Page last updated: 2024-08-22

buthionine sulfoximine and Friedreich Disease

buthionine sulfoximine has been researched along with Friedreich Disease in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's0 (0.00)29.6817
2010's4 (100.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Richardson, TE; Simpkins, JW; Wen, Y; Yang, SH1
Richardson, TE; Simpkins, JW; Wen, Y; Yang, SH; Yu, AE1
Richardson, TE; Simpkins, JW1
Antenora, A; Brescia Morra, V; De Michele, G; Filla, A; Marsili, A; Nesti, C; Pane, C; Puorro, G; SaccĂ , F; Santorelli, FM; Scoppettuolo, P; Tessa, A1

Other Studies

4 other study(ies) available for buthionine sulfoximine and Friedreich Disease

ArticleYear
Estrogen protection in Friedreich's ataxia skin fibroblasts.
    Endocrinology, 2011, Volume: 152, Issue:7

    Topics: Adult; Antioxidants; Buthionine Sulfoximine; Cell Survival; Cells, Cultured; Estradiol; Estrogen Receptor Modulators; Estrogens; Fibroblasts; Friedreich Ataxia; Glutathione; Humans; Male; Neuroprotective Agents; Oxidative Stress; Phenols; Reactive Oxygen Species; Receptors, Estrogen; Receptors, G-Protein-Coupled; Skin; Structure-Activity Relationship

2011
Estrogen prevents oxidative damage to the mitochondria in Friedreich's ataxia skin fibroblasts.
    PloS one, 2012, Volume: 7, Issue:4

    Topics: Aconitate Hydratase; Adenosine Triphosphate; Adult; Buthionine Sulfoximine; Cell Death; Cell Respiration; Cell Survival; Cytoprotection; Estrogen Receptor beta; Estrogens; Fibroblasts; Friedreich Ataxia; Gene Expression Regulation; Glutathione; Humans; Lipid Peroxidation; Membrane Potential, Mitochondrial; Mitochondria; Oxidative Stress; Reactive Oxygen Species; Skin

2012
R- and S-equol have equivalent cytoprotective effects in Friedreich's ataxia.
    BMC pharmacology & toxicology, 2012, Oct-22, Volume: 13

    Topics: Adult; Buthionine Sulfoximine; Cell Survival; Cells, Cultured; Cytoprotection; Equol; Estradiol; Estrogens; Fibroblasts; Friedreich Ataxia; Humans; Oxidative Stress; Protective Agents; Reactive Oxygen Species

2012
Clinical use of frataxin measurement in a patient with a novel deletion in the FXN gene.
    Journal of neurology, 2013, Volume: 260, Issue:4

    Topics: Analysis of Variance; Antimetabolites; Buthionine Sulfoximine; Cell Line, Transformed; Family Health; Female; Frataxin; Friedreich Ataxia; Genetic Testing; Humans; Iron-Binding Proteins; Lymphocytes; Male; Middle Aged; RNA, Messenger; Sequence Deletion; Severity of Illness Index; Trinucleotide Repeat Expansion; Young Adult

2013