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coenzyme a and Acidosis

coenzyme a has been researched along with Acidosis in 39 studies

Research

Studies (39)

TimeframeStudies, this research(%)All Research%
pre-199039 (100.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
WEISS, L; WIELAND, O1
HIBBITT, KG1
Isselbacher, KJ; Tanaka, K1
Bussman, YL; DeVivo, DC; Haymond, MW; Leckie, MP; McDougal, DB; Pagliara, AS1
Ando, T; Kilroy, A; Nyhan, WL; Sweetman, L; Wadlington, WB1
Marsac, C; Stansbie, D; Wallace, SJ1
Dugan, RE; Gilles, BA; Hoganson, GE; Schmidt, MJ; Shug, AL; Steele, J1
Goldstein, L; Tullson, PC1
Callaghan, P; Newman, CG; Wilson, BD; Young, L1
Hsia, YE; Rosenberg, LE; Scully, KJ1
Bau, DC; Gompertz, D; Hughes, EA; Peters, TJ; Storrs, CN1
Cornblath, M; Tildon, JT1
Ackermann, RH; Bässler, KH; Schönerstedt, B; Wagner, K1
Erfle, JD; Sauer, F1
Lemieux, G; Lussier, Y; Martin, P; Plante, GE; Robitaille, P; Vinay, P1
Dierich, C; Huth, W; Seubert, W; von Oeynhausen, V1
Gerald, PS; Kang, ES; Snodgrass, PJ1
Hillman, RE; Keating, JP1
Brandt, IK; Clement, DH; Hsia, YE; Provence, SA1
Cunningham, NF; Patterson, DS1
David, M1
Assan, R1
Williamson, DH1
Boisse, J; Charpentier, C; Perelman, R; Pousset, JP; Rudler, JC1
Blass, JP; Schulman, JD1
Bressler, R; Katz, R; Wittels, B1
Budd, MA; Efron, ML; Isselbacher, KJ; Tanaka, K1
Isselbacher, KJ; Miller, EM; Tanaka, K1
Bremer, J2
Binns, MR; Erfle, JD; Sauer, F1
Hsia, YE; Lilljeqvist, AC; Rosenberg, LE2
Ando, T; Barnes, ND; Donnell, GN; Nyhan, WL; Rasmussen, K1
Hsia, YE; Lilljeqvist, A; Rosenberg, LE1
Lynen, F; Young, DL1

Reviews

5 review(s) available for coenzyme a and Acidosis

ArticleYear
Disorders of the pyruvate dehydrogenase complex.
    Journal of inherited metabolic disease, 1986, Volume: 9, Issue:2

    Topics: Acetyl Coenzyme A; Acetyltransferases; Acidosis; Brain; Carbon Dioxide; Child; Child, Preschool; Coenzyme A; Cranial Nerves; Dihydrolipoamide Dehydrogenase; Dihydrolipoyllysine-Residue Acetyltransferase; Facial Bones; Feedback; Humans; Lactates; Lactic Acid; Leigh Disease; Molecular Weight; Movement Disorders; NAD; Nervous System Diseases; Phosphoric Monoester Hydrolases; Pyruvate Decarboxylase; Pyruvate Dehydrogenase Complex; Pyruvate Dehydrogenase Complex Deficiency Disease; Pyruvates; Pyruvic Acid; Spectrophotometry

1986
Acetoacetate production in starvation ketosis.
    Nutrition reviews, 1968, Volume: 26, Issue:5

    Topics: Acetoacetates; Acidosis; Animals; Coenzyme A; Fatty Acids; Liver; Oxidation-Reduction; Rats; Starvation

1968
Nutritional disorders of ruminants.
    The Proceedings of the Nutrition Society, 1969, Volume: 28, Issue:2

    Topics: Acidosis; Adrenal Cortex Hormones; Animals; Cattle; Cattle Diseases; Coenzyme A; Epinephrine; Female; Gluconeogenesis; Growth Hormone; Insulin; Lipid Metabolism; Liver; Pre-Eclampsia; Pregnancy; Sheep; Sheep Diseases

1969
[Methylmalonyl acidemia].
    Pediatrie, 1968, Volume: 23, Issue:6

    Topics: Acidosis; Coenzyme A; Enzyme Repression; Humans; Isomerases; Malonates

1968
Physiological ketosis, or why ketone bodies?
    Postgraduate medical journal, 1971, Volume: 47

    Topics: Acidosis; Acyltransferases; Animals; Brain; Coenzyme A; Fatty Acids, Nonesterified; Humans; Hydroxybutyrate Dehydrogenase; Ketone Bodies; Organ Specificity; Physical Exertion; Rats; Triglycerides

1971

Other Studies

34 other study(ies) available for coenzyme a and Acidosis

ArticleYear
Increase in liver acetyl-coenzyme A during ketosis.
    Biochemical and biophysical research communications, 1963, Feb-18, Volume: 10

    Topics: Acetyl Coenzyme A; Acidosis; Animals; Coenzyme A; Diabetes Mellitus, Experimental; Humans; Ketosis; Liver

1963
LEVELS OF COENZYME A IN THE LIVER OF NORMAL COWS AND OF COWS SUFFERING FROM PRIMARY KETOSIS.
    Nature, 1964, Oct-10, Volume: 204

    Topics: Acidosis; Animals; Cattle; Cattle Diseases; Coenzyme A; Female; Glutarates; Humans; Ketosis; Lactation; Liver; Proteins; Pyruvates

1964
The isolation and identification of N-isovalerylglycine from urine of patients with isovaleric acidemia.
    The Journal of biological chemistry, 1967, Jun-25, Volume: 242, Issue:12

    Topics: Acidosis; Amino Acids; Chemistry, Clinical; Child; Child, Preschool; Chromatography, Gas; Coenzyme A; Female; Humans; In Vitro Techniques; Leucine; Magnetic Resonance Spectroscopy; Male; Spectrum Analysis; Valerates

1967
The clinical and biochemical implications of pyruvate carboxylase deficiency.
    The Journal of clinical endocrinology and metabolism, 1977, Volume: 45, Issue:6

    Topics: Acidosis; Amino Acids; Bicarbonates; Blood Glucose; Carbohydrate Metabolism, Inborn Errors; Citrates; Citric Acid Cycle; Coenzyme A; Female; Fibroblasts; Humans; Infant; Lactates; Liver; Muscles; Pyruvate Carboxylase Deficiency Disease

1977
Hyperglycinemia and propionyl coA carboxylase deficiency and episodic severe illness without consistent ketosis.
    The Journal of pediatrics, 1975, Volume: 86, Issue:5

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Amino Acids; Citrates; Coenzyme A; Creatinine; Crotonates; Glutamates; Glutamine; Glycine; Humans; Infant; Ketone Bodies; Ketosis; Ligases; Male; Propionates; Pyrrolidonecarboxylic Acid

1975
High-performance liquid chromatography of coenzyme A esters formed by transesterification of short-chain acylcarnitines: diagnosis of acidemias by urinary analysis.
    Analytical biochemistry, 1987, Feb-01, Volume: 160, Issue:2

    Topics: Acidosis; Carnitine; Chromatography, High Pressure Liquid; Coenzyme A; Esterification; Humans

1987
Effects of acute acid-base changes on rat renal pyruvate dehydrogenase. Renal pyruvate dehydrogenase during acid-base alterations.
    Enzyme, 1987, Volume: 37, Issue:3

    Topics: Acid-Base Imbalance; Acidosis; Acidosis, Respiratory; Adenine Nucleotides; Alkalosis; Animals; Coenzyme A; Kidney; Male; NAD; Pyruvate Dehydrogenase Complex; Rats; Rats, Inbred Strains

1987
Neonatal death associated with isovalericacidaemia.
    Lancet (London, England), 1967, Aug-26, Volume: 2, Issue:7513

    Topics: Acidosis; Bicarbonates; Chromatography; Chromatography, Gas; Coenzyme A; Electrolytes; Fatty Acids; Fatty Acids, Nonesterified; Glucose; Hemorrhage; Humans; Hypocalcemia; Infant Mortality; Infant, Newborn; Leucine; Male; Metabolism, Inborn Errors; Valerates

1967
Defective propionate carboxylation in ketotic hyperglycinaemia.
    Lancet (London, England), 1969, Apr-12, Volume: 1, Issue:7598

    Topics: Acidosis; Carbon Isotopes; Child; Coenzyme A; Female; Glycine; Humans; Infant, Newborn; Leukocytes; Malonates; Propionates; Succinates

1969
Localisation of enzymic defect in propionicacidaemia.
    Lancet (London, England), 1970, May-30, Volume: 1, Issue:7657

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Amino Acids; Citric Acid Cycle; Coenzyme A; Consanguinity; Erythrocytes; Esters; Fatty Acids; Glycine; Humans; Hyperglycemia; Infant, Newborn; Ketones; Ligases; Male; Malonates; Mitochondria; Pedigree; Propionates

1970
Succinyl-CoA: 3-ketoacid CoA-transferase deficiency. A cause for ketoacidosis in infancy.
    The Journal of clinical investigation, 1972, Volume: 51, Issue:3

    Topics: Acidosis; Acyltransferases; Adipates; Autopsy; Brain; Cell Fractionation; Coenzyme A; Culture Techniques; Fibroblasts; Glucose; Glyceraldehyde-3-Phosphate Dehydrogenases; Glycolysis; Humans; Infant, Newborn; Keto Acids; Kidney; Male; Metabolism, Inborn Errors; Muscles; Phosphofructokinase-1; Phosphopyruvate Hydratase; Pyruvate Kinase; Skin; Succinates; Sulfurtransferases

1972
Enzymatic changes associated with ketosis in long standing diabetes and prolonged starvation of rats.
    Hoppe-Seyler's Zeitschrift fur physiologische Chemie, 1973, Volume: 354, Issue:1

    Topics: Acetoacetates; Acidosis; Animals; Blood Glucose; Coenzyme A; Diabetes Mellitus; Hydroxybutyrate Dehydrogenase; Insulin; Ketone Bodies; Ketosis; Ligases; Male; Manometry; Mitochondria, Muscle; Oxygen Consumption; Rats; Starvation; Streptozocin; Succinates; Sulfurtransferases; Time Factors

1973
Acetyl coenzyme A and acetylcarnitine concentration and turnover rates in muscle and liver of the ketotic rat and guinea pig.
    The Journal of biological chemistry, 1967, May-10, Volume: 242, Issue:9

    Topics: Acetates; Acidosis; Acyltransferases; Animals; Carbon Dioxide; Carbon Isotopes; Carnitine; Coenzyme A; Fasting; Guinea Pigs; In Vitro Techniques; Liver; Malate Dehydrogenase; Malates; Muscles; NAD; Oxaloacetates; Pyruvates; Rats

1967
The effect of ketone bodies on renal ammoniogenesis.
    The Journal of clinical investigation, 1971, Volume: 50, Issue:9

    Topics: Acetoacetates; Acidosis; Ammonia; Ammonium Chloride; Animals; Bicarbonates; Citric Acid Cycle; Coenzyme A; Depression, Chemical; Dogs; Female; Glutamates; Glutamine; Hydrogen-Ion Concentration; Hydroxybutyrates; Ketoglutaric Acids; Ketone Bodies; Kidney; Kidney Tubules; Lactates; Mannitol; Mitochondria; NAD; Oxaloacetates; Urine

1971
[Mechanism of ketogenesis in various situations of metabolism].
    Hoppe-Seyler's Zeitschrift fur physiologische Chemie, 1972, Volume: 353, Issue:10

    Topics: Acetoacetates; Acetyltransferases; Acidosis; Animals; Carbon Isotopes; Carbon Monoxide; Coenzyme A; Diabetic Ketoacidosis; Fatty Acids; Rats

1972
Methylmalonyl coenzyme A racemase defect: another cause of methylmalonic aciduria.
    Pediatric research, 1972, Volume: 6, Issue:12

    Topics: Acidosis; Ammonia; Carbon Isotopes; Cells, Cultured; Cobamides; Coenzyme A; Fibroblasts; Humans; Infant, Newborn; Isomerases; Liver; Male; Malonates; Metabolism, Inborn Errors; Mitochondria, Liver; Propionates; Succinates; Tritium

1972
Beta-ketothiolase deficiency as a cause of the "ketotic hyperglycinemia syndrome".
    Pediatrics, 1974, Volume: 53, Issue:2

    Topics: Acetoacetates; Acidosis; Acyltransferases; Amino Acid Metabolism, Inborn Errors; Butanones; Carbon Radioisotopes; Child; Chromatography, Thin Layer; Coenzyme A; Dinitrophenols; Fibroblasts; Glycine; Humans; Hydrazones; Hydroxybutyrates; Isoleucine; Malonates; Propionates

1974
Propionicacidemia (ketotic hyperglycinemia): dietary treatment resulting in normal growth and development.
    Pediatrics, 1974, Volume: 53, Issue:3

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Body Height; Body Weight; Carboxy-Lyases; Child; Coenzyme A; Diet Therapy; Dietary Carbohydrates; Dietary Proteins; Female; Follow-Up Studies; Glycine; Humans; Intelligence; Ketone Bodies; Propionates

1974
[Ketogenesis: mechanism, regulation, metabolic repercussions].
    Pathologie-biologie, 1970, Volume: 18, Issue:9

    Topics: Acetoacetates; Acetone; Acidosis; Animals; Cattle; Citric Acid Cycle; Coenzyme A; Fatty Acids; Fatty Acids, Nonesterified; Female; Gluconeogenesis; Glucose; Hormones; Humans; Hydroxybutyrates; Insulin; Ketone Bodies; Lipid Metabolism; Liver; Mice; Prostaglandins; Rabbits; Rats; Uric Acid

1970
Lipid biosynthesis and increase in isovaleric acid of plasma.
    Science (New York, N.Y.), 1972, Jun-23, Volume: 176, Issue:4041

    Topics: Acidosis; Coenzyme A; Humans; Lipids; Valerates

1972
[Methylmalonic acidemia. A new cause of severe ketoacidosis. Study of a case].
    Annales de pediatrie, 1971, Jan-02, Volume: 18, Issue:1

    Topics: Acidosis; Child, Preschool; Coenzyme A; Coma; Humans; Seizures

1971
Measurement of citrate synthase activity in human fibroblasts.
    Clinica chimica acta; international journal of clinical chemistry, 1971, Volume: 33, Issue:2

    Topics: Acidosis; Adenosine Triphosphate; Carbon Isotopes; Cell Line; Chromatography, Paper; Citrates; Coenzyme A; Fibroblasts; Humans; Kinetics; Lactates; Lyases; Methods; Oxaloacetates

1971
The role of carnitine in the intracellular translocation of acyl coenzyme-a derivatives.
    Annals of the New York Academy of Sciences, 1965, Oct-08, Volume: 131, Issue:1

    Topics: Acetoacetates; Acidosis; Adipose Tissue; Animals; Carnitine; Cholesterol; Citrates; Coenzyme A; Diphtheria Toxin; Fatty Acids; Guinea Pigs; In Vitro Techniques; Liver; Mitochondria; Myocardium; Palmitic Acids; Pyruvates

1965
Isovaleric acidemia: a new genetic defect of leucine metabolism.
    Proceedings of the National Academy of Sciences of the United States of America, 1966, Volume: 56, Issue:1

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Butyrates; Caproates; Child, Preschool; Chromatography, Gas; Coenzyme A; Fatty Acids; Female; Humans; Leucine; Male; Propionates; Valerates

1966
Hypoglycin A: a specific inhibitor of isovaleryl CoA dehydrogenase.
    Proceedings of the National Academy of Sciences of the United States of America, 1971, Volume: 68, Issue:1

    Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Animals; Butyrates; Caproates; Carbon Dioxide; Carbon Isotopes; Carnitine; Chromatography, Gas; Coenzyme A; Cyclopropanes; In Vitro Techniques; Isoleucine; Leucine; Male; Oxidoreductases; Plant Poisoning; Rats; Valerates; Vomiting

1971
Pathogenesis of ketonemia.
    Scandinavian journal of clinical and laboratory investigation, 1969, Volume: 23, Issue:2

    Topics: Acetoacetates; Acidosis; Animals; Carnitine; Coenzyme A; Diabetes Mellitus; Fasting; Gluconeogenesis; Ketone Bodies; Liver; Mitochondria, Liver; Oxaloacetates; Rats

1969
[Enzyme system in diabetes].
    Tidsskrift for den Norske laegeforening : tidsskrift for praktisk medicin, ny raekke, 1970, Jan-25, Volume: 90, Issue:2

    Topics: Acidosis; Adipose Tissue; Coenzyme A; Diabetes Mellitus; Fatty Acids; Humans; Hyperglycemia; Insulin; Liver

1970
Turnover rates and intracellular pool size distribution of citrate cycle intermediates in normal, diabetic and fat-fed rats estimated by computer analysis from specific activity decay data of 14C-labeled citrate cycle acids.
    European journal of biochemistry, 1970, Volume: 17, Issue:2

    Topics: Acetates; Acetoacetates; Acidosis; Animals; Aspartic Acid; Carbon Isotopes; Carnitine; Chromatography, Gas; Citrates; Coenzyme A; Computers; Cytoplasm; Diabetes Mellitus, Experimental; Dietary Fats

1970
Vitamin B12-dependent methylmalonicaciduria: amino acid toxicity, long chain ketonuria, and protective effect of vitamin B12.
    Pediatrics, 1970, Volume: 46, Issue:4

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child, Preschool; Coenzyme A; Diet Therapy; Dietary Proteins; Humans; Isoleucine; Ketones; Leucine; Leukocytes; Male; Malonates; Methionine; Nutritional Requirements; Propionates; Threonine; Valine; Vitamin B 12

1970
Propionic acidemia in patients with ketotic hyperglycinemia.
    The Journal of pediatrics, 1971, Volume: 78, Issue:5

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Chromatography, Gas; Coenzyme A; Female; Glycine; Humans; Infant; Ligases; Male; Propionates; Remission, Spontaneous

1971
Methylmalonic aciduria. An inborn error leading to metabolic acidosis, long-chain ketonuria and intermittent hyperglycinemia.
    The New England journal of medicine, 1968, Jun-13, Volume: 278, Issue:24

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Chromatography, Thin Layer; Coenzyme A; Dietary Proteins; Glycine; Humans; Infant; Intellectual Disability; Isomerases; Ketone Bodies; Ligases; Male; Malonates; Vitamin B 12

1968
Importance of the single case.
    The New England journal of medicine, 1968, Jun-13, Volume: 278, Issue:24

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Coenzyme A; Glycine; Humans; Infant; Intellectual Disability; Ketone Bodies; Male; Malonates; Vitamin B 12

1968
Methylmalonic aciduria: metabolic block localization and vitamin B 12 dependency.
    Science (New York, N.Y.), 1968, Nov-15, Volume: 162, Issue:3855

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carbon Dioxide; Carbon Isotopes; Coenzyme A; Humans; Hydro-Lyases; Infant; Isomerases; Leukocytes; Malonates; Metabolism, Inborn Errors; Molecular Biology; Mutation; Propionates; Pyridoxal Phosphate; Succinates; Vitamin B 12; Xanthurenates

1968
Enzymatic regulation of 3-sn-phosphatidylcholine and triacylglycerol synthesis in states of altered lipid metabolism.
    The Journal of biological chemistry, 1969, Jan-25, Volume: 244, Issue:2

    Topics: Acidosis; Acyltransferases; Animals; Carbon Isotopes; Choline; Chromatography, Ion Exchange; Coenzyme A; Diabetes Mellitus, Experimental; Glycerides; Glycerol; Lipid Metabolism; Lipoproteins; Liver; Male; Methods; Microsomes; Palmitic Acids; Phosphatidylcholines; Phosphotransferases; Propylthiouracil; Rats; Triiodothyronine

1969