concanavalin-a and Glycogen-Storage-Disease-Type-II

concanavalin-a has been researched along with Glycogen-Storage-Disease-Type-II* in 1 studies

Other Studies

1 other study(ies) available for concanavalin-a and Glycogen-Storage-Disease-Type-II

ArticleYear
Genetic relationship between lysosomal and lamellar body-specific alpha-glucosidases in human lung.
    Biochimica et biophysica acta, 1986, Sep-12, Volume: 878, Issue:2

    In lamellar bodies isolated from adult human lung at least two acid alpha-glucosidases are present: one similar to the lung lysosomal alpha-glucosidase, and another lamellar body-specific isoenzyme. In the present study we measured the activity of this lamellar body-specific alpha-glucosidase and of lysosomal alpha-glucosidase in a patient with an inherited deficiency of lysosomal alpha-glucosidase. The activity of the lamellar body-specific alpha-glucosidase was not affected in the patient, whereas the lysosomal alpha-glucosidase activity was strongly depressed. The results strongly suggest that the lysosomal alpha-glucosidase and the lamellar body-specific alpha-glucosidase are different gene products.

    Topics: alpha-Glucosidases; Concanavalin A; Glycogen; Glycogen Storage Disease; Glycogen Storage Disease Type II; Humans; Hydrogen-Ion Concentration; Lung; Lysosomes

1986