cystathionine and Cystine Diathesis

cystathionine has been researched along with Cystine Diathesis in 6 studies

Research

Studies (6)

TimeframeStudies, this research(%)All Research%
pre-19906 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Kaye, CI; Nadler, HL1
Christensen, HN; Lemons, RM; Pisoni, RL; Thoene, JG1
Furlong, CE; Oshima, RG; Schneider, JA; Willis, RC1
Ampola, MG1
Kroll, S; Toussaint, W; Zebisch, P2

Reviews

1 review(s) available for cystathionine and Cystine Diathesis

ArticleYear
Phenylketonuria and other disorders of amino acid metabolism.
    Pediatric clinics of North America, 1973, Volume: 20, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Child, Preschool; Counseling; Cystathionine; Cystinosis; Cystinuria; Diet Therapy; Dietary Proteins; Family; Female; Hartnup Disease; Histidine; Homocystinuria; Humans; Hyperglycemia; Infant; Infant, Newborn; Lysine; Maple Syrup Urine Disease; Ornithine; Phenylketonurias; Pregnancy; Proline; Tyrosine

1973

Other Studies

5 other study(ies) available for cystathionine and Cystine Diathesis

ArticleYear
Transport of L-cystine by cultivated skin fibroblasts of normal subjects and patients with cystinosis.
    Pediatric research, 1976, Volume: 10, Issue:7

    Topics: Amino Acids; Biological Transport; Cell Membrane; Cystathionine; Cystine; Cystinosis; Fibroblasts; Humans; Lysosomes; Skin

1976
Elevated temperature produces cystine depletion in cystinotic fibroblasts.
    Biochimica et biophysica acta, 1986, Dec-10, Volume: 884, Issue:3

    Topics: Cells, Cultured; Cystathionine; Cystine; Cystinosis; Fibroblasts; Humans; Kinetics; Methionine; Skin; Temperature

1986
Binding assays for amino acids. The utilization of a cystine binding protein from Escherichia coli for the determination of acid-soluble cystine in small physiological samples.
    The Journal of biological chemistry, 1974, Oct-10, Volume: 249, Issue:19

    Topics: Amino Acids; Amino Acids, Diamino; Bacterial Proteins; Binding Sites; Binding, Competitive; Carbon Radioisotopes; Chromatography, DEAE-Cellulose; Chromatography, Ion Exchange; Cystathionine; Cystine; Cystinosis; Disulfides; Edetic Acid; Escherichia coli; Ethylmaleimide; Fibroblasts; Humans; Hydrogen-Ion Concentration; Isomerism; Kinetics; Lanthanum; Magnesium; Methods; Osmolar Concentration; Penicillamine; Pimelic Acids; Protein Binding; Radioligand Assay; Receptors, Drug; Sodium Chloride

1974
[Hereditary amino acid metabolism disorders. Indications for early diagnosis].
    Fortschritte der Medizin, 1972, Apr-13, Volume: 90, Issue:11

    Topics: Albinism; Alkaptonuria; Amino Acid Metabolism, Inborn Errors; Amino Acids; Arginine; Cystathionine; Cystinosis; Diagnosis, Differential; Glycine; Hartnup Disease; Histidine; Homocystinuria; Humans; Infant; Infant, Newborn; Maple Syrup Urine Disease; Methods; Methylmalonic Acid; Phenylketonurias; Proline; Propionates; Tyrosine

1972
[Diagnosis of inborn amino acid metabolism errors. Important symptoms and laboratory methods].
    Fortschritte der Medizin, 1972, Apr-13, Volume: 90, Issue:11

    Topics: Albinism; Alkaptonuria; Amino Acid Metabolism, Inborn Errors; Amino Acids; Arginine; Clinical Laboratory Techniques; Cystathionine; Cystinosis; Glycine; Hartnup Disease; Histidine; Homocystinuria; Humans; Maple Syrup Urine Disease; Methods; Methylmalonic Acid; Phenylketonurias; Proline; Propionates; Tyrosine

1972