bezafibrate has been researched along with Luft Disease in 7 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 2 (28.57) | 29.6817 |
| 2010's | 4 (57.14) | 24.3611 |
| 2020's | 1 (14.29) | 2.80 |
| Authors | Studies |
|---|---|
| Bottolo, L; Charman, SJ; Chinnery, PF; Gomez-Duran, A; He, L; Hollingsworth, KG; Hopton, S; Horvath, R; Jakovljevic, DG; Newman, J; Parikh, JD; Pyle, A; Robinson, AJ; Steele, H; Stefanetti, RJ; Taylor, RW; Viscomi, C | 1 |
| Ayalon, O; Saada, A; Soiferman, D; Weissman, S | 1 |
| Andresen, BS; Bastin, J; Benoist, JF; Boutron, A; de Lonlay, P; Djouadi, F; Ferdinandusse, S; Fukao, T; Habarou, F; Le Bachelier, C; Olpin, S; Schlemmer, D; Strauss, AW; Visser, G; Wanders, RJ; Yamaguchi, S | 1 |
| Diaz, F; Moraes, CT; Spiegelman, BM; Wenz, T | 1 |
| DiMauro, S | 1 |
| Suomalainen, A; Yatsuga, S | 1 |
| Eymard, B; Laforêt, P; Nicolino, M | 1 |
2 review(s) available for bezafibrate and Luft Disease
| Article | Year |
|---|---|
Pathogenesis and treatment of mitochondrial myopathies: recent advances.
Topics: Animals; Bezafibrate; Disease Models, Animal; DNA, Mitochondrial; Hematopoietic Stem Cell Transplantation; Humans; Mitochondrial Myopathies; Mutation; Nuclear Transfer Techniques | 2010 |
[New approaches for the treatment of metabolic myopathies].
Topics: Bezafibrate; Carnitine O-Palmitoyltransferase; Glycogen Storage Disease; Humans; Hypolipidemic Agents; Metabolism, Inborn Errors; Mitochondrial Myopathies; Muscular Diseases | 2007 |
5 other study(ies) available for bezafibrate and Luft Disease
| Article | Year |
|---|---|
Metabolic effects of bezafibrate in mitochondrial disease.
Topics: Bezafibrate; Humans; Mitochondria; Mitochondrial Myopathies; Organelle Biogenesis | 2020 |
The effect of small molecules on nuclear-encoded translation diseases.
Topics: Acetylcysteine; Aminoimidazole Carboxamide; Bezafibrate; Cytochrome-c Oxidase Deficiency; DNA, Mitochondrial; Electron Transport; Electron Transport Complex IV; Fibroblasts; Gene Expression Regulation; Humans; Membrane Potential, Mitochondrial; Mitochondria; Mitochondrial Myopathies; Mitochondrial Proteins; Mutation; Oxidative Phosphorylation; Peptide Elongation Factor G; Primary Cell Culture; Protein Biosynthesis; Reactive Oxygen Species; Ribonucleotides; Ribosomal Proteins; Small Molecule Libraries; tRNA Methyltransferases | 2014 |
Mitochondrial trifunctional protein deficiency in human cultured fibroblasts: effects of bezafibrate.
Topics: Bezafibrate; Cardiomyopathies; Cell Line; Fibroblasts; Genotype; Humans; Hypolipidemic Agents; Lipid Metabolism, Inborn Errors; Mitochondrial Myopathies; Mitochondrial Trifunctional Protein; Mitochondrial Trifunctional Protein, alpha Subunit; Mitochondrial Trifunctional Protein, beta Subunit; Mutation; Nervous System Diseases; Rhabdomyolysis | 2016 |
Activation of the PPAR/PGC-1alpha pathway prevents a bioenergetic deficit and effectively improves a mitochondrial myopathy phenotype.
Topics: Adenosine Triphosphate; Animals; Bezafibrate; Cytochrome-c Oxidase Deficiency; Disease Models, Animal; Energy Metabolism; Female; Mice; Mice, Inbred Strains; Mice, Transgenic; Mitochondria, Muscle; Mitochondrial Myopathies; Muscle, Skeletal; Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha; Phenotype; PPAR gamma; Reverse Transcriptase Polymerase Chain Reaction; Signal Transduction; Survival Rate; Trans-Activators; Transcription Factors; Transgenes | 2008 |
Effect of bezafibrate treatment on late-onset mitochondrial myopathy in mice.
Topics: Adipose Tissue; Animals; Bezafibrate; Body Temperature; Disease Progression; DNA Helicases; DNA, Mitochondrial; Electron Transport Complex IV; Female; Fibroblast Growth Factors; Hepatomegaly; Lipid Metabolism; Liver; Male; Mice; Mitochondria; Mitochondrial Myopathies; Mitochondrial Proteins; Muscle Fibers, Skeletal; Mutation; Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha; Peroxisome Proliferator-Activated Receptors; RNA, Messenger; Trans-Activators; Transcription Factors; Weight Loss | 2012 |