biotin has been researched along with Cochlear Hearing Loss in 7 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 1 (14.29) | 18.2507 |
2000's | 3 (42.86) | 29.6817 |
2010's | 3 (42.86) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Gow, A; Maheras, KJ; Pindolia, K; Wolf, B | 1 |
Cansever, MS; Kiykim, A; Kiykim, E; Zeybek, CA | 1 |
Anand, A; Chatterjee, A; Hiremagalore, R; Mani, RS; Pandey, N; Rajashekhar, B; Tharakan, A; Xavier, DF | 1 |
Chang, WT; Chen, MS; Huang, PC; Li, AH; Wang, HL; Wu, CY; Yeh, TH | 1 |
Ficicioglu, C; Hoffman, TL; Simon, EM | 1 |
Welling, DB | 1 |
Bhardwaj, B; Rybak, LP; Scott, V; Weberg, AD; Whitworth, C | 1 |
7 other study(ies) available for biotin and Cochlear Hearing Loss
Article | Year |
---|---|
Developmental window of sensorineural deafness in biotinidase-deficient mice.
Topics: Animals; Biotin; Biotinidase; Biotinidase Deficiency; Deafness; Diet; Evoked Potentials, Auditory, Brain Stem; Hearing Loss, Sensorineural; Mice; Mice, Inbred C57BL; Mice, Knockout | 2017 |
Biotinidase deficiency mimicking primary immune deficiencies.
Topics: Biotin; Biotinidase Deficiency; Candidiasis; Child, Preschool; Consanguinity; Dermatitis; Female; Hearing Loss, Sensorineural; Humans; Mouth Diseases; Recurrence; Respiratory Tract Infections; Turkey | 2015 |
Functional Analysis of a Novel Connexin30 Mutation in a Large Family with Hearing Loss, Pesplanus, Ichthyosis, Cutaneous Nodules, and Keratoderma.
Topics: Biotin; Connexin 30; Connexins; DNA Mutational Analysis; Female; Genetic Linkage; Hearing Loss, Sensorineural; Humans; Ichthyosis; Keratoderma, Palmoplantar, Diffuse; Male; Pedigree; Phenotype; Skin Diseases, Genetic | 2016 |
Functional analysis of connexin-26 mutants associated with hereditary recessive deafness.
Topics: Amino Acid Substitution; Animals; Biotin; Cell Communication; Connexin 26; Connexins; Gap Junctions; Genes, Recessive; Hearing Loss, Sensorineural; Humans; Mice; Mutagenesis, Site-Directed; Neuroblastoma; Patch-Clamp Techniques; Structure-Activity Relationship; Transfection; Tumor Cells, Cultured | 2003 |
Biotinidase deficiency: the importance of adequate follow-up for an inconclusive newborn screening result.
Topics: Acidosis, Lactic; Ataxia; Biotin; Biotinidase Deficiency; Brain; Continuity of Patient Care; Hearing Loss, Bilateral; Hearing Loss, Sensorineural; Humans; Infant; Infant, Newborn; Magnetic Resonance Imaging; Male; Muscle Hypertonia; Neonatal Screening; Pakistan; Pennsylvania; Respiratory Sounds; Speech Disorders | 2005 |
Long-term follow-up of hearing loss in biotinidase deficiency.
Topics: Biotin; Biotinidase Deficiency; Child; Female; Follow-Up Studies; Hearing Loss, Sensorineural; Humans; Time Factors; Treatment Outcome | 2007 |
Rat as a potential model for hearing loss in biotinidase deficiency.
Topics: Amidohydrolases; Animals; Biotin; Biotinidase; Disease Models, Animal; Evoked Potentials, Auditory, Brain Stem; Female; Genes, Recessive; Hair Cells, Auditory; Hearing Loss, Sensorineural; Male; Metabolism, Inborn Errors; Microscopy, Electron, Scanning; Organ of Corti; Rats; Rats, Inbred Strains | 1991 |