Page last updated: 2024-08-23

bezafibrate and Muscle Disorders

bezafibrate has been researched along with Muscle Disorders in 18 studies

Research

Studies (18)

TimeframeStudies, this research(%)All Research%
pre-19901 (5.56)18.7374
1990's5 (27.78)18.2507
2000's2 (11.11)29.6817
2010's7 (38.89)24.3611
2020's3 (16.67)2.80

Authors

AuthorsStudies
Chin, MT; Heyman, A; Hornby, B; Jefferies, J; Pu, WT; Takemoto, C; Thompson, R; Vernon, HJ; Wang, S1
Asahina, N; Egawa, K; Hayashi, H; Ishige, M; Isoe, T; Kawakami, S; Kobayashi, K; Kuzume, K; Miyakoshi, T; Nakamagoe, K; Oba, K; Ochi, F; Sameshima, K; Sato, N; Shiraishi, H; Tamaoka, A; Watanabe, A; Watanabe, K; Yamada, K; Yamaguchi, S; Yokoshiki, S1
Andersen, KG; Gregersen, N; Hargreaves, IP; Heaton, R; Lund, M; Olsen, RKJ1
Bilet, L; Bosma, M; Havekes, B; Hesselink, MK; Hoeks, J; Janssen, MC; Jorgensen, J; Paglialunga, S; Sauerwein, H; Schaart, G; Schrauwen, P; Schrauwen-Hinderling, VB; Smeets, JL; Sparks, L; van de Weijer, T; Wildberger, J; Zechner, R1
Andersen, G; Laforêt, P; Madsen, KL; Preisler, N; Vissing, J; Ørngreen, MC1
Bastin, J; Bonnefont, JP; Bresson, JL; Djouadi, F1
Laforét, P; Vissing, J; Ørngreen, MC1
Ding, Y; Li, X; Liu, Y; Ma, Y; Song, J; Wang, Q; Yang, Y1
Harrington, M1
Aubey, F; Bastin, J; Behin, A; Bonnefont, JP; Bresson, JL; Djouadi, F; Eymard, B; Gobin-Limballe, S; Laforêt, P; Mogenet, A; Ricquier, D; Romano, S; Vassault, A1
Albert, V; Bentzinger, CF; Conjard-Duplany, A; Gangloff, YG; Handschin, C; Lin, S; Mazelin, L; Puigserver, P; Romanino, K; Rüegg, MA; Schaeffer, L; Zorzato, F1
Eymard, B; Laforêt, P; Nicolino, M1
Bock, KD; Heidemann, H1
Galiana, J; Marchán, E; Montés, I; Pato, S1
Bresolin, N; Ferrò, MT; Fortunato, F; Gagliardi, E; Messina, C; Mileto, G; Pitrone, F; Toscano, A; Vita, G1
Ichikawa, M; Matsuyama, K; Nakai, A; Nishikata, M; Uchida, T1
Fernández-Solá, J; Fueyo, J; Gómez Manzano, C; Pedro-Botet Montoya, J1
Chan, MK1

Reviews

3 review(s) available for bezafibrate and Muscle Disorders

ArticleYear
Current and future treatment approaches for Barth syndrome.
    Journal of inherited metabolic disease, 2022, Volume: 45, Issue:1

    Topics: Acyltransferases; Animals; Barth Syndrome; Bezafibrate; Cardiolipins; Cardiomyopathies; Clinical Trials as Topic; Enzyme Therapy; Genetic Therapy; Humans; Mice; Muscular Diseases; Neutropenia; Oligopeptides; Peroxisome Proliferator-Activated Receptors

2022
[New approaches for the treatment of metabolic myopathies].
    Revue neurologique, 2007, Volume: 163, Issue:10

    Topics: Bezafibrate; Carnitine O-Palmitoyltransferase; Glycogen Storage Disease; Humans; Hypolipidemic Agents; Metabolism, Inborn Errors; Mitochondrial Myopathies; Muscular Diseases

2007
[Toxic myopathies related to the administration of hypolipidemic agents: are the drugs the only things responsible?].
    Revista clinica espanola, 1995, Volume: 195, Issue:9

    Topics: Adult; Aged; Bezafibrate; Delayed-Action Preparations; Drug Therapy, Combination; Female; Humans; Hypolipidemic Agents; Lovastatin; Male; Muscular Diseases; Simvastatin

1995

Trials

2 trial(s) available for bezafibrate and Muscle Disorders

ArticleYear
Bezafibrate in skeletal muscle fatty acid oxidation disorders: a randomized clinical trial.
    Neurology, 2014, Feb-18, Volume: 82, Issue:7

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Adolescent; Adult; Aged; Bezafibrate; Carnitine O-Palmitoyltransferase; Clinical Protocols; Congenital Bone Marrow Failure Syndromes; Cross-Over Studies; Fatty Acids; Female; Humans; Hypolipidemic Agents; Lipid Metabolism, Inborn Errors; Male; Middle Aged; Mitochondrial Diseases; Muscle, Skeletal; Muscular Diseases; Treatment Outcome; Young Adult

2014
Long-term follow-up of bezafibrate treatment in patients with the myopathic form of carnitine palmitoyltransferase 2 deficiency.
    Clinical pharmacology and therapeutics, 2010, Volume: 88, Issue:1

    Topics: Activities of Daily Living; Acyl-CoA Dehydrogenase, Long-Chain; Adult; Bezafibrate; Carnitine O-Palmitoyltransferase; Exercise Test; Female; Follow-Up Studies; Gene Expression Regulation, Enzymologic; Humans; Hypolipidemic Agents; Lymphocytes; Male; Middle Aged; Mitochondria, Muscle; Muscle, Skeletal; Muscular Diseases; Oxidation-Reduction; Oxygen Consumption; Pain; Palmitoyl Coenzyme A; Pilot Projects; Rhabdomyolysis; Treatment Outcome; Young Adult

2010

Other Studies

13 other study(ies) available for bezafibrate and Muscle Disorders

ArticleYear
Efficacy of bezafibrate for preventing myopathic attacks in patients with very long-chain acyl-CoA dehydrogenase deficiency.
    Brain & development, 2021, Volume: 43, Issue:2

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Adult; Bezafibrate; Child; Congenital Bone Marrow Failure Syndromes; Female; Humans; Lipid Metabolism, Inborn Errors; Male; Mitochondrial Diseases; Muscular Diseases

2021
Bezafibrate activation of PPAR drives disturbances in mitochondrial redox bioenergetics and decreases the viability of cells from patients with VLCAD deficiency.
    Biochimica et biophysica acta. Molecular basis of disease, 2021, 06-01, Volume: 1867, Issue:6

    Topics: Bezafibrate; Congenital Bone Marrow Failure Syndromes; Energy Metabolism; Fibroblasts; Humans; Hypolipidemic Agents; Lipid Metabolism, Inborn Errors; Mitochondria; Mitochondrial Diseases; Muscular Diseases; Oxidative Stress; Peroxisome Proliferator-Activated Receptors

2021
Effects of bezafibrate treatment in a patient and a carrier with mutations in the PNPLA2 gene, causing neutral lipid storage disease with myopathy.
    Circulation research, 2013, Mar-01, Volume: 112, Issue:5

    Topics: Adult; Alleles; Bezafibrate; Fatty Acids; Female; Humans; Hypolipidemic Agents; Lipase; Lipid Metabolism; Lipid Metabolism, Inborn Errors; Muscular Diseases; Mutation; Treatment Outcome

2013
Should the beneficial impact of bezafibrate on fatty acid oxidation disorders be questioned?
    Journal of inherited metabolic disease, 2015, Volume: 38, Issue:2

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Bezafibrate; Carnitine O-Palmitoyltransferase; Congenital Bone Marrow Failure Syndromes; Fatty Acids; Heart Rate; Humans; Lipid Metabolism, Inborn Errors; Lipolysis; Metabolism, Inborn Errors; Mitochondrial Diseases; Muscular Diseases; Oxidation-Reduction; Treatment Outcome

2015
No effect of bezafibrate in patients with CPTII and VLCAD deficiencies.
    Journal of inherited metabolic disease, 2015, Volume: 38, Issue:2

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Bezafibrate; Carnitine O-Palmitoyltransferase; Congenital Bone Marrow Failure Syndromes; Fatty Acids; Humans; Lipid Metabolism, Inborn Errors; Lipolysis; Metabolism, Inborn Errors; Mitochondrial Diseases; Muscular Diseases

2015
Very long-chain acyl-coenzyme A dehydrogenase deficiency in Chinese patients: eight case reports, including one case of prenatal diagnosis.
    European journal of medical genetics, 2015, Volume: 58, Issue:3

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Acyl-CoA Dehydrogenases; Amniotic Fluid; Ascorbic Acid; Asian People; Bezafibrate; Carnitine; Case-Control Studies; China; Chromatography, Liquid; Congenital Bone Marrow Failure Syndromes; DNA, Complementary; Exons; Female; Genetic Testing; Heterozygote; Humans; Infant; Infant Formula; Infant, Newborn; Lipid Metabolism, Inborn Errors; Male; Mitochondrial Diseases; Muscular Diseases; Mutation, Missense; Neonatal Screening; Prenatal Diagnosis; Sequence Alignment; Sequence Analysis, DNA; Tandem Mass Spectrometry; Treatment Outcome; Triglycerides; Vitamin B Complex

2015
Mice, mitochondria and myopathy.
    Lab animal, 2008, Volume: 37, Issue:10

    Topics: Animals; Bezafibrate; Female; Mice; Mice, Knockout; Mitochondria; Mitochondrial Diseases; Muscular Diseases; Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha; Trans-Activators; Transcription Factors

2008
Myopathy caused by mammalian target of rapamycin complex 1 (mTORC1) inactivation is not reversed by restoring mitochondrial function.
    Proceedings of the National Academy of Sciences of the United States of America, 2011, Dec-20, Volume: 108, Issue:51

    Topics: Animals; Bezafibrate; Gene Expression Regulation; Glycogen; Male; Mechanistic Target of Rapamycin Complex 1; Mice; Mice, Knockout; Mice, Transgenic; Mitochondria; Mitochondria, Muscle; Models, Genetic; Multiprotein Complexes; Muscle, Skeletal; Muscular Diseases; Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha; Proteins; TOR Serine-Threonine Kinases; Trans-Activators; Transcription Factors

2011
[Rhabdomyolysis with acute renal failure due to bezafibrate].
    Klinische Wochenschrift, 1981, Apr-15, Volume: 59, Issue:8

    Topics: Acute Kidney Injury; Bezafibrate; Clofibrate; Clofibric Acid; Humans; Male; Middle Aged; Muscular Diseases

1981
Bezafibrate-induced myopathy: no evidence for defects in muscle metabolism.
    European neurology, 1993, Volume: 33, Issue:2

    Topics: Bezafibrate; Biopsy; Carbohydrate Metabolism; Chronic Disease; Humans; Lipid Metabolism; Male; Middle Aged; Mitochondria, Muscle; Muscles; Muscular Diseases; Uremia

1993
Enhanced myopathy following administration of hypolipidemic agents under urethane anesthesia.
    Biological & pharmaceutical bulletin, 1997, Volume: 20, Issue:1

    Topics: Anesthesia; Animals; Bezafibrate; Calcium; Creatine Kinase; Hypolipidemic Agents; Lovastatin; Male; Muscular Diseases; Pravastatin; Rats; Rats, Wistar; Simvastatin; Urethane

1997
[Bezafibrate-induced necrotizing myopathy].
    Medicina clinica, 1991, Mar-23, Volume: 96, Issue:11

    Topics: Bezafibrate; Biopsy; Female; Humans; Middle Aged; Muscles; Muscular Diseases; Necrosis

1991
Sustained-release bezafibrate corrects lipid abnormalities in patients on continuous ambulatory peritoneal dialysis.
    Nephron, 1990, Volume: 56, Issue:1

    Topics: Adolescent; Adult; Aged; Bezafibrate; Cholesterol, HDL; Coronary Disease; Delayed-Action Preparations; Diabetes Complications; Drug Evaluation; Female; Humans; Hypertriglyceridemia; Kidney Failure, Chronic; Lipids; Male; Middle Aged; Muscular Diseases; Peritoneal Dialysis, Continuous Ambulatory

1990