Page last updated: 2024-08-21

chenodeoxycholic acid and Disease Exacerbation

chenodeoxycholic acid has been researched along with Disease Exacerbation in 45 studies

Research

Studies (45)

Timeframe	Studies, this research(%)	All Research%
pre-1990	0 (0.00)	18.7374
1990's	0 (0.00)	18.2507
2000's	5 (11.11)	29.6817
2010's	30 (66.67)	24.3611
2020's	10 (22.22)	2.80

Authors

Authors	Studies
Chen, J; Liu, J; Luo, Y; Shi, J; Su, M; Xu, C; Yang, J; Yang, W; Zang, S; Zhao, F; Zheng, M; Zhou, J	1
Bowlus, C; Gao, L; Gershwin, ME; He, X; Leung, PSC; Wang, L; Woo, E; Yang, G	1
Kowdley, KV; Shah, RA	2
Gulamhusein, AF; Hirschfield, GM	1
Chascsa, DMH; Lindor, KD	1
Dyson, JK; Jones, D; Phaw, NA	1
de Veer, RC; Laschtowitz, A; Schramm, C; Van der Meer, AJ	1
Akca Kalem, S; Bilgic, B; Dogu, O; Emre, M; Gurvit, HI; Hanagasi, HA; Kaleagasi, H; Lohmann, E; Tufekcioglu, Z; Yunisova, G	1
Dhamija, R; Valencia-Sanchez, C; Wingerchuk, DM	1
Andersen, H; Divanovic, S; Haslam, DB; Horrigan, O; Jose, S; Madan, R; Moreno-Fernandez, ME; Mukherjee, A; Setchell, KDR; Sharma, D; Zhang, W	1
Abdelmalek, MF	1
Gershwin, ME; Tanaka, A	1
Carbone, M; Invernizzi, P	1
Hegade, VS; Jones, DEJ; Wong, LL	1
Alvaro, D; Canonico, PL; Carbone, M; Craxi, A; Floreani, A; Gardini, I; Gasbarrini, A; Invernizzi, P; Kruger, P; Lanati, E; Marzioni, M; Mennini, FS; Muratori, L; Ronco, V; Vespasiani Gentilucci, U	1
Floreani, A; Mangini, C	1
Lindor, KD; Silveira, MG	1
Adorini, L; Andersen, JB; Arbelaiz, A; Banales, JM; Bujanda, L; Caro-Maldonado, A; Carracedo, A; Erice, O; Gómez-Vallejo, V; Jimenez-Agüero, R; Labiano, I; Llop, J; Lozano, E; Marin, JJ; Martin, A; Martín-Martín, N; Marzioni, M; Munoz-Garrido, P; O'Rourke, CJ; Olaizola, P; Padro, D; Perugorria, MJ; Santos-Laso, A; Trauner, M	1
Salen, G; Steiner, RD	1
Adorini, L; D'Agati, V; Dobrinskikh, E; Dvornikov, A; Field, A; Garcia, G; Gonzalez, FJ; Gratton, E; Henriksen, K; Herman-Edelstein, M; Hill, A; Jiang, T; Kopp, JB; Krausz, KW; Levi, J; Levi, M; Lucia, S; Luo, Y; Myakala, K; Orlicky, D; Peng, Y; Pruzanski, M; Qiu, L; Ranjit, S; Rosenberg, AZ; Wang, D; Wang, XX; Xie, C	1
Eichler, FS; Hayden, D; Walsh, K; Wong, JC	1
Alexander, GJM; Chapman, MH; Collier, J; Dyson, JK; Hirschfield, GM; Hübscher, S; Jones, DEJ; Patanwala, I; Pereira, SP; Thain, C; Thorburn, D; Tiniakos, D; Walmsley, M; Webster, G	1
Corrigan, M; Jones, D; Jopson, L; Khanna, A; Peterson, P; Rudell, E	1
Asakawa, M; Goto, T; Itoh, M; Kai, T; Kanai, S; Ogawa, Y; Sakai, T; Shirakawa, I; Suganami, T; Yoneyama, T	1
Aguilera, L; Albillos, A; Martínez, J	1
Broermann, A; Feigh, M; Gillum, MP; Hansen, HH; Jelsing, J; Rigbolt, KTG; Rippmann, JF; Schönberger, T; Stierstorfer, B; Tølbøl, KS; Veidal, SS; Vrang, N	1
Gong, JY; Lu, Y; Setchell, KD; Wang, JS; Zhang, MH; Zhao, J	1
Carbone, M; Cristoferi, L; Gerussi, A; Invernizzi, P; Ronca, V	1
Carey, EJ; Yokoda, RT	1
Alukal, JJ; Thuluvath, PJ	1
Brienza, M; Cambieri, C; Dotti, MT; Fiermonte, G; Fiorelli, M; Mignarri, A	1
Björkhem, I; Del Puppo, M; Dotti, MT; Federico, A; Gallus, GN; Magni, A; Mignarri, A	1
Bowlus, CL; Kenney, JT; Navarro, R; Rice, G	1
Dufour, JF; Perazzo, H	1
Kato, T; Koyama, S	1
Banken, R; Chapman, R; Chhatwal, J; Corey, K; Hur, C; Klebanoff, M; Loos, AM; Ollendorf, DA; Pratt, DS; Samur, S	1
Parés, A	1
Abdel-Hamid, MS; Issa, MY; Otaify, GA; Zaki, MS	1
Bull, LN; Elias, MS; Emerick, KM; Green, RM; Knisely, As; Melin-Aldana, H; Strautnieks, S; Thompson, RJ; Whitington, PF	1
Alaggio, R; D'Antiga, L; Giordano, G; Guido, M; Riello, L; Zancan, L	1
Clemen, CS; Dodel, R; Klockgether, T; Lütjohann, D; Spottke, EA; Urbach, H; von Bergmann, K	1
Gadoth, N; Meiner, V; Siman-Tov, T	1
Imamura, M; Kaganoi, J; Kawabe, A; Kondo, K; Shimada, Y; Soma, T; Tsunoda, S	1
Aranha, MM; Camilo, ME; Cortez-Pinto, H; Costa, A; da Silva, IB; de Moura, MC; Rodrigues, CM	1

Reviews

21 review(s) available for chenodeoxycholic acid and Disease Exacerbation

Article	Year
Clinical Management of Primary Biliary Cholangitis-Strategies and Evolving Trends. Clinical reviews in allergy & immunology, 2020, Volume: 59, Issue:2 Topics: Animals; Bile Acids and Salts; Biomarkers; Chenodeoxycholic Acid; Combined Modality Therapy; Disease Management; Disease Progression; Disease Susceptibility; Fibrosis; Humans; Immunotherapy; Liver Cirrhosis, Biliary; Liver Transplantation; Molecular Targeted Therapy; Severity of Illness Index; Symptom Assessment; Treatment Outcome; Ursodeoxycholic Acid	2020
Current and potential treatments for primary biliary cholangitis. The lancet. Gastroenterology & hepatology, 2020, Volume: 5, Issue:3 Topics: Benzothiazoles; Bezafibrate; Bile Acids and Salts; Budesonide; Case-Control Studies; Chenodeoxycholic Acid; Cholagogues and Choleretics; Clinical Trials as Topic; Cyclosporine; Disease Progression; Glucocorticoids; Homeostasis; Humans; Immunologic Factors; Immunosuppressive Agents; Isoxazoles; Liver Cirrhosis, Biliary; Liver Transplantation; Peroxisome Proliferator-Activated Receptors; Receptors, Cytoplasmic and Nuclear; Rituximab; Treatment Outcome; United States; United States Food and Drug Administration; Ursodeoxycholic Acid	2020
Primary biliary cholangitis: pathogenesis and therapeutic opportunities. Nature reviews. Gastroenterology & hepatology, 2020, Volume: 17, Issue:2 Topics: Adaptive Immunity; Animals; Autoimmunity; Bile Acids and Salts; Chenodeoxycholic Acid; Chloride-Bicarbonate Antiporters; Cholagogues and Choleretics; Dihydrolipoyllysine-Residue Acetyltransferase; Disease Progression; Environmental Exposure; Epigenesis, Genetic; Humans; Immunity, Innate; Liver Cirrhosis; Liver Cirrhosis, Biliary; MicroRNAs; Organic Anion Transporters, Sodium-Dependent; Peroxisome Proliferator-Activated Receptors; Receptors, Cytoplasmic and Nuclear; Symporters; Ursodeoxycholic Acid	2020
Emerging therapies for PBC. Journal of gastroenterology, 2020, Volume: 55, Issue:3 Topics: Chenodeoxycholic Acid; Disease Progression; End Stage Liver Disease; Female; Fibric Acids; Humans; Liver Cirrhosis, Biliary; Liver Transplantation; Male; Middle Aged; Ursodeoxycholic Acid	2020
Obeticholic acid for the treatment of nonalcoholic steatohepatitis. Expert review of gastroenterology & hepatology, 2020, Volume: 14, Issue:5 Topics: Anti-Inflammatory Agents, Non-Steroidal; Chenodeoxycholic Acid; Clinical Trials as Topic; Disease Progression; Gastrointestinal Agents; Healthy Lifestyle; Humans; Liver; Liver Cirrhosis; Non-alcoholic Fatty Liver Disease; Receptors, Cytoplasmic and Nuclear	2020
Emerging drugs for the treatment of primary biliary cholangitis. Expert opinion on emerging drugs, 2020, Volume: 25, Issue:2 Topics: Animals; Chenodeoxycholic Acid; Cholagogues and Choleretics; Disease Progression; Drug Development; Humans; Liver Cirrhosis, Biliary; Quality of Life; Ursodeoxycholic Acid	2020
Diagnosis and treatment of primary biliary cholangitis. United European gastroenterology journal, 2020, Volume: 8, Issue:6 Topics: Autoantigens; Autoimmune Diseases; Bezafibrate; Biomarkers; Biopsy; Chenodeoxycholic Acid; Cholagogues and Choleretics; Disease Progression; Drug Therapy, Combination; Elasticity Imaging Techniques; End Stage Liver Disease; Fatigue; Female; Humans; Immunoglobulin M; Liver; Liver Cirrhosis, Biliary; Liver Function Tests; Liver Transplantation; Middle Aged; Off-Label Use; Prognosis; Pruritus; Quality of Life; Severity of Illness Index; Sjogren's Syndrome; Survival Rate; Treatment Outcome; Ursodeoxycholic Acid	2020
Nonalcoholic fatty liver disease: another leap forward. Nature reviews. Gastroenterology & hepatology, 2021, Volume: 18, Issue:2 Topics: Chenodeoxycholic Acid; Disease Progression; Gastrointestinal Agents; Humans; Imaging, Three-Dimensional; Liver; Machine Learning; Non-alcoholic Fatty Liver Disease	2021
What Comes after Ursodeoxycholic Acid in Primary Biliary Cholangitis? Digestive diseases (Basel, Switzerland), 2017, Volume: 35, Issue:4 Topics: Chenodeoxycholic Acid; Cholangitis; Disease Progression; Humans; Liver Cirrhosis, Biliary; Quality of Life; Ursodeoxycholic Acid	2017
Primary biliary cholangitis: Old and novel therapy. European journal of internal medicine, 2018, Volume: 47 Topics: Budesonide; Chenodeoxycholic Acid; Disease Progression; End Stage Liver Disease; Humans; Liver Cirrhosis, Biliary; Liver Transplantation; Randomized Controlled Trials as Topic; Ursodeoxycholic Acid	2018
Investigational drugs in phase II clinical trials for primary biliary cholangitis. Expert opinion on investigational drugs, 2017, Volume: 26, Issue:10 Topics: Animals; Chenodeoxycholic Acid; Cholagogues and Choleretics; Cholangitis; Disease Progression; Drug Design; Drugs, Investigational; Humans; Liver Cirrhosis, Biliary; Ursodeoxycholic Acid	2017
Epidemiology, diagnosis, and treatment of cerebrotendinous xanthomatosis (CTX). Journal of inherited metabolic disease, 2017, Volume: 40, Issue:6 Topics: Animals; Chenodeoxycholic Acid; Cholesterol; Disease Progression; Early Diagnosis; Humans; Xanthomatosis, Cerebrotendinous	2017
Natural history of neurological abnormalities in cerebrotendinous xanthomatosis. Journal of inherited metabolic disease, 2018, Volume: 41, Issue:4 Topics: Adult; Aged; Brain; Chenodeoxycholic Acid; Disease Progression; Female; Humans; Magnetic Resonance Imaging; Male; Nervous System Diseases; Treatment Outcome; Xanthomatosis, Cerebrotendinous	2018
Risk stratification and treatment of primary biliary cholangitis. Revista espanola de enfermedades digestivas, 2019, Volume: 111, Issue:1 Topics: Adult; Age Factors; Alkaline Phosphatase; Biomarkers; Budesonide; Chenodeoxycholic Acid; Cholagogues and Choleretics; Cholangitis; Cholestasis; Disease Progression; Fibric Acids; Glucocorticoids; Humans; Liver Cirrhosis; Liver Transplantation; Middle Aged; Risk Assessment; Risk Factors; Sex Factors; Treatment Failure; Ursodeoxycholic Acid	2019
Precision medicine in primary biliary cholangitis. Journal of digestive diseases, 2019, Volume: 20, Issue:7 Topics: Chenodeoxycholic Acid; Disease Progression; Gastrointestinal Agents; Humans; Liver Cirrhosis, Biliary; Precision Medicine	2019
Primary Biliary Cholangitis and Primary Sclerosing Cholangitis. The American journal of gastroenterology, 2019, Volume: 114, Issue:10 Topics: Adult; Biliary Tract; Chenodeoxycholic Acid; Cholagogues and Choleretics; Cholangitis, Sclerosing; Cholestasis; Clinical Trials as Topic; Disease Progression; Drug Therapy, Combination; End Stage Liver Disease; Humans; Immunologic Factors; Life Expectancy; Prevalence; Prognosis; Treatment Outcome; Ursodeoxycholic Acid	2019
Reversal of NASH fibrosis with pharmacotherapy. Hepatology international, 2019, Volume: 13, Issue:5 Topics: Benzamides; Chalcones; Chenodeoxycholic Acid; Disease Progression; Humans; Imidazoles; Liver; Liver Cirrhosis; Non-alcoholic Fatty Liver Disease; Propionates; Pyridines; Risk Factors; Sulfoxides	2019
Primary Biliary Cholangitis: Medical and Specialty Pharmacy Management Update. Journal of managed care & specialty pharmacy, 2016, Volume: 22, Issue:10-a-s Sup Topics: Chenodeoxycholic Acid; Cholagogues and Choleretics; Cholangitis; Congresses as Topic; Disease Progression; Drug Resistance; Drug Therapy, Combination; Education, Pharmacy, Continuing; End Stage Liver Disease; Evidence-Based Medicine; Formularies as Topic; Humans; Insurance Coverage; Insurance, Pharmaceutical Services; Liver Transplantation; Middle Aged; Prescription Fees; Rare Diseases; Receptors, Cytoplasmic and Nuclear; Satellite Communications; Ursodeoxycholic Acid	2016
The therapeutic landscape of non-alcoholic steatohepatitis. Liver international : official journal of the International Association for the Study of the Liver, 2017, Volume: 37, Issue:5 Topics: Antioxidants; Chalcones; Chenodeoxycholic Acid; Disease Progression; Humans; Hypoglycemic Agents; Insulin Resistance; Liver Cirrhosis; Non-alcoholic Fatty Liver Disease; Pioglitazone; Propionates; Randomized Controlled Trials as Topic; Thiazolidinediones; Vitamin E; Weight Loss	2017
Pathophysiology of cerebrotendinous xanthomatosis. Rinsho shinkeigaku = Clinical neurology, 2016, 12-28, Volume: 56, Issue:12 Topics: Chenodeoxycholic Acid; Cholestanetriol 26-Monooxygenase; Cholestanol; Diagnosis, Differential; Disease Progression; Early Diagnosis; Humans; Mutation; Severity of Illness Index; Xanthomatosis, Cerebrotendinous	2016
Novel Treatment Strategies for Primary Biliary Cholangitis. Seminars in liver disease, 2017, Volume: 37, Issue:1 Topics: Chenodeoxycholic Acid; Cholagogues and Choleretics; Cholangitis; Disease Progression; Fibric Acids; Gastrointestinal Agents; Humans; Liver Cirrhosis, Biliary; Randomized Controlled Trials as Topic; Ursodeoxycholic Acid	2017

Other Studies

24 other study(ies) available for chenodeoxycholic acid and Disease Exacerbation

Article	Year
Ratio of Conjugated Chenodeoxycholic to Muricholic Acids is Associated with Severity of Nonalcoholic Steatohepatitis. Obesity (Silver Spring, Md.), 2019, Volume: 27, Issue:12 Topics: Adult; Bile Acids and Salts; Chenodeoxycholic Acid; Cholic Acids; Cohort Studies; Disease Progression; Female; Humans; Liver; Male; Middle Aged; Non-alcoholic Fatty Liver Disease; Risk Factors	2019
Patients with Lately Diagnosed Cerebrotendinous Xanthomatosis. Neuro-degenerative diseases, 2019, Volume: 19, Issue:5-6 Topics: Adult; Brain; Chenodeoxycholic Acid; Cholestanetriol 26-Monooxygenase; Delayed Diagnosis; Disease Progression; Female; Follow-Up Studies; Gastrointestinal Agents; Humans; Male; Retrospective Studies; Xanthomatosis, Cerebrotendinous	2019
Teaching NeuroImages: Spinal xanthomatosis: A misdiagnosed, treatable cause of progressive myelopathy. Neurology, 2020, 09-15, Volume: 95, Issue:11 Topics: Chenodeoxycholic Acid; Diagnostic Errors; Disease Progression; Female; Humans; Middle Aged; Spinal Cord; Spinal Cord Diseases; Treatment Outcome; Xanthomatosis	2020
Obeticholic acid ameliorates severity of Clostridioides difficile infection in high fat diet-induced obese mice. Mucosal immunology, 2021, Volume: 14, Issue:2 Topics: Animals; Anticholesteremic Agents; Chenodeoxycholic Acid; Clostridioides difficile; Clostridium Infections; Diet, High-Fat; Disease Models, Animal; Disease Progression; Humans; Male; Mice; Mice, Inbred C57BL; Mice, Obese; Obesity; RNA-Binding Proteins	2021
Finding the cure for primary biliary cholangitis - Still waiting. Liver international : official journal of the International Association for the Study of the Liver, 2017, Volume: 37, Issue:4 Topics: Biomarkers; Chenodeoxycholic Acid; Cholagogues and Choleretics; Disease Progression; Humans; Liver Cirrhosis, Biliary; Ursodeoxycholic Acid	2017
Treatment of PBC-A step forward. Liver international : official journal of the International Association for the Study of the Liver, 2017, Volume: 37, Issue:4 Topics: Biomarkers; Chenodeoxycholic Acid; Disease Progression; Humans; Liver Cirrhosis, Biliary; Randomized Controlled Trials as Topic	2017
Primary Biliary Cholangitis: advances in management and treatment of the disease. Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver, 2017, Volume: 49, Issue:8 Topics: Chenodeoxycholic Acid; Cholagogues and Choleretics; Cholangitis; Cholestasis; Disease Progression; Drug Therapy, Combination; End Stage Liver Disease; Humans; Ursodeoxycholic Acid	2017
Differential effects of FXR or TGR5 activation in cholangiocarcinoma progression. Biochimica et biophysica acta. Molecular basis of disease, 2018, Volume: 1864, Issue:4 Pt B Topics: Aged; Aged, 80 and over; Animals; Bile Acids and Salts; Bile Duct Neoplasms; Bile Ducts; Cell Line, Tumor; Cell Movement; Cell Proliferation; Chenodeoxycholic Acid; Cholangiocarcinoma; Cholic Acids; Cohort Studies; Disease Progression; Energy Metabolism; Epithelial Cells; Female; Gastrointestinal Agents; Humans; Male; Mice; Mice, Nude; Middle Aged; Mitochondria; Receptors, Cytoplasmic and Nuclear; Receptors, G-Protein-Coupled; Xenograft Model Antitumor Assays	2018
FXR/TGR5 Dual Agonist Prevents Progression of Nephropathy in Diabetes and Obesity. Journal of the American Society of Nephrology : JASN, 2018, Volume: 29, Issue:1 Topics: Albuminuria; Animals; Bile Acids and Salts; Chenodeoxycholic Acid; Cholesterol; Cholic Acids; Diabetes Mellitus, Experimental; Diabetes Mellitus, Type 2; Diabetic Nephropathies; Disease Progression; Endoplasmic Reticulum Stress; Fibrosis; Glomerular Mesangium; Humans; Kidney Tubules; Male; Mice; Mice, Inbred C57BL; Mice, Inbred DBA; Mitochondria; Obesity; Oxidative Stress; Podocytes; Receptors, Cytoplasmic and Nuclear; Receptors, G-Protein-Coupled; RNA, Messenger; Signal Transduction; Triglycerides	2018
The British Society of Gastroenterology/UK-PBC primary biliary cholangitis treatment and management guidelines. Gut, 2018, Volume: 67, Issue:9 Topics: Alanine Transaminase; Alkaline Phosphatase; Autoantibodies; Bilirubin; Biomarkers; Chenodeoxycholic Acid; Cholagogues and Choleretics; Cholangitis; Disease Progression; Gastroenterology; Humans; Liver Cirrhosis, Biliary; Mitochondria; Predictive Value of Tests; Risk Assessment; Risk Factors; Sensitivity and Specificity; Societies, Medical; Treatment Outcome; United Kingdom; Ursodeoxycholic Acid	2018
Are Clinicians Ready for Safe Use of Stratified Therapy in Primary Biliary Cholangitis (PBC)? A Study of Educational Awareness. Digestive diseases and sciences, 2018, Volume: 63, Issue:10 Topics: Chenodeoxycholic Acid; Cholagogues and Choleretics; Clinical Competence; Disease Progression; Early Diagnosis; Gastroenterologists; Humans; Liver Cirrhosis, Biliary; Risk Factors; Ursodeoxycholic Acid	2018
Obeticholic acid protects against hepatocyte death and liver fibrosis in a murine model of nonalcoholic steatohepatitis. Scientific reports, 2018, 05-25, Volume: 8, Issue:1 Topics: Animals; Body Weight; Cell Death; Chenodeoxycholic Acid; Cytoprotection; Disease Models, Animal; Disease Progression; Gene Knockout Techniques; Hepatocytes; Insulin Resistance; Liver Cirrhosis; Mice; Mice, Inbred C57BL; Non-alcoholic Fatty Liver Disease; Obesity; Receptor, Melanocortin, Type 4; Tumor Suppressor Protein p53	2018
Disease Progression and Pharmacological Intervention in a Nutrient-Deficient Rat Model of Nonalcoholic Steatohepatitis. Digestive diseases and sciences, 2019, Volume: 64, Issue:5 Topics: Animals; Chalcones; Chenodeoxycholic Acid; Cholesterol; Disease Progression; Male; Non-alcoholic Fatty Liver Disease; Nutrients; Propionates; Rats; Rats, Wistar	2019
Δ4-3-oxosteroid-5β-reductase deficiency: Responses to oral bile acid therapy and long-term outcomes. World journal of gastroenterology, 2019, Feb-21, Volume: 25, Issue:7 Topics: Administration, Oral; Chenodeoxycholic Acid; Disease Progression; DNA Mutational Analysis; Dose-Response Relationship, Drug; Female; Gastrointestinal Agents; Humans; Infant, Newborn; Male; Metabolic Diseases; Mutation; Oxidoreductases; Retrospective Studies; Treatment Outcome; Ursodeoxycholic Acid	2019
Enlarging brain xanthomas in a patient with cerebrotendinous xanthomatosis. Journal of inherited metabolic disease, 2015, Volume: 38, Issue:5 Topics: Brain; Chenodeoxycholic Acid; Disease Progression; Humans; Magnetic Resonance Imaging; Male; Middle Aged; Neuroimaging; Xanthomatosis, Cerebrotendinous	2015
Evaluation of cholesterol metabolism in cerebrotendinous xanthomatosis. Journal of inherited metabolic disease, 2016, Volume: 39, Issue:1 Topics: Adolescent; Adult; Bile Acids and Salts; Biomarkers; Chenodeoxycholic Acid; Cholestanol; Cholestenones; Cholesterol; Disease Progression; Female; Humans; Hydroxycholesterols; Lipid Metabolism; Male; Middle Aged; Prognosis; Xanthomatosis, Cerebrotendinous; Young Adult	2016
Long-term clinical impact and cost-effectiveness of obeticholic acid for the treatment of primary biliary cholangitis. Hepatology (Baltimore, Md.), 2017, Volume: 65, Issue:3 Topics: Adult; Biopsy, Needle; Chenodeoxycholic Acid; Cholangitis; Cohort Studies; Cost-Benefit Analysis; Disease Progression; Dose-Response Relationship, Drug; Drug Administration Schedule; Female; Follow-Up Studies; Humans; Immunohistochemistry; Male; Middle Aged; Prospective Studies; Quality-Adjusted Life Years; Risk Assessment; Severity of Illness Index; Time; Treatment Outcome	2017
A novel frameshift mutation in the sterol 27-hydroxylase gene in an Egyptian family with cerebrotendinous xanthomatosis without cataract. Metabolic brain disease, 2017, Volume: 32, Issue:2 Topics: Adult; Age of Onset; Brain; Cataract; Chenodeoxycholic Acid; Cholestanetriol 26-Monooxygenase; Disease Progression; Frameshift Mutation; Humans; Learning Disabilities; Magnetic Resonance Imaging; Male; Pedigree; Psychotic Disorders; Seizures; Xanthomatosis, Cerebrotendinous	2017
Bile composition in Alagille Syndrome and PFIC patients having Partial External Biliary Diversion. BMC gastroenterology, 2008, Oct-20, Volume: 8 Topics: Adolescent; Alagille Syndrome; Bile; Bile Ducts, Intrahepatic; Biopsy; Chenodeoxycholic Acid; Child; Child, Preschool; Cholestasis, Intrahepatic; Cholesterol; Cholic Acid; Digestive System Surgical Procedures; Disease Progression; Gallbladder; Humans; Infant; Lipid Metabolism; Liver; Phospholipids; Treatment Outcome	2008
Titration of bile acid supplements in 3beta-hydroxy-Delta 5-C27-steroid dehydrogenase/isomerase deficiency. Journal of pediatric gastroenterology and nutrition, 2010, Volume: 50, Issue:6 Topics: 3-Hydroxysteroid Dehydrogenases; Biopsy; Chenodeoxycholic Acid; Child; Child, Preschool; Cholagogues and Choleretics; Cholic Acids; Chromatography, Liquid; Dietary Supplements; Disease Progression; Humans; Infant; Infant, Newborn; Isomerases; Liver Diseases; Steroid Metabolism, Inborn Errors; Tandem Mass Spectrometry; Treatment Outcome; Ursodeoxycholic Acid	2010
Cerebrotendinous xanthomatosis: a treatable ataxia. Neurology, 2005, Apr-26, Volume: 64, Issue:8 Topics: Adult; Cerebellar Ataxia; Cerebellum; Chenodeoxycholic Acid; Cholestanol; Cholesterol; Disease Progression; Electroencephalography; Humans; Magnetic Resonance Imaging; Male; Paraparesis, Spastic; Peripheral Nervous System Diseases; Simvastatin; Treatment Outcome; Xanthomatosis, Cerebrotendinous	2005
Could steroids mask the diagnosis of cerebrotendinous xanthomatosis? Journal of the neurological sciences, 2006, Apr-15, Volume: 243, Issue:1-2 Topics: Achilles Tendon; Adult; Brain; Chenodeoxycholic Acid; Cholestanetriol 26-Monooxygenase; Cholestanol; Cholesterol; Diagnosis, Differential; Diagnostic Errors; Disease Progression; Down-Regulation; Humans; Male; Polyradiculoneuropathy, Chronic Inflammatory Demyelinating; Prednisone; Simvastatin; Steroid Hydroxylases; Steroids; Treatment Outcome; Up-Regulation; Xanthomatosis, Cerebrotendinous	2006
Chenodeoxycholic acid stimulates the progression of human esophageal cancer cells: A possible mechanism of angiogenesis in patients with esophageal cancer. International journal of cancer, 2006, Aug-15, Volume: 119, Issue:4 Topics: Adult; Aged; Aged, 80 and over; Animals; Cell Line, Tumor; Chenodeoxycholic Acid; Cyclooxygenase 2; Dinoprostone; Disease Progression; Enzyme Activation; ErbB Receptors; Esophageal Neoplasms; Female; Gene Expression Regulation, Enzymologic; Humans; Interleukin-6; Male; Mice; Middle Aged; Mitogen-Activated Protein Kinases; Neoplasm Transplantation; Signal Transduction; Survival Rate; Vascular Endothelial Growth Factor A	2006
Bile acid levels are increased in the liver of patients with steatohepatitis. European journal of gastroenterology & hepatology, 2008, Volume: 20, Issue:6 Topics: Adult; Bile Acids and Salts; Biopsy; Chenodeoxycholic Acid; Cholic Acid; Chromatography, Gas; Deoxycholic Acid; Disease Progression; Fatty Liver; Fatty Liver, Alcoholic; Female; Humans; Liver; Male; Middle Aged; Severity of Illness Index	2008