Page last updated: 2024-08-23

bezafibrate and Metabolism, Inborn Errors

bezafibrate has been researched along with Metabolism, Inborn Errors in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's0 (0.00)18.2507
2000's1 (25.00)29.6817
2010's3 (75.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Ando, S; Arai, S; Asaka, I; Higaki, Y; Hitomi, H; Kaneoka, H; Kurose, Y; Nakashima, H; Osafune, K; Saito, T; Sakurai, H; Sudo, M; Tanaka, A; Yamada, K; Yamaguchi, S; Yasuno, T1
Bastin, J; Bonnefont, JP; Bresson, JL; Djouadi, F1
Laforét, P; Vissing, J; Ørngreen, MC1
Eymard, B; Laforêt, P; Nicolino, M1

Reviews

1 review(s) available for bezafibrate and Metabolism, Inborn Errors

ArticleYear
[New approaches for the treatment of metabolic myopathies].
    Revue neurologique, 2007, Volume: 163, Issue:10

    Topics: Bezafibrate; Carnitine O-Palmitoyltransferase; Glycogen Storage Disease; Humans; Hypolipidemic Agents; Metabolism, Inborn Errors; Mitochondrial Myopathies; Muscular Diseases

2007

Other Studies

3 other study(ies) available for bezafibrate and Metabolism, Inborn Errors

ArticleYear
Functional analysis of iPSC-derived myocytes from a patient with carnitine palmitoyltransferase II deficiency.
    Biochemical and biophysical research communications, 2014, May-30, Volume: 448, Issue:2

    Topics: Bezafibrate; Carnitine; Carnitine O-Palmitoyltransferase; Cell Differentiation; Cells, Cultured; Fibroblasts; Gene Expression Regulation; Humans; Male; Metabolism, Inborn Errors; Muscle Cells; Palmitoylcarnitine; Pluripotent Stem Cells; Young Adult

2014
Should the beneficial impact of bezafibrate on fatty acid oxidation disorders be questioned?
    Journal of inherited metabolic disease, 2015, Volume: 38, Issue:2

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Bezafibrate; Carnitine O-Palmitoyltransferase; Congenital Bone Marrow Failure Syndromes; Fatty Acids; Heart Rate; Humans; Lipid Metabolism, Inborn Errors; Lipolysis; Metabolism, Inborn Errors; Mitochondrial Diseases; Muscular Diseases; Oxidation-Reduction; Treatment Outcome

2015
No effect of bezafibrate in patients with CPTII and VLCAD deficiencies.
    Journal of inherited metabolic disease, 2015, Volume: 38, Issue:2

    Topics: Acyl-CoA Dehydrogenase, Long-Chain; Bezafibrate; Carnitine O-Palmitoyltransferase; Congenital Bone Marrow Failure Syndromes; Fatty Acids; Humans; Lipid Metabolism, Inborn Errors; Lipolysis; Metabolism, Inborn Errors; Mitochondrial Diseases; Muscular Diseases

2015