creatine has been researched along with Arginino Succinase Deficiency in 3 studies
| Excerpt | Relevance | Reference |
|---|---|---|
| " The goal of this study was to understand the effect on the known toxic metabolite ASA and the assumed toxic metabolite guanidinosuccinic acid (GSA) on developing brain cells, and to evaluate the potential role of creatine (Cr) supplementation, as it was described protective for brain cells exposed to ammonia." | 2.61 | Argininosuccinate neurotoxicity and prevention by creatine in argininosuccinate lyase deficiency: An in vitro study in rat three-dimensional organotypic brain cell cultures. ( Braissant, O; Diez-Fernandez, C; Diserens, G; Häberle, J; Henry, H; Hertig, D; Loup, M; Nuoffer, JM; Vermathen, P, 2019) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 2 (66.67) | 29.6817 |
| 2010's | 1 (33.33) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Diez-Fernandez, C | 1 |
| Hertig, D | 1 |
| Loup, M | 1 |
| Diserens, G | 1 |
| Henry, H | 1 |
| Vermathen, P | 1 |
| Nuoffer, JM | 1 |
| Häberle, J | 2 |
| Braissant, O | 1 |
| van Spronsen, FJ | 1 |
| Reijngoud, DJ | 1 |
| Verhoeven, NM | 1 |
| Soorani-Lunsing, RJ | 1 |
| Jakobs, C | 1 |
| Sijens, PE | 1 |
| Roze, E | 1 |
| Azuar, C | 1 |
| Menuel, C | 1 |
| Guillevin, R | 1 |
1 review available for creatine and Arginino Succinase Deficiency
| Article | Year |
|---|---|
Argininosuccinate neurotoxicity and prevention by creatine in argininosuccinate lyase deficiency: An in vitro study in rat three-dimensional organotypic brain cell cultures.
Topics: Animals; Argininosuccinic Acid; Argininosuccinic Aciduria; Brain; Cells, Cultured; Creatine; Humans; | 2019 |
2 other studies available for creatine and Arginino Succinase Deficiency
| Article | Year |
|---|---|
High cerebral guanidinoacetate and variable creatine concentrations in argininosuccinate synthetase and lyase deficiency: implications for treatment?
Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Argininosuccinate Synthase; Argininosuccinic Aciduri | 2006 |
Usefulness of magnetic resonance spectroscopy in urea cycle disorders.
Topics: Adult; Argininosuccinic Aciduria; Brain Diseases, Metabolic; Creatine; Female; Humans; Magnetic Reso | 2007 |