cystathionine has been researched along with Cystine Diathesis in 6 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 6 (100.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Kaye, CI; Nadler, HL | 1 |
Christensen, HN; Lemons, RM; Pisoni, RL; Thoene, JG | 1 |
Furlong, CE; Oshima, RG; Schneider, JA; Willis, RC | 1 |
Ampola, MG | 1 |
Kroll, S; Toussaint, W; Zebisch, P | 2 |
1 review(s) available for cystathionine and Cystine Diathesis
Article | Year |
---|---|
Phenylketonuria and other disorders of amino acid metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Child, Preschool; Counseling; Cystathionine; Cystinosis; Cystinuria; Diet Therapy; Dietary Proteins; Family; Female; Hartnup Disease; Histidine; Homocystinuria; Humans; Hyperglycemia; Infant; Infant, Newborn; Lysine; Maple Syrup Urine Disease; Ornithine; Phenylketonurias; Pregnancy; Proline; Tyrosine | 1973 |
5 other study(ies) available for cystathionine and Cystine Diathesis
Article | Year |
---|---|
Transport of L-cystine by cultivated skin fibroblasts of normal subjects and patients with cystinosis.
Topics: Amino Acids; Biological Transport; Cell Membrane; Cystathionine; Cystine; Cystinosis; Fibroblasts; Humans; Lysosomes; Skin | 1976 |
Elevated temperature produces cystine depletion in cystinotic fibroblasts.
Topics: Cells, Cultured; Cystathionine; Cystine; Cystinosis; Fibroblasts; Humans; Kinetics; Methionine; Skin; Temperature | 1986 |
Binding assays for amino acids. The utilization of a cystine binding protein from Escherichia coli for the determination of acid-soluble cystine in small physiological samples.
Topics: Amino Acids; Amino Acids, Diamino; Bacterial Proteins; Binding Sites; Binding, Competitive; Carbon Radioisotopes; Chromatography, DEAE-Cellulose; Chromatography, Ion Exchange; Cystathionine; Cystine; Cystinosis; Disulfides; Edetic Acid; Escherichia coli; Ethylmaleimide; Fibroblasts; Humans; Hydrogen-Ion Concentration; Isomerism; Kinetics; Lanthanum; Magnesium; Methods; Osmolar Concentration; Penicillamine; Pimelic Acids; Protein Binding; Radioligand Assay; Receptors, Drug; Sodium Chloride | 1974 |
[Hereditary amino acid metabolism disorders. Indications for early diagnosis].
Topics: Albinism; Alkaptonuria; Amino Acid Metabolism, Inborn Errors; Amino Acids; Arginine; Cystathionine; Cystinosis; Diagnosis, Differential; Glycine; Hartnup Disease; Histidine; Homocystinuria; Humans; Infant; Infant, Newborn; Maple Syrup Urine Disease; Methods; Methylmalonic Acid; Phenylketonurias; Proline; Propionates; Tyrosine | 1972 |
[Diagnosis of inborn amino acid metabolism errors. Important symptoms and laboratory methods].
Topics: Albinism; Alkaptonuria; Amino Acid Metabolism, Inborn Errors; Amino Acids; Arginine; Clinical Laboratory Techniques; Cystathionine; Cystinosis; Glycine; Hartnup Disease; Histidine; Homocystinuria; Humans; Maple Syrup Urine Disease; Methods; Methylmalonic Acid; Phenylketonurias; Proline; Propionates; Tyrosine | 1972 |