carnitine has been researched along with Hypoglycemia in 84 studies
Hypoglycemia: A syndrome of abnormally low BLOOD GLUCOSE level. Clinical hypoglycemia has diverse etiologies. Severe hypoglycemia eventually lead to glucose deprivation of the CENTRAL NERVOUS SYSTEM resulting in HUNGER; SWEATING; PARESTHESIA; impaired mental function; SEIZURES; COMA; and even DEATH.
| Excerpt | Relevance | Reference |
|---|---|---|
| "Long-term treatment with antibiotics containing pivalic acid may decrease serum carnitine concentration and can sometimes be associated with severe hypoglycemia and encephalopathy in infants." | 7.85 | Carnitine-related hypoglycemia caused by 3 days of pivalate antibiotic therapy in a patient with severe muscular dystrophy: a case report. ( Fukuda, M; Ishii, E; Ito, M; Suzuki, Y; Wakamoto, H, 2017) |
| "The mechanism of onset of hypoglycemia in patients with carnitine deficiency has yet to be determined." | 7.74 | Reduced carnitine level causes death from hypoglycemia: possible involvement of suppression of hypothalamic orexin expression during weaning period. ( Doi, T; Fujihara, H; Inubushi, A; Kido, H; Kuwajima, M; Okamoto, T; Sei, H; Sei, M; Sukeno, A; Tsuda, TT; Ueta, Y; Umehara, A, 2007) |
| " She had a high fever, hypocarnitinemic and non-ketotic hypoglycemia, serum levels of total carnitine 7." | 7.74 | Hypocarnitinemic hypoglycemia and heart failure in an infant with a constant parenteral elementary nutrition during measles vaccination-related febrile illness. ( Izumi, T; Maeda, T; Okanari, K; Sato, K; Suenobu, S; Takahashi, M, 2007) |
| "Deficiency of the enzymes of mitochondrial fatty acid oxidation and related carnitine dependent steps have been shown to be one of the causes of the fasting-induced hypoketotic hypoglycemia." | 7.68 | Carnitine-acylcarnitine translocase deficiency with severe hypoglycemia and auriculo ventricular block. Translocase assay in permeabilized fibroblasts. ( Aufrant, C; Brivet, M; Demaugre, F; Pande, SV; Saudubray, JM; Slama, A, 1993) |
| "Since hypoglycemic neonates do not exhibit compensative ketosis, we investigated the possible involvement of carnitine deficiency or omega-oxidation in neonatal hypoglycemia." | 7.67 | Ketogenesis in hypoglycemic neonates. Carnitine and dicarboxylic acids in neonatal hypoglycemia. ( Cartier, B; Divry, P; Maire, I; Sann, L; Vianey-Laud, C, 1987) |
| "Recurrent episodes of hypoglycemia, prostration, vomiting, and hepatomegaly were observed in an infant fed a carnitine-free soy formula." | 7.66 | Dietary-dependent carnitine deficiency as a cause of nonketotic hypoglycemia in an infant. ( Borum, PR; Burr, IM; Greene, HL; Kasselberg, AG; Slonim, AE; Stanley, CA; Tanaka, K, 1981) |
| "In systemic carnitine deficiency, an early phase of nonketotic hypoglycemia and liver dysfunction may precede a late phase of encephalopathy and myopathy." | 7.66 | Nonketotic hypoglycemia: an early indicator of systemic carnitine deficiency. ( Borum, PR; Diamond, MP; Mrak, RE; Najjar, J; Richardson, D; Slonim, AE, 1983) |
| "Severe hypoglycemia has been known to induce mitochondrial swelling followed by neuronal death in the brain." | 5.33 | L-carnitine inhibits hypoglycemia-induced brain damage in the rat. ( Hino, K; Inoue, M; Nishikawa, M; Sato, E, 2005) |
| "Systemic carnitine-deficient juvenile visceral steatosis (JVS) mice exhibit decreased expression of some liver-selective genes including those for the urea cycle enzymes during the infantile period." | 5.30 | Suppressed expression of the urea cycle enzyme genes in the liver of carnitine-deficient juvenile visceral steatosis (JVS) mice in infancy and during starvation in adulthood. ( Horiuchi, M; Mori, M; Musa, DA; Saheki, T; Takiguchi, M; Tomomura, A; Tomomura, M, 1997) |
| "Fraternal twins who had fasting hypoglycemia, hypoketonemia, muscle weakness, and hepatic dysfunction are reported." | 5.27 | Hypoglycemia, hepatic dysfunction, muscle weakness, cardiomyopathy, free carnitine deficiency and long-chain acylcarnitine excess responsive to medium chain triglyceride diet. ( Bier, DM; Brown, BI; Dickie, M; Engel, AG; Glasgow, AM; Perry, LW; Todaro, J; Utter, MF, 1983) |
| "Clinical studies revealed an absence of ketosis on fasting (plasma beta-hydroxybutyrate less than 0." | 5.27 | Medium-chain acyl-CoA dehydrogenase deficiency in children with non-ketotic hypoglycemia and low carnitine levels. ( Baker, L; Coates, PM; Corkey, BE; Gonzales, EL; Hale, DE; Hall, CL; Kelley, RI; Stanley, CA; Williamson, JR; Yang, W, 1983) |
| " Investigations revealed non-ketotic hypoglycemia suggesting FAOD which was later confirmed as carnitine uptake defect with gas chromatography and mass spectrometry and mutation analysis." | 3.85 | Infant with hepatomegaly and hypoglycemia: A setting for fatty acid oxidation defects. ( Pai, G; Poddar, U; Ravindranath, A; Srivastava, A; Yachha, SK, 2017) |
| "Long-term treatment with antibiotics containing pivalic acid may decrease serum carnitine concentration and can sometimes be associated with severe hypoglycemia and encephalopathy in infants." | 3.85 | Carnitine-related hypoglycemia caused by 3 days of pivalate antibiotic therapy in a patient with severe muscular dystrophy: a case report. ( Fukuda, M; Ishii, E; Ito, M; Suzuki, Y; Wakamoto, H, 2017) |
| " Laboratory data showed hypoglycemia and hypocarnitinemia." | 3.74 | Carnitine-associated encephalopathy caused by long-term treatment with an antibiotic containing pivalic acid. ( Ito, T; Koyama, N; Makino, Y; Sugiura, T; Sugiyama, N, 2007) |
| "The mechanism of onset of hypoglycemia in patients with carnitine deficiency has yet to be determined." | 3.74 | Reduced carnitine level causes death from hypoglycemia: possible involvement of suppression of hypothalamic orexin expression during weaning period. ( Doi, T; Fujihara, H; Inubushi, A; Kido, H; Kuwajima, M; Okamoto, T; Sei, H; Sei, M; Sukeno, A; Tsuda, TT; Ueta, Y; Umehara, A, 2007) |
| " She had a high fever, hypocarnitinemic and non-ketotic hypoglycemia, serum levels of total carnitine 7." | 3.74 | Hypocarnitinemic hypoglycemia and heart failure in an infant with a constant parenteral elementary nutrition during measles vaccination-related febrile illness. ( Izumi, T; Maeda, T; Okanari, K; Sato, K; Suenobu, S; Takahashi, M, 2007) |
| "Concerns have been raised as to the safety of using pivaloyl-conjugated beta-lactam antibiotics during pregnancy as they cause carnitine depletion." | 3.71 | Birth outcome and risk of neonatal hypoglycaemia following in utero exposure to pivmecillinam: a population-based cohort study with 414 exposed pregnancies. ( Ebbesen, F; Larsen, H; Møller, M; Nielsen, GL; Schønheyder, HC; Sørensen, HT, 2001) |
| " However, unlike other children with hyperinsulinism, this patient had a persistently elevated blood spot hydroxybutyrylcarnitine concentration when fed, as well as when fasted." | 3.71 | Hyperinsulinism in short-chain L-3-hydroxyacyl-CoA dehydrogenase deficiency reveals the importance of beta-oxidation in insulin secretion. ( Aynsley-Green, A; Berger, R; Clayton, PT; Datta, V; Eaton, S; Edginton, M; Hussain, K; Krywawych, S; Malingre, HE; van den Berg, IE, 2001) |
| "Here, we report the case of a 17-year-old girl who presented in both ten months and five years of age a clinical picture characterized by lethargy leading to apnea and coma, hepatomegaly, hypoglycemia, metabolic acidosis, hyperammoniemia, elevated serum transaminases and absence of ketonuria." | 3.70 | [3-hydroxy-3-methylglutaric aciduria and recurrent Reye-like syndrome]. ( Castro-Gago, M; Eirís, J; Fernández-Prieto, R; Ribes, A; Rodríguez-García, J; Rodríguez-Segade, S, 1998) |
| " Laboratory evaluation revealed hypoglycemia, hyperammonemia, lactic acidemia, hyperuricemia, and mild dicarboxylic aciduria." | 3.70 | Carnitine-acylcarnitine translocase deficiency: metabolic consequences of an impaired mitochondrial carnitine cycle. ( Dorland, L; Duran, M; IJlst, L; Muntau, AC; Roscher, AA; Röschinger, W; Wanders, RJ, 2000) |
| "Deficiency of the enzymes of mitochondrial fatty acid oxidation and related carnitine dependent steps have been shown to be one of the causes of the fasting-induced hypoketotic hypoglycemia." | 3.68 | Carnitine-acylcarnitine translocase deficiency with severe hypoglycemia and auriculo ventricular block. Translocase assay in permeabilized fibroblasts. ( Aufrant, C; Brivet, M; Demaugre, F; Pande, SV; Saudubray, JM; Slama, A, 1993) |
| "Since hypoglycemic neonates do not exhibit compensative ketosis, we investigated the possible involvement of carnitine deficiency or omega-oxidation in neonatal hypoglycemia." | 3.67 | Ketogenesis in hypoglycemic neonates. Carnitine and dicarboxylic acids in neonatal hypoglycemia. ( Cartier, B; Divry, P; Maire, I; Sann, L; Vianey-Laud, C, 1987) |
| "In systemic carnitine deficiency, an early phase of nonketotic hypoglycemia and liver dysfunction may precede a late phase of encephalopathy and myopathy." | 3.66 | Nonketotic hypoglycemia: an early indicator of systemic carnitine deficiency. ( Borum, PR; Diamond, MP; Mrak, RE; Najjar, J; Richardson, D; Slonim, AE, 1983) |
| "Recurrent episodes of hypoglycemia, prostration, vomiting, and hepatomegaly were observed in an infant fed a carnitine-free soy formula." | 3.66 | Dietary-dependent carnitine deficiency as a cause of nonketotic hypoglycemia in an infant. ( Borum, PR; Burr, IM; Greene, HL; Kasselberg, AG; Slonim, AE; Stanley, CA; Tanaka, K, 1981) |
| " As a consequence, long-term administration of pivalic acid containing antibiotics has been associated with depletion of free carnitine, inhibition of energy production and subsequent hypoglycemia." | 1.48 | Hypocarnitinemia Observed in an Infant Treated with Short-Term Administration of Antibiotic Containing Pivalic Acid. ( Fuchigami, T; Ishige, M; Ishige, N; Nakazaki, K; Ogawa, E; Takahashi, S, 2018) |
| "Carnitine transport was reduced to 20% or less of normal in fibroblasts of 140 out of 358 subjects." | 1.46 | Functional and molecular studies in primary carnitine deficiency. ( Balakrishnan, B; Calderon, FRO; Frigeni, M; Longo, N; Mao, R; Pasquali, M; Yin, X, 2017) |
| "Most patients manifested acute encephalopathy and/or hypoglycemia." | 1.43 | Clinical Features of Carnitine Deficiency Secondary to Pivalate-Conjugated Antibiotic Therapy. ( Fukuda, S; Hasegawa, Y; Kobayashi, H; Purevsuren, J; Takahashi, T; Yamada, K; Yamaguchi, S, 2016) |
| "Evolution was complicated by acute renal failure, increased serum levels of transaminases and hypoparathyroidism." | 1.35 | Hypoketotic hypoglycemia with myolysis and hypoparathyroidism: an unusual association in medium chain acyl-CoA desydrogenase deficiency (MCADD). ( Baruteau, J; Bloom, MC; Broué, P; Levade, T; Mesli, S; Redonnet-Vernhet, I, 2009) |
| "Severe hypoglycemia has been known to induce mitochondrial swelling followed by neuronal death in the brain." | 1.33 | L-carnitine inhibits hypoglycemia-induced brain damage in the rat. ( Hino, K; Inoue, M; Nishikawa, M; Sato, E, 2005) |
| "Systemic carnitine-deficient juvenile visceral steatosis (JVS) mice exhibit decreased expression of some liver-selective genes including those for the urea cycle enzymes during the infantile period." | 1.30 | Suppressed expression of the urea cycle enzyme genes in the liver of carnitine-deficient juvenile visceral steatosis (JVS) mice in infancy and during starvation in adulthood. ( Horiuchi, M; Mori, M; Musa, DA; Saheki, T; Takiguchi, M; Tomomura, A; Tomomura, M, 1997) |
| " In conclusion, this study suggests that short-term administration of LA at high dosage to normal and diabetic rats causes an inhibition of gluconeogenesis secondary to an interference with hepatic fatty acid oxidation." | 1.30 | Lipoic acid acutely induces hypoglycemia in fasting nondiabetic and diabetic rats. ( Bashan, N; Gutman, A; Khamaisi, M; Potashnik, R; Rudich, A; Tritschler, HJ, 1999) |
| "Juvenile visceral steatosis (JVS) mice are associated with systemic carnitine deficiency (Kuwajima, et al." | 1.29 | Carnitine transport defect in fibroblasts of juvenile visceral steatosis (JVS) mouse. ( Hanafusa, T; Harashima, H; Hayakawa, J; Kuwajima, M; Lu, K; Matsuzawa, Y; Miyagawa, J; Mizuno, A; Murakami, T; Nakajima, H; Namba, M; Ono, A; Sato, I; Shima, K, 1996) |
| "Fraternal twins who had fasting hypoglycemia, hypoketonemia, muscle weakness, and hepatic dysfunction are reported." | 1.27 | Hypoglycemia, hepatic dysfunction, muscle weakness, cardiomyopathy, free carnitine deficiency and long-chain acylcarnitine excess responsive to medium chain triglyceride diet. ( Bier, DM; Brown, BI; Dickie, M; Engel, AG; Glasgow, AM; Perry, LW; Todaro, J; Utter, MF, 1983) |
| "Thus, this disease is revealed by a coma due to hypoglycemia in a young child; the presence of dicarboxylic aciduria in such a situation is the main evidence for this diagnosis." | 1.27 | [Medium chain acyl-CoA dehydrogenase deficiency. Apropos of a case with demonstration of this enzyme deficiency]. ( Blanc, JF; Collet, JP; David, M; Divry, P; Guibaud, P; Hermier, M; Macabeo, V; Vibert, J, 1984) |
| "Clinical studies revealed an absence of ketosis on fasting (plasma beta-hydroxybutyrate less than 0." | 1.27 | Medium-chain acyl-CoA dehydrogenase deficiency in children with non-ketotic hypoglycemia and low carnitine levels. ( Baker, L; Coates, PM; Corkey, BE; Gonzales, EL; Hale, DE; Hall, CL; Kelley, RI; Stanley, CA; Williamson, JR; Yang, W, 1983) |
| "Of the nine patients with encephalopathy, eight showed improvement in their mental status." | 1.27 | Plasma carnitine deficiency. Clinical observations in 51 pediatric patients. ( Curry, CJ; Hogue, R; Hutchinson, HT; Shug, A; Szabo-Aczel, S; Winter, SC, 1987) |
| "Treatment with carnitine, started during the third period of artificial ventilation, led to some improvement of muscle strength, but he still could not breathe without support." | 1.27 | Glutaric aciduria type II: treatment with riboflavine, carnitine and insulin. ( Blom, W; Giesberts, MA; Mooy, PD; Przyrembel, H; Scholte, HR; van Gelderen, HH, 1984) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 21 (25.00) | 18.7374 |
| 1990's | 15 (17.86) | 18.2507 |
| 2000's | 18 (21.43) | 29.6817 |
| 2010's | 22 (26.19) | 24.3611 |
| 2020's | 8 (9.52) | 2.80 |
| Authors | Studies |
|---|---|
| Li, X | 1 |
| Ma, R | 1 |
| Liu, Y | 1 |
| Kang, L | 1 |
| He, R | 1 |
| Song, J | 1 |
| Ren, J | 1 |
| Li, Y | 2 |
| Huang, M | 1 |
| Men, J | 1 |
| Yang, Y | 1 |
| Alhashem, A | 1 |
| Mohamed, S | 1 |
| Abdelraheem, M | 1 |
| AlGufaydi, B | 1 |
| Al-Aqeel, A | 1 |
| Xu, ZR | 1 |
| Zhu, XY | 1 |
| Lu, W | 1 |
| Sun, WH | 1 |
| Cheng, RQ | 1 |
| Ni, JW | 1 |
| Xi, L | 1 |
| Hussain, K | 2 |
| Luo, FH | 1 |
| Zhang, MY | 1 |
| McGregor, TL | 1 |
| Berry, SA | 1 |
| Dipple, KM | 1 |
| Hamid, R | 1 |
| Zhou, Z | 1 |
| Yang, L | 1 |
| Liao, H | 1 |
| Ning, Z | 1 |
| Chen, B | 1 |
| Jiang, Z | 1 |
| Yang, S | 1 |
| Wang, M | 1 |
| Xiao, Z | 1 |
| Vasta, LM | 1 |
| Reynolds, SM | 1 |
| Sami, S | 1 |
| Schacht, JP | 1 |
| Emerick, JE | 1 |
| Parekh, DS | 1 |
| Vogt, KS | 1 |
| Yu, Y | 1 |
| Shen, LH | 1 |
| Qiu, WJ | 1 |
| Zhang, HW | 1 |
| Ye, J | 1 |
| Liang, LL | 1 |
| Wang, Y | 1 |
| Ji, WJ | 1 |
| Gu, XF | 1 |
| Han, LS | 1 |
| Chen, X | 1 |
| Kimura, B | 1 |
| Nagelberg, J | 1 |
| McCowen, KC | 1 |
| Frigeni, M | 1 |
| Balakrishnan, B | 1 |
| Yin, X | 1 |
| Calderon, FRO | 1 |
| Mao, R | 1 |
| Pasquali, M | 2 |
| Longo, N | 2 |
| Ravindranath, A | 1 |
| Pai, G | 1 |
| Srivastava, A | 1 |
| Poddar, U | 1 |
| Yachha, SK | 1 |
| Nakazaki, K | 1 |
| Ogawa, E | 1 |
| Ishige, M | 1 |
| Ishige, N | 1 |
| Fuchigami, T | 1 |
| Takahashi, S | 1 |
| Pinn, TL | 1 |
| Divers, TJ | 1 |
| Southard, T | 1 |
| De Bernardis, NP | 1 |
| Wakshlag, JJ | 1 |
| Valberg, S | 1 |
| Tarasenko, TN | 1 |
| Cusmano-Ozog, K | 1 |
| McGuire, PJ | 1 |
| Janeiro, P | 1 |
| Jotta, R | 1 |
| Ramos, R | 1 |
| Florindo, C | 1 |
| Ventura, FV | 1 |
| Vilarinho, L | 1 |
| Tavares de Almeida, I | 1 |
| Gaspar, A | 1 |
| Phowthongkum, P | 1 |
| Suphapeetiporn, K | 1 |
| Shotelersuk, V | 1 |
| Hanai, S | 1 |
| Iwata, M | 1 |
| Terasawa, T | 1 |
| van Rijt, WJ | 1 |
| van der Ende, RM | 1 |
| Volker-Touw, CML | 1 |
| van Spronsen, F | 1 |
| Derks, TGJ | 1 |
| Heiner-Fokkema, MR | 1 |
| Gautschi, M | 1 |
| Weisstanner, C | 1 |
| Slotboom, J | 1 |
| Nava, E | 1 |
| Zürcher, T | 1 |
| Nuoffer, JM | 1 |
| Köksal, T | 1 |
| Gündüz, M | 1 |
| Özaydın, E | 1 |
| Azak, E | 1 |
| Virmani, A | 1 |
| Pinto, L | 1 |
| Bauermann, O | 1 |
| Zerelli, S | 1 |
| Diedenhofen, A | 1 |
| Binienda, ZK | 1 |
| Ali, SF | 1 |
| van der Leij, FR | 1 |
| Miller, MJ | 1 |
| Burrage, LC | 1 |
| Gibson, JB | 1 |
| Strenk, ME | 1 |
| Lose, EJ | 1 |
| Bick, DP | 1 |
| Elsea, SH | 1 |
| Sutton, VR | 1 |
| Sun, Q | 1 |
| Graham, BH | 1 |
| Craigen, WJ | 1 |
| Zhang, VW | 1 |
| Wong, LJ | 1 |
| Hisano, Y | 1 |
| Kaneto, H | 1 |
| Kimura, T | 1 |
| Ota, T | 1 |
| Kamao, T | 1 |
| Uno, M | 1 |
| Mizushima, T | 1 |
| Mune, T | 1 |
| Kaku, K | 1 |
| Kobayashi, H | 2 |
| Fukuda, S | 2 |
| Yamada, K | 2 |
| Hasegawa, Y | 2 |
| Takahashi, T | 2 |
| Purevsuren, J | 2 |
| Yamaguchi, S | 2 |
| Sood, V | 1 |
| Rawat, D | 1 |
| Khanna, R | 1 |
| Sharma, S | 1 |
| Gupta, PK | 1 |
| Alam, S | 1 |
| Sarin, SK | 1 |
| Ito, M | 1 |
| Fukuda, M | 1 |
| Suzuki, Y | 1 |
| Wakamoto, H | 1 |
| Ishii, E | 1 |
| Pierron, S | 1 |
| Giudicelli, H | 1 |
| Moreigne, M | 1 |
| Khalfi, A | 1 |
| Touati, G | 1 |
| Caruba, C | 1 |
| Rolland, MO | 1 |
| Acquaviva, C | 1 |
| Hirschey, MD | 1 |
| Shimazu, T | 1 |
| Goetzman, E | 1 |
| Jing, E | 1 |
| Schwer, B | 1 |
| Lombard, DB | 1 |
| Grueter, CA | 1 |
| Harris, C | 1 |
| Biddinger, S | 1 |
| Ilkayeva, OR | 1 |
| Stevens, RD | 1 |
| Saha, AK | 1 |
| Ruderman, NB | 1 |
| Bain, JR | 1 |
| Newgard, CB | 1 |
| Farese, RV | 1 |
| Alt, FW | 1 |
| Kahn, CR | 1 |
| Verdin, E | 1 |
| Baruteau, J | 1 |
| Levade, T | 1 |
| Redonnet-Vernhet, I | 1 |
| Mesli, S | 1 |
| Bloom, MC | 1 |
| Broué, P | 1 |
| Gillingham, MB | 1 |
| Hirschfeld, M | 1 |
| Lowe, S | 1 |
| Matern, D | 1 |
| Shoemaker, J | 1 |
| Lambert, WE | 1 |
| Koeller, DM | 1 |
| Rosa, M | 1 |
| Pascarella, A | 1 |
| Parenti, G | 1 |
| Buono, S | 1 |
| Romano, A | 1 |
| Della Casa, R | 1 |
| Andria, G | 1 |
| Marino, M | 1 |
| Riccio, MP | 1 |
| Bravaccio, C | 1 |
| Takayanagi, M | 1 |
| Fukao, T | 1 |
| Wraige, E | 1 |
| Champion, MP | 1 |
| Turner, C | 1 |
| Dalton, RN | 1 |
| Halonen, P | 1 |
| Salo, MK | 1 |
| Schmiegelow, K | 1 |
| Mäkipernaa, A | 1 |
| Laberge, AM | 1 |
| Mitchell, GA | 1 |
| van de Werve, G | 1 |
| Lambert, M | 1 |
| Bischof, F | 1 |
| Nägele, T | 1 |
| Wanders, RJ | 3 |
| Trefz, FK | 2 |
| Melms, A | 1 |
| Makhseed, N | 1 |
| Vallance, HD | 1 |
| Potter, M | 1 |
| Waters, PJ | 1 |
| Wong, LT | 1 |
| Lillquist, Y | 1 |
| Amat di San Filippo, C | 1 |
| Gordon, N | 1 |
| Hino, K | 1 |
| Nishikawa, M | 1 |
| Sato, E | 1 |
| Inoue, M | 1 |
| Engbers, HM | 1 |
| Dorland, L | 2 |
| de Sain, MG | 1 |
| Eskes, PF | 1 |
| Visser, G | 1 |
| Bodamer, OA | 1 |
| Hussein, K | 1 |
| Morris, AA | 1 |
| Langhans, CD | 1 |
| Rating, D | 1 |
| Mayatepek, E | 1 |
| Leonard, JV | 2 |
| Pierre, G | 1 |
| Macdonald, A | 1 |
| Gray, G | 1 |
| Hendriksz, C | 1 |
| Preece, MA | 2 |
| Chakrapani, A | 1 |
| Makino, Y | 1 |
| Sugiura, T | 1 |
| Ito, T | 1 |
| Sugiyama, N | 1 |
| Koyama, N | 1 |
| Kuwajima, M | 3 |
| Fujihara, H | 1 |
| Sei, H | 1 |
| Umehara, A | 1 |
| Sei, M | 1 |
| Tsuda, TT | 1 |
| Sukeno, A | 1 |
| Okamoto, T | 1 |
| Inubushi, A | 1 |
| Ueta, Y | 1 |
| Doi, T | 1 |
| Kido, H | 1 |
| Okanari, K | 1 |
| Takahashi, M | 1 |
| Maeda, T | 1 |
| Sato, K | 1 |
| Suenobu, S | 1 |
| Izumi, T | 1 |
| Entman, M | 1 |
| Bressler, R | 3 |
| Benzi, G | 1 |
| Gorini, A | 1 |
| Dossena, M | 1 |
| Taglietti, M | 1 |
| Fulle, D | 1 |
| Pastoris, O | 1 |
| Mooy, PD | 1 |
| Przyrembel, H | 1 |
| Giesberts, MA | 1 |
| Scholte, HR | 1 |
| Blom, W | 1 |
| van Gelderen, HH | 1 |
| Duran, M | 2 |
| De Klerk, JB | 1 |
| Wadman, SK | 1 |
| Bruinvis, L | 1 |
| Ketting, D | 1 |
| Collet, JP | 1 |
| Divry, P | 3 |
| Blanc, JF | 1 |
| Guibaud, P | 1 |
| David, M | 1 |
| Macabeo, V | 1 |
| Vibert, J | 1 |
| Hermier, M | 1 |
| Stanley, CA | 3 |
| Hale, DE | 2 |
| Coates, PM | 2 |
| Hall, CL | 1 |
| Corkey, BE | 1 |
| Yang, W | 1 |
| Kelley, RI | 2 |
| Gonzales, EL | 1 |
| Williamson, JR | 1 |
| Baker, L | 1 |
| Slonim, AE | 2 |
| Borum, PR | 2 |
| Mrak, RE | 1 |
| Najjar, J | 1 |
| Richardson, D | 1 |
| Diamond, MP | 1 |
| Glasgow, AM | 1 |
| Engel, AG | 1 |
| Bier, DM | 1 |
| Perry, LW | 1 |
| Dickie, M | 1 |
| Todaro, J | 1 |
| Brown, BI | 1 |
| Utter, MF | 1 |
| Tanaka, K | 2 |
| Kasselberg, AG | 1 |
| Greene, HL | 1 |
| Burr, IM | 1 |
| Linz, DN | 1 |
| Garcia, VF | 1 |
| Arya, G | 1 |
| Hug, G | 1 |
| Tombragel, E | 1 |
| Landrigan, E | 1 |
| Chuck, G | 1 |
| Tsoras, M | 1 |
| Ryan, M | 1 |
| Ziegler, MM | 1 |
| Sewell, AC | 1 |
| Bender, SW | 1 |
| Wirth, S | 1 |
| Münterfering, H | 1 |
| Ijlist, L | 1 |
| Moore, R | 1 |
| Glasgow, JF | 1 |
| Bingham, MA | 1 |
| Dodge, JA | 1 |
| Pollitt, RJ | 2 |
| Olpin, SE | 1 |
| Middleton, B | 1 |
| Carpenter, K | 1 |
| Pande, SV | 1 |
| Brivet, M | 1 |
| Slama, A | 1 |
| Demaugre, F | 1 |
| Aufrant, C | 1 |
| Saudubray, JM | 2 |
| Lu, K | 1 |
| Harashima, H | 1 |
| Ono, A | 2 |
| Sato, I | 1 |
| Mizuno, A | 1 |
| Murakami, T | 1 |
| Nakajima, H | 2 |
| Miyagawa, J | 2 |
| Namba, M | 2 |
| Hanafusa, T | 2 |
| Hayakawa, J | 2 |
| Matsuzawa, Y | 2 |
| Shima, K | 1 |
| Hotta, K | 1 |
| Horikawa, Y | 1 |
| Horiuchi, M | 3 |
| Nikaido, H | 1 |
| Saheki, T | 3 |
| Kono, N | 1 |
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| Tomomura, M | 2 |
| Tomomura, A | 2 |
| Musa, DA | 1 |
| Takiguchi, M | 1 |
| Mori, M | 1 |
| Imamura, Y | 1 |
| Abdullah Abue Musa, D | 1 |
| Kobayashi, K | 1 |
| Eirís, J | 1 |
| Ribes, A | 1 |
| Fernández-Prieto, R | 1 |
| Rodríguez-García, J | 1 |
| Rodríguez-Segade, S | 1 |
| Castro-Gago, M | 1 |
| Shortland, GJ | 1 |
| Walter, JH | 1 |
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| Fleming, PJ | 1 |
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| Doig, M | 1 |
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| Morris, M | 1 |
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| Tritschler, HJ | 1 |
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| Trial | Phase | Enrollment | Study Type | Start Date | Status | ||
|---|---|---|---|---|---|---|---|
| Metabolic Consequences of CPT1A Deficiency in Alaska Native Children[NCT00653666] | 12 participants (Anticipated) | Interventional | 2007-10-31 | Completed | |||
| [information is prepared from clinicaltrials.gov, extracted Sep-2024] | |||||||
4 reviews available for carnitine and Hypoglycemia
| Article | Year |
|---|---|
Long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency: a severe fatty acid oxidation disorder.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Cardiomyopathies; Carnitine; Clinical Enzyme Tests; Fatal Outcome; | 1994 |
Abnormal gene expression causing hyperammonemia in carnitine-deficient juvenile visceral steatosis (JVS) mice.
Topics: Ammonia; Animals; Carnitine; Fatty Liver; Gene Expression Regulation, Enzymologic; Genes, Recessive; | 1997 |
Chronic cardiomyopathy and weakness or acute coma in children with a defect in carnitine uptake.
Topics: Biological Transport; Cardiomyopathies; Carnitine; Cells, Cultured; Child; Child, Preschool; Coma; F | 1991 |
Hypoglycin and hypoglycin-like compounds.
Topics: Amino Acids; Animals; Blood Glucose; Carnitine; Chemical Phenomena; Chemistry; Cholesterol; Coenzyme | 1969 |
3 trials available for carnitine and Hypoglycemia
| Article | Year |
|---|---|
Impaired fasting tolerance among Alaska native children with a common carnitine palmitoyltransferase 1A sequence variant.
Topics: Alaska; American Indian or Alaska Native; Body Mass Index; Carnitine; Carnitine O-Palmitoyltransfera | 2011 |
Randomised controlled trial of L-carnitine as a nutritional supplement in preterm infants.
Topics: Carnitine; Dietary Supplements; Double-Blind Method; Female; Growth; Humans; Hypoglycemia; Infant, N | 1998 |
Screening for medium chain acyl-CoA dehydrogenase deficiency using electrospray ionisation tandem mass spectrometry.
Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Adolescent; Age Distribution; Aging; Carnitine; Chi | 1998 |
77 other studies available for carnitine and Hypoglycemia
| Article | Year |
|---|---|
One potential hotspot ACADVL mutation in Chinese patients with very-long-chain acyl-coenzyme A dehydrogenase deficiency.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Asian People; Carnitine; China; Congenital Bone Marrow Failure S | 2020 |
Molecular and clinical characteristics of very-long-chain acyl-CoA dehydrogenase deficiency: A single-center experience in Saudi Arabia.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Cardiomyopathies; Carnitine; Cohort Studies; Congenital Bone Mar | 2020 |
Altered Serum Amino Acid and Acylcarnitine Profiles in Hyperinsulinemic Hypoglycemia and Ketotic Hypoglycemia.
Topics: Amino Acids; Biomarkers; Carnitine; Case-Control Studies; Child, Preschool; Congenital Hyperinsulini | 2020 |
Management Principles for Acute Illness in Patients With Medium-Chain Acyl-Coenzyme A Dehydrogenase Deficiency.
Topics: Acyl-CoA Dehydrogenase; Carnitine; Child; Emergencies; Fluid Therapy; Glucose; Humans; Hypoglycemia; | 2021 |
[Analysis of a child with carnitine palmitoyl transferase 1A deficiency due to variant of CPT1A gene].
Topics: Carnitine; Carnitine O-Palmitoyltransferase; Child; DNA Mutational Analysis; Female; Humans; Hypogly | 2021 |
Hypoglycemia Due to Acquired Carnitine Deficiency in a Pediatric Patient Receiving Chemotherapy.
Topics: Cardiomyopathies; Carnitine; Child; Humans; Hyperammonemia; Hypoglycemia; Infant; Male; Malnutrition | 2022 |
[Clinical features and gene mutations of 6 patients with carnitine palmitoyltransferase 1A deficiency].
Topics: Aged; Carnitine; Carnitine O-Palmitoyltransferase; Child; Child, Preschool; Female; Humans; Hypoglyc | 2021 |
Fasting hypoglycaemia secondary to carnitine deficiency: a late consequence of gastric bypass.
Topics: Aged; C-Peptide; Carnitine; Fasting; Female; Gastric Bypass; Humans; Hypoglycemia; Insulin; Malnutri | 2021 |
Functional and molecular studies in primary carnitine deficiency.
Topics: Amino Acid Substitution; Animals; Biological Transport; Cardiomyopathies; Carnitine; CHO Cells; Cric | 2017 |
Infant with hepatomegaly and hypoglycemia: A setting for fatty acid oxidation defects.
Topics: Cardiomyopathies; Carnitine; Chromatography, Gas; DNA Mutational Analysis; Early Diagnosis; Hepatome | 2017 |
Hypocarnitinemia Observed in an Infant Treated with Short-Term Administration of Antibiotic Containing Pivalic Acid.
Topics: Anti-Bacterial Agents; Carbon; Carnitine; Humans; Hypoglycemia; Infant; Male; Metabolic Diseases; Ox | 2018 |
Persistent hypoglycemia associated with lipid storage myopathy in a paint foal.
Topics: Animals; Carnitine; Diagnosis, Differential; Fatal Outcome; Female; Horse Diseases; Horses; Hypoglyc | 2018 |
Tissue acylcarnitine status in a mouse model of mitochondrial β-oxidation deficiency during metabolic decompensation due to influenza virus infection.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Animals; Cardiomyopathies; Carnitine; Congenital Bone Marrow Fai | 2018 |
Follow-up of fatty acid β-oxidation disorders in expanded newborn screening era.
Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenase, Long-Chain; Amino Acid Metabolism, Inborn Errors; Ca | 2019 |
Carnitine palmitoyl transferase 1A deficiency in an adult with recurrent severe steato hepatitis aggravated by high pathologic or physiologic demands: A roller-coaster for internists.
Topics: Adult; Anti-Bacterial Agents; Carnitine; Carnitine O-Palmitoyltransferase; Escherichia coli Infectio | 2019 |
Relapsing Hypoglycemia Associated with Hypocarnitinemia Following Treatment with Cefcapene Pivoxil in an Elderly Man.
Topics: Administration, Oral; Aged, 80 and over; Blood Glucose; Cardiomyopathies; Carnitine; Cephalosporins; | 2019 |
Changes in pediatric plasma acylcarnitines upon fasting for refined interpretation of metabolic stress.
Topics: Blood Glucose; Carnitine; Child; Child, Preschool; Fasting; Female; Homeostasis; Humans; Hypoglycemi | 2019 |
Highly efficient ketone body treatment in multiple acyl-CoA dehydrogenase deficiency-related leukodystrophy.
Topics: Brain; Carnitine; Child, Preschool; Coma; Consanguinity; Dietary Fats; Hereditary Central Nervous Sy | 2015 |
3-HMG Coenzyme A Lyase Deficiency: Macrocephaly and Left Ventricular Noncompaction with a Novel Mutation.
Topics: Acetyl-CoA C-Acetyltransferase; Amino Acid Metabolism, Inborn Errors; Carnitine; Diet, Fat-Restricte | 2015 |
The Carnitine Palmitoyl Transferase (CPT) System and Possible Relevance for Neuropsychiatric and Neurological Conditions.
Topics: Animals; Brain; Cardiovascular Diseases; Carnitine; Carnitine O-Palmitoyltransferase; Ceramides; Dia | 2015 |
Recurrent ACADVL molecular findings in individuals with a positive newborn screen for very long chain acyl-coA dehydrogenase (VLCAD) deficiency in the United States.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Alleles; Carnitine; Computer Simulation; Congenital Bone Marrow | 2015 |
Hemodialysis Associated with Severe and Unpredictable Hypoglycemia.
Topics: Aged; Autopsy; Blood Glucose; Cardiomyopathies; Carnitine; Diabetes Mellitus, Type 2; Fatal Outcome; | 2016 |
Clinical Features of Carnitine Deficiency Secondary to Pivalate-Conjugated Antibiotic Therapy.
Topics: Adolescent; Adult; Anti-Bacterial Agents; Brain Diseases; Carnitine; Child; Child, Preschool; Female | 2016 |
Study of Carnitine/Acylcarnitine and Amino Acid Profile in Children and Adults With Acute Liver Failure.
Topics: Adolescent; Adult; Amino Acids; Biomarkers; Carnitine; Carnitine O-Palmitoyltransferase; Child; Chil | 2017 |
Carnitine-related hypoglycemia caused by 3 days of pivalate antibiotic therapy in a patient with severe muscular dystrophy: a case report.
Topics: Anti-Bacterial Agents; Biomarkers; Carnitine; Cephalosporins; Child; Female; Humans; Hypoglycemia; P | 2017 |
[Late onset 3-HMG-CoA lyase deficiency: a rare but treatable disorder].
Topics: Alleles; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromosome Aberrations; | 2010 |
SIRT3 regulates mitochondrial fatty-acid oxidation by reversible enzyme deacetylation.
Topics: Acetylation; Acyl-CoA Dehydrogenase, Long-Chain; Adenosine Triphosphate; Adipose Tissue, Brown; Anim | 2010 |
Hypoketotic hypoglycemia with myolysis and hypoparathyroidism: an unusual association in medium chain acyl-CoA desydrogenase deficiency (MCADD).
Topics: Acute Kidney Injury; Acyl-CoA Dehydrogenase; Carnitine; Child, Preschool; Female; Glucose; Humans; H | 2009 |
Developmental evolution in a patient with multiple acyl-coenzymeA dehydrogenase deficiency under pharmacological treatment.
Topics: Acidosis; Acyl-CoA Dehydrogenase; Amino Acid Metabolism, Inborn Errors; Carnitine; Child Development | 2012 |
Intracellular in vitro probe acylcarnitine assay for identifying deficiencies of carnitine transporter and carnitine palmitoyltransferase-1.
Topics: Biological Transport; Cardiomyopathies; Carnitine; Carnitine Acyltransferases; Carnitine O-Palmitoyl | 2013 |
Fat oxidation defect presenting with overwhelming ketonuria.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Brain Diseases, Metabolic; Carnitine; Female; Humans; Hypoglycem | 2002 |
Investigation of the mechanisms of therapy-related hypoglycaemia in children with acute lymphoblastic leukaemia.
Topics: Adolescent; Alanine; Antineoplastic Combined Chemotherapy Protocols; Blood Glucose; Carnitine; Child | 2003 |
Long-term follow-up of a new case of liver glycogen synthase deficiency.
Topics: Adolescent; Amino Acids; Carnitine; Electroencephalography; Fasting; Female; Follow-Up Studies; Glyc | 2003 |
3-hydroxy-3-methylglutaryl-CoA lyase deficiency in an adult with leukoencephalopathy.
Topics: Adult; Brain Diseases; Carnitine; Female; Fibroblasts; Glutarates; Humans; Hypoglycemia; Leukocytes; | 2004 |
Carnitine transporter defect due to a novel mutation in the SLC22A5 gene presenting with peripheral neuropathy.
Topics: Carnitine; Child, Preschool; Electromyography; Female; Humans; Hypoglycemia; Mutation; Organic Catio | 2004 |
Acyl-CoA dehydrogenase deficiency: varieties with neurological involvement.
Topics: Acyl-CoA Dehydrogenase; Carnitine; Child; Child, Preschool; Chromosome Aberrations; Developmental Di | 2005 |
L-carnitine inhibits hypoglycemia-induced brain damage in the rat.
Topics: Aldehydes; Analysis of Variance; Animals; Apoptosis; Benzimidazoles; Brain Injuries; Carbocyanines; | 2005 |
Rhabdomyolysis in early-onset very long-chain acyl-CoA dehydrogenase deficiency despite normal glucose after fasting.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Blood Glucose; Carnitine; Fasting; Glucose; Humans; Hypoglycemia | 2005 |
Glucose and leucine kinetics in idiopathic ketotic hypoglycaemia.
Topics: Alanine; Amino Acids, Branched-Chain; Basal Metabolism; Calorimetry, Indirect; Carnitine; Case-Contr | 2006 |
Prospective treatment in carnitine-acylcarnitine translocase deficiency.
Topics: Carnitine; Carnitine Acyltransferases; Dicarboxylic Acids; Diet, Fat-Restricted; Dietary Supplements | 2007 |
Carnitine-associated encephalopathy caused by long-term treatment with an antibiotic containing pivalic acid.
Topics: Acidosis; Anti-Bacterial Agents; Brain Diseases, Metabolic; Carnitine; Cephalosporins; Humans; Hypog | 2007 |
Reduced carnitine level causes death from hypoglycemia: possible involvement of suppression of hypothalamic orexin expression during weaning period.
Topics: 3-Hydroxybutyric Acid; Animals; Behavior, Animal; Blood Glucose; Carnitine; Cellulose; Darkness; Fem | 2007 |
Hypocarnitinemic hypoglycemia and heart failure in an infant with a constant parenteral elementary nutrition during measles vaccination-related febrile illness.
Topics: Carnitine; Female; Heart Failure; Humans; Hypoglycemia; Infant; Magnetic Resonance Imaging; Measles | 2007 |
The mechanism of action of hypoglycin on long-chain fatty acid oxidation.
Topics: Acyltransferases; Aniline Compounds; Animals; Carbon Isotopes; Carnitine; Hypoglycemia; Lipid Metabo | 1967 |
Recovery after hypoglycemic brain injury. Action of some biological substances on the cerebral metabolism.
Topics: Acetylcarnitine; Animals; Brain; Carnitine; Cytidine; Dogs; Female; Hypoglycemia; Insulin; Papaverin | 1983 |
Glutaric aciduria type II: treatment with riboflavine, carnitine and insulin.
Topics: Biopsy; Carnitine; Fatty Acid Desaturases; Glutarates; Humans; Hypoglycemia; Infant; Insulin; Male; | 1984 |
The differential diagnosis of dicarboxylic aciduria.
Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Adolescent; Carnitine; Child; Child, Preschool; Dia | 1984 |
[Medium chain acyl-CoA dehydrogenase deficiency. Apropos of a case with demonstration of this enzyme deficiency].
Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Carnitine; Cells, Cultured; Coma; Diagnosis, Differ | 1984 |
Medium-chain acyl-CoA dehydrogenase deficiency in children with non-ketotic hypoglycemia and low carnitine levels.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Carnitine; Child; Child, Preschool; Fasting; Fatty Acids; Fatty | 1983 |
Nonketotic hypoglycemia: an early indicator of systemic carnitine deficiency.
Topics: Brain Diseases; Carnitine; Child; Child, Preschool; Female; Humans; Hypoglycemia; Liver; Male; Muscl | 1983 |
Hypoglycemia, hepatic dysfunction, muscle weakness, cardiomyopathy, free carnitine deficiency and long-chain acylcarnitine excess responsive to medium chain triglyceride diet.
Topics: Cardiomyopathies; Carnitine; Dietary Fats; Diseases in Twins; Female; Humans; Hypoglycemia; Infant; | 1983 |
Dietary-dependent carnitine deficiency as a cause of nonketotic hypoglycemia in an infant.
Topics: Carnitine; Child, Preschool; Dicarboxylic Acids; Female; Humans; Hypoglycemia; Infant; Infant Food | 1981 |
Weanling and adult rats differ in fatty acid and carnitine metabolism during sepsis.
Topics: 3-Hydroxybutyric Acid; Aging; Animals; Bacterial Infections; Blood Glucose; Carnitine; Fatty Acids; | 1995 |
Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency--diagnosis, plasma carnitine fractions and management in a further patient.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Cardiomyopathies; Carnitine; Female; Gastrointestinal Diseases; Hu | 1993 |
Carnitine-acylcarnitine translocase deficiency with severe hypoglycemia and auriculo ventricular block. Translocase assay in permeabilized fibroblasts.
Topics: Carnitine; Carnitine Acyltransferases; Carnitine O-Palmitoyltransferase; Cell Membrane Permeability; | 1993 |
Carnitine transport defect in fibroblasts of juvenile visceral steatosis (JVS) mouse.
Topics: Animals; Betaine; Biological Transport; Carnitine; Cells, Cultured; Fatty Liver; Fetus; Fibroblasts; | 1996 |
Disordered expression of glycolytic and gluconeogenic liver enzymes of juvenile visceral steatosis mice with systemic carnitine deficiency.
Topics: Age Factors; Animals; Blotting, Northern; Carnitine; Disease Models, Animal; Fatty Liver; Fructose-B | 1996 |
Suppressed expression of the urea cycle enzyme genes in the liver of carnitine-deficient juvenile visceral steatosis (JVS) mice in infancy and during starvation in adulthood.
Topics: Age Factors; Animals; Argininosuccinate Synthase; Basic Helix-Loop-Helix Leucine Zipper Transcriptio | 1997 |
[3-hydroxy-3-methylglutaric aciduria and recurrent Reye-like syndrome].
Topics: Acidosis; Adolescent; Apnea; Carnitine; Coma; Diagnosis, Differential; Fatty Liver; Female; Fibrobla | 1998 |
Lipoic acid acutely induces hypoglycemia in fasting nondiabetic and diabetic rats.
Topics: 3-Hydroxybutyric Acid; Alanine; Animals; Blood Glucose; Carnitine; Diabetes Mellitus, Experimental; | 1999 |
Identification of two novel mutations in the hypoglycemic phenotype of very long chain acyl-CoA dehydrogenase deficiency.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Alleles; Carnitine; Child, Preschool; DNA, Complementary; Exons; | 1999 |
Carnitine-acylcarnitine translocase deficiency: metabolic consequences of an impaired mitochondrial carnitine cycle.
Topics: Ammonia; Cardiac Output, Low; Carnitine; Carnitine Acyltransferases; Cells, Cultured; Coma; Consangu | 2000 |
Birth outcome and risk of neonatal hypoglycaemia following in utero exposure to pivmecillinam: a population-based cohort study with 414 exposed pregnancies.
Topics: Abnormalities, Drug-Induced; Adolescent; Adult; Amdinocillin Pivoxil; Carnitine; Denmark; Embryonic | 2001 |
Hyperinsulinism in short-chain L-3-hydroxyacyl-CoA dehydrogenase deficiency reveals the importance of beta-oxidation in insulin secretion.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Amino Acid Sequence; Animals; Base Sequence; Carnitine; DNA Primer | 2001 |
Carnitine levels and the ketogenic diet.
Topics: Adolescent; Adult; Carnitine; Child; Child, Preschool; Dietary Carbohydrates; Dietary Fats; Epilepsy | 2001 |
Recurrent hypoglycemia associated with glutaric aciduria type II in an adult.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Carnitine; Fatty Acid Desaturases; Fatty Acids, Noneste | 1979 |
A case of metabolic mimicry.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Carnitine; Cyclopropanes; Diagnosis, Differential; Fatt | 1979 |
Systemic carnitine deficiency. Report of a fatal case with multisystemic manifestations.
Topics: Adolescent; Autopsy; Carnitine; Humans; Hypoglycemia; Liver; Male; Muscles; Myocardium | 1978 |
Possible deleterious effect of L-carnitine supplementation in a patient with mild multiple acyl-CoA dehydrogenation deficiency (ethylmalonic-adipic aciduria).
Topics: Acyl-CoA Dehydrogenases; Adipates; Carnitine; Child; Humans; Hypoglycemia; Male; Malonates; Riboflav | 1991 |
Transient carnitine-responsive medium-chain dicarboxylic aciduria in an infant with cholestasis, hypoglycemia and cardiac failure.
Topics: Carnitine; Carnitine O-Palmitoyltransferase; Cholestasis; Dicarboxylic Acids; Female; Heart Failure; | 1989 |
Plasma carnitine deficiency. Clinical observations in 51 pediatric patients.
Topics: Adolescent; Brain Diseases; Cardiomyopathies; Carnitine; Child; Child, Preschool; Failure to Thrive; | 1987 |
Ketogenesis in hypoglycemic neonates. Carnitine and dicarboxylic acids in neonatal hypoglycemia.
Topics: 3-Hydroxybutyric Acid; Acetoacetates; Blood Glucose; Carnitine; Creatinine; Dicarboxylic Acids; Fatt | 1987 |
Familial Reye-like syndrome: a presentation of medium-chain acyl-coenzyme A dehydrogenase deficiency.
Topics: Acyl-CoA Dehydrogenase; Carboxylic Acids; Carnitine; Diagnosis, Differential; Fatty Acid Desaturases | 1987 |
Protection of rats by clofibrate against the hypoglycaemic and toxic effects of hypoglycin and pent-4-enoate. An ultrastructural and biochemical study.
Topics: Animals; Carnitine; Clofibrate; Cyclopropanes; Fatty Acids, Monounsaturated; Fatty Acids, Unsaturate | 1985 |
The apparent failure of L-carnitine to prevent the hypoglycaemia and hypothermia caused by hypoglycin or by pent-4-enoic acid in mice.
Topics: Alanine; Animals; Blood Glucose; Body Temperature; Carnitine; Cyclopropanes; Diet; Hypoglycemia; Hyp | 1973 |
Studies of the mechanism of the hypoglycemic action of 4-pentenoic acid.
Topics: Acrylates; Animals; Blood Glucose; Carnitine; Gluconeogenesis; Glucose; Hypoglycemia; Male; Mice; My | 1967 |
Effects of guanidine derivatives on mitochondrial function. I. Phenethylbiguanide inhibition of respiration in mitochondria from guinea pig and rat tissues.
Topics: Adenine Nucleotides; Animals; Carbon Isotopes; Carnitine; Citric Acid Cycle; Coenzyme A; Depression, | 1968 |