caprylates has been researched along with Lipid Metabolism, Inborn Error in 19 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 7 (36.84) | 18.7374 |
1990's | 4 (21.05) | 18.2507 |
2000's | 3 (15.79) | 29.6817 |
2010's | 3 (15.79) | 24.3611 |
2020's | 2 (10.53) | 2.80 |
Authors | Studies |
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Alatibi, KI; Ausserlechner, MJ; Grünert, SC; Hagenbuchner, J; Karall, D; Schilling, O; Tholen, S; Tucci, S; Vockley, J; Wehbe, Z | 1 |
Birkler, RID; Corydon, TJ; Fernandez-Guerra, P; Gregersen, N; Hansen, J; Nochi, Z; Olsen, RKJ; Wibrand, F | 1 |
Burchill, LJ; DeLany, JP; Deward, S; El-Gharbawy, AH; Gillingham, MB; Goldstein, A; Goodpaster, B; Harding, CO; Heitner, SB; Lasarev, MR; Martin, J; Matern, D; Pollaro, J; Rose, S; Shoemaker, J; Vockley, J | 1 |
Shoffner, JM | 1 |
Busanello, EN; Ferreira, GC; Moura, AP; Scaini, G; Schuck, PF; Simon, KR; Streck, EL; Tonin, AM; Wajner, M | 1 |
Bennett, MJ; Butt, Y; Jones, PM | 1 |
Bennett, MJ; Butt, YM; Jones, PM | 1 |
Borba Rosa, R; da Costa Ferreira, G; Dutra-Filho, CS; Duval Wannmacher, CM; Maria, Rde C; Reis de Assis, D; Ribeiro, CA; Santos Perry, ML; Schuck, PF; Terezinha de Souza Wyse, A; Wajner, M | 1 |
Amendt, BA; Felts, SJ; Fritchman, KS; Rhead, WJ | 1 |
Gregersen, N; Hobolth, N; Kølvraa, S; Lauritzen, R; Rasmussen, K; Rosleff, F | 1 |
Brivet, M; Duran, M; Heymans, HS; Ijlst, L; Niezen-Koning, KE; Reijngoud, DJ; Smit, GP; van Spronsen, FJ; Wanders, RJ | 1 |
Ijlst, L; Wanders, RJ | 1 |
de Klerk, JB; Ijlst, L; Przyrembel, H; van Elk, E; Wanders, RJ | 1 |
Bonnefont, JP; Cepanec, C; Colonna, M; Demaugre, F; Leroux, JP; Saudubray, JM | 1 |
Amendt, BA; Rhead, WJ | 1 |
Duran, M; Hofkamp, M; Rhead, WJ; Saudubray, JM; Wadman, SK | 1 |
Bruinvis, L; de Jager, JP; de Klerk, JB; Duran, M; Hofkamp, M; Ketting, D; Mitchell, G; Saudubray, JM; Wadman, SK | 1 |
Beckeringh, TE; Bruinvis, L; Dorland, L; Duran, M; Ketting, D; van Vossen, R; Wadman, SK | 1 |
Schwabe, AD; Valdivieso, VD | 1 |
1 trial(s) available for caprylates and Lipid Metabolism, Inborn Error
Article | Year |
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Triheptanoin versus trioctanoin for long-chain fatty acid oxidation disorders: a double blinded, randomized controlled trial.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Adolescent; Adult; Caprylates; Cardiomyopathies; Carnitine; Child; Dietary Fats; Double-Blind Method; Exercise; Fatty Acids; Female; Humans; Lipid Metabolism, Inborn Errors; Male; Middle Aged; Mitochondrial Myopathies; Mitochondrial Trifunctional Protein; Nervous System Diseases; Oxidation-Reduction; Rhabdomyolysis; Triglycerides; Young Adult | 2017 |
18 other study(ies) available for caprylates and Lipid Metabolism, Inborn Error
Article | Year |
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Lipidomic and Proteomic Alterations Induced by Even and Odd Medium-Chain Fatty Acids on Fibroblasts of Long-Chain Fatty Acid Oxidation Disorders.
Topics: Acyl-CoA Dehydrogenase, Long-Chain; Caprylates; Cardiolipins; Cell Line; Female; Fibroblasts; Genotype; Heptanoates; Humans; Lipid Metabolism, Inborn Errors; Lipidomics; Male; Mitochondria; Phosphatidylcholines; Phosphatidylethanolamines; Proteome; Proteomics; Sphingolipids | 2021 |
Increased antioxidant response in medium-chain acyl-CoA dehydrogenase deficiency: does lipoic acid have a protective role?
Topics: Acyl-CoA Dehydrogenase; Antioxidants; Caprylates; Carnitine; Cell Death; Fibroblasts; Genotype; Glycolysis; Humans; Lipid Metabolism, Inborn Errors; Lipid Peroxidation; Mitochondria; Oxidative Stress; Phenotype; Superoxides; Thioctic Acid | 2020 |
Concerning "Triheptanoin vs trioctanoin for long-chain fatty acid oxidation disorders: A double blinded, randomized controlled trial" by Gillingham et al.
Topics: Caprylates; Fatty Acids; Humans; Lipid Metabolism, Inborn Errors; Oxidation-Reduction; Triglycerides | 2019 |
Toxicity of octanoate and decanoate in rat peripheral tissues: evidence of bioenergetic dysfunction and oxidative damage induction in liver and skeletal muscle.
Topics: Acyl-CoA Dehydrogenase; Animals; Caprylates; Creatine Kinase; Decanoates; Electron Transport; Electron Transport Complex IV; Glutathione; Lipid Metabolism, Inborn Errors; Liver; Male; Mitochondria; Muscle, Skeletal; Oxidation-Reduction; Oxidative Stress; Protein Carbonylation; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances | 2012 |
Accumulation of 3-hydroxy-fatty acids in the culture medium of long-chain L-3-hydroxyacyl CoA dehydrogenase (LCHAD) and mitochondrial trifunctional protein-deficient skin fibroblasts: implications for medium chain triglyceride dietary treatment of LCHAD d
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Caprylates; Cells, Cultured; Decanoates; Fibroblasts; Humans; In Vitro Techniques; Lipid Metabolism, Inborn Errors; Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase; Mitochondrial Trifunctional Protein; Multienzyme Complexes; Oxidation-Reduction; Palmitates; Point Mutation; Skin | 2003 |
Effects of odd-numbered medium-chain fatty acids on the accumulation of long-chain 3-hydroxy-fatty acids in long-chain L-3-hydroxyacyl CoA dehydrogenase and mitochondrial trifunctional protein deficient skin fibroblasts.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Caprylates; Cell Line; Culture Media; Decanoates; Fatty Acids; Fibroblasts; Heptanoates; Humans; Lipid Metabolism, Inborn Errors; Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase; Mitochondrial Diseases; Skin | 2004 |
Inhibition of energy metabolism in cerebral cortex of young rats by the medium-chain fatty acids accumulating in MCAD deficiency.
Topics: Acetates; Acyl-CoA Dehydrogenase; Age Factors; Animals; Antifungal Agents; Antihypertensive Agents; Caprylates; Carbon Radioisotopes; Cerebral Cortex; Citrate (si)-Synthase; Creatine Kinase; Decanoic Acids; Electron Transport; Energy Metabolism; Fatty Acids; Lipid Metabolism, Inborn Errors; Rats; Rats, Wistar | 2004 |
Dicarboxylic aciduria: deficient [1-14C]octanoate oxidation and medium-chain acyl-CoA dehydrogenase in fibroblasts.
Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Butyrates; Butyric Acid; Caprylates; Dicarboxylic Acids; Fibroblasts; Humans; Lipid Metabolism, Inborn Errors; Mitochondria; Oxidation-Reduction | 1983 |
Non-ketotic C6-C10-dicarboxylic aciduria: biochemical investigations of two cases.
Topics: Adipates; Caproates; Caprylates; Child, Preschool; Chromatography, Gas; Decanoic Acids; Dicarboxylic Acids; Fatty Acid Desaturases; Fatty Acids; Glycine; Humans; Hydroxy Acids; Hydroxybutyrates; Hypoglycemia; Infant; Lipid Metabolism, Inborn Errors; Male; Mass Spectrometry; Valerates | 1980 |
A patient with lethal cardiomyopathy and a carnitine-acylcarnitine translocase deficiency.
Topics: Caprylates; Cardiomyopathies; Carnitine Acyltransferases; Carnitine O-Palmitoyltransferase; Cells, Cultured; Fatal Outcome; Female; Fibroblasts; Humans; Infant, Newborn; Leukocytes; Lipid Metabolism, Inborn Errors; Oxidation-Reduction; Palmitates | 1995 |
Fatty acid beta-oxidation in leukocytes from control subjects and medium-chain acyl-CoA dehydrogenase deficient patients.
Topics: 3-Hydroxybutyric Acid; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Caprylates; Fatty Acids; Humans; Hydroxybutyrates; Leukocytes; Lipid Metabolism, Inborn Errors; Mitochondria; Oxidation-Reduction; Palmitates; Time Factors | 1992 |
Octanoate and palmitate beta-oxidation in human leukocytes: implications for the rapid diagnosis of fatty acid beta-oxidation disorders.
Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenase, Long-Chain; Caprylates; Fatty Acid Desaturases; Fatty Acids; Fibroblasts; Humans; In Vitro Techniques; Infant; Leukocytes; Lipid Metabolism, Inborn Errors; Oxidation-Reduction; Palmitic Acid; Palmitic Acids | 1991 |
Infantile form of carnitine palmitoyltransferase II deficiency with hepatomuscular symptoms and sudden death. Physiopathological approach to carnitine palmitoyltransferase II deficiencies.
Topics: Blotting, Western; Butyrates; Caprylates; Carnitine O-Palmitoyltransferase; Death, Sudden; Humans; Infant; Ketone Bodies; Lipid Metabolism, Inborn Errors; Liver Diseases; Male; Molecular Weight; Palmitates | 1991 |
The multiple acyl-coenzyme A dehydrogenation disorders, glutaric aciduria type II and ethylmalonic-adipic aciduria. Mitochondrial fatty acid oxidation, acyl-coenzyme A dehydrogenase, and electron transfer flavoprotein activities in fibroblasts.
Topics: Acyl Coenzyme A; Acyl-CoA Dehydrogenases; Adipates; Animals; Caprylates; Electron Transport; Electron-Transferring Flavoproteins; Fatty Acids; Fibroblasts; Flavin-Adenine Dinucleotide; Flavoproteins; Glutarates; Lipid Metabolism, Inborn Errors; Liver; Malonates; Mitochondria; Palmitoyl Coenzyme A; Succinates; Succinic Acid; Swine | 1986 |
Sudden child death and 'healthy' affected family members with medium-chain acyl-coenzyme A dehydrogenase deficiency.
Topics: Acyl-CoA Dehydrogenase; Caproates; Caprylates; Decanoic Acids; Fatty Acid Desaturases; Fatty Acids; Fatty Acids, Nonesterified; Female; Humans; Infant; Lipid Metabolism, Inborn Errors; Male; Mitochondria, Liver; Oxidation-Reduction; Sudden Infant Death | 1986 |
Octanoic acidemia and octanoylcarnitine excretion with dicarboxylic aciduria due to defective oxidation of medium-chain fatty acids.
Topics: Acyl-CoA Dehydrogenases; Caprylates; Carnitine; Cells, Cultured; Decanoic Acids; Dicarboxylic Acids; Fatty Acids; Fatty Acids, Nonesterified; Female; Fibroblasts; Humans; Infant; Lipid Metabolism, Inborn Errors; Male; Oxidation-Reduction | 1985 |
Octanoylglucuronide excretion in patients with a defective oxidation of medium-chain fatty acids.
Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Caprylates; Carnitine; Fatty Acids; Gas Chromatography-Mass Spectrometry; Humans; Hydrogen-Ion Concentration; Lipid Metabolism, Inborn Errors | 1985 |
Absorption of medium-chain lipids from the rat cecum.
Topics: Animals; Caprylates; Cecum; Chromatography, Thin Layer; Intestinal Absorption; Intestine, Large; Lipid Metabolism, Inborn Errors; Rats | 1966 |