Raia, V; Salvadori, L; Sepe, A; Tosco, A; Venerando, A; Villella, VR; Zolin, A1
Charrier, C; Fraser-Pitt, D; Kowalczuk, A; Mercer, D; O'Neil, D; Robertson, J; Rodger, C; Shand, N1
De Stefano, D; Maiuri, MC1
Devereux, G; Devlin, E; Fraser-Pitt, D; Mercer, D; O'Neil, D; Robertson, J1
Bona, G; Buonpensiero, P; De Gregorio, F; De Rosa, G; De Stefano, D; Di Pasqua, A; Esposito, S; Ferrari, E; Grassia, R; Guido, S; Kroemer, G; Leone, CA; Lusa, S; Maiuri, L; Maiuri, MC; Mehta, A; Raia, V; Salvadori, L; Sana, I; Sepe, A; Stoll, G; Tosco, A1
Chrystyn, H; Cotton, S; Devereux, G; Devlin, E; Fraser-Pitt, D; Griffiths, K; Norrie, J; O'Neil, D; Steele, S1
Fraser-Pitt, D; Lovie, E; Mercer, D; O'Neil, D; Robertson, J1
D'Eletto, M; De Gregorio, F; Esposito, S; Ferrari, E; Izzo, V; Kroemer, G; Maiuri, L; Maiuri, MC; Monzani, R; Raia, V; Rossin, F; Saluzzo, F; Tosco, A; Villella, VR1

Trials

3 trial(s) available for cysteamine and Cystic Fibrosis of Pancreas

ArticleYear
Oral cysteamine as an adjunct treatment in cystic fibrosis pulmonary exacerbations: An exploratory randomized clinical trial.
    PloS one, 2020, Volume: 15, Issue:12

    Topics: Administration, Oral; Adult; Cysteamine; Cystic Fibrosis; Female; Humans; Lung; Male; Medication Adherence; Safety

2020
Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation.
    Autophagy, 2014, Volume: 10, Issue:11

    Topics: Adaptor Proteins, Signal Transducing; Administration, Oral; Adolescent; Adult; Animals; Apoptosis Regulatory Proteins; Beclin-1; Catechin; Cell Membrane; Child; Chlorides; Cystamine; Cysteamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Homozygote; Humans; Interleukin-8; Male; Membrane Proteins; Mice; Mice, Inbred CFTR; Mice, Transgenic; Mutation; Phenotype; Pilot Projects; Sequestosome-1 Protein; Tumor Necrosis Factor-alpha; Young Adult

2014
A novel treatment of cystic fibrosis acting on-target: cysteamine plus epigallocatechin gallate for the autophagy-dependent rescue of class II-mutated CFTR.
    Cell death and differentiation, 2016, Volume: 23, Issue:8

    Topics: Adolescent; Animals; Autophagy; Biomarkers; Catechin; Child; Cysteamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Disease Models, Animal; Drug Therapy, Combination; Homozygote; Humans; Interleukin-8; Lung; Mice; Mice, Knockout; Mutation; Sputum; Tumor Necrosis Factor-alpha

2016

Other Studies

11 other study(ies) available for cysteamine and Cystic Fibrosis of Pancreas

ArticleYear
Inhalable nano into micro dry powders for ivacaftor delivery: The role of mannitol and cysteamine as mucus-active agents.
    International journal of pharmaceutics, 2020, May-30, Volume: 582

    Topics: Administration, Inhalation; Aminophenols; Animals; Cells, Cultured; Chloride Channel Agonists; Cysteamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Drug Compounding; Drug Liberation; Expectorants; Mannitol; Mutation; Nanoparticles; Peptides; Powders; Quinolones; Rats, Inbred F344

2020
(R)-Roscovitine and CFTR modulators enhance killing of multi-drug resistant Burkholderia cenocepacia by cystic fibrosis macrophages.
    Scientific reports, 2020, 12-10, Volume: 10, Issue:1

    Topics: Adolescent; Adult; Burkholderia cenocepacia; Cysteamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Drug Therapy, Combination; Female; Humans; Macrophages; Male; Phagocytosis; Pseudomonas aeruginosa; Roscovitine; Young Adult

2020
Cysteamine-mediated clearance of antibiotic-resistant pathogens in human cystic fibrosis macrophages.
    PloS one, 2017, Volume: 12, Issue:10

    Topics: Autophagy; Bacteria; Blotting, Western; Case-Control Studies; Cell Line; Cysteamine; Cystic Fibrosis; Drug Resistance, Microbial; Enzyme-Linked Immunosorbent Assay; Humans; Macrophages; Microscopy, Confocal; Microscopy, Electron, Transmission

2017
Evaluation of autophagy inducers in epithelial cells carrying the ΔF508 mutation of the cystic fibrosis transmembrane conductance regulator CFTR.
    Cell death & disease, 2018, 02-07, Volume: 9, Issue:2

    Topics: Autophagy; Bronchi; Catechin; Cell Line; Cell Line, Tumor; Cysteamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Epithelial Cells; Humans; Transfection

2018
Autophagy suppresses the pathogenic immune response to dietary antigens in cystic fibrosis.
    Cell death & disease, 2019, 03-15, Volume: 10, Issue:4

    Topics: Animals; Autophagy; Beclin-1; Caco-2 Cells; Cysteamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Cytokines; Epithelial Cells; Gliadin; GTP-Binding Proteins; Heterozygote; Homozygote; Humans; Mice; Mice, Inbred C57BL; Mice, Knockout; Peptide Fragments; Protein Glutamine gamma Glutamyltransferase 2; Transglutaminases

2019
Cysteamine (Lynovex®), a novel mucoactive antimicrobial & antibiofilm agent for the treatment of cystic fibrosis.
    Orphanet journal of rare diseases, 2014, Nov-30, Volume: 9

    Topics: Animals; Anti-Infective Agents; Biofilms; Cysteamine; Cystic Fibrosis; Expectorants; Humans; Male; Mice; Mice, Inbred ICR; Microbial Sensitivity Tests; Mucins; Swine; Treatment Outcome

2014
A Breathe in Cystic Fibrosis Therapy: A New Therapeutic Endeavor for Cysteamine.
    EBioMedicine, 2015, Volume: 2, Issue:10

    Topics: Cysteamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Humans; Respiration

2015
Cysteamine as a Future Intervention in Cystic Fibrosis Against Current and Emerging Pathogens: A Patient-based ex vivo Study Confirming its Antimicrobial and Mucoactive Potential in Sputum.
    EBioMedicine, 2015, Volume: 2, Issue:10

    Topics: Adult; Anti-Bacterial Agents; Anti-Infective Agents; Colony Count, Microbial; Cysteamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Female; Genotype; Humans; Male; Microbial Sensitivity Tests; Mutation; Nontuberculous Mycobacteria; Opportunistic Infections; Sputum; Young Adult

2015
An Open-Label Investigation of the Pharmacokinetics and Tolerability of Oral Cysteamine in Adults with Cystic Fibrosis.
    Clinical drug investigation, 2016, Volume: 36, Issue:8

    Topics: Adult; Area Under Curve; Cysteamine; Cystic Fibrosis; Cystinosis; Female; Half-Life; Humans; Intestinal Absorption; Male; Sputum; Treatment Outcome; Young Adult

2016
Activity of Cysteamine against the Cystic Fibrosis Pathogen Burkholderia cepacia Complex.
    Antimicrobial agents and chemotherapy, 2016, Volume: 60, Issue:10

    Topics: Anti-Bacterial Agents; Biofilms; Burkholderia cepacia complex; Cysteamine; Cystic Fibrosis; Humans; Microbial Sensitivity Tests; Tobramycin

2016
Cysteamine re-establishes the clearance of Pseudomonas aeruginosa by macrophages bearing the cystic fibrosis-relevant F508del-CFTR mutation.
    Cell death & disease, 2017, 01-12, Volume: 8, Issue:1

    Topics: Animals; Beclin-1; Bone Marrow Cells; Cysteamine; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Gene Expression Regulation; Humans; Inflammation; Lung; Macrophages; Mice; Mice, Transgenic; Pseudomonas aeruginosa; Pseudomonas Infections

2017