Page last updated: 2024-10-17

creatine and Inborn Urea Cycle Disorder

creatine has been researched along with Inborn Urea Cycle Disorder in 6 studies

Research Excerpts

ExcerptRelevanceReference
"Creatine synthesis is a major component of arginine metabolism, amounting to more than 20% of the dietary intake of this amino acid."1.36Creatine metabolism and the urea cycle. ( Brosnan, JT; Brosnan, ME, 2010)

Research

Studies (6)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's6 (100.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Auray-Blais, C1
Maranda, B1
Lavoie, P1
Joncquel-Chevalier Curt, M1
Voicu, PM1
Fontaine, M1
Dessein, AF1
Porchet, N1
Mention-Mulliez, K1
Dobbelaere, D1
Soto-Ares, G1
Cheillan, D1
Vamecq, J1
Brosnan, JT1
Brosnan, ME1
Cederbaum, S1
Boenzi, S1
Pastore, A1
Martinelli, D1
Goffredo, BM1
Boiani, A1
Rizzo, C1
Dionisi-Vici, C1
Gropman, AL1

Reviews

2 reviews available for creatine and Inborn Urea Cycle Disorder

ArticleYear
Creatine biosynthesis and transport in health and disease.
    Biochimie, 2015, Volume: 119

    Topics: Amidinotransferases; Amino Acid Metabolism, Inborn Errors; Amino Acid Transport Systems, Basic; AMP-

2015
Patterns of brain injury in inborn errors of metabolism.
    Seminars in pediatric neurology, 2012, Volume: 19, Issue:4

    Topics: Animals; Biological Transport; Blood-Brain Barrier; Brain; Brain Diseases, Metabolic, Inborn; Creati

2012

Other Studies

4 other studies available for creatine and Inborn Urea Cycle Disorder

ArticleYear
High-throughput tandem mass spectrometry multiplex analysis for newborn urinary screening of creatine synthesis and transport disorders, Triple H syndrome and OTC deficiency.
    Clinica chimica acta; international journal of clinical chemistry, 2014, Sep-25, Volume: 436

    Topics: Biomarkers; Creatine; Creatinine; Filtration; Glycine; Humans; Hyperammonemia; Infant, Newborn; Orni

2014
Creatine metabolism and the urea cycle.
    Molecular genetics and metabolism, 2010, Volume: 100 Suppl 1

    Topics: Animals; Creatine; Glycine; Humans; Kidney; Urea; Urea Cycle Disorders, Inborn

2010
"Overcoming barriers: new developments and future directions for urea cycle disorders.". Introduction.
    Molecular genetics and metabolism, 2010, Volume: 100 Suppl 1

    Topics: Creatine; Humans; Hyperammonemia; Urea Cycle Disorders, Inborn

2010
Creatine metabolism in urea cycle defects.
    Journal of inherited metabolic disease, 2012, Volume: 35, Issue:4

    Topics: Adolescent; Adult; Amidinotransferases; Arginine; Child; Child, Preschool; Creatine; Female; Guanidi

2012