bezafibrate has been researched along with Complex IV Deficiency in 4 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 0 (0.00) | 18.7374 |
| 1990's | 0 (0.00) | 18.2507 |
| 2000's | 1 (25.00) | 29.6817 |
| 2010's | 3 (75.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Ayalon, O; Saada, A; Soiferman, D; Weissman, S | 1 |
| Diaz, F; Moraes, CT; Spiegelman, BM; Wenz, T | 1 |
| Bottani, E; Cerutti, R; Civiletto, G; Fagiolari, G; Lamperti, C; Moggio, M; Schon, EA; Viscomi, C; Zeviani, M | 1 |
| Basso, G; Brosel, S; Casarin, A; Cassina, M; Cerqua, C; Clementi, M; Dimauro, S; Doimo, M; Giorgi, G; M Davidson, M; Pertegato, V; Rizzuto, R; Sacconi, S; Salviati, L; Schon, EA; Siviero, R; Trevisson, E | 1 |
4 other study(ies) available for bezafibrate and Complex IV Deficiency
| Article | Year |
|---|---|
The effect of small molecules on nuclear-encoded translation diseases.
Topics: Acetylcysteine; Aminoimidazole Carboxamide; Bezafibrate; Cytochrome-c Oxidase Deficiency; DNA, Mitochondrial; Electron Transport; Electron Transport Complex IV; Fibroblasts; Gene Expression Regulation; Humans; Membrane Potential, Mitochondrial; Mitochondria; Mitochondrial Myopathies; Mitochondrial Proteins; Mutation; Oxidative Phosphorylation; Peptide Elongation Factor G; Primary Cell Culture; Protein Biosynthesis; Reactive Oxygen Species; Ribonucleotides; Ribosomal Proteins; Small Molecule Libraries; tRNA Methyltransferases | 2014 |
Activation of the PPAR/PGC-1alpha pathway prevents a bioenergetic deficit and effectively improves a mitochondrial myopathy phenotype.
Topics: Adenosine Triphosphate; Animals; Bezafibrate; Cytochrome-c Oxidase Deficiency; Disease Models, Animal; Energy Metabolism; Female; Mice; Mice, Inbred Strains; Mice, Transgenic; Mitochondria, Muscle; Mitochondrial Myopathies; Muscle, Skeletal; Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha; Phenotype; PPAR gamma; Reverse Transcriptase Polymerase Chain Reaction; Signal Transduction; Survival Rate; Trans-Activators; Transcription Factors; Transgenes | 2008 |
In vivo correction of COX deficiency by activation of the AMPK/PGC-1α axis.
Topics: Aminoimidazole Carboxamide; AMP-Activated Protein Kinases; Animals; Bezafibrate; Cytochrome-c Oxidase Deficiency; Disease Models, Animal; Electron Transport Complex IV; Gene Knock-In Techniques; Hypoglycemic Agents; Hypolipidemic Agents; Membrane Proteins; Mice; Mice, Knockout; Mice, Transgenic; Mitochondrial Proteins; Molecular Chaperones; Muscle, Skeletal; Oxidative Phosphorylation; Peroxisome Proliferator-Activated Receptor Gamma Coactivator 1-alpha; Ribonucleotides; Signal Transduction; Trans-Activators; Transcription Factors | 2011 |
Copper and bezafibrate cooperate to rescue cytochrome c oxidase deficiency in cells of patients with SCO2 mutations.
Topics: Adenosine Triphosphate; Bezafibrate; Carrier Proteins; Cell Line; Cells, Cultured; Copper; Cytochrome-c Oxidase Deficiency; Electron Transport Complex IV; Fibroblasts; HEK293 Cells; HeLa Cells; Humans; Mitochondrial Proteins; Molecular Chaperones; Mutation | 2012 |