Page last updated: 2024-08-17

coenzyme a and BCKD Deficiency

coenzyme a has been researched along with BCKD Deficiency in 5 studies

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19905 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Goedde, HW; Singh, S; Willers, I1
Elsas, LJ; Pask, BA; Perl, DP; Truster, S; Wheeler, FB1
Blume, KG; Goedde, HW; Lang, K; Möhlenbeck, F; Rotthauwe, HW; Simon, HA1
Danner, DJ; Elsas, LJ; Pask, BA; Priest, JH; Wheeler, FB1
Angielski, S; Lysiak, W; Stepiński, J1

Other Studies

5 other study(ies) available for coenzyme a and BCKD Deficiency

ArticleYear
Heterogeneity in maple syrup urine disease: aspects of cofactor requirement and complementation in cultured fibroblasts.
    Clinical genetics, 1977, Volume: 11, Issue:4

    Topics: Caproates; Carboxy-Lyases; Cells, Cultured; Coenzyme A; Decarboxylation; Fibroblasts; Humans; Hybrid Cells; Keto Acids; Maple Syrup Urine Disease; NAD; Thiamine Pyrophosphate; Valerates

1977
Classical maple syrup urine disease: cofactor resistance.
    Metabolism: clinical and experimental, 1972, Volume: 21, Issue:10

    Topics: Amino Acids; Carbon Isotopes; Cells, Cultured; Coenzyme A; Coenzymes; Female; Fibroblasts; Flavin-Adenine Dinucleotide; Genetics, Medical; Humans; Infant, Newborn; Isoleucine; Keto Acids; Leucine; Male; Maple Syrup Urine Disease; NAD; Pyridoxal Phosphate; Pyruvates; Skin; Thiamine Pyrophosphate; Thioctic Acid; Valine

1972
[Studies on "branched chain oxoacid aciduria" (maple syrup diseases)].
    Medizinische Klinik, 1966, Dec-30, Volume: 61, Issue:52

    Topics: Child, Preschool; Coenzyme A; D-Amino-Acid Oxidase; Female; Humans; Isoleucine; Leucine; Male; Maple Syrup Urine Disease; Oxidoreductases; Valine

1966
Maple syrup urine disease: coenzyme function and prenatal monitoring.
    Metabolism: clinical and experimental, 1974, Volume: 23, Issue:6

    Topics: Adult; Amino Acids; Amniotic Fluid; Carbon Dioxide; Carbon Radioisotopes; Cells, Cultured; Coenzyme A; Decarboxylation; Fasting; Female; Fibroblasts; Genotype; Heterozygote; Humans; Infant, Newborn; Isoleucine; Leucine; Maple Syrup Urine Disease; Maternal-Fetal Exchange; Pregnancy; Prenatal Diagnosis; Radioimmunoassay; Valine

1974
Inhibition of alpha-oxoglutarate and pyruvate oxidation by alpha-oxoderivatives of leucine and valine in rat tissues.
    Acta biochimica Polonica, 1970, Volume: 17, Issue:2

    Topics: Animals; Brain; Caproates; Citrates; Coenzyme A; Humans; Keto Acids; Ketoglutaric Acids; Kidney; Kinetics; Leucine; Malates; Maple Syrup Urine Disease; Metabolism; Mitochondria; Mitochondria, Liver; Mitochondria, Muscle; Myocardium; Oxidoreductases; Pyruvates; Rats; Valerates; Valine; Vibration

1970