Page last updated: 2024-09-05

biotin and Propionic Acidemia

biotin has been researched along with Propionic Acidemia in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (25.00)29.6817
2010's3 (75.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Rafique, M1
Deng, B; Huang, CS; Sadre-Bazzaz, K; Shen, Y; Tong, L; Zhou, ZH1
Chan, IH; Chan, MH; Kwok, JS1
de la Sierra García-Valdecasas, M; del Portal, LR; Delgado, C; Jiménez, LM; Macías, C; Pérez, M1

Other Studies

4 other study(ies) available for biotin and Propionic Acidemia

ArticleYear
Emerging trends in management of propionic acidemia.
    Arquivos brasileiros de endocrinologia e metabologia, 2014, Volume: 58, Issue:3

    Topics: Adolescent; Anti-Infective Agents; Biotin; Carnitine; Child; Child, Preschool; Diet, Protein-Restricted; Female; Humans; Hyperammonemia; Infant; Infant, Newborn; Long-Term Care; Male; Metronidazole; Nutrition Therapy; Propionic Acidemia; Retrospective Studies; Sodium Benzoate; Sodium Bicarbonate; Vitamin B Complex

2014
Crystal structure of the alpha(6)beta(6) holoenzyme of propionyl-coenzyme A carboxylase.
    Nature, 2010, Aug-19, Volume: 466, Issue:7309

    Topics: Acetyl-CoA Carboxylase; Biocatalysis; Biotin; Carbon-Nitrogen Ligases; Carrier Proteins; Catalytic Domain; Cryoelectron Microscopy; Crystallography, X-Ray; Fatty Acid Synthase, Type II; Holoenzymes; Humans; Methylmalonyl-CoA Decarboxylase; Models, Molecular; Mutation; Propionic Acidemia; Protein Binding; Protein Structure, Quaternary; Protein Structure, Tertiary; Protein Subunits; Rhodobacteraceae; Structure-Activity Relationship

2010
Biotin interference on TSH and free thyroid hormone measurement.
    Pathology, 2012, Volume: 44, Issue:3

    Topics: Artifacts; Biotin; Child, Preschool; Diagnostic Errors; Female; Humans; Hyperthyroidism; Immunoassay; Propionic Acidemia; Thyroid Function Tests; Thyroid Hormones; Thyrotropin

2012
Subacute presentation of propionic acidemia.
    Journal of child neurology, 2007, Volume: 22, Issue:12

    Topics: Acidosis; Amino Acids; Biotin; Brain; Carnitine; Diagnosis, Differential; Diet, Protein-Restricted; Disease Progression; Electrophoresis, Capillary; Gastroenteritis; Growth Disorders; Humans; Infant; Magnetic Resonance Imaging; Male; Metabolism, Inborn Errors; Propionates; Propionic Acidemia; Treatment Outcome; Vomiting

2007