cyanides has been researched along with Inborn Errors of Metabolism in 18 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 18 (100.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
INGBAR, SH; JACOB, HS; JANDL, JH | 1 |
WILSON, J | 2 |
Breton-Gorius, J; Coquin, Y; Guichard, J | 1 |
Linnell, JC; Matthews, DM; Wilson, J | 1 |
Bowman, JE; Carson, PE; Frischer, H; Rieckmann, KH | 1 |
Vesell, ES | 1 |
Goldman, AS | 1 |
Kerppola, W | 1 |
Green, WL; Klebanoff, SJ | 1 |
Cooper, MR; Cowan, RJ; Pearce, LA; Richards, F; Spurr, CL | 1 |
Goldfinger, S; Lomtevas, N; Zannoni, VG | 1 |
Klebanoff, SJ | 1 |
Benditt, EP; Page, RC | 1 |
Klebanoff, SJ; Pincus, SH | 1 |
Devadiga, KV; Nayak, KG | 1 |
Adams, JH; Blackwood, W; Wilson, J | 1 |
1 review(s) available for cyanides and Inborn Errors of Metabolism
Article | Year |
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Recent progress in pharmacogenetics.
Topics: Adult; Aged; Alcohol Oxidoreductases; Antipyrine; Asian People; Child, Preschool; Cholinesterases; Cyanides; Dicumarol; Diseases in Twins; Drug Hypersensitivity; Erythrocytes; Favism; Female; Glucosephosphate Dehydrogenase Deficiency; Hemoglobins; Humans; Isoniazid; Liver; Male; Metabolism, Inborn Errors; Middle Aged; Pharmacogenetics; Phenylbutazone; Phenylthiourea; Phenytoin; Pregnancy; Primaquine; Twins; Warfarin | 1969 |
17 other study(ies) available for cyanides and Inborn Errors of Metabolism
Article | Year |
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OXIDATIVE HEMOLYSIS AND ERYTHROCYTE METABOLISM IN HEREDITARY ACATALASIA.
Topics: Acatalasia; Anemia; Anemia, Hemolytic; Ascorbic Acid; Azides; Catalase; Cyanides; Erythrocyte Aging; Erythrocytes; Ethylmaleimide; Genetics, Medical; Glucose; Glucosephosphate Dehydrogenase Deficiency; Glucosephosphates; Glutathione; Hemoglobins; Hemolysis; Hexosephosphates; Humans; Metabolism, Inborn Errors; Methemoglobin; Peroxides; Pharmacology; Phenylhydrazines; Primaquine; Sulfhemoglobin; Sulfhydryl Compounds | 1965 |
SKELETAL MANIFESTATIONS IN LEBER'S HEREDITARY OPTIC ATROPHY. A POSSIBLE DISORDER OF CYANIDE METABOLISM.
Topics: Arachnodactyly; Bone Diseases; Congenital Abnormalities; Cyanides; Fractures, Bone; Genetics, Medical; Humans; Kyphosis; Marfan Syndrome; Metabolism, Inborn Errors; Musculoskeletal System; Optic Atrophy; Optic Atrophy, Hereditary, Leber | 1965 |
Leber's optic neuropathy.
Topics: Action Potentials; Adolescent; Adult; Child; Child, Preschool; Cyanides; Female; Humans; Male; Metabolism, Inborn Errors; Middle Aged; Optic Atrophy; Optic Nerve; Scotoma; Syndrome; Vision Disorders | 1980 |
[Peroxidase activity of neutrophil granules in two cases of congenital myeloperoxidase deficiency].
Topics: Basophils; Catalase; Cyanides; Cytoplasmic Granules; Eosinophils; Histocytochemistry; Humans; Hydrogen-Ion Concentration; Metabolism, Inborn Errors; Microbodies; Microscopy, Electron; Monocytes; Neutrophils; Peroxidase; Peroxidases | 1975 |
Plasma-cobalamins in neuro-ophthalmological diseases.
Topics: Adult; Amblyopia; Child; Child, Preschool; Cyanides; Female; Humans; Male; Metabolism, Inborn Errors; Neuritis; Optic Atrophy; Scotoma; Smoking; Vitamin B 12; Vitamin B 12 Deficiency | 1971 |
Visual test for erythrocytic glucose-6-phosphate dehydrogenase, 6-phosphogluconic dehydrogenase, and glutathione reductase deficiencies.
Topics: Colorimetry; Cyanides; Erythrocytes; Female; Glucosephosphate Dehydrogenase; Glucosephosphate Dehydrogenase Deficiency; Glutathione Reductase; Hemoglobins; Hemolysis; Humans; Indophenol; Male; Metabolism, Inborn Errors; Methemoglobin; Methods; NADP; Oxidation-Reduction; Phenols; Phosphogluconate Dehydrogenase | 1973 |
Effect of ACTH on enzymatic defect produced in vivo by a competitive inhibitor of 3-beta-hydroxysteroid dehydrogenase.
Topics: Adrenal Glands; Adrenal Hyperplasia, Congenital; Adrenocorticotropic Hormone; Androstanes; Animals; Carbon Isotopes; Cyanides; Disease Models, Animal; Female; Hydroxysteroid Dehydrogenases; Isomerases; Metabolism, Inborn Errors; Organ Size; Oxazoles; Pituitary-Adrenal System; Rats | 1970 |
On the occurence of the alpha isomer of diphosphopyridine nucleotide and on the dehydrogenases activated by it, in leucocytes and neoplastic tissues. A metabolic error.
Topics: Animals; Chromatography, Paper; Cyanides; Humans; L-Lactate Dehydrogenase; Leukocytes; Malate Dehydrogenase; Metabolism, Inborn Errors; NAD; NADP; Neoplasms; Neoplasms, Experimental; Oxidoreductases; Rats | 1968 |
Degradation of thyroid hormones by phagocytosing human leukocytes.
Topics: Ascorbic Acid; Azides; Chromatography, Gel; Chromatography, Paper; Cyanides; Electrophoresis, Paper; Humans; Hydrogen Peroxide; In Vitro Techniques; Iodine Isotopes; Lactobacillus acidophilus; Leukocytes; Metabolism, Inborn Errors; Methimazole; Oxygen; Peroxidases; Phagocyte Bactericidal Dysfunction; Phagocytosis; Propylthiouracil; Thyroid Hormones; Thyroxine; Triiodothyronine | 1973 |
Familial spinocerebellar degeneration, hemolytic anemia, and glutathione deficiency.
Topics: Adult; Amino Acids; Anemia, Hemolytic; Ascorbic Acid; Cerebellar Diseases; Cyanides; Electroencephalography; Electromyography; Erythrocytes; Female; Glutathione; Humans; Leukocytes; Male; Metabolism, Inborn Errors; Muscles; Neural Conduction; Peptide Synthases; Potassium; Renal Aminoacidurias; Spinal Cord Diseases; Syndrome | 1974 |
Oxidation of homogentisic acid to ochronotic pigment in connective tissue.
Topics: Acetates; Albinism; Animals; Benzene Derivatives; Carbamates; Catechol Oxidase; Connective Tissue; Copper; Cyanides; Guinea Pigs; Male; Metabolism, Inborn Errors; Models, Chemical; Ochronosis; Organ Specificity; Phenylacetates; Pigments, Biological; Quinones; Skin; Spectrophotometry | 1969 |
Myeloperoxidase: contribution to the microbicidal activity of intact leukocytes.
Topics: Azides; Candida; Chronic Disease; Cyanides; Granuloma; Humans; Hydrogen Peroxide; Infant, Newborn; Infant, Newborn, Diseases; Infections; Lactobacillus acidophilus; Leukocytes; Lymphadenitis; Male; Metabolism, Inborn Errors; Peroxidases; Staphylococcus | 1970 |
Diseases of connective and vascular tissues. IV. The molecular basis for lathyrism.
Topics: Acetaldehyde; Amino Acid Oxidoreductases; Aminopropionitrile; Animals; Carbon Isotopes; Collagen; Collagen Diseases; Cyanides; Elastin; Lathyrism; Lysine; Metabolism, Inborn Errors; Protein Binding; Protein Denaturation; Rats | 1972 |
Hydrogen peroxide utilization in myeloperoxidase-deficient leukocytes: a possible microbicidal control mechanism.
Topics: Azides; Carbon Dioxide; Catalase; Culture Techniques; Cyanides; Diabetes Mellitus; Formates; Glucose; Hexosephosphates; Humans; Hydrogen Peroxide; Latex; Leukocytes; Male; Metabolism, Inborn Errors; Microspheres; Oxidation-Reduction; Peroxidases; Phagocytosis | 1971 |
Hereditary optic atrophy (Leber's disease).
Topics: Adolescent; Cyanides; Humans; Male; Metabolism, Inborn Errors; Optic Atrophy; Smoking | 1969 |
Leber's hereditary optic atrophy: a possible defect of cyanide metabolism.
Topics: Biotransformation; Blood; Brain; Cyanides; Female; Humans; Liver; Male; Metabolism, Inborn Errors; Optic Atrophy; Smoking; Thiocyanates; Transferases; Urine | 1965 |
Further clinical and pathological observations on Leber's optic atrophy.
Topics: Adult; Aged; Cyanides; Female; Humans; Male; Metabolism, Inborn Errors; Microscopy; Middle Aged; Optic Atrophy; Smoking; Urinary Tract Infections | 1966 |