carbamyl phosphate has been researched along with Amino Acid Metabolism Disorders, Inborn in 6 studies
Carbamyl Phosphate: The monoanhydride of carbamic acid with PHOSPHORIC ACID. It is an important intermediate metabolite and is synthesized enzymatically by CARBAMYL-PHOSPHATE SYNTHASE (AMMONIA) and CARBAMOYL-PHOSPHATE SYNTHASE (GLUTAMINE-HYDROLYZING).
| Excerpt | Relevance | Reference |
|---|---|---|
| "Metabolic observations during early stages of hyperammonemia in two infants with ornithine transcarbamylase deficiency suggest that plasma alpha-ketoglutarate concentration ([alpha-KG]) becomes subnormal before the development of hyperammonemic coma." | 3.66 | Plasma alpha-ketoglutarate in urea cycle enzymopathies and its role as a harbinger of hyperammonemic coma. ( Batshaw, ML; Brusilow, SW; Walser, M, 1980) |
| "Orotic aciduria is a reliable indicator of the function of the urea cycle in lysinuric protein intolerance and facilitates monitoring of the treatment of this disease." | 1.26 | Orotic aciduria in lysinuric protein intolerance: dependence on the urea cycle intermediates. ( Rajantie, J, 1981) |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 6 (100.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 0 (0.00) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Spector, EB | 1 |
| Mazzocchi, RA | 1 |
| Colombo, JP | 1 |
| Batshaw, ML | 1 |
| Walser, M | 1 |
| Brusilow, SW | 1 |
| Nagata, N | 1 |
| Akaboshi, I | 1 |
| Yamamoto, J | 1 |
| Matsuda, I | 1 |
| Ohtsuka, H | 1 |
| Katsuki, T | 1 |
| Rajantie, J | 1 |
| Burgess, EA | 1 |
| Oberholzer, VG | 1 |
| Palmer, T | 1 |
| Levin, B | 1 |
1 review available for carbamyl phosphate and Amino Acid Metabolism Disorders, Inborn
| Article | Year |
|---|---|
Some regulatory aspects of urea synthesis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Carbamyl Phosphate; Citric Acid Cycle; Dieta | 1981 |
5 other studies available for carbamyl phosphate and Amino Acid Metabolism Disorders, Inborn
| Article | Year |
|---|---|
The sparse fur mouse: an animal model for a human inborn error of metabolism of the urea cycle.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Carbamyl Phosphate; Disease Models, Animal; | 1983 |
Plasma alpha-ketoglutarate in urea cycle enzymopathies and its role as a harbinger of hyperammonemic coma.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Argini | 1980 |
Ornithine transcarbamylase (OTC) in white blood cells.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Carbamyl Phosphate; Carbon Radioisotopes; Ca | 1980 |
Orotic aciduria in lysinuric protein intolerance: dependence on the urea cycle intermediates.
Topics: Adolescent; Adult; Alanine; Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Carbamyl Phospha | 1981 |
Plasma carnosinase deficiency in patients with urea cycle defects.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Carbamyl Phosphate; Carnosine; Child; Child, Preschool; | 1975 |