Page last updated: 2024-08-21

chenodeoxycholic acid and Muscular Diseases

chenodeoxycholic acid has been researched along with Muscular Diseases in 10 studies

Research

Studies (10)

TimeframeStudies, this research(%)All Research%
pre-19904 (40.00)18.7374
1990's6 (60.00)18.2507
2000's0 (0.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Fujiyama, J; Kuriyama, M; Osame, M; Tokimura, Y; Utatsu, Y1
Meriwether, TW; Nicolau, G; Salen, G1
Berginer, VM1
Kubo, M; Matsuzawa, Y; Miki, H; Nakamura, T; Takemura, K; Tarui, S1
Ishikawa, A; Kondo, R; Miyatake, T; Wakamatsu, N; Yuasa, T1
De Liege, P; Gambert, P; Laurent, A; Lecoz, P; Legrand, A; Mikol, J; Peynet, J; Warnet, A1
Donaghy, M; King, RH; McKeran, RO; Schwartz, MS; Thomas, PK1
Ginsberg, H; Le, NA; Salen, G; Shefer, S; Tint, GS1
Batta, AK; Batta, M; Salen, G; Shefer, S; Tint, GS1
Emerson, RG; Pedley, TA; Rowland, LP; Salen, G; Warner, CL1

Reviews

1 review(s) available for chenodeoxycholic acid and Muscular Diseases

ArticleYear
Cerebrotendinous xanthomatosis: clinical, electrophysiological and nerve biopsy findings, and response to treatment with chenodeoxycholic acid.
    Journal of neurology, 1990, Volume: 237, Issue:3

    Topics: Adult; Biopsy; Brain Diseases; Chenodeoxycholic Acid; Electrophysiology; Humans; Male; Muscular Diseases; Nerve Fibers, Myelinated; Neural Conduction; Peripheral Nerves; Spinal Nerves; Sural Nerve; Tendons; Xanthomatosis

1990

Other Studies

9 other study(ies) available for chenodeoxycholic acid and Muscular Diseases

ArticleYear
Treatment of cerebrotendinous xanthomatosis: effects of chenodeoxycholic acid, pravastatin, and combined use.
    Journal of the neurological sciences, 1994, Volume: 125, Issue:1

    Topics: Adult; Apolipoproteins; Brain Diseases; Chenodeoxycholic Acid; Cholestanol; Cholesterol; Drug Therapy, Combination; Electrophysiology; Humans; Lipids; Lipoproteins; Male; Middle Aged; Muscular Diseases; Phytosterols; Pravastatin; Tendons; Xanthomatosis

1994
Chenodeoxycholic acid inhibits increased cholesterol and cholestanol synthesis in patients with cerebrotendinous xanthomatosis.
    Biochemical medicine, 1975, Volume: 14, Issue:1

    Topics: Achilles Tendon; Adult; Alcohols; Bile; Bile Acids and Salts; Chenodeoxycholic Acid; Cholesterol; Female; Humans; Hydroxymethylglutaryl CoA Reductases; Liver; Male; Middle Aged; Muscular Diseases; Sterols; Xanthomatosis

1975
[Cerebrotendinous xanthomatosis].
    Zhurnal nevropatologii i psikhiatrii imeni S.S. Korsakova (Moscow, Russia : 1952), 1992, Volume: 92, Issue:4

    Topics: Achilles Tendon; Adolescent; Adult; Brain; Brain Diseases, Metabolic; Chenodeoxycholic Acid; Cholestanol; Female; Humans; Muscular Diseases; Xanthomatosis

1992
Combined treatment with chenodeoxycholic acid and pravastatin improves plasma cholestanol levels associated with marked regression of tendon xanthomas in cerebrotendinous xanthomatosis.
    Metabolism: clinical and experimental, 1991, Volume: 40, Issue:7

    Topics: Adult; Anticholesteremic Agents; Bile Acids and Salts; Brain Diseases; Chenodeoxycholic Acid; Cholestanol; Cholesterol; Chromatography, High Pressure Liquid; Drug Therapy, Combination; Heptanoic Acids; Humans; Male; Muscular Diseases; Naphthalenes; Pravastatin; Tendons; Xanthomatosis

1991
[A case of cerebrotendinous xanthomatosis with spastic paraparesis, epilepsy, and bradykinesia].
    Rinsho shinkeigaku = Clinical neurology, 1991, Volume: 31, Issue:6

    Topics: Adult; Brain Diseases; Chenodeoxycholic Acid; Epilepsy; Female; Humans; Movement Disorders; Muscular Diseases; Paraparesis, Tropical Spastic; Tendons; Xanthomatosis

1991
Cerebrotendinous xanthomatosis: treatments with simvastatin, lovastatin, and chenodeoxycholic acid in 3 siblings.
    Neurology, 1991, Volume: 41, Issue:3

    Topics: Adult; Anticholesteremic Agents; Brain Diseases; Chenodeoxycholic Acid; Female; Humans; Lovastatin; Muscular Diseases; Simvastatin; Tendons; Tomography, X-Ray Computed; Xanthomatosis

1991
Chenodeoxycholic acid normalizes elevated lipoprotein secretion and catabolism in cerebrotendinous xanthomatosis.
    Journal of lipid research, 1989, Volume: 30, Issue:5

    Topics: Adult; Brain Diseases; Chenodeoxycholic Acid; Cholesterol; Humans; Lipid Metabolism, Inborn Errors; Lipoproteins; Male; Middle Aged; Muscular Diseases; Tendons; Ursodeoxycholic Acid; Xanthomatosis

1989
Increased plasma bile alcohol glucuronides in patients with cerebrotendinous xanthomatosis: effect of chenodeoxycholic acid.
    Journal of lipid research, 1987, Volume: 28, Issue:8

    Topics: Adult; Brain Diseases; Chenodeoxycholic Acid; Cholestanols; Female; Glucuronates; Humans; Male; Middle Aged; Muscular Diseases; Tendons; Xanthomatosis

1987
Treatment of cerebrotendinous xanthomatosis with chenodeoxycholic acid.
    Annals of neurology, 1985, Volume: 18, Issue:4

    Topics: Adult; Brain Diseases; Chenodeoxycholic Acid; Cholesterol; Evoked Potentials; Humans; Male; Muscular Diseases; Neural Conduction; Tendons; Xanthomatosis

1985