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carbonyl cyanide m-chlorophenyl hydrazone and Peroxisomal Disorders

carbonyl cyanide m-chlorophenyl hydrazone has been researched along with Peroxisomal Disorders in 1 studies

Carbonyl Cyanide m-Chlorophenyl Hydrazone: A proton ionophore. It is commonly used as an uncoupling agent and inhibitor of photosynthesis because of its effects on mitochondrial and chloroplast membranes.
CCCP : A member of the class of monochlorobenzenes that is benzene substituted by 2-(1,3-dinitrilopropan-2-ylidene)hydrazinyl and chloro groups at positions 1 and 3, respectively. It is a mitochondrial depolarizing agent that induces reactive oxygen species mediated cell death.

Peroxisomal Disorders: A heterogeneous group of inherited metabolic disorders marked by absent or dysfunctional PEROXISOMES. Peroxisomal enzymatic abnormalities may be single or multiple. Biosynthetic peroxisomal pathways are compromised, including the ability to synthesize ether lipids and to oxidize long-chain fatty acid precursors. Diseases in this category include ZELLWEGER SYNDROME; INFANTILE REFSUM DISEASE; rhizomelic chondrodysplasia (CHONDRODYSPLASIA PUNCTATA, RHIZOMELIC); hyperpipecolic acidemia; neonatal adrenoleukodystrophy; and ADRENOLEUKODYSTROPHY (X-linked). Neurologic dysfunction is a prominent feature of most peroxisomal disorders.

Research

Studies (1)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (100.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Dansen, TB1
Wirtz, KW1
Wanders, RJ1
Pap, EH1

Other Studies

1 other study available for carbonyl cyanide m-chlorophenyl hydrazone and Peroxisomal Disorders

ArticleYear
Peroxisomes in human fibroblasts have a basic pH.
    Nature cell biology, 2000, Volume: 2, Issue:1

    Topics: Alkalies; Boron Compounds; Carbonyl Cyanide m-Chlorophenyl Hydrazone; Cells, Cultured; Fibroblasts;

2000