Page last updated: 2024-10-17

creatine and BH4 Deficiency

creatine has been researched along with BH4 Deficiency in 11 studies

Research Excerpts

ExcerptRelevanceReference
"Phenylketonuria is characterized by a variable degree of mental retardation and other neurological features whose mechanisms are not fully understood."1.38Pyruvate and creatine prevent oxidative stress and behavioral alterations caused by phenylalanine administration into hippocampus of rats. ( Berti, SL; Castro, FL; Dutra-Filho, CS; Garcia, C; Moraes, TB; Nasi, GM; Nunes, ML; Rojas, DB; Wannmacher, CM, 2012)
"Six treated adult patients with phenylketonuria were investigated repeatedly following reinstitution of a Phe-restricted diet."1.29In-vivo NMR spectroscopy in patients with phenylketonuria: changes of cerebral phenylalanine levels under dietary treatment. ( Koch, HG; Möller, HE; Peters, PE; Ullrich, K; Vermathen, P; Weglage, J, 1995)

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19901 (9.09)18.7374
1990's3 (27.27)18.2507
2000's2 (18.18)29.6817
2010's5 (45.45)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Mezzomo, NJ1
Becker Borin, D1
Ianiski, F1
Dotto Fontana, B1
Diehl de Franceschi, I1
Bolzan, J1
Garcez, R1
Grings, M1
Parmeggiani, B1
da Silva Fernandes, L1
de Almeida Vaucher, R1
Leipnitz, G1
Duval Wannmacher, CM1
Cielo Rech, V1
Bortoluzzi, VT1
Brust, L1
Preissler, T1
de Franceschi, ID1
Wannmacher, CMD1
Dos Reis, EA1
Rieger, E1
de Souza, SS1
Rasia-Filho, AA1
Wannmacher, CM2
Sempere, A1
Arias, A1
Farré, G1
García-Villoria, J1
Rodríguez-Pombo, P1
Desviat, LR1
Merinero, B1
García-Cazorla, A1
Vilaseca, MA1
Ribes, A1
Artuch, R1
Campistol, J1
Berti, SL1
Nasi, GM1
Garcia, C1
Castro, FL1
Nunes, ML1
Rojas, DB1
Moraes, TB1
Dutra-Filho, CS1
Sijens, PE1
Oudkerk, M1
Reijngoud, DJ1
Leenders, KL1
de Valk, HW1
van Spronsen, FJ1
Yokoyama, Y1
Tsuji, S1
Sato, H1
Johannik, K1
Van Hecke, P1
François, B1
Marchal, G1
Smet, MH1
Jaeken, J1
Breysem, L1
Wilms, G1
Baert, AL1
Hájek, M1
Hejcmanová, L1
Prádný, J1
Möller, HE1
Vermathen, P1
Ullrich, K1
Weglage, J1
Koch, HG1
Peters, PE1
Kennaway, NG1
Buist, NR1
Fellman, JH1

Other Studies

11 other studies available for creatine and BH4 Deficiency

ArticleYear
Creatine nanoliposome reverts the HPA-induced damage in complex II-III activity of the rats' cerebral cortex.
    Molecular biology reports, 2019, Volume: 46, Issue:6

    Topics: Animals; Brain; Cerebral Cortex; Creatine; Creatine Kinase; Energy Metabolism; Female; Hippocampus;

2019
Creatine plus pyruvate supplementation prevents oxidative stress and phosphotransfer network disturbances in the brain of rats subjected to chemically-induced phenylketonuria.
    Metabolic brain disease, 2019, Volume: 34, Issue:6

    Topics: Animals; Antioxidants; Blood-Brain Barrier; Brain; Creatine; Disease Models, Animal; Energy Metaboli

2019
Effects of a co-treatment with pyruvate and creatine on dendritic spines in rat hippocampus and posterodorsal medial amygdala in a phenylketonuria animal model.
    Metabolic brain disease, 2013, Volume: 28, Issue:3

    Topics: Amygdala; Animals; CA1 Region, Hippocampal; Cell Count; Coloring Agents; Creatine; Dendritic Spines;

2013
Study of inborn errors of metabolism in urine from patients with unexplained mental retardation.
    Journal of inherited metabolic disease, 2010, Volume: 33, Issue:1

    Topics: Adenylosuccinate Lyase; Adolescent; Adult; Aged; Carnitine; Child; Child, Preschool; Chromium; Cohor

2010
Pyruvate and creatine prevent oxidative stress and behavioral alterations caused by phenylalanine administration into hippocampus of rats.
    Metabolic brain disease, 2012, Volume: 27, Issue:1

    Topics: Animals; Antioxidants; Creatine; Energy Metabolism; Exploratory Behavior; Habituation, Psychophysiol

2012
1H MR chemical shift imaging detection of phenylalanine in patients suffering from phenylketonuria (PKU).
    European radiology, 2004, Volume: 14, Issue:10

    Topics: Adolescent; Adult; Aspartic Acid; Brain Chemistry; Cerebral Ventricles; Choline; Creatine; Female; H

2004
Simultaneous determination of creatinine, creatine, and UV-absorbing amino acids using dual-mode gradient low-capacity cation-exchange chromatography.
    Journal of chromatography. A, 2005, Aug-26, Volume: 1085, Issue:1

    Topics: Amino Acids; Cation Exchange Resins; Chromatography, Ion Exchange; Creatine; Creatinine; Humans; Hyd

2005
Localized brain proton NMR spectroscopy in young adult phenylketonuria patients.
    Magnetic resonance in medicine, 1994, Volume: 31, Issue:1

    Topics: Adolescent; Adult; Aspartic Acid; Brain Chemistry; Choline; Creatine; Female; Humans; Magnetic Reson

1994
Proton in vivo spectroscopy of patients with hyperphenylalaninaemia.
    Neuropediatrics, 1993, Volume: 24, Issue:2

    Topics: Adult; Aspartic Acid; Biopterins; Brain; Brain Chemistry; Brain Diseases; Child; Choline; Creatine;

1993
In-vivo NMR spectroscopy in patients with phenylketonuria: changes of cerebral phenylalanine levels under dietary treatment.
    Neuropediatrics, 1995, Volume: 26, Issue:4

    Topics: Adolescent; Adult; Blood-Brain Barrier; Creatine; Diet; Humans; Magnetic Resonance Imaging; Occipita

1995
The origin of urinary p-hydroxyphenylpyruvate in a patient with hepatic cytosol tyrosine aminotransferase deficiency.
    Clinica chimica acta; international journal of clinical chemistry, 1972, Volume: 41

    Topics: Amino Acid Metabolism, Inborn Errors; Creatine; Creatinine; Cytoplasm; Humans; Imidazoles; Liver; Ph

1972