coenzyme a has been researched along with BCKD Deficiency in 5 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 5 (100.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Goedde, HW; Singh, S; Willers, I | 1 |
Elsas, LJ; Pask, BA; Perl, DP; Truster, S; Wheeler, FB | 1 |
Blume, KG; Goedde, HW; Lang, K; Möhlenbeck, F; Rotthauwe, HW; Simon, HA | 1 |
Danner, DJ; Elsas, LJ; Pask, BA; Priest, JH; Wheeler, FB | 1 |
Angielski, S; Lysiak, W; Stepiński, J | 1 |
5 other study(ies) available for coenzyme a and BCKD Deficiency
Article | Year |
---|---|
Heterogeneity in maple syrup urine disease: aspects of cofactor requirement and complementation in cultured fibroblasts.
Topics: Caproates; Carboxy-Lyases; Cells, Cultured; Coenzyme A; Decarboxylation; Fibroblasts; Humans; Hybrid Cells; Keto Acids; Maple Syrup Urine Disease; NAD; Thiamine Pyrophosphate; Valerates | 1977 |
Classical maple syrup urine disease: cofactor resistance.
Topics: Amino Acids; Carbon Isotopes; Cells, Cultured; Coenzyme A; Coenzymes; Female; Fibroblasts; Flavin-Adenine Dinucleotide; Genetics, Medical; Humans; Infant, Newborn; Isoleucine; Keto Acids; Leucine; Male; Maple Syrup Urine Disease; NAD; Pyridoxal Phosphate; Pyruvates; Skin; Thiamine Pyrophosphate; Thioctic Acid; Valine | 1972 |
[Studies on "branched chain oxoacid aciduria" (maple syrup diseases)].
Topics: Child, Preschool; Coenzyme A; D-Amino-Acid Oxidase; Female; Humans; Isoleucine; Leucine; Male; Maple Syrup Urine Disease; Oxidoreductases; Valine | 1966 |
Maple syrup urine disease: coenzyme function and prenatal monitoring.
Topics: Adult; Amino Acids; Amniotic Fluid; Carbon Dioxide; Carbon Radioisotopes; Cells, Cultured; Coenzyme A; Decarboxylation; Fasting; Female; Fibroblasts; Genotype; Heterozygote; Humans; Infant, Newborn; Isoleucine; Leucine; Maple Syrup Urine Disease; Maternal-Fetal Exchange; Pregnancy; Prenatal Diagnosis; Radioimmunoassay; Valine | 1974 |
Inhibition of alpha-oxoglutarate and pyruvate oxidation by alpha-oxoderivatives of leucine and valine in rat tissues.
Topics: Animals; Brain; Caproates; Citrates; Coenzyme A; Humans; Keto Acids; Ketoglutaric Acids; Kidney; Kinetics; Leucine; Malates; Maple Syrup Urine Disease; Metabolism; Mitochondria; Mitochondria, Liver; Mitochondria, Muscle; Myocardium; Oxidoreductases; Pyruvates; Rats; Valerates; Valine; Vibration | 1970 |